Koj puas tau pom ib tug neeg hauv koj tsev neeg lossis ib tug neeg uas koj paub tam sim ntawd tsaus muag thiab vau thaum lawv tawm dag zog lossis thaum lawv ntshai heev? Qee zaum, tom qab tej yam zoo li no yog mob plawv uas peb tsis tau hnov dua txog, tab sis qhov ntawd tuaj yeem ua rau mob hnyav heev. Ib qho mob zoo li no yog Long QT Syndrome (LQTS). Txawm hais tias lub npe yuav zoo li nyuaj me ntsis, cia peb nkag siab yooj yim.
Kab mob QT ntev (LQTS) yog dab tsi?
Hauv lwm lo lus, Long QT Syndrome (LQTS) yog ib qho teeb meem nrog koj lub plawv lub zog hluav taws xob.
Xav txog koj lub plawv zoo li lub teeb ci ntsa iab ntawm lub koob yees duab. Tom qab nws dhia ib zaug, nws yuav tsum tau them me ntsis ua ntej nws rov dhia dua. Yog li ntawd lub plawv lub zog hluav taws xob yuav tsum tau rov them dua ntawm cov kev dhia. Lub sijhawm uas nws siv rau qhov no tshwm sim yog qhov peb ntsuas ntawm ECG (Electrocardiogram) ua lub sijhawm QT .
Lub sijhawm rov qab them lub zog no ntev dua rau ib tus neeg uas muaj LQTS dua li rau ib tus neeg uas zoo li qub. Qhov no txhais tau tias lub plawv lub zog hluav taws xob siv sijhawm ntev dua los npaj rau lub plawv dhia tom ntej.
Qhov no tshwm sim li cas?
Peb lub plawv lub zog hluav taws xob yog tswj los ntawm cov khoom me me uas muaj hluav taws xob hu ua ions (piv txwv li, sodium, potassium, calcium). Cov ions no txav mus rau hauv thiab tawm ntawm cov leeg nqaij plawv los ntawm cov rooj vag me me hu ua ion channels .
Hauv cov mob Long QT Syndrome, cov ion channels no tsis ua haujlwm zoo lossis lawv ploj txaus. Qhov no ua rau lub plawv rov qab tau zog lig dhau lawm.
Thaum lub sijhawm QT ntev li no, lub plawv dhia ceev ceev, tsis xwm yeem (arrhythmia) tuaj yeem tshwm sim. Hauv cov lus kho mob, peb hu qhov no ua Torsades de Pointes . Qhov no yog ib hom mob txaus ntshai hu ua Ventricular Tachycardia .
Cov hom LQTS tseem ceeb yog dab tsi?
LQTS muaj ob hom tseem ceeb: kev txais los ntawm niam txiv thiab kev tau txais los ntawm niam txiv.
1. LQTS uas tau txais los ntawm noob caj noob ces/Congenital
Qhov no yog los ntawm qhov tsis zoo ntawm caj ces. Qhov ntawd txhais tau tias nws yog los ntawm niam txiv mus rau cov menyuam. Ntawm no kuj muaj ntau hom kab mob tseem ceeb.
| Hom kab mob LQTS uas yug los ntawm yug los | Ib qho lus piav qhia yooj yim |
|---|---|
| Kab mob Romano-Ward | Qhov no yog hom mob uas feem ntau tshwm sim. Hauv qhov no, ib tug ntawm cov niam txiv yuav muaj LQTS. Muaj 50% feem pua uas tus menyuam yuav tau tus mob no. Kev hnov lus (hnov lus) ntawm cov neeg no yog ib txwm muaj. |
| Jervell thiab Lange-Nielsen Syndrome | Qhov no tsis tshua muaj. Hauv qhov no, ob leeg niam txiv yog cov neeg nqa cov noob LQTS (tej zaum lawv yuav tsis muaj tsos mob). Muaj 25% feem pua uas tus menyuam yuav tau txais tus mob no. Cov menyuam uas muaj tus mob no feem ntau yug los lag ntseg. |
| Timothy Syndrome | Qhov no kuj yog ib hom mob uas tsis tshua muaj. Nws tsis yog tsuas yog cuam tshuam rau lub plawv xwb, tab sis kuj cuam tshuam rau lwm qhov ntawm lub cev thiab. |
2. Tau txais LQTS
Qhov no tsis yog los ntawm tej yam caj ces. Tej zaum ib txhia neeg yuav yug los nrog qhov tsis muaj zog me ntsis hauv lawv cov ion channels. Tab sis qhov ntawd tsis yog teeb meem. Txawm li cas los xij, qhov mob no tuaj yeem tshwm sim los ntawm qee yam sab nraud.
