I mit hmaa thil dum te te lo inhnim pil lai i hmu ngai em? A nih loh leh i mit hmuh chu a fiah lo deuh mai thei em? Hengte hi thil pangngai a ni thei a, mahse a chang chuan i mit chhunga harsatna awm chhinchhiahna a ni thei bawk. Vawiin hian chutiang mit natna hmuh tur awm lo pakhat, enkawl dik a nih chuan control theih tur chungchang kan sawi dawn a ni.
Hei hi eng nge ni (Birdshot Chorioretinopathy)?
A awlsam zawngin, Birdshot Chorioretinopathy, a tawi zawngin BSCR hi mit chhunga awm, inflammatory disease awm lo tak a ni. Chronic condition a ni lo va, hun rei lote chhungin a dam lo tihna a ni a, persistent condition a ni. Enkawl dik loh chuan mit hmuhna a tidanglam reng thei a, mit hmuhna pawh a hloh vek thei bawk .
(BSCR) hi natna khirh tak a ni a, natna pawl pakhat ``Uveitis'' an tih, mit chhunga tissue te tichhe thei a ni. A bik takin: swelling of:
- Retina : Hei hi kan mit hnung lama light-sensitive membrane a ni. Camera chhunga film awm ang mai a ni. Thlalak kan hmuhte hi hetah hian record a ni.
- Choroid : Hei hi mit (retina) hnuaiah a awm a. Hei hi mit peng var nena retina thlunzawmtu membrane a ni a, retina-ah thisen a pe a, chu chu a chawm tihna a ni.
He natna langsar ber chu retina thuk tak leh choroid chunglam layer-a hmun te te, oval, cream rawng a lo lang hi a ni. A lan chhuah hmasak ber chu mit hmaa thil dum (floaters) , mit hmuh lohna , emaw a pahnih emaw a ni fo. Hetiang dinhmun hian mit pahnih a nghawng tlangpui .
Hun a kal zel a, he chhiatna hian cystoid macular edema emaw glaucoma emaw ang chi dinhmun a thlen thei a ni. Damdawi awm lo mah se, Birdshot Chorioretinopathy hi enkawl theih natna a ni . Enkawlna hlawhtling tur chuan a hmaa hriatchhuah a pawimawh hle.
Birdshot Chorioretinopathy hi tuin nge vei?
Dik tak chuan he natna hi tu chungah pawh a lo awm thei a ni. Mahse kum chanve vel, puitling var kum 40 leh 60 inkar ah a tam ber a, naupang tan he natna hi an vei hi a tlem hle.
Hetiang ang natna dang (Birdshot Chorioretinopathy) hi a awm em?
Ni e, natna dang engemaw zat, Uveitis group-a natna dangte pawh hian Birdshot Chorioretinopathy nen hian symptom inang an nei thei a ni. Chuvangin, enkawl dan tur dik tak i dawn theih nan diagnosis dik tak neih a pawimawh hle. BSCR nena inang thei natna thenkhat chu:
- Lymphoma (cancer chi khat) 1.1.
- Sarcoidosis (natna, taksa peng hrang hranga hliam tenau te thlentu) .
- `(Sympathetic ophthalmia)` (Mit hliam avanga lo awm uveitis chi khat)
- Syphilis (mipat hmeichhiatna hmanga kai theih natna) .
- `(Presumed ocular histoplasmosis syndrome (POHS))` (Fungal infection avanga mit tichhe thei dinhmun)
- `(Tuberculosis)` (Tuberculosis) 2019 a ni.
