Puas yog koj tus menyuam cia li tsis hais lus lawm? Puas yog nws yog Landau-Kleffner Syndrome?

Koj tus menyuam ib txwm khiav ncig thiab ua si thiab tham lus zoo nkauj heev. Tab sis nws puas hais lus tsis tau zoo tam sim ntawd? Los yog koj puas tau pom tias nws nyuaj rau nkag siab koj hais dab tsi? Nws puas qee zaum qaug dab peg? Yog tias koj tus menyuam muaj ib lossis ntau yam ntawm cov no, koj yuav tsum tshawb nrhiav. Vim tias qhov no yuav yog vim muaj ib qho mob tsis tshua muaj hu ua Landau-Kleffner Syndrome (LKS) . Tsis txhob txhawj, cia peb tham txog qhov no kom meej.

Kab mob Landau-Kleffner yog dab tsi?

Hais yooj yim xwb, Landau-Kleffner Syndrome (LKS) yog ib yam mob uas cuam tshuam rau peb cov menyuam lub hlwb. Qhov tseem ceeb hauv qhov no yog tias tus menyuam lub peev xwm hais lus thiab nkag siab lus (uas peb hu ua Aphasia hauv kev kho mob) maj mam lossis tam sim ntawd txo qis. Tsis tas li ntawd, feem ntau ntawm cov menyuam uas muaj tus mob no tuaj yeem raug kev txom nyem los ntawm kev qaug dab peg, uas tshwm sim thaum pw tsaug zog.

Xav txog nws, muaj ntau cov lus me me hluav taws xob mus thiab los hauv peb lub hlwb. Cov teeb liab hluav taws xob no yog cov uas pab peb ua haujlwm kom zoo thaum peb hais lus, hnov, xav, thiab ua txhua yam. Cov menyuam yaus uas muaj LKS muaj qee qhov tsis zoo hauv lub teeb liab hluav taws xob no hauv lawv lub hlwb. Qhov no yog vim li cas lawv thiaj muaj teeb meem nkag siab lus thiab hais lus.

Leej twg raug kev cuam tshuam ntau tshaj plaws los ntawm qhov teeb meem LKS no?

Tus mob no, hu ua LKS, feem ntau pom muaj rau cov menyuam yaus hnub nyoog ntawm 3 thiab 8 xyoo. Txawm li cas los xij, qee zaum nws tuaj yeem cuam tshuam rau cov menyuam yaus hnub nyoog li 2 xyoos, nrog rau cov menyuam loj dua, xws li cov hluas. Kuj tseem hais tias cov tub hluas muaj feem yuav mob no ntau dua li cov ntxhais.

LKS cuam tshuam li cas rau kuv tus menyuam?

Yog koj tus menyuam muaj tus kab mob LKS, lawv yuav maj mam poob lawv lub peev xwm hais lus. Lawv kuj tseem yuav muaj teeb meem nkag siab txog yam koj hais thiab lwm tus hais. Qhov no yog yam peb hu ua (aphasia) .

Xav txog seb, koj tus menyuam yav tas los nws hais paj huam, hu nkauj, thiab nrog koj tham tas li. Tiamsis tam sim no nws tsis hais ib lo lus li, lossis nws tsuas ntsia koj thaum koj hais lus, zoo li nws tsis nkag siab dab tsi, nws nyuaj npaum li cas los ua siab ncaj?

Kwv yees li ntawm 70% ntawm cov menyuam yaus uas muaj tus kab mob LKS yuav muaj mob qaug dab peg, lossis mob qaug dab peg, thaum pw tsaug zog. Ib txhia menyuam yaus kuj tseem yuav muaj cov mob qaug dab peg no thaum nruab hnub.

Puas yog Landau-Kleffner syndrome zoo ib yam li autism?

Tsis yog, qhov no yog kev nkag siab yuam kev uas feem ntau pom. Landau-Kleffner Syndrome tsis yog autism. Txawm li cas los xij, cov tsos mob ntawm ob qho tib si qee zaum yuav zoo sib xws, yog li nws tuaj yeem nyuaj rau qhia qhov txawv. Cov kws kho mob feem ntau kuaj mob ob yam mob los ntawm kev ua cov kev kuaj EEG (electroencephalograms) thaum tus menyuam tseem sawv thiab pw tsaug zog.

