Omwana wo afuna ebizimba ebitali bya bulijjo ku mubiri gwe? Kino kiyinza okuba akabonero ka Complex Lymphatic Anomalies (CLA)!

Oluusi tutya nnyo bwe tulaba enkyukakyuka entonotono mu mibiri gy’abaana baffe, si bwe kiri? Naddala nga tetumanyi bulungi bintu ebyo kye biruwa. Leero tugenda kwogera ku mbeera etali ya bulijjo naye nga nkulu nnyo gye tulina okumanya. Kino kiyitibwa Complex Lymphatic Anomalies , oba (CLA) mu bufunze. Abantu abamu era nga bakiyita (Lymphangiomatosis) emabegako. Kale oyinza okuwulira amannya gano gombi.

Okusooka, ka tulabe, Complex Lymphatic Anomalies (CLA) kye ki?

Mu ngeri ennyangu, Complex Lymphatic Anomalies (CLA) mbeera etali ya bulijjo naye nga eyinza okuzaalibwa omwana mw’afuna ebizimba ebitali bya bulabe ebiyitibwa lymphatic malformations oba lymphangiomas mu nkola y’amazzi g’omwana. Ebizimba bino bisobola okukula ne biyingira mu magumba g’omwana, ebitundu ebiyunga n’ebitundu ebirala, ne bivaako okwonooneka.

Lowooza omwana waffe ne bw’aba alina embeera eno ng’azaalibwa, ebiseera ebisinga obubonero butandika okulabika ng’akuze katono, mpozzi nga wayise emyaka mitono. Y’ensonga lwaki oluusi kikeeredde okutegeera kino.

Kale, Enkola eno ey’Ensimbi (Lymphatic System) kye ki?

Okay, kati osanga weebuuza enkola y’amazzi (lymphatic system) kye ki. Mu ngeri ennyangu, nkola ya kwekuuma eyeewuunyisa mu mubiri gwaffe. Kiringa abajaasi mu nsi yaffe. Enkola eno ey’amazzi (lymphatic system) eyamba omubiri gwaffe okutangira endwadde n’okuzirwanako singa zibeera. Kitundu kikulu nnyo mu baserikale b’omubiri gwaffe.

Enkola y’amazzi (lymphatic system) ekolebwa omukutu gw’obutuli obutonotono obuyitibwa emisuwa gy’amazzi, endwadde ng’ennywanto, n’ebitundu ng’ennywanto. Emisuwa gino egy’amazzi (lymphatic vessels) giringa obutuli obutono. Bakung’aanya amazzi g’omusaayi okuva mu bitundu by’omubiri, ne bagasengejja, ne bagayonja, oluvannyuma ne bagazza mu musaayi. Guno si mulimu gwa kyewuunyo?

Waliwo ebika bya CLA bibiri: Isolated ne Systemic.

Complex Lymphatic Anomalies zisobola okwawulwamu ebika bibiri ebikulu:

1. Isolated CLAs: Kino bwe kiba nga ebizimba bisibiddwa mu kitundu kimu eky’omubiri gw’omwana. Okugeza, ziyinza okukosa ekifuba kyokka. Mu mbeera eno, amawuggwe n’ebitundu ebigonvu eby’ekifuba (mediastinum) bye bisinga okukosebwa.

2. Systemic CLAs: Mu mbeera eno, ebizimba bino bisobola okubeera mu bifo ebingi ku mubiri gw’omwana, gamba ng’amagumba, ekifuba n’olubuto.

Mu ngeri eno, obubonero n’obujjanjabi biyinza okwawukana okusinziira ku kitundu ekikoseddwa.

Bika ki ebikulu eby’obulwadde bwa Complex Lymphatic Anomalies (CLA)?

Waliwo ebika bya CLA ebikulu bina. Wadde nga buli kika kirina obubonero obumu, mbeera za njawulo. Era enkyukakyuka mu buzaale ezizireeta nazo za njawulo.

