Koj puas tau xav tias koj pom tej yam me me dub ntab rau ntawm koj ob lub qhov muag? Los yog tej zaum koj qhov muag tsis pom kev zoo me ntsis? Tej zaum qhov no yog ib qho zoo li qub, tab sis qee zaum lawv yog ib qho cim qhia tias muaj teeb meem hauv koj lub qhov muag. Hnub no peb yuav tham txog ib qho mob qhov muag uas tsis tshua muaj uas tuaj yeem tswj tau yog tias kho kom zoo.
Qhov no yog dab tsi (Birdshot Chorioretinopathy)?
Hais yooj yim xwb, Birdshot Chorioretinopathy, lossis luv luv BSCR, yog ib yam kab mob o uas tshwm sim hauv lub qhov muag. Nws tsis yog ib yam mob ntev , txhais tau tias nws tsis zoo dua hauv lub sijhawm luv luv, tab sis yog ib yam mob uas kav ntev. Yog tias tsis kho kom zoo, nws tuaj yeem ua rau pom kev hloov pauv mus tas li lossis txawm tias poob qhov muag tag nrho.
(BSCR) yog ib qho mob hnyav uas yog ib pawg kab mob hu ua "Uveitis", uas ua rau cov nqaij hauv lub qhov muag puas tsuaj. Nws feem ntau yog o ntawm:
- Retina : Qhov no yog daim nyias nyias uas rhiab lub teeb nyob tom qab peb lub qhov muag. Nws zoo li daim zaj duab xis hauv lub koob yees duab. Cov duab peb pom raug kaw cia ntawm no.
- Choroid : Qhov no nyob hauv qab lub retina. Qhov no yog daim nyias nyias uas txuas lub retina mus rau qhov dawb ntawm lub qhov muag, thiab muab cov ntshav rau lub retina, uas yog, pub nws noj.
Qhov tshwj xeeb tshaj plaws ntawm tus kab mob no yog cov pob me me, oval, xim dawb tshwm sim hauv qhov tob ntawm lub retina thiab txheej sab saud ntawm choroid. Cov tsos mob thaum ntxov feem ntau suav nrog cov khoom dub ntab rau ntawm lub qhov muag (floaters) , pom kev tsis meej , lossis ob qho tib si. Tus mob no feem ntau cuam tshuam rau ob lub qhov muag .
Raws li lub sijhawm dhau mus, qhov kev puas tsuaj no tuaj yeem ua rau muaj cov mob xws li cystoid macular edema lossis glaucoma . Txawm hais tias tsis muaj kev kho mob, Birdshot Chorioretinopathy yog ib qho kab mob uas kho tau . Kev kuaj pom thaum ntxov yog qhov tseem ceeb rau kev kho mob kom zoo.
Leej twg thiaj tau txais Birdshot Chorioretinopathy?
Tseeb tiag, tus kab mob no tuaj yeem tshwm sim rau txhua tus neeg. Tab sis nws feem ntau tshwm sim rau cov neeg laus hnub nyoog nruab nrab, cov neeg dawb hnub nyoog ntawm 40 thiab 60 xyoo. Nws tsis tshua muaj menyuam yaus uas muaj tus kab mob no.
Puas muaj lwm yam kab mob zoo li no (Birdshot Chorioretinopathy)?