Puas muaj lwm lub npe rau LKS?

Yog lawm, qee zaum cov kws kho mob kuj hu qhov mob no ua "Acquired Aphasia with Epilepsy." Uas yog, nws txhais tau tias ib yam dab tsi zoo li "kev hais lus tsis meej uas tshwm sim nrog qaug dab peg thiab tau txais tom qab."

Tus mob LKS no feem ntau tshwm sim li cas?

Kab mob Landau-Kleffner yog ib yam mob uas tsis tshua muaj. Cov kws tshawb fawb nyuaj rau hais tias muaj pes tsawg tus neeg muaj tus kab mob no. Nws tsis tshua muaj li ntawd.

Dab tsi ua rau muaj tus mob Landau-Kleffner syndrome?

Feem ntau, feem ntau ntawm cov menyuam yaus uas muaj LKS tsis tuaj yeem nrhiav tau qhov ua rau lawv tus mob. Qhov no yog qhov tseeb. Yog li ntawd, tsis txhob xav ntau dhau lossis liam koj tus kheej.

Txawm li cas los xij, kwv yees li 20% ntawm cov menyuam yaus uas muaj LKS muaj qee qhov kev hloov pauv (kev hloov pauv) hauv lawv cov noob caj noob ces. Tshwj xeeb, kev hloov pauv hauv ib qho noob caj noob ces hu ua (GRIN2A) tau pom tias muaj feem cuam tshuam rau qhov no. Cov kev hloov pauv caj noob ces no tuaj yeem tau txais los ntawm ib tug ntawm cov niam txiv. Txawm li cas los xij, tsis yog txhua tus neeg uas muaj kev hloov pauv caj noob ces no yuav muaj LKS. Qee tus menyuam kuj tseem yuav muaj kev hloov pauv hauv lwm cov noob caj noob ces. Qee zaum, tus menyuam yuav muaj qhov kev hloov pauv caj noob ces no thawj zaug (qhov no hu ua kev hloov pauv de novo ) yam tsis muaj leej twg hauv tsev neeg.

Cov kws tshawb fawb ntseeg tias cov kev hloov pauv caj ces no ua rau lub hlwb lub cev hluav taws xob tsis ua haujlwm zoo, ua rau cov teeb liab ntawd ua haujlwm tsis raug. Cov teeb liab tsis zoo no yog cov ua rau muaj cov tsos mob ntawm LKS.

Tseem tab tom tshawb nrhiav seb puas muaj kev sib txuas ntawm LKS thiab peb lub cev tiv thaiv kab mob . Nws ntseeg tau tias qhov mob no yuav tshwm sim los ntawm kev teb tsis muaj zog uas lub cev tiv thaiv kab mob cov hlwb tawm tsam lub cev cov hlwb.

Cov tsos mob ntawm Landau-Kleffner syndrome yog dab tsi?

Tsis yog txhua tus menyuam uas muaj tus kab mob LKS muaj cov tsos mob zoo ib yam. Nws yuav txawv ntawm ib tus menyuam mus rau ib tus menyuam.

Yog koj tus menyuam muaj LKS, koj yuav pom tej yam zoo li no:

