Cia peb kawm txog kev kuaj hws kom pom tias koj puas muaj cystic fibrosis.

Koj tus me nyuam puas muaj teeb meem ua pa nyuaj, lossis muaj teeb meem tsis nce phaus? Los yog koj puas pom ib yam dab tsi zoo li hnoos tas li lossis lub suab ua pa nrov hauv siab? Qee zaum, tom qab cov no, tej zaum yuav muaj ib yam kab mob uas peb tsis tau hnov ​​​​​​dua txog, tab sis nws yog ib qho tseem ceeb heev uas yuav tsum paub txog. Qhov ntawd yog qhov peb yuav tham txog hnub no. Qhov no hu ua Cystic Fibrosis , qee zaum luv ua (CF) . Cia peb saib nws yog dab tsi, nws raug kuaj mob li cas, thiab tshwj xeeb tshaj yog qee cov ntsiab lus txog 'Kev Ntsuas Hws' uas ua rau qhov no.

Cystic Fibrosis yog dab tsi tiag?

Hais yooj yim xwb, cystic fibrosis yog ib yam kab mob uas tau txais los ntawm niam txiv . Qhov ntawd yog, nws yog ib yam dab tsi uas tuaj yeem kis tau los ntawm niam txiv mus rau cov menyuam. Qhov tshwm sim hauv qhov no yog tias qee cov kua dej hauv peb lub cev, tshwj xeeb tshaj yog cov hnoos qeev, ua tuab thiab nplaum heev. Xav txog nws, cov hnoos qeev hauv lub ntsws thiab sinuses ntawm tus neeg noj qab haus huv puas tsis nplua zoo li dej? Nws yog qhov uas ua rau peb txoj hlab pa huv thiab tshem tawm cov kab mob.

Tab sis rau cov neeg uas muaj cystic fibrosis, cov hnoos qeev no tuab heev, zoo li kua nplaum. Yog li cov hnoos qeev tuab no tau tso rau hauv cov kabmob tseem ceeb xws li lub ntsws thiab lub txiav , cuam tshuam rau lawv txoj haujlwm ib txwm. Tshwj xeeb tshaj yog thaum cov hnoos qeev tuab no sib sau ua ke hauv lub ntsws, cov hlab pa pib raug thaiv. Tom qab ntawd nws nyuaj heev rau ua pa, thiab kev kis kab mob tuaj yeem tshwm sim ntau zaus. Yog tias lub txiav raug cuam tshuam, teeb meem zom zaub mov thiab kev tsis noj qab haus huv tuaj yeem tshwm sim. Tsis yog qhov no xwb, nws kuj tseem tuaj yeem cuam tshuam rau qhov chaw xws li lub siab, txoj hnyuv, thiab qhov chaw mos.

Kab mob cystic fibrosis yog ib yam kab mob uas mob ntev mus ntev los . Qhov no txhais tau tias nws yuav mob mus ntev thiab tsis kho tau tag nrho. Nws kuj suav tias yog ib yam kab mob uas mob zuj zus tuaj . Qhov no txhais tau tias cov tsos mob yuav maj mam zuj zus tuaj thiab tej zaum yuav muaj teeb meem tshwm sim. Yog vim li ntawd nws thiaj li tseem ceeb heev uas yuav tsum paub txog nws thaum ntxov thiab tswj nws kom zoo.

Cov tsos mob ntawm qhov no rau cov menyuam yaus yog dab tsi?

Yog tias ib tug me nyuam yaus, tshwj xeeb tshaj yog ib tug me nyuam mos, muaj mob cystic fibrosis, lawv yuav muaj ib lossis ntau yam ntawm cov tsos mob no. Tsis yog txhua tus me nyuam yuav muaj tag nrho cov tsos mob no ib zaug, thiab qhov hnyav ntawm cov tsos mob yuav txawv ntawm ib tug me nyuam mus rau ib tug me nyuam. Nws yog ib qho tseem ceeb uas yuav tsum nco ntsoov qhov ntawd.

