Omwana wo omuto alina obuzibu mu kussa nga buno? Ka twogere ku "Double Aortic Arch"!

Omwana wo omuto oluusi awulira ng’alina obuzibu mu kussa? Aziyira ng’aliisa oba ng’ayonsa? Oba akola amaloboozi ag’ekyewuunyo ng’assa? Wadde nga zino ziyinza okuba endwadde eza bulijjo ez’abaana, wayinza okubaawo embeera ey’amaanyi ennyo, naye esobola okujjanjabibwa, emabega wa kino. Embeera emu ng'eyo etali ya bulijjo naye nga nkulu gy'olina okumanya eyitibwa "Double Aortic Arch." Katukyogereko mu bujjuvu leero.

Mu ngeri ennyangu, omusuwa omukulu ogutwala omusaayi okuva ku mutima gw’omwana wo okutuuka mu mubiri gwe gwonna gwe guyitibwa aorta . Ebiseera ebisinga kiba kibya kimu ekinene. Ekitundu ekikoonagana eky'omusuwa guno waggulu w'omutima kiyitibwa aortic arch .

Wabula mu mwana alina "Double Aortic Arch", "aortic arch" eno ekolebwa mu bibiri. Kwe kugamba, omusuwa ogw'omusaayi ogwongezeddwayo guyungibwa ku "aortic arch" eno enkulu, ne gukola arch eyokubiri. Ebisenge bino ebibiri bikwatagana, ne bikola empeta okwetooloola omudumu gw’empewo (trachea) n’omudumu gw’emmere (esophagus) gw’omwana . Teebereza, kiki ekibaawo singa empeta eno ezibikira? Wano omwana w’atandika okufuna obubonero obw’amaanyi ng’okukaluubirirwa okussa, okukola amaloboozi ng’assa, n’okukaluubirirwa okumira emmere.

"Aortic arch" eno ekolebwa mu mitendera egy'olubuto egy'olubereberye ennyo, wakati wa wiiki bbiri n'omusanvu. Mu kiseera kino, omutima n’emisuwa bikula mu ngeri enzibu ennyo. Ebitundu ebimu bitondebwa, era oluvannyuma lw’akaseera tebikyakyetaagisa ne bibula. "Double aortic arch" ekolebwa olw'ekintu nga kino. Nga wiiki ey'okutaano ey'olubuto, omusuwa ogwalina okubula, olw'ensonga ezitamanyiddwa, tegubula era "double aortic arch" eno ekolebwa. Kino kizibu ky’omutima ekizaalibwa , ekitegeeza nti omwana azaalibwa nabwo.

Embeera eno eyitibwa "double aortic arch," eri mu kibinja ky'obulema bw'omutima obuzaalibwa nabwo obuyitibwa "vascular rings." Bino bireetera omwana omudumu gw’empewo n’omumwa gwa nnabaana okunyigirizibwa.

"Empeta z'emisuwa" zino ze ziruwa?

Okay, "Vascular Rings", nga bwe nnagambye emabegako, embeera "aortic arch" gy'ekula mu ngeri etaali ya bulijjo, ekiyinza okuvaako empewo y'omwana (trachea), payipu y'emmere (esophagus), oba byombi okunyigirizibwa. Bino biba bizibu bya mutima ebizaalibwa nabyo ebitatera kulabika . Lowooza ku kino, abaana nga omu ku buli 100 azaalibwa n’ekika ky’obulema bw’omutima obuzaalibwa nabwo. Naye "empeta y'emisuwa" ekosa abalongo omu yekka ku buli 10,000. Kiba kya bbula bwe kityo.

Bika ki ebikulu ebya "Vascular Rings"?