• Xav tias nws tsis hnov ​​koj thaum koj tham: Tej zaum nws yuav tsis teb thaum koj nrog nws tham. Zoo li nws tsis hnov ​​koj.
• Nyuaj nkag siab txog yam koj thiab lwm tus hais: Tej zaum koj yuav tsis nkag siab txawm tias yog cov lus qhia yooj yim los xij.
• Kev hais lus tsis zoo lossis tsis muaj zog hais lus tag nrho: Ib tug menyuam uas yav dhau los hais lus zoo yuav tsis hais lus li lawm, lossis tsuas yog hais tau ob peb lo lus xwb uas nyuaj heev.
• Kev qeeb ntawm kev loj hlob tshiab: Tsis muaj peev xwm ua tej yam raws li lub hnub nyoog.
• Kev hloov pauv ntawm lub hlwb lossis kev kawm nyuaj: Koj yuav tsis muaj kev txaus siab rau kev ua haujlwm hauv tsev kawm ntawv thiab muaj teeb meem nco qab tej yam.
• Kev hloov pauv tus cwj pwm: Tus me nyuam chim siab rau cov teeb meem lus no, uas tuaj yeem ua rauTej teeb meem kev coj cwj pwm xws li tsis nyob twj ywm, tsis muaj peev xwm tsom ntsoov (qhov no yuav zoo ib yam li cov tsos mob ntawm Attention-Deficit Hyperactivity Disorder - ADHD), npau taws, thiab nyob tsis tswm yuav tshwm sim.

Xav txog seb ib tug me nyuam yaus yuav xav li cas thaum nws tsis muaj peev xwm qhia nws niam nws txiv txog yam nws xav hais, thaum nws tsis nkag siab lawv hais li cas? Qhov kev tsis muaj peev xwm thiab kev chim siab ntawd qee zaum yog qhov uas tshwm sim los ntawm hom kev coj cwj pwm no.

Cov menyuam yaus uas muaj LKS feem ntau yog:

• Tej zaum koj yuav tsis muaj peev xwm hais lus.
• Muaj feem ntau dua ntawm kev qaug dab peg.
• Kuj tseem muaj feem ntau dua uas yuav muaj teeb meem kev coj cwj pwm (xws li Attention-Deficit Hyperactivity Disorder - ADHD) .

Cov kws kho mob kuaj mob Landau-Kleffner syndrome li cas?

Feem ntau, ua ntej tus menyuam pib mob LKS, kev loj hlob ntawm tus menyuam, xws li kev hais lus thiab kev taug kev, yog qhov ib txwm muaj rau lawv lub hnub nyoog. Tej zaum koj yuav pom tias lawv hais lus tau hloov pauv tam sim ntawd. Los yog, koj tus kws kho mob yuav pom cov tsos mob no thaum koj coj koj tus menyuam mus ntsib kws kho mob.

LKS yuav nyuaj me ntsis rau kev kuaj mob, yog li nws yog ib qho tseem ceeb uas yuav tsum qhia rau koj tus kws kho mob txog txhua qhov kev hloov pauv uas koj pom hauv koj tus menyuam tus cwj pwm, txawm tias yog qhov me tshaj plaws los xij.

Cov kws kho mob siv cov kev kuaj twg los kuaj mob LKS?

Koj tus menyuam tus kws kho mob yuav pom zoo kom ua cov kev kuaj no:

• Kev kuaj hluav taws xob ntawm lub hlwb (EEG): Qhov no ntsuas qhov ua haujlwm hluav taws xob ntawm koj tus menyuam lub hlwb. Qhov no yog kev kuaj mob uas tsis mob. Nws tso cai rau tus kws kho mob pom tias koj tus menyuam lub hlwb ua haujlwm li cas.
• Qhov kev kuaj (EEG) no feem ntau ua ob zaug, ib zaug thaum tus menyuam pw tsaug zog thiab ib zaug thaum lawv tsim . Thaum peb mus pw tsaug zog, peb lub hlwb nthwv dej maj mam qeeb. Txawm li cas los xij, thaum peb nkag mus rau hauv kev pw tsaug zog tob (REM pw tsaug zog theem), lub hlwb nthwv dej rov ua haujlwm dua. Txawm li cas los xij, cov ntaub ntawv (EEG) ntawm cov menyuam yaus uas muaj LKS qhia tau tias kev ua haujlwm nthwv dej tsis zoo ntawm lub hlwb txuas ntxiv mus thoob plaws txhua theem ntawm kev pw tsaug zog.
• Kev ntsuas kev hnov ​​lus / Kev ntsuas kev hnov ​​lus: Qhov kev ntsuas no yog ua los saib seb tus menyuam puas hnov ​​lus tau. Qee zaum, nws kuj tseem yuav tsum tau xyuas seb qhov teeb meem kev hnov ​​lus puas yog qhov ua rau muaj teeb meem lus.
• MRI ntawm lawv lub hlwb: Qhov no pab kom paub tseeb tias tsis muaj lwm yam mob loj, xws li qog hauv hlwb.
• Kev ntsuam xyuas los ntawm tus kws kho mob hlwb: Qhov no yog ib qho tseem ceeb kom tau txais kev ntsuam xyuas tus cwj pwm, kev txawj ntse, thiab kev kawm ntawm tus menyuam.