Yog lawm, ntau lwm yam kab mob, suav nrog lwm yam kab mob hauv pawg Uveitis, tuaj yeem muaj cov tsos mob zoo ib yam li Birdshot Chorioretinopathy. Yog li ntawd, nws yog ib qho tseem ceeb heev kom tau txais kev kuaj mob kom raug kom koj thiaj li tau txais kev kho mob kom raug. Qee cov kab mob uas zoo ib yam li BSCR yog:
- Lymphoma (ib hom mob qog noj ntshav)
- Sarcoidosis (ib yam kab mob uas ua rau me me o ntawm ntau qhov ntawm lub cev)
- `(Sympathetic ophthalmia)` (Ib hom mob uveitis uas tsis tshua muaj tshwm sim los ntawm kev raug mob ntawm lub qhov muag)
- Syphilis (kab mob sib kis los ntawm kev sib deev)
- `(Puas yog mob qhov muag histoplasmosis syndrome (POHS))` (Ib yam mob uas cuam tshuam rau lub qhov muag los ntawm kev kis kab mob fungal)
- `(Tub Kab Mob Ntsws)` (Tub Kab Mob Ntsws)
- `(Vogt-Koyanagi-Harada syndrome)` (ib yam kab mob uas cuam tshuam rau lub paj hlwb, cuam tshuam rau qhov muag thiab pob ntseg)
Kuj tseem muaj ib pawg kab mob o uas hu ua "White dot syndromes", uas kuj tuaj yeem qhia cov tsos mob ntawm BSCR. Cov no ua rau "mob" rau lub retina thiab choroid. Qee qhov piv txwv yog:
- `(Acute posterior multifocal placoid pigment epitheliopathy (APMPPE))`
- `(Multifocal choroiditis thiab panuveitis (MCP))`
- `(Multiple evanescent white dot syndrome (MEWDS))`
- `(Kev kho mob choroidopathy sab hauv (PIC))`
Vim li cas qhov no thiaj hu ua (Birdshot Chorioretinopathy)?
Qhov no yog ib yam kab mob tshiab, thawj zaug tau piav qhia hauv xyoo 1949. Txog rau xyoo 1980 ob tug kws kho qhov muag thiaj li muab lub npe no rau "(Birdshot Chorioretinopathy)". Qhov laj thawj yog vim muaj cov xim dawb thiab txiv kab ntxwv oval tawg thoob plaws hauv retina. Lub npe no los ntawm qhov tseeb tias cov qauv ntawm cov chaw no zoo li cov qauv ntawm cov mos txwv me me (birdshot) siv los tua noog. Xav txog, muaj cov chaw hauv lub qhov muag, zoo li cov mos txwv uas tawg thaum rab phom raug tua.
Puas muaj lwm lub npe rau qhov no?
Yog, muaj ntau lub npe siv rau tus kab mob (Birdshot Chorioretinopathy):
- `(Kab mob ntsws Birdshot chorioretinitis)`
- '(Birdshot retinochoroiditis)'
- '(Birdshot retinochoroidopathy)'
- `(Kab mob ntsws Birdshot)`
- `(BSCR)` (lub npe luv)
- `(Posterior uveitis)` (uveitis uas tshwm sim tom qab lub qhov muag)
- `(Kab mob choroiditis)`
Birdshot Chorioretinopathy muaj ntau npaum li cas?
Qhov no yog ib yam kab mob tsis tshua muaj . Cov kws tshawb fawb ntseeg tias nws cuam tshuam tsawg dua ib tus neeg hauv ib puas txhiab tus neeg. Qhov no txhais tau tias txawm tias nyob hauv Sri Lanka, tej zaum yuav muaj cov neeg uas muaj tus kab mob no, tab sis tus lej tsawg heev.
Dab tsi ua rau muaj Birdshot Chorioretinopathy?
Cov kws tshawb nrhiav tseem tsis tau paub meej tias yog vim li cas tus kab mob no thiaj li tshwm sim , tab sis lawv xav tias nws yog ib yam kab mob autoimmune . Hais yooj yim xwb, peb lub cev tiv thaiv kab mob, lub cev tiv thaiv kab mob, ua yuam kev tawm tsam peb cov nqaij noj qab haus huv.
Ntau tshaj 90% ntawm cov neeg uas kuaj pom tias muaj tus kab mob (BSCR) muaj ib hom noob tiv thaiv kab mob (ib hom molecule uas ua rau lub cev tiv thaiv kab mob) hu ua '(HLA-A29)' hauv lawv lub cev. Qhov no yog ib yam dab tsi uas tau txais los ntawm niam txiv. Txawm li cas los xij, '(HLA-A29)' tsis tsim nyog los tsim (Birdshot Chorioretinopathy). Tsis tas li ntawd, nws muaj peev xwm muaj cov noob tiv thaiv kab mob no tab sis tsis tsim tus kab mob.