Nov yog qee yam ntawm cov yam ntxwv no:

• Tsis vam meej: Txawm hais tias tus menyuam mos noj mis zoo thiab noj mov zoo tom qab, nws yuav tsis hnyav dua thiab zoo li hnyav dua piv rau lwm tus menyuam mos uas muaj hnub nyoog zoo sib xws.
• Cov quav xoob los yog roj: Qee zaum koj tus menyuam cov quav yuav xoob heev, dej, los yog roj. Qee zaum cov quav yuav muaj ntxhiab tsw phem.
• Ua pa nyuaj:Ib txwm xav tias ua pa nyuaj, zoo li koj ua tsis taus pa.
• Ua pa nrov tsis tu ncua: Lub suab ua pa nrov tsis tu ncua los ntawm hauv siab. Qhov no kuj tuaj yeem tshwm sim rau cov mob xws li mob hawb pob, tab sis nws yog ib qho tsos mob uas pom ntau dua hauv CF.
• Kab mob ntsws ntau zaus: Piv txwv li, mob ntsws thiab mob ntsws ntsws feem ntau yog ib qho uas muaj ntau. Yog tias koj muaj kab mob ntsws ib lossis ob zaug hauv ib hlis, nws yog ib yam uas yuav tsum txhawj xeeb txog.
• Kab mob ntsws rov tshwm sim dua: Kab mob ntsws ntau zaus nyob rau hauv cov qhov ntswg (sinuses). Tej yam xws li qhov ntswg txhaws thiab ntswg ntws.
• Hnoos tas li, tej zaum yuav muaj cov phlegm: Hnoos tas li uas tsis zoo dua. Tej zaum yuav yog hnoos uas tsim cov hnoos qeev tuab.
• Kev loj hlob qeeb: Tus menyuam qhov siab thiab qhov hnyav zoo li loj hlob qeeb dua li lwm tus menyuam uas muaj hnub nyoog zoo sib xws.
• Qee zaum daim tawv nqaij ntawm tus menyuam saj ntsev: Ib txhia niam txiv kuj qhia tias thaum lawv txhuam lawv tus menyuam daim tawv nqaij hws, nws yuav hnov ​​ntsev.

Yog tias koj xav tias koj tus menyuam me muaj ib lossis ntau yam ntawm cov tsos mob no, qhov zoo tshaj plaws ua yog mus ntsib kws kho mob menyuam yaus kom tau txais lus qhia.

Kev kuaj hws yog dab tsi thiab nws ua dab tsi?

Cov kws kho mob kuaj mob cystic fibrosis los ntawm kev kuaj tus neeg mob kom zoo zoo, mloog lawv cov tsos mob, thiab ua ntau yam kev kuaj mob. Qhov no suav nrog kev kuaj noob caj noob ces - uas yog kev kuaj ntshav uas nrhiav kev hloov pauv hauv cov noob caj noob ces - duab X-ray hauv siab thiab qhov ntswg, thiab kev kuaj kev ua haujlwm ntawm lub ntsws.

Txawm li cas los xij, qhov kev kuaj mob tseem ceeb tshaj plaws thiab paub tseeb tshaj plaws los xyuas kom meej tias koj puas muaj cystic fibrosis lossis tsis yog qhov kev kuaj hws. Qhov no yog ib qho kev kuaj yooj yim heev, tsis mob. Nws ntsuas qhov ntau ntawm chloride hauv koj cov hws. Koj puas paub tias cov ntsev peb noj yog ua los ntawm ob hom tshuaj hu ua chloride thiab sodium. Yog li, qhov ntau ntawm chloride hauv cov hws ntawm cov neeg uas muaj cystic fibrosis yog siab dua li ntawm ib tus neeg ib txwm.

Qhov laj thawj rau qhov no yog vim tias, vim yog qhov tsis zoo ntawm cov noob caj noob ces uas ua rau muaj cystic fibrosis, qhov ua haujlwm ntawm cov protein uas pab chloride txav mus los ntawm peb cov hlwb raug cuam tshuam. Yog li ntawd, chloride tsis tuaj yeem nkag mus lossis tawm hauv cov hlwb kom raug. Qhov no yog thaum chloride sib sau ua ke tsis zoo hauv cov hws. Txawm hais tias nws yuav zoo li yooj yim heev, qhov no yog lub hauv paus tseem ceeb rau kev kuaj mob no.

Feem ntau, cov kws kho mob pom zoo kom ua qhov kev kuaj hws no yog tias ib tug menyuam muaj feem yuav tau txais cystic fibrosis (piv txwv li, yog tias ib tug neeg hauv tsev neeg muaj tus kab mob), lossis yog tias lawv muaj cov tsos mob uas peb tau tham ua ntej. Qee zaum, cov kwv tij neej tsa ntawm tus menyuam kuj raug hais kom ua qhov kev kuaj no. Qhov no yog los saib seb lawv puas tau txais cov noob caj noob ces no thiab seb lawv cov menyuam puas muaj feem yuav tau txais cov noob caj noob ces no yav tom ntej.

