I hmui a lo hring nghal vek tih i hmu ngai em, a nih loh leh i mit a hring chhuak tih i hmu ngai em? A châng chuan i hmai zawng zawng, i kut leh ke thlengin a lo hring chhuak ṭhin. Hetiang thil a thlen hian hlauhna tlem a awm hi thil pangngai a ni. A tam zawkah chuan hei hi angioedema tih natna avanga lo awm a ni. Hemi chungchang hi chipchiar takin han sawi ila, awlsam takin, okay?
Angioedema chu eng nge ni? A awlsam zawngin i hrethiam ang u!
A awlsam zawngin sawi ila, Angioedema hi kan vun hnuaia tissue te, a bik takin dermis, vun chhung lam emaw, mucous membrane hnuaia layer te lo hring chhuak a ni. Hei hi thil pakhat avanga thil thleng (reaction) angin a thleng thin. Urticaria , a nih loh leh hives tih natna i hre tawh mai thei . Angioedema leh hives hi a awm dun fo a, a chhan pawh a inang hle. Heng pahnihah hian kan thisen kalna kawng te tak te atang hian tui a luang lut a, chu chuan a hmunte chu a ti hring chhuak thin.
Angioedema hi a tlangpuiin a intan nghal a, ni khat emaw ni hnih emaw chhungin a reh thei. A tam zawk chu hmui leh mit vel a ni . Mahse, han ngaihtuah teh, he hliam hian kan thawkna kawng a nghawng a nih chuan a hlauhawm hle thei a, nunna pawh a tichhe thei a ni . Chuvangin chu lam pawh kan fimkhur a ngai a ni.
Angioedema chi hrang hrangte chu engte nge ni?
Angioedema hi chi hrang hrang a awm a. Hriselna lama pawl hrang hrangte chuan an thliar hrang hrang thei a, mahse a tlangpuiin chi hrang hrang kan hmuchhuak thei a ni.
1. Acute allergic angioedema awm thei a ni
Hei hi i hriat leh tawn tam ber chi a ni ngei ang. I allergy nei thil i tawn hian a thleng thin . Hei hi i ei tawh (ei tur, in tur), damdawi i ei tawh, i khawih tawh (entir nan, natural rubber latex atanga siam thil) a ni thei. Insect emaw spider emaw in a seh hnuah pawh a awm thei bawk.
Acute allergic angioedema hi a lo awm rang hle , a tlangpuiin minute tlemte atanga darkar khat emaw darkar hnih emaw chhungin, allergen a awm hnuah. He swelling hi hives nen a awm fo thin.
2. Non-allergic drug reaction avanga angioedema
Hetiang angioedema hi damdawi i ei hnuah a awm nghal lo. Hetiang non-allergic reaction thlentu damdawi chi khat ber chu angiotensin-converting enzyme inhibitors , emaw ACE inhibitors emaw a tawi zawngin ACEIs emaw an ni.Heng damdawi te hi thisen kalna kawng tizau nan te, thinlung natna enkawl nan te, thisen sang tihhniam nan te hman a ni tlangpui. Nonsteroidal anti-inflammatory drugs (NSAIDs) , ibuprofen leh naproxen te pawhin he angioedema chi hi a thlen thei bawk.
3. A chhan hriat loh angioedema (Idiopathic angioedema) .
" Idiopathic" tih thumal hi "a chhan hriat loh" tihna a ni. Chuvangin he angioedema chi hi a chhan chiang tak hmuh a harsa hle. A hring hi hmai, kut, ke leh keah a awm tlangpui. Mi thenkhat chuan immune system lama harsatna leh stress an nei thei bawk.
4. Hereditary angioedema (HAE) a awm thei lo.
Hei hi hereditary angioedema , a tawi zawngin HAE tia hriat bawk a ni. Hei hi i nu leh pa hnen atanga i genes hmanga i hmuh thin a ni. Naupangte chuan nu leh pa pakhat chauhvin gene nei mah se, a nih loh leh natna an neih pawhin an rochun thei a ni. Mi thenkhat chuan spontaneous genetic mutations vangin he angioedema chi hi an nei thei bawk. Mi 50,000 zinga 1 velin hetiang hereditary angioedema (HAE) hi an vei thei niin an chhut. Hei hi chi thum a awm a, chungte chu eng emaw ti takin kan thisena C1 protein leh/ emaw C1 esterase inhibitor level nen a inzawm a ni.
5. Acquired C1 inhibitor tlakchhamna angioedema
Hei hian angioedema a thlen bawk a, mahse thlahtu a ni lo. Acquired tih awmzia chu tlakchhamna neia piang i ni lo va, nakin lawkah i nei chho tihna a ni. Chi dang ang bawkin he angioedema chi hian i larynx, emaw thlipui (windpipe) a nghawng thei a, asphyxiation a thlen thei bawk. B-cell lymphoma ang chi natna i neih chuan he natna hi Acquired C1 inhibitor deficiency an ti a.
