Xav txog seb, koj noj qab nyob zoo thiab koj ib sab caj npab lossis ob txhais ceg tsis muaj zog thiab koj tsaug zog tas. Los yog koj lub cev tag nrho qaug zog heev uas koj tsis tuaj yeem txav mus los. Nws yog ib qho ib txwm muaj uas koj yuav ntshai heev thaum muaj tej yam zoo li no tshwm sim. Muaj ntau tus neeg xav tias qhov no yog vim qaug zog lossis lwm yam. Txawm li cas los xij, qee zaum yuav muaj ib qho laj thawj kho mob tom qab qhov no uas yuav tsum tau tham txog kom tob dua. Niaj hnub no peb tab tom tham txog ib qho mob uas tsis tshua muaj tab sis tseem ceeb heev uas yuav tsum paub txog.
Hais yooj yim xwb, Primary Periodic Paralysis (PPP) yog dab tsi?
Kab Mob Plawv Tsis Tshwm Sim, lossis luv luv PPP, yog ib pawg mob tsis tshua muaj uas cuam tshuam rau peb cov leeg nqaij. Qhov tshwm sim yog tias, yam tsis muaj lus ceeb toom , koj cov leeg nqaij cia li qaug zog, tawv, lossis tuag tes tuag taw tag. Mob no tuaj yeem kav ntev li ob peb feeb rau qee tus neeg, thaum rau lwm tus nws tuaj yeem kav ntev li ob peb hnub.
Qhov laj thawj tseem ceeb rau qhov no yog nyob hauv peb cov leeg nqaij. Xav txog tias peb cov leeg nqaij muaj cov channel me me. Cov channel no yog qhov chaw uas cov zaub mov tseem ceeb xws li potassium, sodium, thiab calcium nkag mus thiab tawm hauv cov cell. Rau cov leeg nqaij kom ua haujlwm tau zoo, qhov ntau ntawm cov zaub mov no sab hauv thiab sab nraud ntawm lub cell yuav tsum nyob rau hauv qhov sib npaug zoo meej. Qhov tshwm sim rau ib tus neeg uas muaj PPP yog tias qhov sib npaug no ploj mus vim muaj qhov tsis zoo hauv cov channel no. Tom qab ntawd cov leeg nqaij tsis tuaj yeem ua haujlwm tau zoo.
Feem ntau, cov tsos mob no pib thaum yau lossis thaum hluas, tab sis qee tus neeg yuav tsis pom cov tsos mob kom txog thaum lawv muaj hnub nyoog 60 lossis 70 xyoo.
Cov kab mob no muaj hom kab mob dab tsi tseem ceeb?
PPP muab faib ua ntau hom tseem ceeb. Qhov kev faib tawm no feem ntau yog cuam tshuam los ntawm qhov tsis zoo ntawm cov channel mineral uas muaj nyob hauv koj cov leeg nqaij.
| Hom mob | Muaj dab tsi tshwm sim (hauv cov lus yooj yim) |
|---|---|
| Kev Mob Plawv Tsis Tshwm Sim (hypokalemic periodic paralysis) (hypoKPP) | Qhov tshwm sim hauv qhov no yog tias cov potassium theem hauv cov ntshav poob qis sai sai. |
| Kab mob Hyperkalemic Periodic Paralysis (hyperKPP) | Qhov tshwm sim hauv qhov no yog tias cov potassium theem hauv cov ntshav sai sai nce ntxiv. |
| Paramyotonia Congenita | Ntawm no, qhov sib npaug ntawm sodium thiab potassium hauv cov leeg nqaij raug cuam tshuam. |
| Kab mob Andersen-Tawil (ATS) | Hauv qhov xwm txheej no, cov txheej txheem ntawm potassium txav mus rau hauv thiab tawm ntawm cov cell tsis tshwm sim kom raug. Cov theem ntawm potassium hauv cov ntshav yuav siab, qis, lossis ib txwm muaj. |
Qee zaum, cov leeg nqaij tsis muaj zog tuaj yeem yog los ntawm lwm yam mob. Piv txwv li, Thyrotoxic Periodic Paralysis (TPP) . Qhov no yog ib qho mob uas cov qog thyroid tsim cov tshuaj thyroid ntau dhau. Qhov no nrog rau cov ntshav potassium qis, uas tuaj yeem ua rau muaj cov tsos mob zoo ib yam li HypoKPP.
Cov ua rau muaj qhov teeb meem no yog dab tsi thiab cov yam "ua rau muaj" qhov teeb meem no yog dab tsi?
