Chak lo leh nunna nei lo anga inhriatna? ALS (Amyotrophic Lateral Sclerosis) chungchang hi han sawi ila

Ni tin hna awlsam tak tak, no lâk te, i sam hrual te, a nih loh leh stairs chhoh te ang chite chu a harsa zual hle tih han ngaihtuah teh. I ke ruhte chu a hring vek ang maiin i hria em, i taksa ruhte chu a nghing ang maiin, a nih loh leh i thusawi laiin i thusawi chu a hlim lo ang maiin i hria em? Hengte hi natna khirh tak, mi tam takin an ngaihthah hmasak ber a ni a, mahse a ni thei. Vawiin hian chutiang natna pakhat, ALS, emaw Amyotrophic Lateral Sclerosis emaw chungchang kan sawi dawn a ni.

A awlsam zawngin, ALS chu eng nge ni?

ALS hi kan nervous system tichhe thei natna a ni. A dik taka sawi chuan kan thluak leh ruhro chhunga nerve cell, a nih loh leh neurons tichhe thei natna a ni. Heng neurons te hi motor neurons kan ti a. An hna ber chu kan thluak atanga thuchah lak a, kan taksa peng hrang hranga thawn hi a ni. "I kut phar rawh", "i ke hmalam dah rawh", "i hmui hawng rawh" tih ang chi chetna zawng zawng hi heng thuchahte hian a thunun vek a ni.

I thluak atanga i taksa ruh thlenga telephone line ang maiin ngaihtuah rawh. ALS a lo awm chuan heng telephone line te hi a chhe zauh zauh thin. Tichuan thluak atanga message rawn thawn te hian taksa ruh (muscles) a thleng tha tawk lo. Message te chu a inthlak danglam thin. A tawpah chuan connection chu a bo vek a ni. Chuvang chuan taksa ruhte hian hna thawk tura thupek an hmu lo va, zawi zawiin an lo tlem a, an atrophy ta a ni. Damdawi lamah chuan hei hi atrophy kan ti a ni.

He natna hi hmân laiin Lou Gehrig natna tia hriat a ni a. Chu chu kum 1920 leh 30 chho vela baseball player lar tak pakhatin he natna a vei vang a ni. He natna hi damdawi a la awm lo . Mahse lungngai suh, natna thunun thei tur, a natna lan chhuah dan tihtlem nan leh nun nuam tak hmang turin enkawlna hrang hrang siam a ni.

ALS natna hi chi hnih a awm a.

He natna hi a lo awm dan azirin chi hnihah then theih a ni.

Eng symptoms nge fimkhur tur?

ALS natna lan chhuah dan hi mi hrang hrangah a inang lo thei a, taksa peng hrang hrangah natna hi a intan thei bawk. Mahse, a lan chhuah dan tlangpui thenkhat a awm.

Heng symptoms te hi kut pakhat emaw ke pakhat atanga intan hmasain, hun kal zelah taksa hmun dangah a darh thei a ni. Natna zual zel dan hi mi zawng zawng tan a inang vek lo.

Engvangin nge ALS hi a lo awm? Risk factors te chu engte nge ni?

Dik tak chuan zirchiangtute chuan ALS thlen chhan chiang tak an la hmu lo a , mahse a thlentu nia ngaih thil engemaw zat a awm.

• Genetics: A hmaa kan sawi tawh ang khan chhungkaw zinga ALS hi genetic mutations avanga lo awm a ni. Tin, sporadic ALS vei zinga za zela tlemte hian genetic influence an nei thei tih hmuhchhuah a ni bawk.
• Environment factors: Lead leh mercury ang chi chemical tha lo tak tak te, virus thenkhat emaw, taksa hliam na tak tak te pawh hi chutianga thlentu nia ngaih a ni.