Qhov kev kuaj hws no ua li cas? Puas yog ib yam dab tsi uas yuav tsum ntshai?

Qhov kev kuaj hws no ua tau rau txhua tus neeg txhua lub hnub nyoog. Txawm li cas los xij, cov menyuam mos tshiab yuav tsis muaj peev xwm tsim hws txaus rau qhov kev kuaj no hauv ob peb hnub thawj zaug ntawm lawv lub neej. Yog li ntawd, qhov kev kuaj no feem ntau yog ua rau cov menyuam mos hnub nyoog ntawm ob thiab plaub lub lis piam , thaum lawv tuaj yeem tsim hws txaus.

Qhov kev sim no yooj yim heev rau ua, thiab nws tsis mob kiag li. Yog li ntawd, tsis txhob ntshai nws, puas yog? Nov yog qhov tshwm sim:

1. Ua ntej, tus neeg ua haujlwm kho mob, txawm yog tus kws saib mob lossis tus kws kho mob, yuav muab ib daim gel lossis kua uas muaj cov tshuaj hu ua pilocarpine pleev rau ntawm daim tawv nqaij ntawm tus menyuam txhais tes (feem ntau yog sab caj npab) lossis ceg. Pilocarpine yog ib yam tshuaj uas ua rau cov qog hws ua haujlwm.

2. Tom qab ntawd, ob lub electrodes raug muab tso rau ntawm thaj chaw thiab muab ib qho me me, tsis muaj teeb meem hluav taws xob los txhawb cov qog hws thiab tsim cov hws. Qhov no ua li ntawm 5 feeb. Tsis muaj qhov khaus lossis mob hlo li. Tus me nyuam yuav hnov ​​​​​​me ntsis tingling lossis sov so hauv lawv txhais tes lossis ko taw, tab sis tsuas yog qhov ntawd xwb. Feem ntau cov menyuam mos tsis hnov ​​​​​​qhov no.

3. Tom qab ntawd, cov electrodes raug tshem tawm, thaj chaw ntawm daim tawv nqaij raug ntxuav, thiab muab ib lub cuab yeej tshwj xeeb los sau cov hws (xws li ib lub kauj yas, ib daim ntawv lim dej, lossis ib daim ntaub gauze) tso rau ntawm thaj chaw ntawd. Qhov no raug tso rau hauv qhov chaw li 30 feeb kom sau cov hws.

4. Thaum kawg, cov qauv hws uas tau sau los no raug xa mus rau chav kuaj mob kom ntsuas qhov ntau ntawm cov chloride uas muaj nyob.

Tag nrho qhov kev xeem yuav siv sijhawm li ib teev. Nws yuav yooj yim dua los ua kom koj tus menyuam nyob twj ywm yog tias koj muaj ib qho khoom ua si lossis ib lub raj mis mis nyob ze.

Cov txiaj ntsig ntawm qhov kev xeem no hais li cas?

Zoo, tam sim no cia peb saib seb cov txiaj ntsig ntawm qhov kev kuaj hws no hais li cas. Yog tias tus menyuam muaj cystic fibrosis, qhov kev kuaj hws yuav qhia tias muaj ntau dua li qub ntawm chloride hauv lawv cov hws.

Hais txog cov nqi ntsuas, cov no yog raws li nram no (cov nqi no yuav txawv me ntsis ntawm chav kuaj mus rau chav kuaj, tab sis feem ntau zoo li no):

• Yog tias koj tus menyuam cov tshuaj chloride siab dua 60 mmol/L (millimol/liter) : Nws muaj feem ntau tias lawv muaj cystic fibrosis.Feem ntau, yog tias muaj qhov tshwm sim zoo li no tshwm sim, qhov kev kuaj ntawd yuav ua dua los xyuas kom meej.
• Tus menyuam cov tshuaj chloride tsawg dua 30 mmol/L (millimol/liter) (qee cov lus qhia hais tias tsawg dua 40 mmol/L): Nws hais tau tias nws tsis muaj mob cystic fibrosis.
• Yog tias koj tus menyuam cov chloride theem nyob nruab nrab ntawm 30 thiab 59 mmol/L ( qee qhov chaw 40-59 mmol/L): Qhov no suav hais tias yog qhov tshwm sim nruab nrab lossis ciam teb . Hauv qhov no, qhov kev kuaj mob yuav tsum tau rov ua dua . Cov kev kuaj ntxiv, xws li kev kuaj noob caj noob ces, kuj tseem yuav tsum tau ua kom tshem tawm qee hom CF tsis zoo.

