Kan zînga ṭhenkhat chuan kan pianpui hrisêlna engemaw zat kan nei thei a. Chung zinga ṭhenkhat chu a tlem hle. Mahse tunlai damdawi lam thiamna changkang tak avangin heng dinhmun tam tak hi kan thunun thei a, nun pangngai kan hmang thei ta a ni. Carglumic Acid hi damdawi bik a ni a, chutiang natna hlauhawm tak, genetic condition nei tan chuan doctor-te chuan thisenah thil tha lo tak ammonia an tih level a sang a ni. Hemi chungchang hi vawiin hian han sawi ila.
Carglumic Acid hi eng damdawi nge ni?
A awlsam zawngin sawi ila, he damdawi Carglumic Acid an tih hi Urea Cycle Disorders (UCDs) an tih natna enkawlna atan hman a ni.
Kan taksa hi factory lian tak angin han ngaihtuah teh. Taksain kan ei protein a hman hnuah, bawlhhlawh awm chhunte zinga pakhat chu ammonia . He ammonia hi kan taksa tan a toxic hle a, a bik takin thluak tan a toxic hle. Mi hrisel takah chuan urea cycle hian he toxic ammonia hi thil hlauhawm lo takah a chantir a, chu chu urea an ti a, chu chu zun-ah a paih chhuak leh thin.
Mahse, urea cycle disorder (UCD) vei tan chuan he thil hi a thleng dik lo. Chuvang chuan toxic ammonia chu taksa atanga lakchhuah ai chuan thisenah a pungkhawm thin. Hei hi hyperammonemia an ti a . Hei hi dinhmun hlauhawm tak a ni thei.
Chutah chuan he damdawi Carglumic Acid an tih hi a rawn pui ta a ni. He damdawi hian urea cycle a thawk tha lo a pui a, thisenah ammonia level a tihhniam bawk. Hei hian ammonia tam lutuk avanga hriselna lama harsatna lian tham (thluak chhiatna ang chi) a tihziaawm theih nan a pui a ni.
A pawimawh ber: Hei hi natna damdawi a ni lo. Mahse, natna thunun thei tur leh a kaihhnawih hlauhawmna tihziaawm thei tur enkawlna pawimawh tak a ni.
Damdawi ei hmaa doctor hnena hrilh tur thil
He damdawi hi a pek hma che chuan doctor chuan zawhna tlem a zawt ang che. Hengte pawh hi i chiang tur a ni.
- Carglumic Acid, damdawi dang, ei tur, ei tur rawng, emaw, a vawn that theihna tur allergy i neih chuan .
- Naupai emaw naupai tum emaw i nih chuan .
- Nu i fa hnute pe mek i nih chuan .
I himna atan he thu hi i doctor hnena pek a pawimawh hle.
Engtin chiah nge he damdawi hi ka hman ang?
Hei hi he thuziak pawimawh ber a ni. He damdawi hman dan hi a danglam bik hle. Chuvangin, heng step te hi uluk takin hre reng ang che.
| Step hrang hrang | Eng nge tih tur |
|---|---|
| 1. Liquid thlan dan | Tablet hmin nan hian tui thianghlim chauh hman tur a ni. Hemi atan hian tui dang (bawnghnute, thei in tur) emaw ei tur (buhfai, yogurt) emaw hman khap tlat a ni . |
| 2. Slice buatsaih dan | Heng tablets te hi ei vek suh, ei suh, chil suh . Doctor-in a tih angin tablet pakhat emaw a chanve emaw ei thin ang che. |
| 3. Melting tih a ni | Tablet pek zat (e.g. tablet pakhat emaw tablet chanve emaw) chu tui 2.5 ml tal (teaspoon chanve vel)-ah hmin rawh . A hmin hnuah in nghal rawh. |
| 4. Dose kimchang ei | Heng pill te hi tuiah a inthiar kim lo. White pieces a la awm. Chuvangin, damdawi i in zawh chuan, chu no khatah tui tlem tal dah belh la, uluk takin silfai la, chu tui pawh chu in rawh . Chumi hnuah chauh chuan a dose kimchang chu taksaah a lut ang. |
Naupangte hnena pek a nih chuan
He damdawi hi doctor-in a bik takin, nausen piang thar leh naupang tan pawh a pe thei a ni. Mahse, fimkhurna bik a neih avangin damdawi lam thupekte chu dik taka zawm a ngai a ni.
