Yu pikin gɛt vein na in at we tan lɛk sɔd? Lɛ wi lan bɔt dis sik wae nɔr kin bɔrku (Scimitar Syndrome)!

"O, i tan lɛk se wi smɔl wan de gɛt prɔblɛm fɔ blo, i de wisɛf ivin we i de gi pikin in bɛlɛ... sɔntɛnde in skin kin luk blu..." Yu dɔn ɛva ɛkspiriɛns sɔntin lɛk dis? Ɔ yu dɔn si dis apin to pɔsin we yu sabi in pikin? Sɔntɛnde, dɛn sik ya kin kam bikɔs ɔf sɔm at prɔblɛm dɛn we dɛn kin bɔn pikin dɛn wit. Tide wi go tɔk bɔt wan pan dɛn kayn at sik ya we nɔ kin bɔku, bɔt we impɔtant fɔ no bɔt.

Wetin na di sik we dɛn kɔl Scimitar Syndrome?

Dɛn kɔl dis sik we dɛn kɔl Scimitar Syndrome . Di nem de saund likl strenj, no bi so? ‘Scimitar’ de tɔk bɔt sɔd we gɛt kɔba tip, we dɛn bin de yuz trade trade na di Midul Is. pan dis kכndyushכn, sכmtεm di pulmonari vein we de kכri bכdi frכm di rayt lכng to di at, kin apia lεk sכd we kכba pan εks-ray. Yu nɔ tink se i rili intrestin aw di nem kam?

Fɔ tɔk am simpul wan, dis na wan at prɔblɛm we dɛn bɔn wit . dat min se, wan kכndyushכn we de apin we di pikin stil de na di bεlε. Dɔktɔ dɛn kɔl dis wan kayn sik we dɛn kɔl Partial Anomalous Pulmonary Venous Return (PAPVR). Dat min se, wan prɔblɛm de na di we aw di blɔd vesel dɛn we de kɔmɔt na di lɔng dɛn kin kɔnɛkt to di at.

Bɔrku men sayn dɛm de wae yu kin si pan dis kayn tin:

• di rayt lכng nכ de fulכp divεlכp (haypoplastik rayt lכng). dis min se i sכm εn i nכ de wok bכku pas di lכng we de na di כda say.
• di men at we de kכri bכdi go na di rayt lכng (rayt pulmonary atεri) nכ de divεlכp fayn fayn wan (hypoplastic right pulmonary artery). Dis kin mek bak di blɔd we de rich na di rayt lɔng.

Wi go ebul fɔ ɔndastand smɔl bɔt di wɔndaful we aw wi at de wok?

So, fɔ rili ɔndastand wetin de apin wit Scimitar Syndrome, lɛ wi fɔs luk aw wɛlbɔdi at de wok, okay? Tink bɔt wi at as pɔmp we de wok fayn fayn wan. I de pɔmp blɔd ɔlsay na wi bɔdi, de ɛn nɛt.

Dis na wetin kin apin:

1. we dεn yus, כksijεn- po bכdi frכm כ lsay na di bכdi de kכlekt εn go bak na di rayt say na di at.

2. dis blכd we nכ gεt כksijεn we de kכmכt na di rayt say na di at de sεnd to di lכng dεm, tru di pulmonary arteries .

3. insay di lכng dεm, dis bכdi de `oksijen`, jכs lεk aw dכti wata dεn de filta εn klin.

4. Dɔn, dis blɔd we gɛt bɔku ɔksijɛn kin go bak na di lɛft say na di at tru di pulmonari vein dɛn, we na di vein dɛn we de kɔmɔt na di lɔng dɛn to di at .

5. di lεft say na di at de pכmp dis bכdi we gεt כksijεn to di wan ol bכdi, tru di big bכdi we dεn kכl di aorta .

Dis na aw ɔl sɛl na wi bɔdi kin gɛt ɔksijɛn. Yu nɔ tink se dis na tin we rili kɔmpleks ɛn we rili wɔndaful?