6. Vibration avanga thisen zam (Vibratory angioedema) .
Hetiang dinhmunah hian swelling hi vibrations chhunzawm zel avanga lo awm a ni. Entirnan, motor khalh emaw, tlan emaw, jog emaw, massage chak tak i neih emaw, chutiang thil dang i tih emaw chuan hetiang hi a thleng thei a ni. Vibratory angioedema hi natna dang pakhat a ni a , chu chu chronic inducible urticaria an ti a ni . Chutah chuan pawn lam thil, khaw lum, lum, tui, pressure, vibration te chhanna atan hives a lo lang thin. Itchy welts hi a awm chhunzawm zel a, kar ruk vel a awm thin.
Tute nge angioedema vei tam zawk?
Dik tak chuan tu pawhin angioedema an nei thei. American mipui 20% leh 25% inkar chuan an dam chhungin vawi khat tal angioedema leh/ emaw urticaria an nei dawn niin an chhut. Chuvangin he dinhmun hi Sri Lanka-ah pawh a awm fo.
Angioedema natna lan chhuah dan chu engte nge ni? Engtin nge i hriat chian?
Angioedema natna lan chhuah dan tlangpui chu:
- Facial swelling or puffiness , a bik takin mit leh hmui vel, hmui leh lei te pawh huamin. Zingkar i harh a, rang takin i hmui a lo hring chhuak a, tawng harsa ang maiin i hria ang tih han ngaihtuah teh.
- I intestines a inflamed chuan digestive problems i nei thei . Hei hian pum na, luak chhuak, luak chhuak, leh luak chhuak te a huam a ni.
- Kut, ke emaw, mipat hmeichhiatna hmun emaw a hring chhuak.
- Thisen sang inthlak danglam hian luak chhuak emaw muhil emaw ang chi thil a thlen thei .
- Kawng, kawr emaw, thawkna kawng emaw a hring hian thawk leh tawng a ti harsa thei hle. Hei hi thil hlauhawm ber a ni. Hetiang thil hi a thleng a nih chuan medical emergency a ni. Damdawi in pan nghal a ngai!
A pawimawh ber: I beng a hring a, thawk harsa ang maia i inhriat chuan fiamthu a ni lo. Damdawi lam thurawn zawng nghal rawh.
Engvangin nge angioedema hi a lo awm? A chhante chu engte nge ni?
Angioedema awm chhan hi angioedema i neih chi hrang hrang a zirin a inang lo. Mahse, a chhan tam ber chu allergy a ni . Allergy hi a thlen thei chi hrang hrang a awm a:
- Food allergy: A chhan ber chu bawnghnute, artui, cashew ang chi nut, leh seafood te, shellfish ang chi te hi a ni.
- Damdawi allergy: Antibiotics penicillin leh sulfa damdawi, nonsteroidal anti-inflammatory drugs (NSAIDs), leh imaging test thenkhata contrast media hman te hian hetiang hi a thlen thei a ni. Heng allergy chi hrang hrangte hian hives a thlen thei a ni.
- Venom: Insect seh atanga poison chhuak a ni a, rannung brown recluse spider ang chi te hian a chhuak tlem hle.
- Natural rubber latex: Latex hi kutkawr, balloon, condom, leh medical catheter te siamna atana hman tur a ni. I doctor chuan latex allergy i neih leh neih loh a zawt che a ni mai thei.
A chhan dangte chu C1 inhibitor protein-a hereditary leh a hnu lama harsatna awm te, damdawi lama thil thleng, itching emaw rash awm lo (hengte hi allergy pangngai a ni lo), leh vibrational movement te a ni.
Angioedema hi a kai theih em?
Ni lo, a ni lo tak zet.Mi dang hnen atangin angioedema i kai thei lo va, midang hnenah pawh i kai thei lo. Natna hrik kai theih a ni lo.
Engtin nge angioedema hi i hriat theih ang? Doctor ten eng nge an zawn?
Eng ang angioedema nge i neih tih chiang taka hriat a harsa thei. I doctor chuan taksain a enfiah hmasa ang che, mahse a tam zawkah chuan a hring chu awlsam takin a lang thei. Tichuan zawhna tlemte an zawt ang che:
- Engtik lai khan nge a lo hring tan?
- I ei, i in, i ei, a nih loh leh i khawih nia i ngaih thil eng emaw chu i chhân lêtna thlentu ni thei nia i hriat?
- Tunah hian eng damdawi leh supplement nge i ei mek?
- Hetiang reaction hi a awm tawh em?
- I chhungkuaah hian hetiang hian swelling hi an nei tawh em?
Heng zawhnate hi zawh bakah hian i doctor chuan thisen test emaw vun test emaw allergy awm leh awm loh enfiah turin a ti thei bawk , a nih loh leh C1 inhibitor protein nena inzawm angioedema enfiah turin thisen test a ti thei bawk.
Angioedema hi eng enkawlna nge ni?
Angioedema enkawl dan hi i neih chi hrang hrang a zirin a inang lo.
- For severe allergic reactions , i doctor chuan injectable epinephrine injection a pe thei che a, chu chu engtik lai pawhin i hnenah i dah thei ang. He injection hi emergency-a 911 (Sri Lanka-ah 1990) i biak hunah i inpe tur a ni.
