Darthlalang-ah i en a, i pum chhungah i thisen kalna kawng (veins) te chu chiang takin a lang tih i hmu ngai em, a bik takin i pum chhungah i hmu thei em? A chang chuan hei hi hmuh a hlauhawm deuh thei. Hei hi eng nge ni tak tak? Hei hi hlauh tur thil a ni em? Vawiin hian he natna hi kan sawi dawn a, medical science-ah chuan ‘Caput Medusae’ tia hriat a ni. Hei hi natna a ni lo va, taksa chhungril lama harsatna lian tham tak min petu vaukhânna pawimawh tak a ni .
He ‘Caput Medusae’ hi eng nge ni?
A awlsam zawngin sawi ila, Caput Medusae chu i pum vun hnuaia thisen kalna kawngte a lo hring a, a lo lian a, a lo hring chhuak a ni. Vawi tam tak chu heng vein te hi kawng tinrengah a bul chhuak chhuak niin a lang a, i pum lairil atanga ni êng lo chhuak ang maiin a lang.
He hming mak tak hi Greek thawnthu atanga lo chhuak a ni. Chutah chuan hmeichhe pakhat ‘Medusa’ tih a lang a, a lu-ah hian sam aiah rul a awm. A kawr vela thisen kalna kawng chu Medusa lu atanga rul chhuak ang mai a ni a, hei vang hian doctor-te chuan ‘Caput Medusae’ tiin an vuah a, chu chu ‘Medusa lu’ tihna a ni. Ṭhenkhat chuan ‘palm tree sign’ an ti bawk.
A pawimawh ber chu hetiang vein lo lang hian taksa chhunga thisen kal dan tur tikhawtlai engemaw zat a awm tihna a ni. Chuvangin hei hi vun lama harsatna mai mai anga ngaihthah a tha lo.
Engvangin nge hetiang hi a lo awm? Hei hi entirnan han hrethiam ila.
Colombo panna kawngpui lian tak chu lirthei tam takin a dang ang tih han ngaihtuah teh. Chuti a nih chuan lirthei te hian eng nge an tih? An tumna hmun chu a rang thei ang bera thlen an tum a, side road, gravel road te tak te te an zawh thin. Mahse heng side road te hi lirthei tam tak tuar thei tura siam a ni lo. Chuvang chuan chu kawngte chu rang takin a inkhar a, a khat nghal bawk.
Kan taksaa thisen kalna kawng (blood vessel system) hi a inang vek a. Pum chhunga thisen kalna kawng lian tak (portal vein emaw inferior vena cava) chu eng emaw vanga a block chuan thisen a kal thei lo. Hei hi obstruction an ti a .
Tichuan taksa chuan he thisen block hi ‘side road’ ang maia vein te tak te dang hmangin thawn chhuah a tum thin. Heng vein te te hi kan pum vun hnuaia awm te hi an ni. Heng vein te tak te, te tak te atanga thisen tam tak a kal thut chuan an tuar thei lo va, an lo hring chhuak a, an bulge a, kan mit hmuh theihin an awm ta a ni. Chu chu Caput Medusae kan tih chu a ni. Damdawi lamah chuan he kawng dang hi collateral circulation an ti a.
Caput Medusae awm chhan berte chu engte nge ni?
Hetiang dinhmun hi chhan lian tak pahnih a awm a. An pahnih hian serious an nih avangin hei hi hriat a pawimawh hle.
| Chhan | Hrilhfiahna awlsam tak |
|---|---|
| Portal Hypertension a ni | Hei hi a chhan tam ber a ni. Kan thin kal tlanga thisen kalna kawng lian ber chu ‘portal vein’ an ti a. Hei hi he vein-a thisen sang vang a ni. Hei hi liver cirrhosis vang a ni fo thin . Thin natna a lo awm a, a khauh a, a hliam a nih chuan thisen chu awlsam takin a luang chhuak thei lo. |
| Inferior Vena Cava Syndrome a awm a, a natna hi a tha lo hle | Hei hi kan taksa hnuai lam atanga thinlung thlenga thisen phurtu vein lian ber a ni. He vein hi thisen zam, tumor, emaw, pianpui natna Budd-Chiari syndrome ang chi emaw hmangin a block thei a ni. |
Hei hi eng symptom dang nge a zui thei ang?