Cov tsos mob ntawm Birdshot Chorioretinopathy yog dab tsi?
Cov tsos mob ntawm tus kab mob no yuav txawv ntawm ib tus neeg mus rau ib tus neeg. Qhov noIb yam kab mob uas zuj zus tuaj yog ib yam kab mob uas maj mam zuj zus tuaj rau lub sijhawm ntawm ntau lub hlis mus rau ntau xyoo.
Cov tsos mob thawj zaug ntawm Birdshot Chorioretinopathy feem ntau yog:
- Pom cov khoom dub ntab ua ntej lub qhov muag (floaters)
- Pom kev tsis meej
Feem ntau qhov mob no tsis ua rau mob qhov muag lossis liab . Txawm li cas los xij, koj yuav muaj cov hauv qab no:
- Kev pom kev hloov pauv lossis kev pom kev txo qis.
- Kev pom kev tsis meej lossis nyuaj rau txiav txim siab qhov deb.
- Ntshav siab hauv qhov muag (ntshav siab hauv qhov muag).
- Kev dig muag hmo ntuj (nyctalopia) (pom tsis zoo thaum hmo ntuj).
- Teeb meem pom xim (`(kev dig muag xim)`), nyuaj rau paub qhov txawv ntawm qee yam xim (`(dyschromatopsia)`.
- Kev rhiab heev rau lub teeb ci lossis lub teeb ci ntsa iab (photophobia).
Tej zaum ib txhia neeg yuav muaj kev hloov pauv ntawm qhov muag pom kev lossis teeb meem kev xav. Piv txwv li:
- Cov nyhuv ntawm lub kiv cua qab nthab : Thaum koj kaw koj ob lub qhov muag, nws zoo li lub kiv cua qab nthab lossis lub tshuab cua ntsawj tab tom tig.
- Pom kev ci ntsa iab lossis lub teeb ci ntsa iab (photopsia) lossis pom cov duab tsis zoo (metamorphopsia) .
- Pom kev tsis meej, ci ntsa iab, zoo li saib los ntawm dej lossis iav qias neeg .
Hauv cov mob hnyav, tej yam mob xws li cataracts lossis glaucoma tuaj yeem tshwm sim. Cov no tuaj yeem ua rau pom kev tsis meej txawm tias tom qab kho qhov o. Birdshot Chorioretinopathy kuj tseem tuaj yeem ua rau muaj teeb meem hauv nruab nrab ntawm lub retina, xws li cystoid macular edema thiab epiretinal membranes.
Yuav kuaj mob Birdshot Chorioretinopathy li cas?
Kab mob no qee zaum nyuaj me ntsis rau kev kuaj mob vim tias nws yog ib yam kab mob tsis tshua muaj thiab tej zaum yuav tsis pom cov pob tshwj xeeb thaum pib mob.
Cov kws kho qhov muag feem ntau kuaj mob BSCR los ntawm kev kuaj qhov muag. Lawv kuj ua qhov kev kuaj ntshav los xyuas seb koj puas muaj HLA-A29 antibody.
Cov kws kho mob yuav siv ntau yam kev kuaj mob los saib xyuas koj lub cev dhau sijhawm. Nws yog ib qho tseem ceeb uas yuav tsum sib txuas lus nrog koj tus kws kho mob kom tau txais kev kho mob uas koj xav tau.
Puas muaj kev kho mob tag nrho rau Birdshot Chorioretinopathy?
Tu siab kawg li, tsis muaj ib txoj kev kho tau tag nrho rau tus kab mob no. Txawm li cas los xij, yog tias tus kab mob raug kuaj pom thiab kho thaum ntxov , cov tsos mob yuav raug txo kom tsawg thiab tus kab mob yuav raug tiv thaiv kom tsis txhob loj zuj zus.
Nco ntsoov: qhov tseem ceeb tshaj plaws yog kuaj mob thaum ntxov thiab pib kho!
