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Oyebi Carcinome médullaire rénale (RMC), cancer oyo emonanaka mingi te kasi ya makasi mpe ekómaka na ba reins?

MBBS

Medically reviewed by MBBS — Updated on Jul 15, 2026 · 8 min read

Oyebi Carcinome médullaire rénale (RMC), cancer oyo emonanaka mingi te kasi ya makasi mpe ekómaka na ba reins?
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Osilá koyoka lolenge moko ya kanser oyo emonanaka mingi te mpe ya makasi mpe ekómaka na ba reins, mingimingi epai ya bilenge? Mbala mosusu te. Oyo ezali Carcinome médullaire rénale, to RMC na mokuse. Atako emonanaka mingi te, ekoki kozala na ntina mingi koyeba yango, mingimingi mpo na bato mosusu. Atako oyo ezali mwa likambo ya monene, kobanga te. Tólobela yango na ndenge ya pɛtɛɛ mpe ya kososola lelo.

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RMC ezali mpenza nini?

Na mokuse, Carcinome médullaire rénale (RMC) ezali lolenge moko ya kanser ya rein. Kasi ezalaka mingi te, ezalaka makasi mingi, mpe epalanganaka noki. Emonanaka mingi na bilenge, mingi mingi baye bazali na bokono ya makila oyo babengaka bokono ya sickle cell to trait ya sickle cell.

Tango tolobeli cancer ya rein, lolenge oyo emonanaka mingi ezali carcinome ya ba cellules rénales. RMC ezali mpe sous-type ya carcinome ya ba cellules rénale. Kasi ata moko te kati na bato 100 oyo bazali na kanser ya rein azwaka maladi yango ya RMC. Ezali bongo rare.

Nini epesaka kanser oyo?

Bato ya siansi mpe minganga bamoni naino te ntina ya sikisiki ya likambo yango, kasi ezali na likambo moko ya ntina mingi oyo emonisami.

Ba reins na biso ezalaka na eteni oyo babengaka médulle rénale. Moto oyo azali na condition ya sickle cell tango mosusu azalaka na ba globules rouges oyo ebongwanaka na forme ya sickle. Tango esalemi, ba cellules ekoki kokangama esika moko pe kokanga misisa ya makila na eteni ya médulle rénale ya rein.

Kokangama wana ya makila ebebisaka baselile oyo ezali na esika yango. Mingimingi, gène moko oyo babengi INI1 (oyo babengaka mpe SMARCB1) na baselile wana ebebi. Gène oyo ya INI1 esalaka lokola mobateli oyo epekisaka ba cellules ekoma cancer. Tango ba cellules ya cancer ya RMC e examiner, gène oyo ya INI1 ezwamaka na kati na yango te. Na yango minganga batalaka soki gène oyo ya INI1 ezali mpo na kondimisa soki tumeur ezali RMC to te.

Nazali mpe na likama ya kozwa RMC?

Ezali pasi koloba exactement nani ako développer likambo oyo. Kozala na moto na libota na yo oyo azali na RMC ebakisaka te likama na yo ya kozwa yango. Yango elingi koloba ete ezali likambo oyo etambolaka na mabota te.

Facteur principal ya risque ezali trouble ya makila oyo babengaka hémoglobinopathie sickle. Elingi koloba kozala na maladi ya sickle cell to trait ya sickle cell. Mais très rarement , batu oyo bazangi ba conditions oyo bakoki pe ko développer RMC. Babengaka yango “carcinome ya ba cellules rénales, oyo e classifié te na phénotype médullaire” (RCCU-MP).

Soki otali ba statistiques:

  • Emonanaka mingi epai ya mibali koleka basi.
  • Mbala mingi ezwamaka na rein ya mobali.
  • Mbala mingi, maladi yango ezwamaka na mbula ya bolenge, kati na mbula 11 tii 39.

Ezali na ntina mpo na bilenge, mingimingi baoyo bazali na maladi ya sickle cell to ezaleli ya sickle cell, koyeba bilembo yango, mpamba te koyeba yango nokinoki ekoki kosala ete lisalisi ezala pɛtɛɛ. Soki bilembo bizali komonana, kende kotala monganga mbala moko.

Ba symptômes ya RMC ezali nini?

Ezali na bilembo mingi oyo emonanaka mingi mpo na maladi yango. Soki ozali na moko to mingi ya biloko yango, ekozala malamu koluka toli ya monganga nokinoki.

