Ffenna tukimanyi nti omusaayi mu mubiri gwaffe tegulinga mazzi, wabula mazzi agalina obuzito obumu. Naye teebereza, kiki ekibaawo singa omusaayi guno gweyongera nnyo okusinga ogwa bulijjo, ng’ebitoomi ebinene? Kifuuka kizibu omusaayi guno omunene okutambula mu misuwa emirungi mu mubiri gwaffe gwonna. Kiba ng’ebitosi ebinene ebisibira munda mu payipu. Mu ngeri eno, omusaayi gugonza ng’amata ga muwogo, n’okutambula kw’omusaayi mu mubiri ne kukosebwa, kye tuyita Hyperviscosity Syndrome mu ddagala. Kino si kintu kitono, naye oluusi embeera ey’akabi ennyo, eyinza okutta omuntu. Ka twogere ku nsonga eno mu ngeri ennyangu, mu ngeri gy’osobola okutegeera.
Lwaki omusaayi guzitowa mangu?
Ekisooka okutegeera nti Hyperviscosity Syndrome si bulwadde ku bwabwo. Bubonero bw’embeera endala esirifu. Nga okusesema bwe kabonero k’omusujja oba ekifuba. Okugonza kw’omusaayi kusinga kuva ku butaffaali oba puloteyina ez’enjawulo ezisukkiridde mu musaayi.
Mu ngeri ennyangu, singa omuwendo gw’obutoffaali obumyufu, obutoffaali obweru, obutoffaali obukola omusaayi oba obutoffaali obukola omusaayi mu musaayi gweyongera mu ngeri etaali ya bulijjo, omusaayi gugonvuwa.
Omulongooti wansi gulaga ezimu ku mbeera z’obujjanjabi enkulu eziyinza okuvaako embeera eno.
| Embeera eziyinza okuvaako omusaayi okuzimba | Ennyinyonnyola ennyangu |
|---|---|
| Obulwadde bwa Waldenström obw’obulwadde bwa Macroglobulinemia (WB) . | Kino kye kisinga okuvaako omuntu okubeera n’obuzito obusukkiridde. Kino kika kya kookolo w’omusaayi abeera mu busimu bw’amagumba n’ebitundu by’omubiri ebiyitibwa lymphatic tissues. Kiva ku kukola ekirungo kya puloteyina ekitali kya bulijjo ekisusse, ekivaako omusaayi okugonza. |
| Obulwadde bwa Myeloma obuyitibwa Multiple Myeloma | Kino nakyo kika kya kookolo akwata obutoffaali bwa plasma. Puloteeni ezitali za bulijjo ezikolebwa obutoffaali bwa kookolo zireetera omusaayi okugonza. |
| Obulwadde bwa polycythemia Rubra Vera | Buno bulwadde bwa magumba. Mu mbeera eno, obutoffaali obumyufu bukolebwa mu ngeri etafugibwa. Omuwendo gw’obutoffaali obumyufu bwe gweyongera, n’obuzito bw’omusaayi bweyongera nnyo. |
| Obulwadde bwa Leukemia | Mu bulwadde bwa leukemia, kookolo w’omusaayi, wabaawo obutoffaali obweru obuyitiridde. Obutoffaali buno buyinza okuba nga tebulina ngeri ya bulijjo. Kino kiyinza okuvaako emisuwa okuzibikira n’omusaayi okugonza. |
| Obuzibu bw’ebitundu ebikwatagana | Okuzimba omusaayi oluusi kuyinza okubaawo mu ndwadde nga endwadde z’enkizi, naye kino tekitera kubaawo. |
| Ebirala ebitatera kuleetawo | Wayinza okubaawo ebirala ebiwerako ebivaako obulwadde buno, gamba nga cryoglobulinaemia (obulwadde obuleeta okuzimba emisuwa), obutaba na mukka gwa oxygen obutawona (obutaba na oxygen obutawona), n’obujjanjabi obumu obwa kookolo (Retinoic acid therapy). |
Owulira otya ng’omusaayi gwo guzitowa? Obubonero bwe buliwa?
Lowooza ku kino, buli kitundu ky’omubiri mu mubiri gwaffe, okuva ku bwongo okutuuka ku nsonga z’engalo zaffe, kitambuzibwa omusaayi, nga kitambuza omukka gwa oxygen n’ebiriisa. Kale omusaayi guno bwe guzibikira, ebitundu ebyo tebifuna bye byetaaga. Eno y’ensonga lwaki obubonero bulabika. Obubonero buno busobola okwawukana okusinziira ku muntu, era busobola n’okwawukana okusinziira ku bulwadde obw’olubereberye obwaleetera omusaayi okugonza.
Buno bwe bumu ku bubonero obutera okulabika:
Obubonero obukosa obwongo n’obusimu
Obwongo busobola okusinga okukosebwa olw’omusaayi okutambula obubi.
- Omutwe ogw’amaanyi n’okuziyira
- Obuzibu mu kulaba: okulaba okuzibu, okulaba emirundi ebiri, oluusi okubulwa okulaba okw’amangu
- Obuzibu mu kuwulira: okukendeera oba okubulwa okuwulira
- Okukonziba
- Okukoowa ennyo n’otulo (Lethargy) .