Leej twg thiaj li koom tau nrog kuv pab neeg kho mob?
Koj pab neeg saib xyuas yuav pom zoo rau kev kho mob, saib xyuas koj, thiab kho koj cov tshuaj raws li koj tus mob thiab cov kev mob tshwm sim. Koj pab neeg yuav suav nrog:
- Kws Kho Qhov Muag : Tus kws kho mob tseem ceeb uas kho qhov muag.
- Kws Kho Mob Ntsws : Vim tias qee yam kev kho mob cuam tshuam rau lub raum.
- Kws kho mob tiv thaiv kab mob ntawm qhov muag: Ib tug kws kho mob uas muaj kev cob qhia tshwj xeeb hauv cov teeb meem ntawm lub cev tiv thaiv kab mob ntawm lub qhov muag.
- Kws Kho Mob Pob Txha: Ib tug kws kho mob uas tshwj xeeb hauv cov kab mob ntsig txog kev o ntawm lub cev, vim qhov no kuj yog ib qho kab mob ntawm kev o.
- Kws Kho Mob Pob Txha : Vim tias qee qhov kev kho mob cuam tshuam rau cov pob txha.
Yuav kho tus mob Birdshot Chorioretinopathy li cas?
Kev kho mob rau tus kab mob no nyob ntawm seb koj tus mob hnyav npaum li cas thiab nws hloov pauv li cas raws sijhawm. Lub hom phiaj tseem ceeb ntawm kev kho mob yog kom txo qhov o ntawm koj lub qhov muag thiab tiv thaiv lossis rov qab kho qee qhov kev pom kev uas tau ploj mus .
Feem ntau cov kws kho mob yuav xub muab tshuaj corticosteroids (ib hom tshuaj steroid) ntau ntau rau lawv kom tswj tau qhov muag o. Tom qab ntawd, maj mam txo cov tshuaj kom txo tau qhov kev pheej hmoo ntawm cov kev mob tshwm sim. Koj tuaj yeem tau txais tshuaj steroids hauv cov hauv qab no:
- Cov tshuaj qhov muag
- Cov tshuaj noj
- Ib lub cuab yeej me me uas raug phais cog rau hauv lub qhov muag (intravitreal implant)
- Kev txhaj tshuaj
- Muab rau hauv cov leeg ntshav (IV - intravenously)
Muaj coob tus neeg kuj yuav tsum tau noj cov tshuaj uas tiv thaiv kab mob mus sij hawm ntev . Cov tshuaj no tiv thaiv koj lub cev tiv thaiv kab mob kom tsis txhob tawm tsam koj ob lub qhov muag. Ib lossis ntau yam hauv qab no siv tau:
- `(Cov neeg ua haujlwm alkylating)`
- `(Cov tshuaj tiv thaiv kev zom zaub mov)`
- `(Cov tshuaj lom neeg)` (tshuaj lom neeg)
- `(T-cell transduction/calcineurin inhibitors)`
Kev kho mob Birdshot Chorioretinopathy (Birdshot Chorioretinopathy) puas tuaj yeem ua rau muaj kev phiv?
Yog, kev siv cov tshuaj steroids thiab cov tshuaj tiv thaiv kab mob mus sij hawm ntev tuaj yeem ua rau muaj kev phiv loj heev . Piv txwv li, teeb meem plab hnyuv (mob qog, mob qog) lossis teeb meem pob txha (osteoporosis) tuaj yeem tshwm sim. Cov tshuaj no kuj tseem tuaj yeem ua rau muaj kev pheej hmoo ntawm kev mob cataracts lossis glaucoma.
Koj tus kws kho mob yuav saib xyuas koj seb puas muaj tej yam tshwm sim tsis zoo thiab yuav muab lwm yam tshuaj rau koj yog tias tsim nyog. Yog tias koj noj tshuaj steroids, koj tus kws kho mob yuav xyuas koj seb koj puas muaj pob txha poob (osteoporosis) thiab koj puas muaj feem yuav pob txha tawg.