• Obuzibu bw’amazzi mu bitundu by’omubiri (GLA):Embeera eno etera okukwata ebitundu by’omubiri gw’omwana eby’enjawulo. Okugeza ebizimba bino bisobola okubeera mu magumba, enseke, ekibumba, amawuggwe, n’ebitundu ebigonvu eby’ekifuba (mediastinum).
• Obulwadde bwa Kaposiform Lymphangiomatosis (KLA): Kino kye kika kya CLA ekisinga okuba eky’amaanyi era ekisaasaana amangu. Mu KLA, emisuwa gy’amazzi agatambuza amazzi g’amazzi mu mubiri gw’omwana gwonna gigaziwa. Kino kizireetera okulumba n’okwonoona ebitundu by’omubiri, amagumba n’ebitundu ebizibeetoolodde.
• Central Conduction Lymphatic Anomaly (CCLA): Abaana abalina CCLA nabo balina emisuwa gy’amazzi egyagazi. Wabula mu CCLA, emisuwa gino egyagaziye gisinga kubeera mu mubiri. Kino kiyinza okukosa enkola y’okugaaya emmere n’okulemesa omwana okufulumya obulungi amazzi g’omusaayi mu mubiri.
• Obulwadde bwa Gorham-Stout (GSD): Era obumanyiddwa nga Gorham’s disease, embeera eno ereetera amagumba amangi okusaanuuka olw’okutondebwa kw’emisuwa gy’amazzi mu magumba. Era kiyitibwa "obulwadde bw'amagumba obubula." Kiyinza okukosa eggumba lyonna. Wabula abaana abalina GSD batera okufiirwa amagumba mu mbavu, ekiwanga, eggumba ly’omu bulago, n’omugongo gw’omumwa gwa nnabaana.

Embeera eno eya CLA etera etya?

Complex Lymphatic Anomalies mu butuufu mbeera etali ya bulijjo nnyo . Olw’okuba tezitera nnyo, oluusi kiyinza okuba ekizibu abasawo okuzizuula obulungi. N’olwekyo, bw’oba ​​olina obubonero, kikulu nnyo okugenda ew’omusawo omukugu mu bwangu.

Kiki ekivaako CLA eno?

Abasawo n’abanoonyereza bakyagezaako okuzuula ekivaako CLA. Wabula okunoonyereza okwakakolebwa kulaga nti embeera eno eyinza okuva ku nkyukakyuka z’obuzaale ez’obuzaale ezisiigibwa okuva mu bazadde okutuuka ku baana, awamu n’enkyukakyuka mu buzaale bw’omubiri ezibaawo oluvannyuma lw’okuzaalibwa. Kino kitegeeza nti kikwatagana n’obuzaale.

Ani ali mu bulabe bw’okulwala CLA?

Complex Lymphatic Anomalies zisobola okukwata omuntu yenna. Okusingira ddala, obubonero bw’embeera eno butera okulabika mu buto oba mu myaka gy’obuvubuka. Kale, embeera eno ne bw’ebaawo ng’azaalibwa, kiyinza okutwala ekiseera obubonero okulabika.

Kale, bubonero ki obwa CLA?

Obubonero buyinza okwawukana okusinziira ku mwana alina obulwadde buno. Ate era, obubonero bwawukana okusinziira ku nkola y’ebitundu by’omubiri ekoseddwa n’engeri gyeri ey’amaanyi. Ebiseera ebisinga, obulwadde buno bugenda bugenda mpola. N’olwekyo, tuyinza obutafaayo nnyo ku bumu ku bubonero obwo, oba tuyinza okulowooza nti buva ku bulwadde obulala.

Singa enkola y’okussa kw’omwana wo ekosebwa:

Mu kiseera kino, obubonero obulinga obwa asima buyinza okulabika.

• Okusesema okutambula obutasalako.
• Obuzibu mu kussa (dyspnea).
• Okuwunya ( eddoboozi ery’okufuuwa ) ng’ossa.

Singa amagumba g’omwana wo akosebwa:

• Obulumi mu magumba oba mu binywa.
• Ne bw'ogwa akatono kuyinza okuvaako okumenya .
• Okuzirika mu bitundu by’omubiri.
• Obulumi oba obunafu obuva ku kunyigirizibwa kw'obusimu .