Yuav kho tus mob Landau-Kleffner li cas?

Thaum kho cov menyuam yaus uas muaj tus kab mob LKS, cov kws kho mob feem ntau siv tshuaj, kev kho kev hais lus, thiab kev kho tus cwj pwm . Qhov pib kho kev hais lus sai dua, qhov zoo dua uas tus menyuam muaj feem rov qab tau nws cov txuj ci lus.Qee zaum, cov kws kho mob kuj tseem yuav pom zoo kom noj zaub mov tshwj xeeb (kev noj zaub mov ketogenic) los tswj kev qaug dab peg.

Cov tshuaj twg muab rau LKS?

Koj tus kws kho mob yuav sau ntawv kom koj noj cov tshuaj xws li:

• Cov tshuaj Anticonvulsant: Cov no yog siv los tswj cov qaug dab peg.
• Corticosteroids: Cov no ua haujlwm los ntawm kev txo cov haujlwm ntawm lub cev tiv thaiv kab mob thiab tswj cov mob xws li o hauv lub hlwb.

Puas yog phais rau LKS?

Tsis tshua muaj cov kws kho mob ua tau kev phais hlwb hu ua Multiple Subpial Transections . Txawm li cas los xij, tseem tsis tau meej tias qhov kev phais no yuav pab tau koj ntau npaum li cas. Yog li ntawd, nws yog ib qho tseem ceeb uas yuav tsum tshuaj xyuas qhov zoo thiab qhov tsis zoo ntawm kev phais ua ntej koj ua qhov no.

Tom qab pib kho mob, kuv tus menyuam yuav zoo sai npaum li cas?

Tsis muaj leej twg "qhov no yog txoj kev zoo tshaj plaws" los kho tus mob LKS. Koj tus menyuam yuav maj mam zoo dua los ntawm kev kho kev hais lus thiab lwm yam kev kho mob. Txawm li cas los xij, qee zaum, koj tus menyuam yuav tsis teb zoo rau kev kho mob. Koj tus kws kho mob yuav saib xyuas koj tus menyuam tus mob tsis tu ncua thiab hloov kho txoj kev npaj kho mob raws li qhov xav tau.

Kuv ua tau dab tsi los txo qhov kev pheej hmoo ntawm kuv tus menyuam uas yuav muaj tus kab mob Landau-Kleffner syndrome?

LKS yog ib yam mob uas muaj los ntawm noob caj noob ces. Qhov no txhais tau tias koj yeej ua tsis tau dab tsi los tiv thaiv Landau-Kleffner Syndrome lossis txo koj txoj kev pheej hmoo ntawm kev mob no. Nws tsis yog koj qhov txhaum.

Puas kho tau Landau-Kleffner syndrome kom zoo tag nrho?

Muaj ib txhia menyuam rov qab muaj peev xwm hais lus thiab nkag siab lus. Lwm tus yuav rov qab tau qee yam kev txawj hais lus. Cov menyuam uas pib muaj cov tsos mob tom qab muaj hnub nyoog 6 xyoo thiab cov uas pib kho kev hais lus thaum ntxov muaj lub sijhawm zoo tshaj plaws los rov zoo. Qaug dab peg feem ntau tsis ua li ntawd thaum lawv loj hlob tuaj.

Yog tias kuv tus menyuam muaj LKS, kuv yuav tsum xav li cas?