PPP yog tshwm sim los ntawm qhov tsis zoo ntawm cov noob caj noob ces . Hais yooj yim xwb, nws yog tshwm sim los ntawm qhov tsis zoo ntawm cov noob caj noob ces uas tswj cov channel hauv cov leeg nqaij uas peb tau tham txog ua ntej. Feem ntau, ib tug menyuam tau txais cov noob caj noob ces tsis zoo no los ntawm ib tug ntawm lawv niam lawv txiv. Txawm li cas los xij, tsis tshua muaj, ib tug menyuam tuaj yeem muaj tus kab mob txawm tias niam txiv tsis muaj cov noob caj noob ces no los xij.
Tam sim no cia peb saib seb dab tsi ua rau cov leeg nqaij tsis muaj zog. Cov no yuav txawv ntawm ib tus neeg mus rau ib tus neeg.
- Kev Noj Haus: Noj cov khoom noj uas muaj potassium ntau dhau (hauv hyperKPP) lossis potassium tsawg (hauv hypoKPP). Tsis tas li ntawd, noj cov khoom noj uas muaj carbohydrates ntau (hmoov txhuv nplej siab/qab zib).
- Kev Ua Si : Thaum so tom qab ua si hnyav.
- So: Zaum tib qho chaw ntev, thaum sawv ntxov, lossis tom qab pw tsaug zog.
- Lwm yam ua rau: Kev ntxhov siab, raug cua txias heev, haus dej cawv, thiab qee yam tshuaj (piv txwv li, tshuaj so cov leeg nqaij, qee yam tshuaj hawb pob, tshuaj tua kab mob).
Cov tsos mob tseem ceeb yog dab tsi?
Cov tsos mob tseem ceeb yog cov leeg nqaij tsis muaj zog tam sim ntawd lossis tuag tes tuag taw tag nrho. Qhov no tuaj yeem cuam tshuam rau ib sab caj npab lossis ceg ib zaug, lossis tag nrho lub cev rau lwm lub sijhawm.
Ntxiv rau qhov tsos mob tseem ceeb no, qee tus neeg kuj tseem yuav muaj lwm cov tsos mob thaum lawv ntsib qhov tsis muaj zog no:
- Cov leeg nqaij ntawm lub ntsej muag tsis muaj zog
- Mob nqaij thiab mob nqaij tawv
- Lub plawv dhia tsis xwm yeem
- Ua pa nyuaj los yog nqos nyuaj
HypoKPP (hom potassium qis)
Cov tsos mob yuav tshwm sim ntau zaus li ib zaug hauv ib hnub, lossis tsis tshua muaj li ib xyoos ib zaug. Lawv tuaj yeem kav ntev li ib teev lossis ob hnub, lossis lawv tuaj yeem kav ntev li ob lossis peb hnub. Raws li lub sijhawm dhau mus, cov leeg nqaij yuav qaug zog tas mus li.
HyperKPP (hom potassium ntau ntxiv)
Qhov tsis muaj zog yuav luv luv xwb, tiam sis nws yuav tshwm sim ntau zaus. Cov tsos mob yuav tshwm sim sai sai, thiab qee zaum yuav kav ntev li ob peb feeb xwb. Txawm tias tsis muaj zog los xij, koj yuav hnov cov leeg nqaij ntswj lossis mob.
Kab mob Andersen-Tawil (ATS)
Ntxiv rau qhov nqaij ntshiv tsis muaj zog, kuj pom muaj lwm yam tsos mob ntawm lub cev.
- Lub plawv dhia ceev lossis tsis xwm yeem
- Kab mob Scoliosis
- Cov ntiv tes uas muaj cov ntaub thaiv
- Me dua li tes thiab taw nruab nrab
- Qee qhov kev hloov pauv ntawm lub ntsej muag (piv txwv li, lub hauv pliaj dav, pob ntseg qis)
Yuav ua li cas thiaj kuaj tau tus kab mob no kom meej?
Vim tias PPP yog ib yam mob uas tsis tshua muaj thiab nws cov tsos mob zoo ib yam li lwm yam kab mob uas feem ntau pom, nws yuav siv sijhawm me ntsis los kuaj mob kom raug. Yog li ntawd, yog tias koj muaj cov tsos mob no, nws yog qhov zoo tshaj plaws mus ntsib kws kho mob uas tshwj xeeb hauv cov kab mob ntsig txog lub paj hlwb (Neurologist) .
Koj tus kws kho mob yuav nug cov lus nug zoo li no los kuaj mob:
- Cov tsos mob no pib thaum twg?
- Puas muaj leej twg hauv tsev neeg muaj tus mob zoo sib xws?
- Yuav ua li cas thaum muaj kev qaug zog?
