I naute pum chhunga taksa peng hrang hrang a lo chhuak tawh em? He cloacal exstrophy an tih hi i zir dawn teh ang!

Nausen piang thar pum chu a lo insiam tha lo a, a chhunga awm tur taksa peng thenkhat a lo chhuak tih an hmuh chuan nu emaw, pa emaw chuan engtiang chiahin nge an hlau ang? Ngaihtuah thiam a har takzet. Mahse, lungngai suh. Hei hi thil awm lo tak ni mahse, a enkawlna tur a awm. He Cloacal Exstrophy an tih hi i hriatthiam theih tur awlsam takin i sawi dawn nia.

He cloacal exstrophy hi eng nge ni?

A awlsam zawngin sawi ila, Cloacal Exstrophy hi piansualna a ni a, naute chu an pum chhunga an lo seilian laiin an pum chhung bang a lo insiam tha lo a ni. Ngaihtuah teh, pum hnuai lam chu a inkhar tha lo a, naute zung leh a ril thenkhat, emaw, taksa peng dang emaw chu membrane te tak tein a khuh a, taksa atangin a chhuak chhuak ta a ni. Hei hi hmuh a har takzet. Hetiang dinhmun hian naute serh a nghawng bawk.

Hei hi congenital urinary anomaly tia hriat a ni bawk . Chumi awmzia chu nausen pum chhunga a la awm laia harsatna lo awm a ni tihna a ni. But don’t worry, after a few corrective surgeries , pian tirh atanga tan leh hun engemaw chen a awm hnuah, he natna vei naupang tam zawk chu nun pangngai, hlim takin an nung zel a ni.

Hei hian naute chu engtin nge a nghawng? OEIS complex chu eng nge ni?

Cloacal Exstrophy hi harsatna dang engemaw zat a awm avangin OEIS complex emaw OEIS syndrome emaw tia hriat a ni bawk. Eng nge an nih i en ang u:

Omphalocele chu eng nge ni?

Hei hi naute pum ruh, belly button bula awmte chu a inzawm tha lo a, hawnna a siam chuan a thleng thin. He hawnna hmang hian bladder, large intestine leh a chang chuan taksa peng dang, liver ang chi te chu a rawn chhuak chhuak thin. Mahse heng organ te hi an pop out mai lo va, protective membrane in a khuh a ni.

Exstrophy tih hi eng nge ni?

Hei hi naute bladder wall chu chhung lam ni lovin pawn lam a hawi lai a ni. Hei hi bladder exstrophy an ti a . Bladder hi a zungpui ni lovin a flat a, pahnih ah pawh a inthen thei bawk. Tin, pum ruh leh pelvic ruh emaw, kawr vel ruh te pawh a inzawm tha lo. Chuvang chuan pelvis chu a sir lehlamah a inzar pharh a, lehkhabu hawn zau tak ang mai a ni.

Imperforate anus tih hi eng nge ni?

Chutiang a nih chuan naute hnute, kan ek kan luhna kawngkhar chu a lo insiam tha lo. A block thei a, chutiang hawnna chu a awm lo thei bawk. Colon hi a tawi hle a, bladder nen pawh a inzawm thei bawk.

Spinal defects hi eng nge ni?

Naute pali zinga pathum vel chu cloacal exstrophy vei an niSpina bifida tih pawh a awm thei a, chutah chuan ruh ruhte chu a inkhar tha lo va, chu chuan ruhro chhehvela tuiin a khat sac (nerve nei pawh a ni thei) chu gap kaltlangin a rawn chhuak thei a ni.

Pawimawh: Naute chuan heng zawng zawng hi a nei thei a, a then chauh pawh a nei thei bawk. Heng zawng zawng hi Doctor ten uluk takin an enfiah vek ang.

Hei hian mipat hmeichhiatna peng hrang hrangah nghawng a nei em?

Ni e, Cloacal Exstrophy hian naute serh a nghawng bawk.

• Mipa naupang a nih chuan: Mipa zang chu a flat emaw, a tawi emaw, dinglam leh veilam emaw-ah a inthen thei bawk.
• Hmeichhia a nih chuan: Clitoris hi hmun hnih ah then theih a ni a, dinglamah pakhat leh vei lamah pakhat a awm thei bawk. Vaginal opening pahnih a awm thei bawk.

Hetiang dinhmun hi engtiang chiahin nge a awm?

Hei hi a awm lo hle a ni . A tlangpuiin naute piang 250,000 zinga pakhat atanga 400,000 zinga pakhat vel a ni. Tin, mipa naupangte hian hmeichhia aiin a let hnih atanga a let thum velin he natna hi an vei tam zawk bawk.

Exstrophy-epispadius complex (EEC) hi eng chi hrang hrang nge ni?

Cloacal exstrophy hi nau piangsual pawl pakhat , Exstrophy-Epispadias Complex (EEC) tia koh a ni. Dik tak chuan pawl zingah chuan a na ber chi a ni. Naute hian he group-ah hian condition pakhat chauh a nei thei a, a nih loh leh engemaw zat an nei dun thei bawk.

EEC category-a condition dangte chu:

• Epispadias: Hetiang dinhmunah hian naute zun (urethra), taksa atanga zun chhuahna tube chu a lo insiam tha lo.
• Bladder exstrophy: Hetiang dinhmunah hian naute bladder chu a chhung lam atanga pawn lam a inher thin.

Eng thilin nge cloacal exstrophy hi a thlen?

Doctor-te chuan naute ṭhenkhatin he natna hi an neih chhan chiang takin an hre lo a, mahse naupai kum thum chhunga tissue pakhat cloacal membrane an tih chu a tear emaw, a rupture emaw a nih chuan a thleng niin an ngai.

