A châng chuan i naute piang thar chu thawk a harsat a, chaw ei a harsat a, a sen hring pawh a ni tih i hre tawh mai thei. Chûngte chu a châng chuan i naute thinlunga harsatna tê tê a awm tih chhinchhiahna a ni thei bawk. Chu chu a dik a, nau piang laia thinlung natna awm chu Atrioventricular Canal Defect an ti a, chu chu vawiinah hian kan sawi dawn a ni.
Hei hi eng nge ni (Atrioventricular Canal Defect)?
A awlsam zawngin sawi ila, Atrioventricular Canal Defect hi thinlung natna a ni a, nau piang lai hian a awm reng a ni. Doctor te chuan AVSD - Atrioventricular Septal Defect an ti fo thin . A dik tak chuan thinlung lama harsatna engemaw zat inzawmkhawm a ni. A bulpui ber chu thinlung lai takah hian bang chhungah khur emaw khur emaw a awm a (hei hi septum kan ti a) . Tin, thinlung chhunga valve te hnathawh that loh a huam tel bawk.
Tui pipe-a khur ang maiin han ngaihtuah teh. Thinlung hrisel takah chuan kan thinlung veilam atanga oxygen tamna thisen pump chhuah hi a tlangpuiin dinglam atanga oxygen tlakchhamna thisen nen a inhmeh lo. Mahse he khur avang hian chu oxygen tamna thisen chu oxygen tlakchhamna thisen nen a inhmeh ta a ni. A tam zawkah chuan he khur hian thisen tam lutuk chu lungah a kal tir thin. Tichuan taksa dang zawng zawnga thisen kal zat chu a tlahniam ta a ni. Hetiang hian rei tak a awm chuan a chang chuan a lehlamah a kal thei bawk. Chu chu oxygen tlachham thisen tam zawk taksaah a kal a, a tlem zawk chu lungah a kal tihna a ni. Chutiang a nih chuan taksaa oxygen level a tlahniam a, vun chu a sen thei a ni. Cyanosis kan ti a ni .
Hei hian thinlung chu a thawkrim zawk a, chu chuan hriselna lama harsatna dang a thlen thei a, chu chu congestive heart failure .
Hei (Atrioventricular Canal Defect) hi enkawl that loh chuan a chang chuan naupang nun a nghawng thei a ni. Operation tel lo chuan hetiang natna nei naupangte hi hun rei lote chhung chauh an dam thei a, chu chu kum hnih atanga kum thum vel a ni. Mahse, lungngai suh! A tha ber chu hei hi siamthatna tur surgery hi a hlawhtling hle a ni. Doctor-te chuan he natna hi a nasat hmain, naute pian hma pawhin an hre thei a ni.
A vaiin, United States ang ramah chuan kum tin naute 1,700 zinga pakhat vel chu he natna nei hian an piang a ni. Hei hi pianpui heart defect zawng zawng zinga 3% leh 5% inkar a ni.
He dinhmun hi hming dang engemaw zatin an ko bawk. I doctor chuan heng hming zinga pakhat hi a hmang thei ang:
- A rilru a buai em em a, a rilru a hah em em bawk a. Atrioventricular septal defect (AVSD) .
- Endocardial cushion a chhiat vang a ni
Atrioventricular Canal Defect chi hrang hrang a awm em?
Ni e, he thinlung chhiatna hi chi hrang hrangin a lo thleng thei a ni. Chu chu thinlung chhunga khur lian leh te leh valve awm zat ang chi thilah a innghat tihna a ni.
A kim vek (Atrioventricular Canal Defect) a ni.
Hemiah hian thil thleng chu thinlung pindan chunglam pahnih ( atria kan ti) leh a hnuai lam pindan pahnih ( ventricles kan ti) te hi a ni .(called) Thinlung pindan pahnih inkarah hian khur lian tak a lo awm a. Chu chu thinlung pindan palite hi a inzawm khawm vek tihna a ni. A tlangpuiin upper leh lower chamber inkarah hian valve pahnih a awm tur a ni. Mahse hetiang a nih chuan valve lian pakhat chauh a awm. A flap chu a inhawng tha lo thei a, a khar tha lo thei bawk.
A then (Atrioventricular Canal Defect thenkhat) 10. A rilru a hah lutuk chuan a rilru a buai em em a.
Chutiang a nih chuan, chu khur chu thinlung pindan chunglam pahnih inkar (hei hi a tam ber) emaw, a hnuai lam pindan pahnih inkar emaw a ni. Chamber palite hi a inzawm vek lo. Upper leh lower chamber inkarah hian valve pahnih a awm a. Mahse valve pakhat (a tam zawkah chuan mitral valve, upper chamber (left atrium) leh lower chamber (left ventricle) veilam sir inkar a awm) hian hna a thawk tha lo.