Koj tus kws kho mobKuj tseem yuav pom zoo kom kuaj xyuas qhov ntom ntawm pob txha. Cov tshuaj (bisphosphonates) kuj tseem yuav raug sau tseg kom tiv thaiv kev poob pob txha.
Kuv xav tau hom kev saib xyuas mus sij hawm ntev li cas (BSCR)?
Yuav tsum paub txog tej kev hloov pauv lossis tej teeb meem hauv koj tus mob. Koj tus kws kho mob yuav kuaj ntshav thiab zis kom paub seb koj lub raum, siab, thiab pob txha ua haujlwm zoo npaum li cas. Tej zaum koj yuav tsum tau kuaj qhov muag tas li, kuaj qhov muag pom kev, thiab kuaj qhov muag sib xws (OCT).
Kuv puas txo tau kuv txoj kev pheej hmoo ntawm kev mob Birdshot Chorioretinopathy?
Tam sim no tseem tsis tau muaj ib txoj kev los tiv thaiv tus kab mob no. Feem ntau, cov neeg ntseeg tias nws yog los ntawm ib hom noob tiv thaiv kab mob (antigen) uas tau txais los ntawm cov tswv cuab hauv tsev neeg.
Kev kuaj qhov muag tsis tu ncua tuaj yeem pab nrhiav tau cov cim qhia ntxov ntawm tus kab mob, yog li koj tuaj yeem tau txais kev kho mob raws sijhawm yog tias xav tau. Qhia rau koj tus kws kho mob yog tias muaj leej twg hauv koj tsev neeg muaj teeb meem qhov muag.
Yuav ua li cas thiaj paub tias muaj tus kab mob Birdshot Chorioretinopathy?
Qhov kev xav txog tus kab mob no txawv ntawm ib tus neeg mus rau ib tus neeg . Nws nyob ntawm seb tus mob hnyav npaum li cas thiab kev kho mob zoo li cas. Hauv cov mob me me, kev kho mob tuaj yeem pab tswj lossis txhim kho qhov muag pom kev.
Thaum twg kuv yuav tsum nrhiav kev pab kho mob rau (Birdshot Chorioretinopathy)?
Nws yog ib qho tseem ceeb uas yuav tsum nrhiav kev kuaj mob thiab kho mob sai sai los ntawm kws kho qhov muag rau Birdshot Chorioretinopathy. Txawm tias koj qhov muag pom kev zoo los xij, kev kuaj qhov muag tuaj yeem pom qhov o me me.
Qhia rau koj tus kws kho mob txog tej yam kev mob tshwm sim, kev hloov pauv ntawm cov tsos mob, lossis kev pom kev los ntawm koj cov tshuaj. Koj yuav tau txais lwm yam tshuaj yog tias xav tau. Koj tus kws kho mob yuav nrog koj tham txog cov kev xaiv uas zoo tshaj plaws rau koj.
Cov Lus Xaus Kawg coj mus tsev
(Birdshot Chorioretinopathy) yog ib yam kab mob uas tsis tshua muaj tab sis kho tau . Yog li ntawd, tsis txhob ntshai. Qhov tseem ceeb tshaj plaws yog mus kuaj koj ob lub qhov muag tsis tu ncua thiab ua raws li koj tus kws kho mob cov lus qhia . Raws li lub sijhawm dhau mus, koj tus kws kho mob yuav qhia koj yuav ua li cas tiv thaiv koj lub zeem muag thiab tiv thaiv cov teeb meem. Ces koj yuav pom lub ntiaj teb kom meej meej ntev dua. Saib xyuas koj ob lub qhov muag, vim lawv muaj nqis heev!
Birdshot Chorioretinopathy, Cov Kab Mob Qhov Muag, Kev Pom Kev Tsis Zoo, Uveitis, Retina, Cov Kab Mob Autoimmune, Kev Kho Mob Qhov Muag











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Tsis muaj lus teb tau muab tso tawm. Ntxiv koj cov lus tawm ntawm no thawj zaug.
Ntxiv koj cov lus