- Allergic angioedema tan chuan i doctor chuan antihistamine emaw steroid emaw a pe thei ang . Chungte chu pill angin ei theih a ni a, liquid (oral) angin ei theih a ni a, thisenah pawh ei theih a ni.
- If you have a non-allergic drug reaction , i doctor chuan a natna thlentu damdawi ai chuan a danglamna tha tak a hmu ang. Doctor thurawn tel lo chuan i damdawi ei kha bansan ngai suh.
In lama damdawi atan chuan a hring tihziaawmna turin ice hnawih te, tui lum taka inbual te, a hringna hmunah puan lum leh hnim hnawih te hi a ni. Hengte hian localized swelling, hmui zawng zawnga swelling, mit puffy tan emaw a thawk tha thei hle.
Hereditary, idiopathic, emaw acquired C1 inhibitor deficiency angioedema , i neih chuan specialist hnenah i refer mai thei. Hereditary angioedema (HAE) enkawlna emaw venna atana hman damdawi thenkhat chu:
- C1 esterase inhibitor (recombinant) (Ruconest®) hmanga tihdam theih a ni.
- C1 inhibitor (mihring) (Berinert®, Cinryze®, Haegarda®) te hi a tha hle a ni.
- Ecallantide (Kalbitor®) hmanga siam a ni.
- Icatibant (Firazyr®) hmanga siam a ni.
- Lanadelumab (Takhzyro®) hmanga tihdam theih a ni.
- Berotralstat (Orladeyo®) chuan a rawn ti a.
Angioedema ven dan tur a awm em?
Ni e, kawng engemaw zat a awm.
- Allergy-related angioedema , i neih chuan ei leh in, damdawi, a nih loh leh thil dang (triggers) allergic reaction thlentu ei lohvin i veng thei ang.
- ACEI damdawi (ACE inhibitors) i ei laiin non-allergic angioedema i nei a nih chuan damdawi dang hman dan tur chungchangah i doctor nen inbiakna neihpui tur a ni.
Angioedema vei chuan eng nge a beisei theih ang?
Angioedema vei tam zawk hi chu rei tak an awm lo . Anmahni chauhin an rel tlangpui. Amaherawhchu, natna khirh takah chuan thawkna kawng hawn reng turin enkawl a ngai thin.
Angioedema hian thihna a thlen thei em? Hei hi a hlauhawm em?
Mi thenkhat tan chuan allergic angioedema hian anaphylaxis an tih - thawkna kawng leh lung natna nasa tak a thlen thei. Hei hi nunna atana hlauhawm tak a ni thei . Doctor-te chuan he natna vei te chu allergy na tak enkawlna atan injectable epinephrine (EpiPen®, Auvi-Q®, Adrenaclick® leh brand dang) keng turin an fuih a ni.
Eng pawh ni se, angioedema hian thawkna kawng a nghawng hi medical emergency a ni fo thin. Chuvangin enkawl vat a ngai a ni. A châng chuan thawk chhuahnaah ṭanpui tûrin tracheostomy (thlipui hrualna kawngkhar siam) an tih surgery tih a ngai thei bawk.
Angioedema ka neih chuan engtin nge ka in enkawl ang?
Angioedema i neih chuan allergy triggers i pumpelh tur a ni . I doctor-in episode dang a awm loh nan damdawi a pe a nih chuan a tih ang chiah khan ei thin ang che. Injectable epinephrine keng turin an hrilh che a nih chuan, i keng reng tur a ni. I chhungte leh i thiante hman dan zirtir rawh.
Engtikah nge Doctor ka hmuh ang?
Allergy na tak i neih a, i thawkna kawng a tichhe a nih chuan 1990 (emergency ambulance service) call nghal rawh.
A na lo zawkah chuan angioedema i neih chhunzawm zel chuan doctor pan rawh. Invenna tur kawng hrang hrang an sawiho thei bawk. Enkawlna dangte chu oral antihistamines leh steroids te hi a ni. Idiopathic, enkawl harsaDoctor thenkhat chuan angioedema (idiopathic angioedema) tan hian monoclonal antibody Omalizumab (Xolair®) an hmang a.
A tawp berah chuan hriat reng tur pawimawh ber berte
I mit, hmui emaw kut emaw a hring nia i hriat chuan vun natna angioedema an tih a ni thei. Hei hi allergy i neih chuan a thleng tam zawk. Chutiang thil chu engtikah nge a thlen a, engtikah nge a thlen tih ziak la, i allergy nei thilte chu pumpelh dan zir rawh. I chhungte midang pawhin hetiang hi an nei tih i hriat chuan i doctor hnenah hrilh rawh. I chhungkuaah chuan he natna hi a kal zel em tih enfiah turin test neih a rawt thei a ni. Allergy avanga angioedema i neih chuan injectable epinephrine i bulah dah a pawimawh hle a, i thawkna kawng a hring chuan thawk a titawp thei a ni. Hlauthawng suh, mahse hei hi hriat chian a, a tul anga hmalak hi a finthlak hle.
` Angioedema, hring, allergy, vun natna, emergency care, epinephrine, urticaria











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