Singa enkola y’omwana wo ey’okugaaya emmere ekoseddwa:

• Okugaziwa kw'olubuto n'okulumwa olubuto .
• Okukendeera kw’omusaayi n’okukoowa buli kiseera.
• Embiro.
• Emmere tewooma.
• Okuziyira n’okusiiyibwa.
• Okugejja awatali nsonga.

Singa enkola y’omusulo gw’omwana wo ekosebwa:

• Omusaayi mu musulo (hematuria).
• Obulumi mu mabbali .
• Puleesa mu baana.

Omwana wo bw’aba alina obubonero bumu oba obusingawo ku buno, nsaba onoonye omusawo amagezi. Buno si bubonero obukwata ku CLA, naye kikulu okwekebeza.

Abasawo bazuula batya embeera eno eya CLA?

Olw’okuba CLA mbeera etali ya bulijjo ate ng’obubonero bwayo bwawukana, oluusi kiyinza okuba ekizibu abasawo okuzuula embeera entuufu. Okuva bwe kiri nti kitera okukosa amawuggwe n’amagumba g’abaana, omusawo w’omwana wo ayinza okulagira okukeberebwa nga:

• Bronchoscopy: Okukebera oba waliwo yinfekisoni oba ebirala ebitali bya bulijjo mu mifulejje gy’empewo.
• Okukebera enkola y’amawuggwe: Pima engeri amawuggwe go gye gakola obulungi.
• Whole-body MRI: Okukebera ebintu ng’ebitundu by’omubiri ebikoseddwa, ebiwundu by’amagumba oba amazzi mu lubuto.
• X-rays: Okwongera okwekenneenya amagumba agalabika nga gateeberezebwa oba nga galumiziddwa ku MRI. X-ray z’ekifuba nazo zisobola okunoonya ebitali bya bulijjo mu mawuggwe.

Oluusi abasawo batwala akatundu akatono ak’ennywanto n’ebitundu by’omubiri (biopsy) ne babikebera nga bakozesa microscope. Wadde ng’okukebera kuno kusobola okuzuula ddala CLA, oluusi kuyinza okuleeta ebizibu, gamba ng’okukung’aanya amazzi g’omusaayi okwetoloola amawuggwe (chylothorax). Olw’ensonga eno, abasawo batera okwesigama ku kukeberebwa okutali kwa maanyi okusobola okuzuula obulwadde buno.

CLA ejjanjabwa etya?

Olw’okuba CLA esobola okukosa ebitundu by’omubiri gw’omwana ebiwerako, abasawo bakolera wamu, kwe kugamba, bakozesa enkola ey’enjawulo okuteekateeka obujjanjabi obusaanira omwana. Bw’oba ​​ojjanjaba CLA, essira lisinga kulissa ku kufuga bubonero bw’omwana. Kino okukikola, osobola okukola ebintu nga:

• Okusimba amagumba: Ku kwonooneka kw’amagumba mu mbeera nga GSD.
• Endya erimu ebirungo ebizimba omubiri oba endya mu misuwa (total parenteral nutrition oba TPN).
• Sclerotherapy: Okukendeeza oba okuziyiza ebizimba oba emisuwa gy’amazzi.
• Okulongoosa: Okuggyawo ebizimba oba okuyingiza obupiira obutonotono (shunts) okwanguyiza amazzi g’omusaayi okutambula.
• Obujjanjabi bw’amasannyalaze oba eddagala eriweweeza ku bulwadde: Okukendeeza ku bizimba ebitali bya kookolo (bino bikozesebwa mu mbeera zokka ez’amaanyi ennyo, eziteeka obulamu mu matigga).

Gye buvuddeko, obujjanjabi obugendereddwamu obugenderera enkyukakyuka mu buzaale obuleeta embeera eno nabwo bukozesebwa. Enzijanjaba zino era ziragiddwa okuba ennungi ng’obujjanjabi obw’olunyiriri obusooka ku CLA.

Obulwadde bwa Complex Lymphatic Anomalies (CLA) busobola okuziyizibwa?