- `(Vogt-Koyanagi-Harada syndrome)` (natna pakhat, nervous system tichhe thei, mit leh hriatna tichhe thei)
Inflammatory diseases group pakhat ``White dot syndromes'' an tih pawh a awm a, BSCR symptoms pawh a lantir thei bawk. Chungte chuan retina leh choroid-ah ``lesion'' a siam thin. Entirna thenkhat chu:
- `(Acute posterior multifocal placoid pigment epitheliopathy (APMPPE)) a awm a, a natna hi a lar hle
- `(Multifocal choroiditis leh panuveitis (MCP))`
- `(Multiple evanescent white dot syndrome (MEWDS)) tih a ni a, a rilru a hah lutuk a, a rilru a buai em em bawk a
- `(Punctate chhungril lam choroidopathy (PIC))`
Engvangin nge hei hi Birdshot Chorioretinopathy an tih?
Hei hi a takah chuan natna thar tak a ni a, kum 1949-a sawi hmasak ber a ni a, kum 1980-ah khan mit lam doctor pahnih chuan "(Birdshot Chorioretinopathy)" tih hming an vuah a ni. A chhan chu a spot te hi retina zawng zawngah a darh vek a, a rawng chu cream leh orange a ni . Heng a hming hi heng spot te pattern hi sava kah nana hman thin bullet te tak te (birdshot) te pattern ang deuh a nih vang a ni. Ngaihtuah teh, mit chhungah hian hmun hrang hrang a awm a, chu chu silai kah laia silai mu darh chhuak ang chi hi a ni.
Hei hi hming dang a awm em?
Ni e, natna hming dang engemaw zat hman a awm bawk (Birdshot Chorioretinopathy):
- `(Sava kah chorioretinitis)`
- `(Sava kah natna (Birdshot retinochoroiditis))`
- `(Birdshot retinochoroidopathy)`
- `(Sava thlalak uveitis)`
- `(BSCR)` (hming tawi) .
- `(Posterior uveitis)` (mit hnung lama awm uveitis) .
- `(Vitiliginous choroiditis)` tih a ni
Birdshot Chorioretinopathy hi engtiang chiahin nge a awm?
Hei hi natna hmuh tur awm lo tak a ni . Zirchiangtute chuan mi sang za zinga pakhat aia tlem loin a nghawng niin an ngai. Chumi awmzia chu Sri Lanka-ah pawh he natna vei hi an awm thei a, mahse a tlem hle.
Eng thilin nge Birdshot Chorioretinopathy hi a thlen?
Researcher-te chuan he natna thlen chhan dik tak hi an la hre lo a , mahse autoimmune disease a nih an ring . A awlsam zawngin kan taksa invenna system, immune system hian kan taksa hrisel tak takte chu a rawn bei sual a ni.
(BSCR) vei hmuhchhuah zinga 90% aia tam chuan an taksaah antibody gene (immune system tichaktu molecule) `(HLA-A29)` an nei a. Hei hi nu leh pate rochun thil a ni. Amaherawhchu, `(HLA-A29)` hi a lo awm a ngai lo (Birdshot Chorioretinopathy). Tin, he antibody gene hi nei mahse natna hi a lo awm lo thei bawk.
Birdshot Chorioretinopathy natna lan chhuah dan chu engte nge ni?
He natna lan chhuah dan hi mi hrang hrangah a inang lo thei. HeiNatna zual zel chu thla tam tak atanga kum tam tak chhunga zawi zawiin a zual zel a ni.
Birdshot Chorioretinopathy chhinchhiahna hmasa ber chu:
- Mit hmaa thil dum leng (floaters) hmuh .
- Mit hmuh a fiah lo
Hetiang dinhmun hian mit na leh sen a thlen lo tlangpui . Mahse, a hnuaia mite hi i tawng thei a ni:
- Mit a danglam emaw, mit a tlahniam emaw.
- Peripheral vision tlahniam emaw, hlat zawng teh harsa emaw.
- Mit chhunga pressure sang (ocular hypertension) a awm.
- Zan lama mitdelna (nyctalopia) (zan lama mitdelna).
- Color vision lama harsatna (`(color blindness)`), rawng thenkhat thliar hran harsa (`(dyschromatopsia)`.
- Eng eng emaw, eng eng emaw laka sensitivity (photophobia).