Damdawi dose khat ka ei loh chuan engtin nge ni ang?
Dose i miss a nih chuan i hriatreng veleh ei nghal rawh. Mahse, i dose leh tur hun a lo thleng tawh a nih chuan missed dose kha skip la, i dose leh tur chu a hun ruatah ei rawh. Double dose ei ngai suh.
Damdawi dose a san chuan engtin nge ni ang?
Damdawi pek aia tam i ei nia i hriat chuan damdawi in hnai ber Emergency Department (ETU) pan nghal rawh. A nih loh leh, Colombo National Hospital-a National Poisons Information Center-ah zawhfiah theih a ni.Call la, thurawn la rawh.
Side effect awm thei te chu engte nge ni?
Damdawi dang ang bawkin Carglumic Acid hian side effect engemaw zat a nei thei a ni. Hengte hi fimkhur a pawimawh hle.
| Side effect hrang hrangte thliar hranna | |
|---|---|
| Side effect na tak tak, doctor hnena hriattir nghal tur | |
Severe Allergic Reactions: Hengte hi a tlem hle a, mahse a hlauhawm hle.
| |
| Side effects hlauhawm lo tlangpui, mahse a awm reng chuan doctor hnenah hriattir tur a ni | |
| Luak chhuak | Pum a na |
| Kawthalo | Lu na |
| Chaw chakna | |
He list-a tel lo symptom dang danglam tak i neih chuan i doctor nen pawh chutiang lam chu sawipui rawh.
Damdawi hi engtin nge dik taka kan dahkhawm ang?
He damdawi hman tangkai dan hi i dah danah a innghat a, chuvangin heng thupekte hi dik takin zawm rawh.
- A hawn hmain: Damdawi bottle chu hawn a nih loh chuan fridge-ah dah rawh .
- A hawn hnuah: Bottle i hawn hnuah room temperature (15 leh 30 degree Celsius inkar) ah dah tur a ni . Refrigerah dah leh tawh suh . Moisture lakah venghim rawh. Bottle cap chu khar nghet takin dah la.
- Disposal: Bottle hawn atanga thla khat hnuah , emawExpiry date a liam hnuah damdawi la awm zawng zawng chu paih vek rawh.
- Hriselna: Damdawi hi naupang leh ran vulhte hmuh theih lohna hmunah dah fo ang che.
He damdawi hi i tan chauh pek a ni. I damdawi lam dinhmun a zirin a dose tur chu tihfel a ni tawh. Chuvang chuan he damdawi hi eng vangin pawh midang hnenah insem lo tur a ni.
Take-Home Thuchah a ni
- Carglumic Acid hi urea cycle disorder (UCD) nei te tan damdawi bik a ni a, thisenah toxic ammonia awm zat tihhniam nan a ni.
- He pill hi a pumin ei ngai suh. Tui tlemteah hmin fo la, in nghal rawh. Damdawi i in cup kha i in hmain tuiin silfai hmasa phawt ang che.
- Allergy symptom na tak tak i neih chuan i hmai, hmui, emaw, i rilru a na emaw a nih chuan damdawi in Emergency Department (ETU) ah kal nghal rawh.
- Damdawi bottle chu hawn hmain refrigerator-ah dah la, hawn hnuah room temperature-ah dah rawh. Damdawi la awm zawng zawng chu hawn atanga thla khat chhungin paih vek tur a ni.
- Damdawi ei kha bansan suh la, a dose thlak suh la, doctor thurawn tel lovin midang hnenah pe suh. Doctor hnenah checkup neihpui fo ang che.











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