Ekifo ekya kitaka ku mubiri gwo kifuuka kimyufu n’okusiiwa ng’okisiiga? Kino kiyinza okuba nga kya Urticaria Pigmentosa!

Wali olabye ku mubiri gw’omwana wo oba ogwa kitaka ekimyufu? Mpozzi wamala kusikasika mpola ekifo ekyo n’olugalo, era amangu ago ekifo ekyo ne kifuuka ekimyufu, ne kitandika okusiiwa, waggulu ne walabika akazimba akatono. Bw’oba ​​nga kino kikumanyidde, kikulu nnyo okumanya embeera gye twogerako leero.

Mu ngeri ennyangu, Urticaria Pigmentosa kye ki?

Urticaria Pigmentosa kika kya bikuta ebibeera ku lususu. Businga kulabibwa mu baana abato n’abato abakulu. Mu butuufu ngeri ya mbeera eyitibwa `mastocytosis'.

Kati oyinza okuba nga weebuuza `mastocytosis` kye ki. Kyangu nnyo. ``mast cells`` kika kya butoffaali kya njawulo mu baserikale b'omubiri gwaffe. Balinga abakuumi b'omulambo. Olw’ensonga ezimu obutoffaali buno obuyitibwa mast cells bwe bukuŋŋaanyizibwa ekisusse mu kitundu kimu eky’olususu, tukiyita Urticaria Pigmentosa. Wabula obutoffaali buno obuyitibwa mast cells tebusobola kukuŋŋaanyizibwa mu lususu lwokka, wabula oluusi mu bitundu ebirala ng’amagumba n’ebyenda. Olwo ne kifuuka embeera eyitibwa ``systemic mastocytosis``. Naye teweeraliikiriranga, ebiseera ebisinga, Urticaria Pigmentosa mu baana ekoma ku lususu.

Lwaki ekintu nga kino kibaawo?

Ensonga enkulu lwaki kino kiri bwe kityo ye ``mast cells`` ze twayogeddeko emabegako. Zino kika kya butoffaali obweru obukolebwa mu busimu bwaffe obw’amagumba. Obutoffaali buno busangibwa mu mibiri gyaffe gyonna naddala gye tukwatagana n’ensi ey’ebweru, gamba ng’olususu, amawuggwe n’ebyenda. Ekintu ng’obuwuka bwe kiyingira mu mubiri, obutoffaali buno obuyitibwa mast cells bufulumya eddagala eriyitibwa ``histamine`` okuyamba okukuuma omubiri.

Urticaria Pigmentosa eva ku nkyukakyuka mu buzaale ereetera obutoffaali buno obuyitibwa mast cells okukuŋŋaanyizibwa ekisusse mu lususu. Enkyukakyuka eno mu buzaale etera okubaawo ng’omwana akyali mu lubuto. Kyokka, si kintu ekisikira abazadde okutuuka ku baana . Ekituufu ekivaako enkyukakyuka eno tekinnazuulibwa.

Singa abantu abakulu bafuna embeera eno, eyinza okuba ey’amaanyi katono. Kiyitibwa `indolent systemic mastocytosis`. Mu mbeera eno, obutoffaali obuyitibwa mast cells bukuŋŋaanyizibwa mu bifo ng’obusimu bw’amagumba ng’oggyeeko olususu. Tekitera nnyo, embeera eno esobola okukulaakulana n’efuuka embeera ya kookolo eyitibwa `mast cell leukemia`. Naye ate, bino bintu bya bbula nnyo . Ebitundu 99% ebya Urticaria Pigmentosa ebibeera mu baana si bya maanyi nnyo.

Bubonero ki obulaga obulwadde buno?

Akabonero akakulu era akasinga okweyoleka bwe kabonero ka `Darier` ke twayogeddeko. Kwe kugamba, ebitundu ebya kitaka bifuuka bimyufu era nga bisiiwa nga bisiigiddwa. Okugatta ku ekyo, abantu abamu nabo bayinza okufuna obubonero buno wammanga.