Mi thenkhat chuan mit lama danglamna danglam tak emaw, hriatna lama harsatna emaw an nei thei. Entir nan:
- Ceiling fan effect : I mit i khar chuan ceiling fan emaw thlipui emaw a inher ang maiin a lang.
- Eng emaw, eng emaw eng (photopsia) emaw, a pianzia danglam (metamorphopsia) hmuh emaw .
- Mit hmuh theih loh, eng mawi tak, tui emaw glass bawlhhlawh emaw atanga thlir ang maia .
A nasat chuan mitdel emaw glaucoma emaw ang chi natna a awm thei. Hengte hian a hring enkawl hnuah pawh mit a tichhe nasa thei hle. Birdshot Chorioretinopathy hian retina lairil lamah harsatna a thlen thei bawk a, chu chu cystoid macular edema leh epiretinal membranes te hi a ni.
Engtin nge Birdshot Chorioretinopathy hi hmuhchhuah a nih?
He natna hi a chang chuan hriat harsa deuh a ni thei a , a chhan chu natna hmuh tur awm lo tak a nih avangin natna lan chhuah tirh lamah a hmun hrang hrang a lang lo thei bawk.
Mit lam doctor-te chuan mit enfiahna hmangin BSCR hi an hmuchhuak fo thin. HLA-A29 antibody i neih leh neih loh enfiah nan thisen test an nei bawk.
Doctor-te chuan test hrang hrang hmangin hun kal zelah an enfiah thei che a ni. I mamawh enkawlna i hmuh theih nan i doctor nen inbiak reng a pawimawh.
Birdshot Chorioretinopathy hi damdawi kimchang tak a awm em?
Vanduaithlak takin he natna hi tihdamna famkim a la awm lo . Amaherawhchu, natna hi a hmaa hriatchhuah a, enkawl a nih chuan , a natna lan chhuah dan a reh thei a, natna a zual zel loh nan a veng thei bawk.
Hriat tur: a pawimawh ber chu natna hi hriat hmasak a, enkawl tan hi a ni!
Ka treatment team-ah hian tute nge tel thei ang?
I care team chuan enkawlna tur an rawt ang che a, an enkawl ang che a, i dinhmun leh a side effects a zirin i damdawi ei turte pawh an siamrem ang. I team-ah hian:
- Ophthalmologist : Mit enkawltu doctor ber.
- Nephrologist : A chhan chu enkawlna thenkhatin kal (kidney) a nghawng vang a ni.
- Ocular immunologist: Mit immune system lama harsatna awm thei chungchanga specialised training nei doctor a ni .
- Rheumatologist: Taksa chhunga inflammation nena inzawm natna hrang hranga specialist doctor , a chhan chu hei pawh hi inflammation natna a nih vang a ni.
- Orthopedist : A chhan chu enkawlna thenkhatin ruh a nghawng vang a ni.
Birdshot Chorioretinopathy hi engtin nge enkawl a nih?
He natna enkawlna hi i dinhmun nasat dan leh hun kal zelah a inthlak danah a innghat a ni. Enkawlna tum ber chu i mit a hring chhuak tihziaawm a , mit hmuhna hloh tawh thenkhat ven emaw siam that leh emaw hi a ni .
Doctor-te chuan mit natna control nan corticosteroids (steroid damdawi chi khat) dose sang tak an pe hmasa tlangpui. Tichuan, a dose chu tihhniam zauh zauh a ni a, chu chuan side effects a thlen theihna tur a ti tlem a ni. Steroid hi a hnuaia mi ang hian i ei thei ang:
- Mit a tlakbuak
- Damdawi ei tur
- Thil te tak te, mit chhunga surgery hmanga dah (intravitreal implant) .
- Injection pek a ni
- Vein pakhatah pek (IV - thisen kal tlanga) .