Waliwo ebika ebikulu ebiwerako ebya "empeta z'emisuwa" zino. Ka tulabe kye bali:

• Double Aortic Arch: Mu kino, "aortic arches" bbiri (kkono ne ddyo) zeetoolodde omukka n'omumwa gwa nnabaana. Guno gwe mulamwa omukulu gwe twogerako.
• Right aortic arch with aberrant left subclavian artery and left ligamentum: Wano waliwo ekisenge ky’omusuwa gumu, naye kiri ku ludda olwa ddyo olw’omusuwa gw’omukka (mu budde obutuufu ku kkono). Mu mbeera eno, omusuwa gwa kkono ogwa subclavian ogugabira omusaayi mu mikono gy’omwana, gutandikira ku aorta ne guyita emabega w’omusuwa gw’omukka n’omumwa gwa nnabaana. Empeta eno ey’emisuwa emalirizibwa nga yeegatta ku ligamentum arteriosus eya kkono, ekisigalira ky’omusuwa gw’omusaayi ogwaliwo mu bulamu bw’omwana ali mu lubuto ate ne gubula.
• Left aortic arch with aberrant right subclavian artery: Wano, omusuwa ogwa ddyo ogwa subclavian guyita emabega w’omukka n’omumwa gwa nnabaana, ne gubinyiga.
• Innominate artery compression: Omusuwa ogutaliiko (brachiocephalic) ttabi lya aorta. Mu mbeera eno, kitandikira ku ludda olwa kkono olw’omukka, oluvannyuma n’eyita mu maaso g’omukka okudda ku ddyo. Kino kiteeka puleesa ku nnyindo.
• Pulmonary artery sling: Omusuwa gw’amawuggwe ogwa kkono gutandikira ku musuwa gw’amawuggwe ogwa ddyo ne guyita wakati w’omukka n’omumwa gwa nnabaana.

Ekibaawo mu bino byonna, omukutu gw’empewo oba omusulo gukosebwa mu ngeri emu oba endala.

Waliwo ebika bya "Double Aortic Arch"?

Yee, waliwo ebika bisatu ebikulu ebya "double aortic arch." Bino byawulwamu ekisenge ki ekinene, n’okumanya oba ekikondo ekyo ekinene kiri ku ludda olwa ddyo oba olwa kkono olw’omukka.

• Dominant right arch with a small left arch: Kino kye kika ekisinga okumanyibwa, kibeerawo mu bitundu nga 80 ku buli 100.
• Dominant left arch with a small right arch: Kino kirabibwa mu mbeera nga 10 ku buli 100.
• Balanced arches: Kino nakyo kirabibwa mu mbeera nga 10 ku buli 100.

Kika ki ekya "vascular ring" ekisinga okulabibwa?

Abasawo baali balowooza nti "double aortic arch" kye kika kya "vascular ring" ekisinga okukozesebwa. Naye okunoonyereza okupya kuzudde nti "right aortic arch" mu butuufu esinga kubeerawo.

Naye waliwo ekirala. Abalongo abalina "right aortic arch" batera okuba n'obulema obulala obw'omutima obuzaalibwa okusinga abalongo abalina "double aortic arch." Kyokka, tebatera kuzuulibwa nga bazaalibwa. Kino kiri bwe kityo kubanga "right aortic arch" eyinza obutaleeta bubonero mu biseera ebisooka. Kale, okulongoosa ekizibu kino kiyinza okwetaagisa wakati w’emyezi 6 ne 18 egy’obukulu.

Embeera eyitibwa ``Double Aortic Arch'' kye kika ky'empeta y'emisuwa ekisinga okubeerawo . N’olwekyo, omusawo w’omwana wo asobola okuzuula ekizibu kino nga bukyali. Bw'ogeraageranya n'abalongo abalina ebika ebirala eby'empeta z'emisuwa, abalongo abalina ``Double Aortic Arch'' bayinza okwetaaga okulongoosebwa nga wayiseewo akaseera katono nga bamaze okuzaalibwa.

Bubonero ki obulaga nti alina "Double Aortic Arch"?

Obubonero bwa "double aortic arch" butera okubaawo ng'omudumu gw'empewo, omusuwa gw'omwana oba byombi binyigiriziddwa. Okunyigirizibwa kuno kuyinza okukosa okussa kw’omwana, okuliisa kw’omwana oba enkola y’omutima.

Ebiseera ebisinga, obubonero buno bulabika mu baana abato (naddala singa embeera eno ya maanyi), naye oluusi busobola okulabika nga wa myaka esatu, oba ne mu myaka gy’obutiini.

Abaana abamu bayinza okuzuulibwa obubi nti balina asima kubanga obubonero bufaanagana. Embeera eno ezuulibwa ng’obujjanjabi bwa asima bulemereddwa era n’okwongera okukeberebwa.