Cov laj thawj tseem ceeb yog:
- Qee cov tshuaj: Qee cov tshuaj tua kab mob, tshuaj antidepressants, tshuaj antiarrhythmics, thiab tshuaj diuretics.
- Cov ntsev hauv lub cev txo qis: Cov potassium, magnesium, lossis calcium hauv cov ntshav txo qis.
- Lwm yam ua rau: Kev noj zaub mov tsis zoo xws li anorexia nervosa, kev puas tsuaj rau lub paj hlwb, thiab qee yam tshuaj lom.
Cov tsos mob no yuav yog dab tsi?
Qhov txaus ntshai tshaj plaws txog LQTS yog tias kwv yees li 50% ntawm cov neeg tsis muaj tsos mob dab tsi . Txawm li cas los xij, thaum cov tsos mob tshwm sim, lawv feem ntau yog qhov hnyav. Cov tsos mob no tshwm sim thaum lub plawv dhia txaus ntshai uas tau hais ua ntej hu ua Torsades de Pointes tshwm sim.
| Cov tsos mob tseem ceeb | Ua li cas rau nws? |
|---|---|
| Ua tsis taus pa | Vim yog lub plawv dhia tsis xwm yeem, lub hlwb tsis tau txais ntshav txaus. Qhov no tuaj yeem ua rau tsis nco qab thiab vau. |
| Qaug dab peg | Qee zaum ib qho mob hu ua qaug dab peg tuaj yeem tshwm sim vim yog cov ntshav ntws mus rau lub hlwb tsawg dua. |
| Kev Nres Plawv | Yog tias tus qauv plawv dhia txaus ntshai ntawd txuas ntxiv mus, lub plawv yuav tsis dhia kiag li. |
| Kev Tuag Tam Sim Ntawd | Kev plawv nres tuaj yeem ua rau tuag taus yog tias tsis kho tam sim ntawd. Qee zaum, qhov no yog thawj cov tsos mob ntawm ib tus neeg uas muaj LQTS. |
Cov xwm txheej uas cov tsos mob yuav tshwm sim ntau dua:
- Thaum koj ua si lossis tom qab koj ua tiav.
- Thaum lub sijhawm muaj kev txhawb siab sai sai, hnyav heev (piv txwv li, thaum ntshai heev, poob siab).
- Thaum pw tsaug zog los yog thaum sawv ntxov tam sim ntawd los ntawm kev pw tsaug zog.
Leej twg muaj feem yuav mob no ntau dua?
Cov neeg hauv qab no muaj feem yuav mob LQTS ntau dua:
- Cov txheeb ze ze (niam txiv, kwv tij neej tsa, menyuam) ntawm ib tus neeg uas muaj LQTS.
- Cov neeg uas muaj keeb kwm tsev neeg ntawm kev nco tsis meej, qaug dab peg, lossis tuag tam sim ntawd thaum tseem hluas.
- Cov menyuam yaus uas yug los lag ntseg (vim muaj kev pheej hmoo ntawm Jervell thiab Lange-Nielsen Syndrome).
- Cov neeg uas muaj lwm yam kab mob plawv xws li cardiomyopathy.
- Cov neeg uas siv cov tshuaj uas ua rau lub sijhawm QT ntev dua.