He natna vei theihna tipungtu thilte:

• Kum: Kum 55 leh 75 inkar te hi an hlauhawm zawk.
• Mipa leh hmeichhia: Kum 55 hnuai lam zingah hian hmeichhia aiin mipain he natna hi an vei tam zawk.
• Sipai hna: Zirchianna thenkhatah chuan sipai (a bik takin ram pawn) lo thawk tawhte chu ALS vei theihna a sang hle tih hmuhchhuah a ni. Hei hi chemical tha lo tak tak nena inzawmna emaw, taksa tihchakna nasa tak vang emaw a ni thei.

He natna hi engtin nge doctor hian a hriat theih ang?

ALS hi test khata hriat theih a ni lo. Natna dang tam tak, a lan chhuah dan ang chi hi a awm nual. Chuvangin, i doctor chuan natna dang a awm loh nan test hrang hrang a kalpui thei a ni.

Hengte hi test tih dan tlangpui chu a ni:

• Thisen leh zun test: Taksa chhunga damdawi lam thil dang awm leh awm loh enfiah thin ang che.
• Electromyogram (EMG): Hei hian taksa peng hrang hrangte electrical activity a test thin.
• Nerve Conduction Study: Nerve kal tlanga thuchah a kal chak dan a teh thin.
• Magnetic Resonance Imaging (MRI) hmanga tihchhuah a ni a:MRI scan hmangin thluak leh ruhroah chhiatna emaw, tumor emaw a awm leh awm loh enfiah thin a ni.

ALS enkawlna tur engte nge ni?

A hmaa kan sawi tawh ang khan ALS damdawi leh damdawi a awm lo. Mahse, enkawlna engemaw zat a awm a, chu chuan natna lan chhuahna a tikhawtlai thei a, damlote chu nuam zawk leh mahni inrintawkna nei zawka an nun theih nan a pui thei bawk.

I doctor leh i medical team te chuan enkawlna hrang hrang an rawt thei a, chungte chu:

Damdawi chi hrang hrang

Damdawi chi hrang hrang a awm a, chu chuan natna zual zelna tikhawtlai thei leh a lan chhuah dan thenkhat control thei a ni. `Riluzole` leh `Edaravone` te hi a lian ber pahnih a ni. Tin, taksa ruh khauh, ruh chhuak, natna, leh lungngaihna ang chi thil atan damdawi hranpa pek a ni bawk.

Therapies leh Rehabilitation hrang hrangte

• Physical Therapy: Exercise leh thurawn a pe a, chu chuan taksa ruhte a tichak thei a, ruhkawr a nghet lo thei lo va, a rei thei ang bera mahni inrintawkna neiin i thawk thei bawk.
• Occupational Therapy: Wheelchair leh kea kalna hmanrua te hman dan tur leh nitin hna awlsam zawka thawh dan tur a zirtir thin.
• Speech Therapy: A rei thei ang bera thusawi thiamna vawng reng tur te, ei tur him taka ei theihna tur te, leh a tul chuan inbiakpawhna kawng dang hman dan tur te zirtirna.

Ei leh in lama tanpuina

Chaw ei harsat hian taksa rihna a ti tlahniam thei. Chuvang chuan nutritionist thurawn zawm a, ei leh in awlsam tak leh a tul anga ei tur pe thei ei hi a pawimawh hle. A then phei chuan feeding tube hmangin hnar emaw, pum emaw hmangin chaw ei tur chu pum chhungah direct-in a thlen thei bawk.

Thâwkna Support

Natna a zual zel chuan thawkna ruhte chu a chak lo chho zel a. Chutih hunah chuan hnar leh hmui chunga mask vuah hmanga boruak thlentu `Noninvasive Ventilation (NIV),` ang chi hmanrua a ngai mai thei. A tawp berah chuan lung chhunga boruak pump chhuaktu machine (mechanical ventilation) puihna a ngai mai thei.

I rilru hriselna pawh a pawimawh hle.

ALS ang natna i vei tih hriat a, chu natna nena nunpui chu a buaithlak hle thei a ni. Lungngaihna, beiseina nei lo, thinrim, lungngaihna, leh lungkhamna ang chi hriatna a awm thei.