Qhov tseem ceeb tshaj plaws yog tias cov txiaj ntsig no yuav tsum tau txhais los ntawm tus kws kho mob. Yog li, thaum cov txiaj ntsig los txog, qhov zoo tshaj plaws ua yog tham nrog tus kws kho mob txog nws thiab ua raws li nws cov lus qhia. Tsis txhob ntshai.

Koj yuav npaj koj tus menyuam li cas rau kev kuaj hws? Koj puas xav tau ua dab tsi tseem ceeb?

Qhov no yooj yim heev rau niam thiab txiv. Koj tsis tas yuav ua dab tsi tshwj xeeb los npaj koj tus menyuam rau kev kuaj hws.

• Tsis tas yuav hloov lossis tsum tsis txhob noj zaub mov ntawm tus menyuam (piv txwv li noj zaub mov, khoom noj khov yog tias muab), tej yam ua si, lossis tshuaj uas tus menyuam noj ua ntej qhov kev kuaj no. Ua kom nws zoo li qub.
• Tsuas yog ib qho xwb, tsis txhob siv tshuaj pleev lossis tshuaj pleev rau ntawm koj tus menyuam daim tawv nqaij li 24 teev ua ntej qhov kev kuaj mob. Tshwj xeeb tshaj yog tsis txhob siv dab tsi rau ntawm caj npab lossis ceg uas tab tom kuaj mob. Qhov no tuaj yeem cuam tshuam rau cov txiaj ntsig ntawm kev kuaj mob.

Saib seb, nws yooj yim heev. Hnav khaub ncaws sib dua thiab xis rau koj tus menyuam hnub uas yuav xeem.

Cov yam tseem ceeb tshaj plaws uas peb yuav tsum nco ntsoov los ntawm zaj dab neeg no (Cov Lus Qhia Coj Mus Tsev)

Zoo, yog li kuv vam tias koj tam sim no nkag siab zoo txog yam peb tau tham txog hnub no, Cystic Fibrosis thiab Sweat Test. Txawm hais tias qhov no yuav zoo li yog ib qho nyuaj, nws tsis nyuaj thaum koj nkag siab txog cov hauv paus. Los ntawm yam peb tau tham, ntawm no yog qee yam uas yuav tsum nco ntsoov:

• Cystic fibrosis (CF) yog ib yam kab mob caj ces uas ua rau lub cev cov hnoos qeev tuab, tshwj xeeb tshaj yog cuam tshuam rau lub ntsws thiab lub plab zom mov.
• Paub txog cov tsos mob: Yog tias koj muaj ib lossis ntau yam ntawm cov tsos mob no, xws li poob phaus, ua pa luv luv tas li, hnoos tsis tu ncua, lossis quav roj, mus ntsib kws kho mob thiab tham txog lawv.
• Kev kuaj hws yog qhov kev kuaj tseem ceeb tshaj plaws thiab txhim khu kev qha rau kev lees paub cystic fibrosis: nws ntsuas cov chloride hauv hws.
• Qhov kev kuaj no tsis mob thiab muaj kev nyab xeeb: yog li ntawd tsis txhob ntshai coj koj tus menyuam mus rau qhov no.
• Nws yog ib qho tseem ceeb heev uas yuav tsum paub txog tus kab mob thaum ntxov:Vim tias yog li ntawd, cov kev kho mob thiab kev tswj hwm tsim nyog tuaj yeem pib sai, txo cov teeb meem uas tus menyuam yuav ntsib thiab pab lawv ua neej zoo dua thiab noj qab haus huv dua.

Yog koj lossis ib tug neeg koj paub muaj teeb meem no, qhov zoo tshaj plaws uas yuav tsum ua yog tsis txhob ntshai lossis ntseeg txhua yam koj pom hauv internet, tab sis nrog ib tus kws kho mob uas tsim nyog tham. Lawv yuav coj koj kom zoo thiab muab kev txhawb nqa uas koj xav tau.

` Cystic Fibrosis, kev kuaj hws, chloride, kev kho mob menyuam yaus, cov kab mob caj ces, cov kab mob ntsws