Mi tam tak pawhin immunosuppressant hi hun rei tak chhung an ei a ngai bawk . Heng damdawi te hian i immune system in i mit a beih loh nan a titawp thin. A hnuaia mi pakhat emaw, a aia tam emaw hman theih a ni:
- `(Alkylating agents)` tih a ni
- `(Antimetabolite damdawi)`
- `(Biologic agents)` (damdawi chi hrang hrang) .
- `(T-cell transduction/calcineurin inhibitor)`
Birdshot Chorioretinopathy (Birdshot Chorioretinopathy) enkawlna hian side effect a nei thei em?
Ni e, hun rei tak chhunga steroid leh immunosuppressant hman hian side effect na tak a thlen thei a ni . Entirnan, chaw kawng lama harsatna (ulcer, ulcer) emaw ruh lama harsatna (osteoporosis) emaw a awm thei. Heng damdawi te hian mitdel emaw glaucoma emaw vei theihna a tipung thei bawk.
I doctor chuan side effect i neih leh neih loh a enfiah ang che a, a tul chuan damdawi dang a pe ang che. Oral steroids i ei a nih chuan i doctor chuan ruh hloh (osteoporosis) leh ruh tliak theihna i neih leh neih loh a enfiah ang che.
I doctor chuBone density scan pawh tih a tha thei bawk. Ruh hloh loh nan damdawi (bisphosphonates) pawh pek theih a ni.
Eng ang long-term monitoring nge ka mamawh (BSCR)?
I dinhmun a inthlak danglam emaw, harsatna emaw a awm chuan hre reng ang che . I doctor chuan thisen leh zun test a ti ang a, i kal, thin leh ruhro te a thawk tha em tih a enfiah ang. Tin, mit enfiah fo te, visual field test te, leh optical coherence tomography (OCT) scan te pawh i mamawh ngei ang.
Birdshot Chorioretinopathy ka vei theihna tur ka tihtlem thei ang em?
Tun dinhmunah he natna laka inven dan tur hriat a la awm lo . A tam zawkah chuan chhungkaw member atanga rochun antibody gene (antigen) bik avanga lo awm niin an ngai.
Mit enfiah fo hian natna chhinchhiahna hmasa ber a hriat theih avangin a tul chuan a hun taka enkawl i hmu thei a ni. I chhungte zingah mit lama harsatna nei an awm chuan doctor hnenah hrilh rawh.
Birdshot Chorioretinopathy hi eng nge a hmalam hun?
He natna thlirna hi mi hrang hrangah a inang lo . A natna nasat dan leh enkawlna hlawhtlinnaah a innghat. A nasat loh chuan enkawlna hian mit hmuhna a vawng reng thei a, a tichak thei bawk.
Engtikah nge (Birdshot Chorioretinopathy) tan hian damdawi lam thurawn ka lak ang?
Birdshot Chorioretinopathy vei hi mit lam doctor hnen atangin rang taka hriatchhuah leh enkawl a pawimawh hle. I mit chu a tha ang tih pawhin mit enfiahna chuan low-level swelling a hmu thei a ni.
I damdawi ei avanga side effects, symptoms inthlak danglamna, emaw vision te chu i doctor hnenah hrilh rawh. A tul chuan damdawi dang pek i ni thei bawk. I doctor chuan i tana tha ber tur duhthlan tur a sawipui ang che.
Take-Home Thuchah hnuhnung ber
(Birdshot Chorioretinopathy) hi natna hmuh tur awm lo mahse enkawl theih a ni . Chuvangin hlauthawng suh. A pawimawh ber chu i mit enfiah fo a, i doctor rawtna zawm hi a ni . Hun a kal zel a, i doctor chuan i mit ven dan tur leh harsatna lo thleng tur ven dan tur a hrilh ang che. Tichuan khawvel hi chiang takin i hmu thei tawh dawn a ni. I mit kha enkawl la, a hlu em em a ni!
` Birdshot Chorioretinopathy, Mit Natna, Mit Tih lohna, Uveitis, Retina, Autoimmune Natna, Mit Enkawlna











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