Elembo ya maladi Ndimbola
Pasi na esika ya rein Pasi oyo ezalaki ntango nyonso koyokama na ngámbo nyonso mibale ya libumu mpe na nse ya mokɔngɔ (kaka likoló ya libumu).
Makila na kati ya makila Mikila ya langi ya rozɛ, ya motane to ya motane. Ntango mosusu ekoki kozala na makila oyo ezali komonana na miso te.
Tumor ya libumu Liboke to masse oyo eyokaka lokola liboke na ngambo moko ya libumu.
Kokita ya kilo mpo na ntina te Kokita ya kilo nokinoki na boumeli ya ntango mokuse, kozanga ete básala milende.
Fièvre mbala na mbala mpe motoki na butu Soki ozali na fièvre mbala na mbala mpo na ntina mosusu te mpe ozali kosukola mingi na butu na boye ete nkasa na yo ekómaka na mai.

Ndenge nini monganga ayebaka likambo yango?

Ntango okoyebisa biso bilembo na yo, likambo ya liboso monganga akosala ezali kotala yo. Na nsima, okoki kolanda makambo yango.

1. Ezali na ntina mingi.Echographie: Yango ekoki kopesa likanisi ya moke soki ezali na eloko moko lokola tumor na ba reins.

2. CT to IRM: Soki ba suspecter tumor, bakoki ko commander CT to IRM mpo na kozua photo claire ya tumeur. Na kotalela bililingi yango, monganga akoki koyeba soki ekoki kozala na kanser.

3. Biopsie: Soki ba suspecter makasi cancer, basalaka test oyo pona ko confirmer yango. Yango esɛngaka kokɔtisa ntonga ya malamu na esika oyo tumor ya rein ezali, kozwa mwa eteni moke mpenza ya misisa mpe kotala yango na mikroskope.

4. Test génétique : Ba cellules oyo ezuami na biopsie e vérifier soki ezali na gène INI1 oyo ebundisaka cancer oyo tolobelaki liboso.

  • Soki gène INI1 ezangi , emonisami lokola RMC.
  • Soki gène INI1 ezangi mpe mobeli azali na état ya sickle cell te , ezwamaka lokola RCCU-MP.
  • Soki gène INI1 ezali , ezali RMC te, kasi lolenge mosusu ya tumeur.

Ba traitements nini pona likambo oyo?

Lokola RMC ezali kanser oyo epalangani nokinoki, oyo ezali makasi, esengeli kosalisa yango ezala nokinoki mpe na makasi ndenge moko.

  • Chimiothérapie: Oyo ezali nkisi ya liboso oyo bato mingi basalelaka. Esɛngaka kopesa nzoto bankisi oyo ebomaka baselile ya kanser.
  • Lipaso: Kolongola tumor oyo ezali na kanser mpe mbala mosusu rein oyo ezokaki.
  • Thérapie à rayonnements: Kobebisa baselile ya kanser na kosaleláká ba faisceaux ya radiation ya makasi.

Lokola maladi yango emonanaka mingi te, bolukiluki ezali naino kosalama. Bato ya siansi bazali ntango nyonso koluka bankisi ya sika mpe ya malamu mpo na RMC.

Est-ce que moyen ya kopekisa RMC ezali?

Likambo ya mawa, sikawa ezali na lolenge moko te eyebani mpo na kopekisa RMC ekola, mpe ezali mpe na test moko te mpo na koyeba yango yambo bilembo bima.

Eloko eleki malamu oyo okoki kosala ezali ya kozala na bokebi . Soki oyebi ete ozali na maladi ya sickle cell to ezaleli ya sickle cell, zalá na bokɛngi mpo na bilembo oyo tolobeli awa na likoló. Soki ozali na makambo oyo ezali kotungisa yo, kende mbala moko epai ya monganga na yo.

Mbala mingi, ntango bamoni maladi yango, kanser esilá kopalangana na ba ganglions lymphatiques to na binama mosusu lokola mimpululu, foie mpe mikuwa. Yango wana, koyeba yango nokinoki ezali lolenge malamu ya kozwa matomba ya malamu koleka.

Message ya Komema na Ndako

  • Carcinome médullaire rénale (RMC) ezali lolenge ya cancer ya rein oyo emonanaka mingi te kasi ya makasi mingi oyo ezwamaka mingi mingi na bilenge.
  • Likambo monene oyo ekoki kosala ete moto akóma na maladi yango ezali kozala na maladi moko ya makila oyo babengaka sickle cell disease to sickle cell trait .
  • Pasi ya mokɔngɔ/libumu, makila na makila, libumu na libumu, mpe kokita ya kilo oyo ekoki kolimbolama te ezali bilembo minene.
  • Soki ozali na maladi ya sickle cell mpe ozali komona elembo moko to mingi ya bilembo oyo tolobeli awa na likoló, kende mbala moko epai ya monganga na yo kozanga koumela.
  • Na bokono oyo, koyeba yango noki mpe kobanda lisalisi ezali libaku malamu ya kobikisa bomoi ya bato.
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