- Koj puas tau xav tias muaj ib yam khoom noj lossis ib yam dab tsi ua rau qhov no ua rau muaj?
Ntxiv rau, yuav muaj ntau yam kev kuaj mob uas yuav ua tau los xyuas kom meej tias muaj tus kab mob no:
- Kev kuaj ntshav: Xyuas cov qib potassium, cov tshuaj hormones thyroid, thiab lwm yam.
- Electromyography (EMG): Siv los ntsuas kev ua haujlwm ntawm cov leeg nqaij thiab cov hlab ntsha.
- Electrocardiogram (EKG): Siv los xyuas seb lub plawv dhia puas khiav tsis tu ncua.
- Kev kuaj mob nqaij: Siv ib daim nqaij me me los kuaj xyuas.
Yuav kho thiab tswj li cas?
Txoj kev kho mob tseem ceeb rau qhov no yog nrhiav thiab zam cov teeb meem uas ua rau muaj teeb meem . Qhov no txhais tau tias hloov qee yam kev noj haus thiab kev tawm dag zog.
Tsis tas li ntawd xwb, muaj cov tshuaj los tswj cov potassium hauv lub cev.
- Cov tshuaj Dichlorphenamide (Keveyis) tau pom zoo los kho ob qho tib si hypoKPP thiab hyperKPP.
- Cov kws kho mob qee zaum kuj pom zoo kom siv tshuaj hu ua Acetazolamide (Diamox) .
- Cov tshuaj potassium muab rau cov neeg uas muaj HypoKPP.
- Ib tug neeg uas muaj HyperKPP tej zaum yuav tswj tau qhov qaug zog los ntawm kev haus dej qab zib (piv txwv li, dej qab zib) thaum nws pib haus.
Qhov tseem ceeb tshaj plaws yog, tsis txhob tsum noj lossis tsum tshuaj ntawm koj tus kheej. Ua txhua yam tsuas yog raws li koj tus kws kho mob qhia xwb. Yog tias koj muaj qhov tsis muaj zog sai sai, ua pa nyuaj, lossis mob hauv siab, mus rau Chav Kho Mob Thaum Muaj Xwm Ceev (ETU) ntawm lub tsev kho mob ze tshaj plaws tam sim ntawd.
Koj tuaj yeem tswj tau qhov mob no rau ntau yam los ntawm kev hloov me me rau koj txoj kev ua neej.
- Khoom Noj: Yog tias koj muaj hyperKPP (potassium ntau), koj yuav tsum tsis txhob noj cov khoom noj uas muaj potassium ntau xws li txiv tsawb, txiv lws suav, broccoli, thiab txiv laum huab xeeb. Yog tias koj muaj hypoKPP (potassium tsawg), koj yuav tsum tsis txhob noj cov khoom noj uas muaj carbohydrate ntau xws li mov ci, pasta, mov, thiab khoom qab zib. Nrhiav cov lus qhia zoo los ntawm koj tus kws kho mob txog qhov no.
- Kev Ua Si: Ib yam li kev ua si ntau dhau, kev tsis ua si kuj tsis zoo. Tham nrog koj tus kws kho mob txog qib kev ua si uas haum rau koj.
Cov Lus Qhia Txog Kev Coj Mus Tsev
- Kab mob Primary Periodic Paralysis (PPP) tsis yog tsuas yog kev tsis taus ntawm lub cev xwb, nws yog qhov teeb meem caj ces uas tshwm sim hauv cov ion channels ntawm cov leeg nqaij.
- Muaj tej yam ua rau mob no. Yuav tsum nco ntsoov txog tej yam xws li kev noj zaub mov, kev tawm dag zog, thiab kev ntxhov siab, thiab nrhiav thiab zam tej yam uas cuam tshuam rau koj.
- Yog tias muaj cov tsos mob tshwm sim, nws yog ib qho tseem ceeb heev uas yuav tsum mus ntsib kws kho mob tshwj xeeb kom paub tseeb tias muaj tus kab mob.
- Muaj ntau tus neeg uas muaj peev xwm tswj tau qhov mob no thiab ua neej nquag los ntawm kev hloov pauv lawv txoj kev ua neej thiab noj tshuaj uas lawv tus kws kho mob tau sau tseg.
- Ua raws li koj tus kws kho mob cov lus qhia tas li. Tsis txhob txiav txim siab ntawm koj tus kheej, xws li noj tshuaj lossis hloov koj cov zaub mov noj.
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Tsis muaj lus teb tau muab tso tawm. Ntxiv koj cov lus tawm ntawm no thawj zaug.
Ntxiv koj cov lus