Nws yuav siv sijhawm ntev rau koj tus menyuam kom rov zoo los ntawm LKS. Tej zaum koj yuav pom qee qhov kev txhim kho raws sijhawm. Tsis tas li ntawd, qee zaum kev txawj lus yuav zoo dua thiab tom qab ntawd poob qis dua (qhov no hu ua kev rov qab mob dua) . Koj tus kws kho mob yuav pom zoo kom mus kawm cov chav kawm tshwj xeeb lossis kawm lus piav tes , nyob ntawm seb koj tus menyuam xav tau dab tsi.

Txoj kev taug kev no nyuaj heev. Tab sis koj tsis yog tib leeg xwb. Cov kws kho mob, cov kws kho kev hais lus, koj tsev neeg, thiab cov phooj ywg txhua tus nyob ntawd los pab koj thiab koj tus menyuam. Qhov tseem ceeb tshaj plaws yog kev hlub thiab kev ua siab ntev rau koj tus menyuam, tsis txhob tso tseg kev cia siab.

Kuv yuav saib xyuas kuv tus menyuam uas muaj LKS li cas?

Ua raws li koj tus kws kho mob cov lus qhia kom zoo zoo kom koj tus menyuam noj qab nyob zoo. Yog tias koj tus menyuam muaj cov tsos mob tshiab, qhia rau koj tus kws kho mob paub tam sim ntawd. Ua li no, lawv tuaj yeem tau txais kev kho mob tsim nyog tam sim ntawd.

Landau-Kleffner Syndrome ua rau cov menyuam yaus uas ib txwm loj hlob tsis muaj peev xwm hais lus thiab nkag siab lus. Cov menyuam yaus uas muaj LKS muaj kev ua haujlwm tsis zoo ntawm lub hlwb thaum pw tsaug zog thiab feem ntau muaj qaug dab peg. Cov kws kho mob kho LKS nrog tshuaj thiab kev kho kev hais lus. Raws li lub sijhawm thiab nrog kev kho mob kom zoo, cov menyuam yaus tuaj yeem rov qab tau lawv cov kev txawj hais lus.

Tej yam tseem ceeb uas yuav tsum nco ntsoov (Cov Lus Qhia Coj Mus Tsev)

• LKS yog ib qho mob uas tsis tshua muaj tab sis mob hnyav heev: nws tuaj yeem ua rau tus menyuam tsis hais lus thiab nkag siab lus.
• Qaug dab peg feem ntau tshwm sim thaum pw tsaug zog: Qhov no yog ib qho tseem ceeb ntawm LKS.
• Qhov ua rau tsis pom txhua lub sijhawm: Txawm hais tias cov yam ntxwv caj ces yuav ua lub luag haujlwm hauv ntau kis, kuj tseem yuav tsis muaj qhov ua rau tshwj xeeb.
• Tsis txhob xav tias nws yog autism: Ob qho no tuaj yeem paub qhov txawv los ntawm kev kuaj (EEG).
• Kev kuaj mob thiab kev kho mob thaum ntxov yog qhov tseem ceeb heev: kev kho mob hais lus pib sai npaum li cas, qhov tshwm sim zoo dua.
• Kev kho mob zoo sib txawv ntawm ib tug me nyuam mus rau ib tug me nyuam: qee tus me nyuam zoo tag nrho, lwm tus zoo ib nrab. Kev ua siab ntev thiab kev txhawb nqa tas mus li yog qhov tseem ceeb heev.
• Koj tsis nyob ib leeg: Cov lus qhia kho mob, kev txhawb nqa tsev neeg, thiab kev hlub yog lub zog zoo rau ib tug me nyuam kom kov yeej qhov xwm txheej no.

Vam tias cov ntaub ntawv no yuav pab tau koj. Yog tias koj tus menyuam muaj cov tsos mob no, thov mus ntsib kws kho mob sai li sai tau.

Landau -Kleffner Syndrome, LKS, qaug dab peg, teeb meem hais lus, teeb meem lus, cov kab mob menyuam yaus, kev ua haujlwm ntawm lub hlwb, EEG