Abalwadde ba Urticaria Pigmentosa abasoba mu 75% baana abali wansi w’emyaka 10. Mu baana abasinga obungi, embeera eno ekoma ku lususu era etereera n’emyaka.

Omusawo akizuula atya kino?

Emirundi egisinga omusawo asobola bulungi okuzuula embeera eno ng’atunuulira ebifo ebiri ku lususu lwo n’akebera akabonero ka Darier. Tekyetaagisa kukeberebwa birala.

Wabula singa wabaawo okubuusabuusa oba embeera eno tekoma ku lususu lwokka wabula ng’ekosezza n’ebitundu by’omubiri ebirala, omusawo ayinza okukuwa amagezi okukebera bino wammanga.

• Okukebera omusaayi (`Blood count`): Manya ku bika n'obungi bw'obutoffaali obw'enjawulo mu musaayi.
• Okukebera mu musaayi (serum tryptase test): Kukebera oba waliwo enziyiza mu musaayi efulumizibwa obutoffaali obuyitibwa mast cells.
• Bone density scan: Laba amagumba go bwe galina amaanyi.
• Okukebera obusigo bw’amagumba: Kukebera oba obusigo bw’amagumba bukola obutoffaali obulamu.

Enkola z’obujjanjabi n’engeri y’okufuga obulwadde buno

Amawulire amalungi gali nti eri abaana abasinga obungi, Urticaria Pigmentosa ejja kugonjoola ku bwayo nga bakaddiye . Tewali bujjanjabi bwa njawulo buziyiza amabala amapya okutondebwa. Ebifo ebiriwo bisobola okutwala emyaka okuggwaawo.

Kasita embeera eno ekoma ku lususu, ebiseera ebisinga tekyetaagisa bujjanjabi bwa maanyi. Omusawo ayinza okukuwa amagezi bino wammanga okuyamba okuddukanya obubonero bwo:

• Eddagala eriweweeza ku buwuka obuleeta endwadde mu kamwa: Lifuga okusiiwa n’okuzimba.
• Ebizigo bya corticosteroid: Siiga mu bitundu ebisiiwa.
• Cromolyn sodium: Eddagala eriweebwa okujjanjaba obubonero ng’okusiiyibwa n’ekiddukano.
• EpiPen: Ekyuma ekiweebwa abantu abalina allergy ey’amaanyi ennyo (anaphylactic reaction) okukozesa mu mbeera ey’amangu. Kino si buli muntu nti kyetaaga.

Ebintu by’olina okwewala naddala

Ekisinga obukulu mu bulwadde buno kwe kubeera wala n’ebintu ebivaako obubonero obusajjula, kwe kugamba, ebintu ebivaako amabala okusiiwa n’okumyuuka.

Ekikulu: Bw’oba ​​ggwe oba omwana wo weetaaga okumira eddagala eriwonya embeera endala, kakasa nti otegeeza omusawo wo ku Urticaria Pigmentosa.

Ebizibu bisobola okubaawo?

Si bulijjo nnyo, embeera eno esobola okugenda mu maaso okutuuka ku `systemic mastocytosis`. Abantu nga bano bali mu bulabe obw’amaanyi obw’okulwala alergy ey’amaanyi eyitibwa `anaphylactic shock`, eyinza okutta obulamu. Bw’ofuna obubonero ng’okukaluubirirwa okussa n’okubulwa amagezi , olina okugenda amangu ddala mu kitongole ky’eddwaaliro eky’abalwadde ab’amangu (ETU) .

Ebizibu ebirala ebiva mu bulwadde bwa mastocytosis obw’ensengekera (systemic mastocytosis) mulimu:

• Osteoporosis: Okunafuwa kw’amagumba.
• Cytopenia: Okukendeera kw’obutoffaali bw’omusaayi mu mubiri.
• Obuzibu mu kibumba.
• Kookolo (tatera kubaawo).

Nate, bino bizibu ebitatera kubaawo nnyo. Zino tezitera nnyo mu baana abalina obulwadde bwa Urticaria Pigmentosa.