Obubonero bw’okussa

Abalongo n'abaana nga 91 ku buli 100 abalina "double aortic arch" bafuna obubonero buno obukwata ku kussa. Bbo bali:

• Eddoboozi eryewuunyisa nga ossa (eddoboozi ery’amaanyi eriyitibwa `stridor` oba eddoboozi ery’okuwunya eriyitibwa `wheezing`) .
• Okusesema okuwulikika nga "seal barking." Kino kifaananako n'okusesema okubaawo mu mbeera eyitibwa "croup."
• Obulwadde bw'endwadde z'omu bitundu by'omubiri ebya wansi enfunda eziwera .

Obubonero bw’omu lubuto n’ekyenda

Abalongo n'abaana nga 40 ku buli 100 abalina "double aortic arch" bafuna obubonero buno obw'okugaaya emmere. Mulimu:

• Okuziyira ng’oyonsa oba ng’oliisa.
• Okukaluubirirwa okumira (dysphagia) . Kino kitera okweyoleka ng’omwana atandise okulya emmere enkalu.
• Obuzibu mu kugejja .
• Emmere edda waggulu mu mumiro (`Regurgitation/reflux`) .

Obubonero bw’omutima

Abalongo n'abaana nga 30 ku buli 100 abalina "double aortic arch" bafuna obubonero obukwatagana n'omutima. Mu bino mulimu:

• Obulumi mu kifuba .
• Eddoboozi ly’omutima eritali lya bulijjo (`Heart murmur`) .
• Olususu lwa bbululu (cyanosis) .

Kiki ekivaako "Double Aortic Arch"?

Ekituufu ekivaako "double otic arch" tekinnazuulibwa . Wadde embeera eno etera okulabibwa mu baana abafumbirwa nga bayita mu "in-vitro fertilization" (IVF) , ekituufu ekivaako tekimanyiddwa.

Double aortic arch nayo esobola okukwatagana n’embeera endala ez’obujjanjabi. Abaana nga 12 ku buli 100 abalina ekizibu ky’omusuwa omubiri (double aortic arch) balina obuzibu obulala obw’omutima obuzaalibwa nabwo, gamba nga ventricular septal defect (VSD) ne tetralogy of Fallot . Okugatta ku ekyo, abaana nga 20 ku buli 100 abalina double aortic arch balina embeera z’obuzaale nga chromosome 22q11 deletion ne trisomy 21 (Down syndrome) .

Otegeera otya "Double Aortic Arch"?

Double aortic arch ezuulibwa mu butanwa oba ng’obubonero butandise. Oluusi, kizuulibwa mu butanwa ng’oli lubuto, oluvannyuma lw’okuzaala, oba mu kukebera ebifaananyi okukolebwa olw’ensonga endala. Okuva mu 2004, omuwendo gw’abantu abazuulibwa n’embeera eno nga bayita mu sikaani nga bali embuto gweyongedde. Kino kya mugaso nnyo, kuba obujjanjabi busobola okutegekebwa amangu ddala ng’omwana amaze okuzaalibwa.

Oba, kiyinza okuzuulibwa ng’obubonero bulabika ng’omwana amaze okuzaalibwa. Omusawo w’omwana wo ajja kwogera naawe ku bubonero n’oluvannyuma akole okukebera.

Okukebera okuzuula "Double Aortic Arch".

Ebikulu ebikozesebwa okuzuula embeera eno bye bino:

• X-ray y’ekifuba: Kino kitera okukeberebwa okusooka .
• Okukebera CT.
• Echocardiogram (Echo) test: Kino kisinga okuyamba okuzuula oba waliwo obulema obulala ku mutima.
• Okukebera MRI (MRI).

Oluusi omwana ayinza okukolebwa okukebera empewo y’omwana. Kino kiyinza okukolebwa mu kwanukula obuzibu mu kussa nga tebannazuulibwa nti alina double aortic arch. Oba, kiyinza okukolebwa nga tebannalongoosebwa okuyamba omusawo alongoosa okufuna endowooza ennungi ku bigenda mu maaso.