Caput Medusae hi a hnuaia natna lian zawk chhinchhiahna pakhat chauh a ni. Chuvangin, a rualin symptom dang i tawng ve thei bawk.
A lan chhuah dan tlangpui
- Ke leh ke a hring (Edema) .
- Pum natna nasa tak, pum chhunga tui a khat (ascites) .
- Pum a na
- Liver lian tak, dinglam sir a ribs hnuaiah palpable
A chhan a zirin symptom bik a inang lo
Heng symptoms te hian i doctor chu a chhan hriat theihna turin a pui ang.
- Liver cirrhosis vang a nih chuan:
- Vun leh mit sen (Jaundice) .
- Vun a na lutuk
- Zun dum (tea ang chi) .
- Pale stools (leilung ang chi) .
- Spider angiomas (thisen kalna sen, spider web ang maia lang) chu rilru leh taksa chunglam a ni
- Thisen zam (Deep Vein Thrombosis - DVT) vang a nih chuan:
- Taksa hmun khatah (e.g., ke pakhat) a hring nghal vat a.
- A hmun chu a sen emaw, a dum emaw a ni a, khawih pawhin a lum hle
Engtin nge doctor chuan a chhan dik tak chu a hmuh theih?
Hetiang symptom i hriat veleh doctor pan vat a pawimawh hle. Doctor chuan a enfiah hmasa ang che a, i symptoms te ngun takin a ngaithla ang che. Tichuan, a chhan dik tak hriat theih nan test eng emaw zat an ti ang.
Hei atan hian test hman ber chu a pum ultrasound scan a ni . Hei hian pum chhunga taksa peng leh thisen kalna kawngte chu a hmu thei a ni.
A bik takin he scan hian tortuous veins-a thisen kalna lam a en a ni.
- Thisen hi ke atanga a luang thla a nih chuan , a nih a rinawm ber chu Portal Hypertension an tih natna a ni a, chu chu cirrhosis of the liver vang a ni.
- Thisen chu thinlung lam hawiin chunglam a luang a nih chuan inferior vena cava a block vang pawh a ni thei .
He thil awlsam tak hian doctor chuan natna thlentu chu a hre chiang thei a ni.
Hei hi eng enkawlna nge ni?
A pawimawh ber chu, enkawlna hian Caput Medusae vun hmuh theih chauh a enkawl lo va, a hnuaia awm dan pawh a enkawl a ni . A chhan bulpui ber enkawl a nih chuan heng varicose veins te pawh hi hun kal zelah a tlahniam thei bawk.
- A chhan chu paih theih a nih chuan: Entîr nân, thil dang tihbo theih, thisen zam ang chi a nih chuan, chu daltu chu paih chhuah chu doctor-te thil tum hmasa ber a ni.
- A chhan chu natna khirh tak a nih chuan: Natna khirh tak, cirrhosis of the liver ang chi a nih chuan natna enkawl dan tur leh a harsatnate control turin enkawlna bik pek thin a ni.
A then phei chuan portal hypertension hian chaw ei kawng a thisen zam a ti hring a, thisen a chhuah chuan thisen sang tihhniam nan hmanraw bik hman a ni.
- TIPS (Transjugular Intrahepatic Portosystemic Shunt): Hei hi X-ray kaihhruaina hnuaiah liver kaltlangin tube te tak te dahin portal vein leh liver chhunga vein dang inkarah shunt siam a ni. Hei hian thisen block chu kalna tur kawng thar a siam a, pressure a tihhniam phah a ni.
- DSRS (Distal Splenorenal Shunt): Hei hi surgical procedure a ni a, chu chu liver atanga splenic vein lakchhuah a, left kidney vein nena inzawm a ni. Hei hian pressure a tihziaawm bawk.
Take-Home Thuchah a ni
- I pum chhunga vein bulging i hmuh chuan Caput Medusae a ni thei. Khawngaihin hei hi ngaihthah suh u.
- Hei hi natna a ni lo va, taksa chhunga natna khirh tak dang (a tam zawkah chuan thin natna) chhinchhiahna a ni.
- Hetiang symptom hi i hriat chuan chhungkaw doctor pan vat a pawimawh hle. A chhan hriat chian a hma chuan enkawlna a hlawhtling zawk ang.
- Natna hnuaia awm hi enkawl that loh chuan nunna atana hlauhawm tak tak, liver failure emaw kidney failure emaw a awm thei a ni.

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