Obubonero obukwatagana n’okuvaamu omusaayi
Omusaayi bwe gugonvuwa, okufuga okulungi okutambula kw’omusaayi kutaataaganyizibwa, ekiyinza okuvaako omusaayi okuvaamu omusaayi mu ngeri etasuubirwa.
- Okunyiga ebiwundu ebyangu
- Okuvaamu omusaayi mu bitundu by’omubiri (mucosal bleeding), ennyindo) .
- Okuvaamu omusaayi okulala okutali kwa bulijjo (e.g., omusaayi mu musulo) .
Obubonero obulala obw’amaanyi
Bino biraga nti ebitundu by’omubiri ebikulu byonooneddwa.
- Puleesa (Peesa) .
- Omutima okulemererwa: okulumwa mu kifuba, okussa obubi
- Okulemererwa kw’ekibumba
- Okuzimba omusaayi (Thrombosis) .
- Obulwadde obw’amaanyi (Sepsis) .
Bw’oba ggwe oba omuntu gw’omanyi alina obubonero buno obumu oba obusingawo, kikulu nnyo okulaba omusawo amangu ddala awatali kulwa.
Embeera eno ey’akabi ogijjanjaba otya?
Obulwadde bwa Hyperviscosity Syndrome bwa mangu mu by’obujjanjabi kubanga singa tebujjanjabwa, busobola okufa enjala y’ebitundu ebikulu ng’obwongo, omutima n’ensigo olw’omukka gwa oxygen, ekivaako okwonooneka okw’olubeerera oba n’okulemererwa. N’olwekyo, kyetaagisa nnyo okufuna obujjanjabi obw’amangu.
Enteekateeka y’obujjanjabi etera okubaamu emitendera ebiri.
1. Obujjanjabi obw’amangu, obw’ekiseera ekitono
Ekisooka kwe kufuga obubonero n’okukendeeza amangu ku buzito bw’omusaayi. Emu ku ddagala erisinga okukozesebwa ku kino ye Plasmapheresis .
Plasmapheresis nkola efaananako n’okulongoosa omusaayi. Omusaayi gwo omutono guggyibwa mu mubiri gwo, ne guyisibwa mu kyuma eky’enjawulo, era plasma erimu obutoffaali obw’enjawulo obuleetera omusaayi gwo okuzimba, n’eyawulwamu n’eggyibwamu. Olwo obutoffaali obumyufu n’omweru obulamu butabulwamu amazzi agadda mu kifo kyabyo ne budda mu mubiri gwo.
Kino kiyinza okukendeeza amangu omusaayi okuzimba n’okukomya okwonooneka kw’ebitundu by’omubiri. Wabula kiri eri ttiimu yo ey’abasawo okusalawo oba obujjanjabi buno butuufu eri buli muntu era oba bwetaagisa.
2. Obujjanjabi obw’ekiseera ekiwanvu (okujjanjaba obulwadde obusirikitu) .
Oluvannyuma lw’okukendeeza ku buzito bw’omusaayi, ekiddako ekisinga obukulu kwe kujjanjaba obulwadde obwasooka obwali buguleeta . Kubanga obulwadde obwo bwe butajjanjabwa, omusaayi guyinza okuddamu okugonza.
- Singa ekivaako kookolo nga Multiple Myeloma oba Leukemia , obujjanjabi obulwanyisa kookolo nga chemotherapy buweebwa.
- Singa ekivaako kibeera kya polycythaemia , obujjanjabi buweebwa okuggyawo obutoffaali obumyufu obw’enjawulo oba okukendeeza ku buvaamu.
- Bwe kiba embeera endala ey’obujjanjabi, abasawo bajja kuteesa ku bujjanjabi obw’enjawulo obw’okubujjanjaba.
Ku kino, ttiimu y’abasawo omuli abakugu mu by’omusaayi, kkansa n’abasawo b’ekibumba bajja kwegatta okukukola enteekateeka y’obujjanjabi esinga obulungi gy’oli.
Obubaka Obutwala Awaka
- Hyperviscosity Syndrome mbeera omusaayi mwe gufuuka omugonvu ng’amafuta ga muwogo, ne guziyiza omusaayi okutambula mu mubiri.
- Buno si bulwadde bwa njawulo. Bubonero bw’embeera endala ey’amaanyi, gamba nga kookolo w’omusaayi.
- Tobuusa maaso bubonero ng’okulumwa ennyo omutwe, okukyuka mu kulaba, okuvaamu omusaayi mu ngeri etaali ya bulijjo oba okukoowa ennyo.
- Eno mbeera ya mangu ey'obujjanjabi . Laba omusawo amangu ddala ng’olaba obubonero. Bwe kiba kyetaagisa, genda mu ddwaaliro mu kitongole ekijjanjaba abalwadde ab’amangu (ETU) mu bwangu.
- Obujjanjabi buzingiramu okugonza omusaayi amangu (nga plasmapheresis) n’okujjanjaba obulwadde obusirikitu.











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