So wetin kin apin pan Scimitar Syndrome?

Naw yu go dɔn ɔndastand aw wɛlbɔdi at de wok. Wetin kin apin to pɔsin we gɛt Scimitar Syndrome na dat di blɔd we fɔ de kɔmɔt na in lɔng fɔ gɛda ɔksijɛn ɛn go na di lɛft say na di at, instead fɔ kam da we de , de go di rɔng we ɛn go na di rayt say na di at.

Imajin if yu kɔnɛkt bak wan paip we de briŋ wata to os to di rɔng ples, sɔntɛm to wata tank we yu dɔn yuz. Dɔn wetin fɔ apin nɔ go apin di rayt we. Wan tin kin apin usay dɛn miks klin wata ɛn dɔti wata.

insay dis, wan כ mכr vein dεm (pulmonary veins) we nכmal fכ kכri כksijεn bכdi frכm di rayt lכng de kכnekt to di rayt say na di at insted fכ di lεft sayd. Dis kin mek sɔm pan di blɔd we gɛt ɔksijɛn go bak na di lɔng dɛn. I kin mek bak di rayt say na di at wok tranga wan.

Sɔntɛnde, di rayt lɔng nɔ kin gɛt blɔd frɔm di pulmonary arteries , bɔt i kin kɔmɔt dairekt frɔm di aorta . di aorta na di men blɔd vesel we de kɛr blɔd go na di wan ol bɔdi. So na smɔl prɔblɛm de de bak. Dis kin put strɛs pan di at we nɔ nid fɔ de.

Aw kɔmɔn tin dis kin apin? Yu tink se wi fɔ fred we wi nɔ nid fɔ fred?

Dis kin tan lɛk se yu de mek yu fred, bɔt Scimitar Syndrome na wan sik wae nɔr kin bɔrku. Statistikin sho se na wan to tri pikin dɛn nɔmɔ i kin afɛkt pan ɛvri 100,000 pikin dɛn. Dɛn kin si bak se i kin bɔku tu tɛm pan gyal pikin dɛn pas bɔy pikin dɛn.

So, nɔ panik we yu nɔ nid, bikɔs dis nɔ kin apin so ɔltɛm. Bɔt, i rili impɔtant fɔ mek wi no bɔt dis.

Wetin na di rizin dɛn we mek dɛn de du dis? Wetin mek dis de apin?

Bɔku tɛm, ivin dɔktɔ dɛn kin gɛt prɔblɛm fɔ no di rayt tin we kin mek pɔsin gɛt Scimitar Syndrome. Bɔt sɔm tin dɛn de we kin mek di pikin gɛt prɔblɛm wit in at we i bɔn wit. Dɛn tin ya na:

• Jɛnɛtiks: Sɔntɛnde, di jenɛtik kɔndishɔn dɛn we dɛn kin pas tru jɛnɛreshɔn kin gɛt impak.
• Sɔm mɛrɛsin dɛn we dɛn kin tek we uman gɛt bɛlɛ: Fɔ ɛgzampul, sɔm mɛrɛsin dɛn we kin mek pɔsin gɛt akni lɛk `(Isotretinoin - Accutane®)` kin denja. Na dat mek dɛn kin advays yu nɔ fɔ tek ɛni mɛrɛsin we yu gɛt bɛlɛ if yu nɔ gɛt dɔktɔ advays.
• Di tin dɛn we de apin na di say we i de: If di mama de smok ɔ drink rɔm we i gɛt bɛlɛ, dɛn kayn tin ya kin afɛkt di we aw di pikin in at de gro.
• Sכm infεkshכn dεm na di mama: fכ egzampl, if di mama gεt infεkshכn lεk rubεla we i bεlε, i kin afekt di pikin in at divεlכpmεnt.
• di mama in sik dεm we nכ de kכntro: If dεn nכ kכntrכl sik dεm lεk dayabitis mεlitכs fayn fayn wan we i bεlε, i kin afekt di pikin bak.