Okukebera obuzaale kuyamba okuzuula embeera z’obuzaale.

Owonya otya "Double Aortic Arch"?

Okulongoosebwa kwetaagisa okutereeza embeera ya "double aortic arch." Ne ku balongo abatalina bubonero, okulongoosa kusinga kukolebwa wakati w’emyezi 6 ne 9. Abalongo abalina obubonero naddala singa obubonero buba bwa maanyi, bayinza okwetaaga okulongoosebwa nga bukyali.

Just think, embeera "double aortic arch" yasooka okuzuulibwa mu 1737. Okulongoosebwa okwasooka ku yayo kwakolebwa mu 1947. Okuva olwo tutuuse wala nnyo! Abalongo abalina obuzibu buno mu kuzaalibwa basobodde okuwangaala obulamu obuwanvu era nga balamu olw’obujjanjabi obw’okulongoosebwa.

Okulongoosa "Double Aortic Arch".

Okulongoosa "Double Aortic Arch" tekulina bulabe nnyo, era ebivaamu biba bya buwanguzi nnyo . Omwana wo tajja kwetaaga kuyungibwa ku "cardiopulmonary bypass" (ekyuma ky'omutima-amawuggwe) .

Okulongoosa kuno kukolebwa nga bakozesa enkola eyitibwa "lateral thoracotomy." Kino kitegeeza nti omusawo alongoosa asala ku ludda olumu olw’ekifuba ky’omwana, wakati w’embavu bbiri. Kino kitera okukolebwa ku ludda olwa kkono, kubanga awo abalongo abasinga we babeera n'akawoowo ako akatono aka "extra" aka rib cage. Okukebera ebifaananyi okukolebwa nga tannalongoosebwa kisobozesa omusawo alongoosa okulaba obulungi munda mu mubiri gw’omwana n’okuteekateeka okulongoosebwa okusinziira ku ekyo.

Omusawo alongoosa akozesa enkola ya "ligating and dividing" . Kino kitegeeza nti akasenge akatono kasibibwa okuyimiriza omusaayi okuyita mu kyo. Oluvannyuma bagisala ne bagitunga. Enkola eno eddibwamu okutuusa ng’ekisenge kyawuddwamu ddala era nga puleesa ku payipu y’empewo n’omumwa gwa nnabaana eweddewo.

Omwana wo ajja kumala wiiki nga emu mu ddwaaliro, olwo awonye akomewo awaka.

Obujjanjabi bw'obulwadde bwa "Kommerell diverticulum" (`Kommerell diverticulum - KD`) .

Tekitera kubaawo, abalongo abamu abalina "double aortic arch" nabo bayinza okuba n'ekintu ekiyitibwa "Kommerell diverticulum (KD)." Kino kisinga kubeera mu baana abalina "right aortic arch," naye era tekitera kubaawo nnyo nga balina "double aortic arch."

`KD` eno ye `aneurysm`, omusuwa ogukula mu `aorta` ekka okumpi ne `aortic arch`. Okubumbulukuka kuno kuyinza okutwala ekifo n’okunyiga ku payipu y’empewo n’emmere y’omwana. Kiyinza obutaleeta buzibu bwonna obw’amangu. Wabula abasawo abalongoosa baagala nnyo okuggyawo kino nakyo nga bakola `double aortic arch` okuziyiza obuzibu oluvannyuma.

Okujjanjaba obulema bw’omutima obulala

Omwana wo bw’aba n’obulema obulala obw’omutima obwetaagisa okulongoosebwa, buyinza okujjanjabibwa mu kiseera kye kimu n’omusuwa ogw’emirundi ebiri. Kino kiyinza okwetaagisa enkola eyitibwa ``median sternotomy'' , nga eno erimu okusala wansi wakati mu kifuba. Omusawo alongoosa omwana wo ajja kukuteesa ku ngeri esinga obulungi gy’oli, okusinziira ku nsonga ezeetaaga okujjanjabibwa.

Bizibu ki ebiyinza okuva mu kulongoosebwa?

Obulabe bw'ebizibu okuva mu kulongoosa omusuwa ogw'emirundi ebiri butono nnyo . Tekitera kubaawo, omwana ayinza okufuna obuzibu mu kuliisa oba okussa obutasalako. Singa wabaawo obuzibu bwonna obw’okussa obutasalako, butera okuggwaawo mu mwaka gumu nga bamaze okulongoosebwa.