A rilru a buai em em a, a rilru a hah em em bawk a. Transitional Atrioventricular Canal Defect
Hemiah hian a chunglam chamber pahnih inkarah hian khur a awm a, a hnuai lam pahnih inkarah hian khur te tak te a awm bawk. Upper leh lower chamber (AV valve) inkar valve pahnih hi a hranpaa awm a ni.
Inthlauhna nei lo Atrioventricular Canal Defect kimchang tak
Lung chhiatna tluantlingah chuan valve lian tak pakhat a awm dan kha i hre reng em? Chu valve chu a dang aiin lower chamber (ventricle) pakhat hnaih zawkah a awm a. Tichuan thisen tam zawk dawngtu chamber chu a dang aiin a lian ta zawk a ni. Doctor-te chuan chu chamber te tak te chu ‘hypoplastic’ an ti a.
Hei hi eng symptoms nge ni?
He heart defect symptoms hi i naute pian hma pawhin a lang thei a ni. I naute hian heng zinga pakhat tal a nei em tih enfiah rawh:
- Blue skin color (Cyanosis): A bik takin hmui, lei leh kut zungtang ang chi hmunah te.
- Bawnghnute in harsa: Bawnghnute tlem in hnua chau leh chau lutuk.
- Bawnghnute in hnua thawk hah.
- Chau vat: Thil tlemte tih hnuah pawh chau.
- Lung na tak tak.
- Thâwk harsa (Dyspnea) emaw thawk rang.
- Weight gain hi zawi zawiin a thleng thin.
- Pum emaw ke emaw a hring (edema) a awm.
- Pulse chak lo tak.
Mahse, naute harsatna chi khat emaw, inthlak danglam emaw nei te chuan a tir lamah chuan heng natna hi an lantir lo mai thei. Heng chhinchhiahnate hi naupan laiah emaw, tleirawl lai emaw, puitlingah pawh a lang thei.
Engvangin nge hetiang (Atrioventricular Canal Defect) hi a lo awm?
Researcher te chuan Atrioventricular Septal Defect (AVSD) thlentu hi eng nge ni tih chiang takin an la hre lo . Genetic leh environmental factors inzawmkhawm niin an ngai . Mahse thil pakhat chu a chiang hle: he thinlung natna leh Down syndrome -ah hian inzawmna nghet tak a awm a ni. Down syndrome vei naute 40% vel chuan AVSD an nei a ni.
Hei hi eng risk factors nge a nghawng?
Mithiamte chuan hetiang thil thlentu risk factor dik tak hi an la hre chiang lo. Genetic influence a awm thei bawk. Nu emaw, pa emaw a\anga gene danglam lo kal chhuah chuan naute chu a pum chhunga a la awm laiin thinlung natna a vei theihna a tipung thei mai thei.
Chu bakah chuan naupai laiin a hnuaia thilte hian i naute hian pianpui thinlung natna a vei theihna a tipung thei bawk:
- Damdawi thenkhat.
- Dan loa ruihhlo (Recreational drugs).
- Zu awmna in tur.
- Environment toxin emaw chemical emaw nena inzawmna.
- Nutrient emaw vitamin emaw tlakchhamna.
- Thau lutuk.
- Zuk leh hmuam thil siam.
- Natna khirh tak tak Diabetes Mellitus emaw Hypertension emaw control loh.
- Viral natna chi hrang hrang, influenza (flu) emaw, flu emaw.
Atrioventricular Canal Defect avanga harsatna awm thei te chu engte nge ni?
He natna hi a nasat em em a, chu chu enkawl tha a nih loh tihna a nih chuan heng ang harsatna hi a awm thei a ni:
- Lung chak dan pangngai lo (Arrhythmia).
- Congestive heart failure a awm thin.
- Lung natna (Endocarditis) a awm thei.
- Lung lam panna thisen kalna kawngah thisen sang (Pulmonary hypertension).
He natna hi engtin nge an hriat chhuah?
Thu lawmawm tak chu a tam zawkah chuan doctor-te chuan naute pian hmain Atrioventricular Septal Defect chu test tlemte hmangin an hmuchhuak thei a ni:
- Prenatal ultrasound: Hei hian nausen pum chhunga a chetna thlalak a hmu thei a, thinlung pawh a tel. Septal defect lian tak a hmuchhuak thei bawk .
- Fetal echocardiogram: Hei hian ultrasound aiin thinlung thlalak a lang chiang zawk. Doctor chuan thinlung insiam dan leh thisen a pump dan chu a hrechiang zawk thei a ni.