Di impɔtant tin na dat, bɔku tɛm, dis nɔto ɛnibɔdi in fɔlt. So nɔ blem yusɛf.

Us sayn dɛn de sho se yu gɛt dis sik?

De sayn dɛm fɔ Scimitar Syndrome nɔr kin di sem fɔ ɔlman. Sɔm pikin dɛn kin sho sɔm sayn dɛn jɔs afta dɛn bɔn dɛn . Tin dɛn we yu fɔ tek tɛm wit dɛn kayn tɛm dɛn de na:

• I nɔ izi fɔ blo ɛn chok we yu de gi pikin in bɛlɛ.
• di skin εn di lip dεm we de kכl blu/grεy (cyanosis): Dis kin apin we di bכdi nכ de gεt inof כksijεn.
• Fɔ blo kwik kwik wan.
• Swel (edema) na di leg, bɛlɛ, ɛn rawnd di yay.

Bɔt sɔm pikin dɛn nɔ kin sho ɛni sayn te dɛn big. Sɔm kin kɔntinyu fɔ gɛt ɛni sayn te dɛn big. Bɔt if di sayn dɛn de sho se dɛn dɔn big, dɛn kin gɛt:

• Infεkshכn dεm na di lכng bכku tεm.
• I nɔ kin izi fɔ yu fɔ blo (dyspnea) we yu de du ɛksɛsayz ɔ we yu de tray tranga wan.

Aw dɔktɔ dɛn kin no bɔt dis? (Diagnosis) .

Dɔktɔ dɛn gɛt bɔku tɛst fɔ ɛp fɔ no if pɔsin gɛt Scimitar Syndrome. dis kin luk tin dεm lεk di sayz fכ di rayt lכng na pikin כ big man εn di kכndishכn fכ di rayt pulmonari at.

• Chɛst X-ray: Dis kin mek yu no bɔt di at, di lɔng, di say dɛn we di briz de blo, ɛn di blɔd vesel dɛn. Yu kin si di ‘Scimitar’ shep pan dis.
• CT scan: Dis kin tek X-ray frɔm difrɛn angul dɛn fɔ mek ditayla tri-dimɛnshɔnal imej dɛn fɔ di insay pat na di bɔdi.
• MR angiography: Dis na tɛst we dɛn kin yuz magnɛtik wev ɛn kɔmpyuta fɔ luk di blɔd vesel dɛn ditayli.
• Transthoracic echocardiogram (TTE): Dis tan lɛk ɔltra saund skan. I kin luk gud wan pan aw di at de wok, di chɛmba dɛn, di valv dɛn, ɛn di blɔd we de flɔ.
• Cardiac catheterization: Insay dis prosidur, dɛn kin injekt spɛshal day insay di blɔd vesel dɛn ɛn tek X-ray fɔ si aw di blɔd de flɔ tru di vessels. Dɛn kin yuz am bak fɔ no di prɛshɔn we de na di at ɛn di lɔng dɛn.

Nɔ fred fɔ aks bɔt dɛn tɛst ya. Dɔktɔ dɛn kin du dɛn tin ya fɔ no di sik kɔrɛkt wan ɛn fɔ gi dɛn di bɛst tritmɛnt.

Yu tink se tritmɛnt de fɔ dis? (Di we aw dɛn kin trit am)

Yɛs, di men tritmɛnt fɔ Scimitar Syndrome na ɔpreshɔn.

• Fɔ bebi dɛn, if dɔktɔ dɛn no dis sik, dɛn kin tɛmpt dɛn fɔ du ɔpreshɔn insay di fɔs tu mɔnt we dɛn de liv . Bikɔs di mɔ we dɛn kɔrɛkt dis prɔblɛm kwik kwik wan, na di mɔ i go bɛtɛ fɔ di pikin in divɛlɔpmɛnt ɛn wɛlbɔdi tumara bambay.
• Fɔ big pipul dɛn, .Nɔto ɔlman we gɛt Scimitar Syndrome go nid ɔpreshɔn pas dɛn gɛt siriɔs sik dɛn (e.g., dɛn kin gɛt infɛkshɔn na dɛn lɔng ɔltɛm, dɛn kin gɛt siriɔs shɔt briz). Bɔt if di sayn dɛn we de sho se di sik rili bad, i kin nid fɔ du ɔpreshɔn.