Ebizibu ebiva mu kulongoosa okutereeza double aortic arch n’obulema obulala ku mutima bisobola okwawukana. Teesa ku bulabe n’ebizibu bino byonna n’omusawo alongoosa omwana wo.

"Double Aortic Arch" esobola okuziyizibwa?

Nedda, embeera eyitibwa "double aortic arch" tesobola kuziyizibwa . Kintu ekikula nga bukyali ng’olubuto era nga kibeerawo ng’azaalibwa.

Ebiseera by'omu maaso eby'abantu abalina "Double Aortic Arch" bye biruwa?

Abalongo n'abaana abalongooseddwa "Double Aortic Arch" balina ebiseera eby'omu maaso ebirungi ennyo . Basobola okubeera n’okukola emirimu egya bulijjo awatali kuziyizibwa kwonna.

Oluvannyuma lw’okulongoosebwa, omwana wo ayinza okusigala ng’assa amaloboozi okumala omwaka mulamba. Kino kiri bwe kityo kubanga omudumu gw'empewo gw'omwana tegukula mu bujjuvu olw'ekisenge kya "double aortic arch." Kale, kijja kutwala ekiseera omudumu gw’empewo okufuuka ogw’amaanyi.

Tekitera nnyo, abalongo n’abaana bayinza okuba nga bakyalina obubonero bw’okussa oluvannyuma lw’omwaka ogusukka mu gumu nga balongooseddwa.

Ekisinga obukulu kwe kutwala omwana wo okwekebejjebwa buli kiseera n’obuulira omusawo wo bw’oba ​​olina obubonero bwonna obugenda mu maaso. Okulabirira okugoberera okumala ebbanga eddene kikulu nnyo eri buli mwana eyalongoosebwa omutima.

Ddi lwe nnina okuyita omusawo w’omwana wange?

Bw’olaba obubonero obupya, oba ng’obubonero obuliwo bulabika bweyongera, yogerako n’omusawo w’omwana wo amangu ago. Abalongo n’abaana abato bakyuka nnyo ne kiba nti oluusi kiyinza okuba ekizibu okumanya ekitali kya bulijjo n’ekitali kya bulijjo. Naye omwana wo bw'aba alina okusesema okwo "okulinga envumbo" oba eddoboozi ery'okuwunya , buulira omusawo wo amangu ago. Kiyinza okuba obulwadde obwa bulijjo obw’obuto. Naye si bulijjo, kiyinza okuba akabonero k’ekizibu ky’omutima ekikosa obusobozi bw’omwana wo okussa.

Ddi lw’osaanidde okukuba ku 911 (ennamba ey’amangu)?

"Double aortic arch" esobola okuteeka puleesa ey'obulabe eri obulamu bw'omwana wo ku payipu y'empewo. Singa olususu lw’omwana wo lulabika nga lwa bbululu (cyanosis) , oba omwana wo bw’aba alina obuzibu obw’amaanyi mu kussa , kuba 911 mu bwangu.

Bibuuzo ki bye nnina okubuuza omusawo w’omwana wange?

Singa omwana wo azuulibwa nti alina "double aortic arch," kya bulijjo ggwe okuba n'ebibuuzo bingi. Kikulu okumanya embeera y’omwana wo omuli ddi lwe yeetaaga okulongoosebwa, n’okumanya oba omwana wo alina obuzibu obulala mu bulamu. Oyinza okwagala okubuuza ebibuuzo nga:

• Omwana wange alina okulongoosebwa ddi?
• Okulongoosa kukolebwa wa? Ani agikola?
• Bubonero ki bwe nnina okwegendereza awaka?
• Kiki kye nnyinza okukola okusobola okwanguyiza omwana wange okusigala awaka?
• Omwana wange alina obuzibu obulala ku mutima?
• Nteekwa okukeberebwa obuzaale bw’omwana wange oba ab’omu maka gange abalala?
• Ebiseera by’omwana wange eby’omu maaso binaaba bitya?