Naute a pian hnuah doctor chuan naute thinlung thawk chu stethoscope hmangin a ngaithla thei a ni . "Ring tak" ri danglam tak ( heart murmur kan ti a) hriat a nih chuan, chu chu khur chhunga thisen luang ri a ni thei.
Nau piang hnua test dang tih thinte chu:
- Chest X-ray: Naute thinlung lian leh te, a pianzia enfiah thin ang che.
- Electrocardiogram (EKG/ECG): Naute thinlunga electric hnathawh dan enfiah thin ang che.
- Echocardiogram: Naute thinlung insiam dan chipchiar taka en.
- Cardiac catheterization: Naupang dinhmun nasat dan zir belh rawh.
- Cardiac Magnetic Resonance Imaging (Heart MRI): Naute thinlung peng hrang hrang leh an hnathawh dan en rawh.
A châng chuan naute hian septal defect te tak te a neih chuan a tir lamah chuan symptoms a nei lo mai thei. Chutiang a nih chuan, doctor-in chu natna chu a hriat chhuah hma kum engemaw zât a la liam mai thei.
Hei hi eng enkawlna nge ni?
Atrioventricular Canal Defect enkawlna hman tlanglawn ber chu open-heart surgery a ni . He surgery-ah hian surgeon chuan naute thinlunga khur chu a patch a , a khar thin. If the defect is complete , heart valve pakhat chu pahnih ah then a ni a, valve hrang hrang pahnih a siam a, pakhat chu dinglamah leh pakhat chu vei lamah a ni.
Naute AV canal defect inthlau lo nei chu operation vawi tam tak neih a ngai thei a, chu chu Fontan procedure an tih surgery-ah a tawp thei a ni.
He surgery hi a rang thei ang bera tih a tha ber a, chu chu natnain thinlung a tihchhiat vek hmain. Naute tam zawk chuan an dam chhung thla ruk chhungin he surgery hi an nei thin. Naute thenkhat, a then defect nei mahse symptomatic nei lo te chuan an dam chhung kum thum chhungin he surgery hi an nei thei a ni.
A châng chuan, naute chu zai tûra a hrisel tawk lo a nih chuan, a nih loh leh a rit lo a nih chuan, a rihna leh chakna a pun hma loh chuan a natna lan chhuah dân thunun nan damdawi pek theih a ni.
- Diuretics hi taksa atanga tui tam lutuk paih chhuaktu damdawi a ni.
- Digoxin hian naute thinlung chu a tichak zawk a ni.
- ACE inhibitor hian thisen kalna kawng a tizau a, thisen kal a ti awlsam bawk.
Hun rei lote chhunga tihdam theih dang chu pulmonary artery banding tih hi a ni. Hei hian pulmonary artery kaltlangin naute lung a thisen kal chu a ti tlem a ni. Naute pulmonary artery banding nei tawhte chu a hnuah permanent repair an nei thei bawk.
Enkawlna hnuah harsatna a awm thei em?
Ni e, a châng chuan operation hnuah hetiang thil hi a thleng thei a:
- Heart block: Chumi awmzia chu heart pulse signal hian thinlung hnuai lam a thleng dik lo tihna a ni.
- AV valve veilam emaw dinglam emaw a leak.
- Chamber hnuai lam bang chhunga khur (Ventricular septal defect) a awm.
- AV valve veilam emaw dinglam emaw a narrowing (Stenosis) a ni.
- Aortic valve hnuaia thisen kal tikhawtlai (Subaortic stenosis).
Hei (Atrioventricular Canal Defect) hi a veng thei lo em ni?
Hei hi (Atrioventricular Septal Defect) lo awm tur hi ven theih a ni tak tak lo, a chhan chu genetic cause nen a inzawm fo thin a ni.
Mahse, naupai i nih chuan i nautein pianpui thinlung natna a neih theihna tur tihziaawm nan hengte hi i ti thei ang:
- Dan loa ruihhlo, zu leh zuk leh hmuam thilte chu pumpelh vek rawh.
- Natna laka invenna atana i mamawh vaccine zawng zawng la rawh.
- I taksa rihna hrisel tak vawng reng rawh.
- Chronic health conditions i neih chuan uluk takin enkawl rawh.
- Nau neih hmaa vitamin, a bik takin folic acid hi doctor-in a rawt angin ei thin ang che.
Ka fa hian hetiang dinhmun hi a nei a nih chuan hmalam hun chu eng ang nge ni ang?
Operation tel lo chuan naupang AV canal defect nei te chu kum hnih atanga kum thum chauh an dam thei. Ṭhenkhat chu puitling tleirawl thlengin an nung a ni.
Mahse thu lawmawm tak chu chu repair surgery nei naupang zinga 90% vel chu chu enkawlna hnuah kum 10 hnuah an nung a ni . Chumi awmzia chu operation an neih hnu kum 10 tal an dam leh tlangpui tihna a ni. 65% vel chu operation an neih hnu kum 20 hnuah an dam.