Bɔku tin dɛn de we dɔktɔ we de mɛn in at kin du we dɛn de du di ɔpreshɔn:

• di pulmonari vein, we kכnekt na di rכng ples , de rirout to di lεft say na di at. Sɔntɛnde, dɛn kin yuz spɛshal pat dɛn fɔ dis.
• If nɔto dat, dɛn kin put di vein dairekt insay di lɛft say na di at.
• Na smɔl tɛm nɔmɔ dɛn kin du nyumonia fɔ pul di rayt lɔng we nɔ de divɛlɔp fayn ɛn we nɔ de wok fayn. Bɔt, dɛn kin jɔs du dis we ɔda tin nɔ de fɔ du.

We wi go ebul fɔ mek dis nɔ apin?

Infakt, no we nɔ de fɔ mek dɛn nɔ gɛt wan sik we dɛn bɔn wit at lɛk Scimitar Syndrome kpatakpata, bikɔs na di tin dɛn we de mek pɔsin gɛt jɛnɛtiks kin afɛkt am bak.

Bɔt tin dɛn de we mama kin du we i gɛt bɛlɛ fɔ mek i gɛt mɔ chans fɔ bɔn pikin we gɛt wɛlbɔdi:

• Nɔ drink rɔm, sigrɛt, ɛn ɔda drɔgs kpatakpata we yu gɛt bɛlɛ.
• Bifo yu tek ɛni mɛrɛsin, tɔk to yu dɔktɔ bɔt di bad tin dɛn we i kin du ɛn di bɛnifit dɛn we i kin gɛt.
• If yu nɔ gɛt di rubɛla vaysin , i impɔtant fɔ gɛt am bifo yu gɛt bɛlɛ, bikɔs we yu gɛt rubɛla we yu gɛt bɛlɛ i kin afɛkt di pikin in at.
• If yu gɛt sik dɛn we nɔ de mɛn lɛk dayabitis , kɔntrol dɛn fayn fayn wan we yu gɛt bɛlɛ.
• Tek fɔlik asid ɛn ɔda vaytamɛn dɛn we yu kin gɛt bifo yu bɔn lɛk aw yu dɔktɔ tɛl yu.

Aw layf go tan lɛk wit dis sityueshɔn? (Fyuchɔ vishɔn)

Pipul dɛn we dɛn kin du ɔpreshɔn fɔ Scimitar Syndrome kin gɛt fayn fayn tin dɛn fɔ du fɔ lɔng tɛm . Bɔrku pipul nɔr kin gɛt ɛni sayn bak afta dɛn dɔn du dɛn ɔpreshɔn.

Bɔt sɔm tɛm, mɔ pan bebi ɛn smɔl pikin dɛn, di pulmonari vein we dɛn chenj di rod kin smɔl. If dis apin, dɛn kin nid fɔ gɛt ɔda tritmɛnt.

Sɔm big pipul dɛm wae gɛt Scimitar Syndrome kin liv wɛl bɔdi layf wae nɔr gɛt ɛni sayn. Bɔt fɔ ɔda big pipul dɛn, dis sik kin mek dɛn gɛt ɔda prɔblɛm dɛn na dɛn at. If dɛn kayn tin ya apin, di kwaliti fɔ layf kin afɛkt. If di sayn dɛm de kam (lɛk fɔ blo bad bad wan, infekshɔn na in lɔng), i kin nid fɔ du ɔpreshɔn. Yu kin nid bak fɔ du spɛshal tɛst fɔ chɛk if yu gɛt ay blɔd prɛshɔn na di at dɛn we de na yu lɔng.

Ɔda at sik dɛn de we gɛt fɔ du wit Scimitar Syndrome?