"Obulwadde bwa Aortic Arch Syndrome" kye ki? Kyawukana ku "Double Aortic Arch"?

Yee, tobuzaabuza byombi. "Aortic Arch Syndrome" kika kya "Vasculitis" ekitali kya bulijjo nnyo . Era kimanyiddwa nga "Takayasu's arteritis" .

"Vasculitis" kwe kuzimba ebisenge by'emisuwa gyo. Kiyinza okubeera mu misuwa gyonna, ne mu misuwa emitono ennyo, emisuwa eminene. "Takayasu's arteritis" buzimba bwa misuwa egy'obunene obwa wakati n'obunene. Kisinga kubeera mu "aortic arch" n'amatabi gaayo amanene. Eno y'ensonga lwaki era kiyitibwa "aortic arch syndrome."

Obulwadde bw'emisuwa bwa Takayasu (era obumanyiddwa nga "aortic arch syndrome") bubaawo mu bavubuka abakulu n'abavubuka abakulu . Kino kizibu kya njawulo ddala okusinga ku "double aortic arch" ey'obuzaale gye twayogeddeko emabegako, era obujjanjabi obwetaagisa bwa njawulo.

Okuzaala omwana ebiseera ebisinga kiba kiseera kya ssanyu n’okujaguza. Kyokka bw’okizuula nti omwana wo alina obulwadde bw’omutima, oba ng’ali lubuto oba ng’amaze okuzaalibwa, essanyu eryo lidda mu kifo ky’okweraliikirira n’obutali bukakafu. Bw'oba waakakizuula nti omwana wo alina "double aortic arch," osanga weebuuza ekiddako.

Tofaayo. Ttiimu yo ey’abasawo ejja kukuyamba okuyita mu bino byonna mutendera ku mutendera. Omutendera ogusooka wagukwata dda, kwe kumanya ebisingawo ku mbeera y’omwana wo. Amawulire amalungi gali nti okulongoosa double aortic arch tekulina bulabe nnyo era kugenda bulungi. Singa omwana wo aba n’obulema obulala ku mutima oba embeera z’obuzaale, obujjanjabi buyinza okukaluba katono. Kyokka, olw’enkulaakulana mu kulabirira abaana abaakazaalibwa, osobola okuyamba omwana wo okufuna okulabirira okutuufu kwe yeetaaga, okudda engulu, n’okubeera n’obuto obw’essanyu.

Kale, bintu ki ebikulu bye tulina okujjukira okuva mu bye twogeddeko? (Obubaka Obutwala Awaka)

Okay, ka tufunze ebimu ku bintu by'olina okukuuma mu birowoozo okuva ku bye twogeddeko ku bikwata ku "Double Aortic Arch" eno:

• "Double aortic arch" bulwadde bwa mutima obuzaalibwa nabwo . Omusuwa gw’omwana gwawulwamu ebitundu bibiri ebiyitibwa arches, ekivaako okunyigirizibwa kw’omusuwa gw’omukka n’omumwa gwa nnabaana.
• Obubonero obukulu bwe buzibu okussa, okuwunya, okukaluubirirwa okumira, n’okukwatibwa endwadde enfunda eziwera mu kussa .
• Embeera eno ezuulibwa nga bayita mu kukeberebwa nga `CT scan`, `MRI`, `Echocardiogram` . Oluusi osobola n’okuzuulibwa ng’oli lubuto.
• Obujjanjabi buno kwe kulongoosa . Okulongoosa kuno tekulina bulabe nnyo era kukola bulungi.
• Ku mwana oluvannyuma lw’okulongoosebwaOsobola okubeera n’obulamu obwa bulijjo era obulungi.
• Omwana wo bw’aba alina obubonero ng’okukaluubirirwa okussa oba okuziyira, genda mangu omusawo amagezi .
• Tofaayo . Olw’okukulaakulana kw’eddagala ery’omulembe, embeera eno esobola okujjanjabibwa obulungi. Ttiimu yo ey’abasawo ejja kukuwa obuyambi bwe weetaaga.

` Double Aortic Arch, Obulwadde bw’omutima obuzaalibwa, Empeta z’emisuwa, Okusannyalala kw’abaana abawere, Obulamu bw’abaana abawere, Okulongoosa omutima