Mahse hei hi hre reng ang che: Operation hnuah pawh Atrioventricular Canal Defect (AVCD) nei chuan thinlung pangngai tak a nei lovang. An thinlung hnathawh dan enfiah nan hunbi neia echocardiogram an neih chhunzawm a ngai dawn a ni. Hei hian harsatna eng pawh chu a hmain a man thei ang.
Chu khur chunga patch dah chu a tlangpuiin dam chhung a daih thei. Mahse hun kal zelah chuan heart valve siamthat zinga pakhat chu a leak tan thei a ni. Chutiang a nih chuan mi 10% leh 20% inkar chuan operation vawi hnihna an mamawh ang .
Mi tam zawk chuan operation hnuah damdawi emaw, operation dang emaw an mamawh lo. Mahse, cardiac arrhythmias hi a hnuah a awm thei a ni. Chutiang a nih chuan doctor chuan ablation ang chi, minimally invasive procedures tih a rawt thei a ni.
Engtin nge ka fa ka enkawl ang?
I fate taksa tihchakna chu i tihtlem a ngai mai thei . Hemi chungchang hi i fate pediatric cardiologist - naupangte thinlung natna lama tui doctor hnenah zawt rawh.
Naupang atrioventricular septal defect (AVSD) nei te chu ha enkawltu pan hmain antibiotics ei hmasak phawt theih a ni. Hei hian thinlung natna chi khat endocarditis an tih chu a veng thei a ni . Hemi chungchang hi i fate cardiologist nen pawh inbia ang che.
Engtikah nge ka fa hian doctor a hmuh ang?
I fa chu an pediatric cardiologist hnenah hun bi neiin i hruai ngei tur a ni . I fa thinlungah harsatna eng pawh a awm leh awm loh an enfiah thei a ni. Naupang thenkhat AV canal defects nei te chuan operation hnuah enkawl belh an ngai mai thei. Patch chu a leak thei a, a nih loh leh valve siamthat tawh chu a leak emaw a tawi thei bawk.
Naupang AV canal defect nei chuan neurological emaw developmental disorder a nei thei bawk . Chumi kawngah chuan ṭanpuina an mamawh thei bawk.
I fa a lo upa tawh chuan puitling congenital heart specialist hnenah insawn tur a ni a, kum khatah vawi khat tal check-up nei turin a kal tur a ni.
Ka fa doctor hnenah eng zawhna nge ka zawh ang?
I fa doctor hnenah zawhna i zawt thei ang:
- Ka fa hian eng ang AV canal defect nge a neih?
- Eng natna nge a zual zel tih tilangtu symptoms te chu engte nge ni?
- Engtikah nge operation a mamawh ang?
- Ka fa hian operation hnuah damdawi a mamawh dawn em?
- Ka fa thiltih hi ka tihtlem a ngai dawn em ni?
I nau piang thar hian Atrioventricular Canal Defect ang chi thinlung natna a nei tih i hriat hian rilru natna hrang hrang neih hi thil pangngai a ni. Mahse i naute doctor-te chu tanpui turin an awm a, i naute tan a tha ber tih an duh a ni. I naute dinhmun atana thil chiang tak chu zawng chhuak rawh. I hriat chian loh thil a awm chuan i doctor hnenah zawt la. Tun hi i naute hriselna atana i sawisel hun a ni.
Chuti a nih chuan, heng zawng zawng atang hian eng thil nge kan hriat reng tur?
- Atrioventricular Canal Defect hi thinlung natna a ni a, nau piang lai hian a awm thin. A chhan ber chu thinlunga khur leh valve-a harsatna awm vang a ni.
- A hmaa hriatchhuah leh a hun taka zai hi a pawimawh hle. Heng surgery te hi a hlawhtling hle.
- Down syndrome nei naute hian he natna hi an nei tam zawk.
- Operation hnuah pawh hun rei tak chhung medical supervision neih a ngai a ni. I dam chhung zawngin cardiologist nen in inzawm reng a ngai a ni.
- Naupai i nih chuan nunphung hrisel zawm leh damdawi lam thurawn zawm hian i naute pianpui thinlung natna vei theihna a tihziaawm thei a ni.
- Hlau suh, Doctor te chu nang leh i naute tanpui turin an awm reng a ni. Zawhna zawt la, hriattir ni rawh.
` Lung natna, pianpui thinlung natna, naute thinlung, thinlunga khur, Atrioventricular Canal Defect, AVSD, naupang thinlung natna











💬 Comments (0)
Comment a la awm lo. Hetah hian i comment hi a vawikhatna atan add rawh.
I comment kha add rawh