Yɛs, bɔrku pipul dɛm wae gɛt Scimitar Syndrome kin gɛt ɔda prɔblɛm wit dɛn at ɛn blɔd. Sɔm dɛn kin bɔn wit bɔku bɔku at prɔblɛm dɛn. Ɔ, Scimitar Syndrome kin mek ɔda prɔblɛm dɛn.

Ɔda tin dɛn we kin apin we gɛt fɔ du wit dis na:

• Atrial Septal Defect (ASD): na ol bitwin di tu כp chεmba dεm na di at.
• כs shu lכng: Na abnכmal kכnεkshכn bitwin tu pat dεm na di lכng.
• Pulmonary hypertension: I gɛt ay prɛshɔn na di at dɛn na di lɔng dɛn.
• Pulmonary sequestration (accessory lung): na wan pat pan di lכng tisu we nכ de wok, we de kכmכt wit abnכmal bכdi saplai.
• Tetralogy of Fallot: Na kɔmɔn at prɔblɛm we nid tritmɛnt fɔ pɔmp blɔd to di lɔng dɛn na di pikin dɛn.
• Ventricular Septal Defect (VSD): na ol bitwin di tu lכw pכmp chεmba dεm na di at.

We yu yɛri dɛn tin ya, dat kin mek yu fred mɔ. Bɔt, mɛrɛsin de fɔ ɔl dɛn sik ya. De tin wae impɔtant pas ɔl na fɔ tɔk to yu dɔktɔ, ɔndastand yu kɔrɛkt sik, ɛn gɛt di tritmɛnt wae yu nid.

Impɔtant kwɛstyɔn dɛn fɔ aks yu dɔktɔ

If yu kam fɔ no se yu ɔ yu pikin gɛt Scimitar Syndrome, yu kin aks yu dɔktɔ kwɛstyɔn dɛn lɛk dɛn wan ya:

• Wetin na de tin wae kin mek pɔrsin gɛt Scimitar Syndrome?
• Mi/mi pikin nid ɔpreshɔn?
• Wetin kin apin if dɛn nɔ du yu ɔpreshɔn?
• Aw fɔ manej at wɛlbɔdi wit Scimitar Syndrome?
• If a gɛt dis sik, wetin na di chans fɔ mek mi pikin sɛf gɛt am?
• If a gɛt fɔs pikin we gɛt Scimitar Syndrome, wetin na di chans fɔ mek mi sɛkɔn pikin sɛf gɛt am?

Nɔ ɛva fred ɔ shem fɔ aks dɛn kwɛstyɔn ya. I rili impɔtant fɔ klin ɔl di dawt dɛn we de na yu maynd.

Fɔ dɔn, tin dɛn fɔ mɛmba (Take-Home Message) .

Scimitar Syndrome na wan sik we nɔ kin apin so ɔltɛm, we pɔsin kin bɔn wit in at we kin afɛkt di rayt lɔng ɛn di blɔd vesel dɛn we de kɔnɛkt am to di lɔng.

Sɔm pikin dɛn nɔ kin sho ɛni sayn, bɔt ɔda wan dɛn kin nid fɔ ɔpreshɔn insay di fɔs tu mɔnt we dɛn de liv.

Bebi dɛn we nid ɔpreshɔn ali kin nid mɔ tritmɛnt leta bikɔs di blɔd vesel we dɛn dɔn chenj kin smɔl. Bɔt bɔku big pipul ɛn pikin dɛn we dɛn dɔn ɔpreshɔn fɔ Scimitar Syndrome de liv rili gud wɛlbɔdi ɛn liv nɔmal layf.

Wi op se dis infɔmeshɔn go ɛp yu. If yu gɛt ɛni ɔda kwɛstyɔn bɔt dis, mek shɔ se yu tɔk to yu dɔktɔ. Stay wit wɛlbɔdi!

`Scimitar Syndrome, at sik, bɔn pikin we nɔ fayn, lɔng, blɔd we de go ɔlsay, pikin in simptom, ɔpreshɔn