Yog tias ib tug neeg hauv koj tsev neeg tau kuaj pom tias muaj LQTS, nws yog ib lub tswv yim zoo kom mus kuaj mob. Ua ntej, qhia rau koj tus kws kho mob txog qhov ntawd. Nws yuav xa koj mus kuaj ECG.
Koj paub li cas yog tias koj muaj LQTS?
Txoj kev tseem ceeb los kuaj qhov no yog los ntawm ECG (Electrocardiogram).Kuaj. Tus kws kho mob ntsuas lub sijhawm QT ntawm ECG. Feem ntau, yog tias lub sijhawm no ntev dua 450 milliseconds, yuav raug xav tias muaj LQTS.
Tsis tas li ntawd xwb, tus kws kho mob yuav pom zoo kom ua ntau yam kev kuaj ntxiv:
- Kev kuaj ntshav: Xyuas seb cov ntsev hauv lub cev muaj pes tsawg, xws li potassium thiab magnesium.
- Kev Ntsuas Kev Nyuaj Siab Thaum Ua Si: Saib seb koj lub plawv ua haujlwm li cas hloov pauv thaum lub sijhawm ua si.
- Kev Ntsuas Lub Plawv (Holter Monitor): Muaj ib lub cuab yeej me me tso rau ntawm koj lub hauv siab kom kaw koj lub plawv dhia tas li rau 24 teev lossis ntau dua.
- Kev kuaj noob caj noob ces: Tshawb xyuas seb puas muaj kev hloov pauv noob caj noob ces uas cuam tshuam nrog LQTS.
Cov kev kho mob rau qhov no yog dab tsi?
Txawm hais tias LQTS kho tsis tau tag nrho los xij, muaj kev kho mob uas tuaj yeem pab tswj cov tsos mob, tiv thaiv kev pheej hmoo ntawm kev tuag tam sim ntawd, thiab ua lub neej ib txwm muaj.
| Txoj kev kho mob | Kev piav qhia |
|---|---|
| Cov tshuaj | Muaj coob tus neeg (txawm tias cov uas tsis muaj tsos mob los xij) tau txais cov tshuaj beta-blocker . Cov no pab tswj lub plawv dhia me ntsis thiab txo qhov kev teb ntawm lub plawv rau cov kev xav tam sim ntawd. |
| Cov khoom siv |
|
| Kev phais mob | Kev puas tsuaj ntawm lub plawv sab laug (LCSD) rau cov neeg mob uas muaj kev pheej hmoo siab uas nyuaj rau tswj nrog cov tshuaj thiab cov khoom sivQhov kev phais no suav nrog kev tshem tawm qee cov hlab ntsha uas mus rau lub plawv, txo qhov kev teb ntawm lub plawv rau cov kev xav tam sim ntawd. |
Tej yam yuav tsum xav txog thaum nyob nrog LQTS
Nrog LQTS, koj ua tau lub neej zoo li qub thiab puv npo. Txawm li cas los xij, muaj ob peb yam uas koj yuav tsum paub txog hauv koj lub neej txhua hnub.
1. Suab nrov tam sim ntawd thiab kev ntxhov siab ntawm lub hlwb
Rau cov neeg uas muaj qee hom LQTS, suab nrov tam sim ntawd (piv txwv li, lub tswb ceeb toom, lub xov tooj nrov) lossis kev poob siab lossis kev ntshai tam sim ntawd tuaj yeem ua rau muaj kev phom sij.
- Qhia rau tsev neeg thiab cov phooj ywg tias nws tsis muaj kev nyab xeeb rau kev thuam koj.
- Siv cov moos ceeb toom uas nrov nrov xwb, tsis txhob siv cov uas tso suab paj nruag maj mam.
2. Kev tawm dag zog thiab kev ua si nawv
Rau cov neeg uas muaj qee hom LQTS, kev ua si sib tw thiab kev tawm dag zog hnyav tuaj yeem muaj kev pheej hmoo tshwj xeeb.
- Nco ntsoov nug koj tus kws kho mob seb cov kev tawm dag zog twg tsim nyog thiab tsis tsim nyog rau koj.