Ebyembi, nedda . CLA ebaawo ng’oli lubuto, era ekituufu ekivaako tekimanyiddwa. Kale, tewaaliwo ky’oyinza kukola kulemesa mwana wo kufuna mbeera eno.

Bizibu ki ebiyinza okuva mu CLA?

CLA esobola okuteeka omwana wo mu kabi olw’oku:

• Ascites: Amazzi agakuŋŋaanyizibwa mu lubuto.
• Okumenya amagumba.
• Chylothorax ne Chylopericardium: Okukung’aanya amazzi ag’amata (chyle) agalimu amazzi g’ennywanto n’amasavu mu luwuzi olubikka amawuggwe (pleura) oba ensawo eyeetoolodde omutima (pericardium).
• Amawuggwe agagwa / pneumothorax.
• Ekibumba okulemererwa.
• Okusannyalala.
• Okufulumya amazzi mu mutima.
• Okufulumya amazzi mu nnyindo (pleural effusion) n’okuzimba amawuggwe (cardiogenic pulmonary edema).

Ebimu ku bizibu bino biyinza okuba eby’amaanyi ennyo, n’olwekyo kikulu okumanya obubonero n’okugoberera ebiragiro by’omusawo.

Omuntu alina CLA ebiseera by’omu maaso biruwa?

Tewali ddagala eriwonya obulwadde bwa Complex Lymphatic Anomalies (CLA). Ebiseera by’omwana wo eby’omu maaso bisinziira ku nkola z’omubiri ezikoseddwa n’obubonero bwe buli obw’amaanyi.

Pleural effusions ze zisinga okutta abantu abalina CLA. Kyokka singa omwana ajjanjabibwa bulungi n’okumuddukanya obulungi, asobola okuyambibwa okubeera n’obulamu obwa bulijjo.

Ddi lwe nnina okulaba omusawo?

Omwana wo bw’aba alina obubonero buno, laba omusawo mu bwangu:

• Obulumi mu lubuto oba mu byenda.
• Singa mu musulo mubaamu omusaayi.
• Okusesema obutasalako, okuwunya oba okukaluubirirwa okussa.
• Okuziyira, obukoowu oba okugejja mu ngeri etategeerekeka.

Bw’oba ​​olina ekimu ku bino, nsaba olabe omusawo awatali kulwa.

Kiki kye nsaana okubuuza omusawo?

Oyinza okubuuza omusawo w’omwana wo ebibuuzo nga bino:

• Bitundu ki eby’omubiri gw’omwana wange embeera eno gy’akosezza?
• Bujjanjabi ki obuliwo eri omwana wange?
• Omwana wange yeetaaga okulongoosebwa?
• Nsaanidde okumanya obubonero bw’ebizibu?

Kikulu nnyo okubuuza ebibuuzo bino n’okufuna okutegeera okutegeerekeka ku mbeera.

Nsembayo, nnina okugamba nti...

Bw’okizuula nti omwana wo alina obulwadde bwa CLA (lymphangiomatosis), kya bulijjo okuwulira ng’otya n’okweraliikirira engeri gye kinaakwata ku bulamu bwe n’ebiseera bye eby’omu maaso. Bangi ku ffe tuyinza okuba nga tetuwulirangako ku bulwadde buno. Era tewali kye wandikoze okukiziyiza.

Ekisooka okuyamba omwana wo kwe kumanya obulungi obulwadde buno, obubonero bwabwo, n’obujjanjabi bwabwo. Laba omusawo mukugu mu ndwadde z’ennywanto. Basobola okuddamu ebibuuzo byo ne bakuwa obujjanjabi obw’enjawulo omwana wo bw’aba yeetaaga.

Wadde nga tewali ddagala lya CLA, obujjanjabi obulungi n’okuddukanya obulungi omwana wo bisobola okuyamba omwana wo okubeera n’obulamu obw’essanyu n’obulamu obulungi. N’olwekyo, sigala ng’oli mugumu era okole omwana wo ekisinga obulungi.

` Complex Lymphatic Anomalies, Lymphangiomatosis, Endwadde z’enkola y’amazzi, Ebizimba mu baana, Osteomalacia, Obubonero bw’amawuggwe, Endwadde z’abaana ezitatera kulabika