- Ua luam dej muaj kev phom sij tshwj xeeb rau ib txhia neeg. Muaj kev pheej hmoo ntawm kev poob dej yog tias koj tsis nco qab hauv dej. Tsis txhob mus ua luam dej ib leeg.
3. Yuav tsum ceev faj tshwj xeeb nrog cov tshuaj!
Qhov no yog qhov tseem ceeb tshaj plaws. Txawm tias ntau yam tshuaj uas siv ntau zaus kuj ua rau LQTS mob hnyav dua.
- Qhia rau txhua tus kws kho mob uas kho koj tias koj muaj LQTS.
- Ua ntej koj yuav muab tshuaj rau lwm yam mob, nrog koj tus kws kho mob tham.
- Tsis txhob yuav cov tshuaj uas yuav tau yam tsis tas yuav muaj daim ntawv yuav tshuaj los ntawm lub tsev muag tshuaj lossis lwm qhov chaw yam tsis tau sab laj nrog kws kho mob (tshwj tsis yog cov tshuaj xws li paracetamol thiab aspirin xwb).
Kuv yuav tsum mus ntsib kws kho mob thaum twg?
Thaum koj raug kuaj pom tias muaj LQTS, koj yuav tsum mus ntsib koj tus kws kho mob tsawg kawg ib xyoos ib zaug kom kuaj xyuas koj lub cev. Zoo tshaj plaws yog mus ntsib kws kho mob electrophysiologist, uas yog ib tus kws kho mob tshwj xeeb hauv kev kho mob plawv dhia tsis zoo.
Yog tias koj tus menyuam muaj tus mob no, koj yuav tsum tau mus ntsib kws kho mob tsis tu ncua vim tias qhov ntau npaum li cas ntawm cov tshuaj yuav tsum tau hloov kho raws li lawv qhov hnyav.
Kuv yuav tsum mus rau ETU (Chav Kho Mob Thaum Muaj Xwm Ceev) thaum twg?
Yog tias ib tug neeg tsis nco qab thiab ntog, hu rau lub tsheb thauj neeg mob tam sim ntawd. Lub sijhawm ntawd, yog tias muaj ib tug neeg tau kawm ua CPR (cardiopulmonary resuscitation), ua rau nws. Hauv qhov xwm txheej zoo li no, txhua ob feeb tseem ceeb.
Cov Lus Qhia Txog Kev Coj Mus Tsev
- Kab mob QT ntev (LQTS) yog ib qho mob caj ces lossis mob uas tau los ntawm noob caj ces uas lub plawv lub zog siv sijhawm ntev dhau los rov qab them tau.
- Cov tsos mob tseem ceeb yog kev tsis nco qab sai sai, qaug dab peg, thiab lub plawv tsis ua haujlwm yam tsis paub meej. Txawm li cas los xij, ntau tus neeg yuav tsis muaj tsos mob dab tsi li.
- Yog tias leej twg hauv koj tsev neeg muaj tus mob no lossis muaj keeb kwm ntawm kev tuag tam sim ntawd thaum tseem hluas, nws yog ib qho tseem ceeb heev uas koj yuav tsum tau kuaj ECG.
- Ua ntej noj tshuaj twg los tau (txawm tias yog lwm yam mob los xij), nrog koj tus kws kho mob tham kom paub tseeb tias nws muaj kev nyab xeeb rau koj.
- Yog tias koj kho mob kom zoo (tshuaj, khoom siv ICD) thiab hloov koj txoj kev ua neej, ib tug neeg uas muaj LQTS yuav muaj peev xwm ua neej tau zoo thiab noj qab nyob zoo. Koj tsis tas yuav ntshai, tiam sis nws yog ib qho tseem ceeb uas yuav tsum ceev faj.
💬 Comments (0)
Tsis muaj lus teb tau muab tso tawm. Ntxiv koj cov lus tawm ntawm no thawj zaug.
Ntxiv koj cov lus