Cloaca hi naute chi thlah dan, chaw ei dan leh zun kawng inzawmkhawmna hmun a ni. A tlangpuiin heng system-a taksa peng hrang hrangte hi he cloacal membrane hian a inthen darh thin. Chuvangin he membrane hi a rupture chuan abdominal wall hi a insiam kim lo. Organ te hi an thang tha lo hle a, an inzawm dik lo pawh a ni thei. A tawpah chuan taksa peng thenkhat chu pum chhunga gap hmangin an rawn chhuak ta a ni.

Hetiang natna lan chhuah dan hi engte nge ni?

Cloacal exstrophy symptoms hi pian hnu lawkah hmuh theih a ni. I naute hian a hnuaia mite hi a tawng thei a ni:

• Organ te chu pum chhunga khur atang hian a lo chhuak a, chu chu sac ang maia insiam chhungah a ni.
• Sac ang chi hi ruh hnung lama gap atang hian a rawn chhuak a (hei hi Spina Bifida a ni).
• Penis emaw vagina emaw chu pahnih a inthen ang maiin a lang.

Engtin nge doctor-te hian hei hi an hriat chhuah?

Cloacal exstrophy hi naupai laiin nau neih hmaa ultrasound scan hmangin hriat theih a ni fo. I doctor pawhin nausen MRI scan neih a rawt thei bawk. Hei hian i naute taksa peng hrang hrangte thlalak chiang zawk a pe thei a ni. Heng scan te hian hetiang hi a lantir thei a:

• Bladder atang hian zun a luang tha lo.
• Pubic bones te hi an inthen a.
• Genitals size pangngai aia te zawk.
• Omphalocele tih awmzia chu naute pum chhungah umbilical cord a innghah hniam lutuk tihna a ni.

I naute a pian hnuah i doctor chuan MRI scan , abdominal ultrasound , emaw imaging scan dang emaw a ti thei ang. Hengte hian taksa peng hrang hrang hnathawh dan leh natna nasat dan a teh thei a ni. Heng zawng zawng hmang hian i doctor chuan i naute enkawlna tur ruahmanna tha ber a siam ang.

Cloacal Exstrophy hi engtin nge enkawl a nih?

Nau piang thar cloacal exstrophy vei apiang chu operation neih a ngai dawn a ni . He surgery-ah hian taksa peng hrang hrang lo chhuakte chu taksa chhungah dah lehin, pum leh hnungzang chhunga gap awmte chu khar a ni. I naute hian kum engemaw zat chhungin operation vawi tam tak a nei ngei ang. Hei hi staged reconstruction an ti a .

Nau piang zin enkawlna

Hetiang enkawlna hi naute a pian veleh tan a ni:

• Bladder siam thar leh a, taksa peng hrang hrangte chu pum chhungah dah leh a, pum chhunga gap awm chu khar.
• Stoma siam chhuah . Hei hi pum chhunga khur a ni a, chu chuan intestine lian atanga bawlhhlawh a kal tlang thei a ni. He stool hi pawn lam pouch (colostomy pouch) ah an khawl khawm thin. He colostomy pouch hi hun eng emaw chen atan a ni thei a, surgery dang tih a nih hma chuan.
• Spine chhunga gap awm chu khar.

Naupan lai atanga enkawl dan

Naute chu a upa deuh deuh chuan, chu chu naupan laiah hetiang hian enkawl a ni:

• Pelvic ruhte chu ruh surgery (osteotomy) tih a ni. Hei hian pelvis chu awlsam zawkin a khar thei a, naute a lo seilian chhoh zel chuan bladder tanpui tha zawk a pe bawk.
• Reproductive organs leh urinary tract te pawh siam that chhoh mek a ni.
• Anal opening siam a ni. Colon a sei tawk a nih chuan doctor chuan pull-through surgery hmangin colon chu anus nen a inzawm tir thei a ni. Chumi hnuah chuan stoma chu a khar ta a ni. Naute hian colostomy pouch a mamawh tawh dawn lo.

Hetiang dinhmun atang hian eng harsatna nge lo awm thei?

Surgery hmanga enkawlna hnuah cloacal exstrophy vei naupang tam zawk chu active, full life an hmang thin . Naupang thenkhat chu an lo puitlin chuan operation tam zawk an mamawh mai thei.

Cloacal exstrophy hian a hnuaia risk condition te hi a thlen thei a ni.

• Nau pai theih lohna.
• Kal natna te, kal natna te, kal (kidney stones) te, kal (kidney failure) te.
• Sexual dysfunction, mipat hmeichhiatna lama harsatna, etc.
• Urinary incontinence leh fecal incontinence te a awm bawk.

I doctor zawh tur thil

I naute doctor hnenah hetiang thil hi i zawt thei ang:

• Ka naute hi hriselna lama harsatna dang a vei theihna a sang zawk em?
• Cloacal Exstrophy enkawlna tha ber chu eng nge ni?
• Ka naute hian surgery engzat nge a mamawh ang?
• Operation hnuah eng complication nge ka fimkhur tur?
• Ka fa lo awm tur pawhin Cloacal Exstrophy a vei theihna chance engzat nge awm?

I naute hian Cloacal Exstrophy, emaw OEIS syndrome a nei tih i hriat chuan hlauhna leh lungkhamna i neih hi thil pangngai a ni. Mahse, nangmah chauh i ni lo tih hre reng ang che.

Hriat reng tur pawimawh ber chu

I naute hian Cloacal Exstrophy a vei tih i hriat chuan i rilru a buai leh hlauthawng tih hi thil awmdan pangngai a ni. Mahse, lungngai suh . I doctor leh medical team te chuan nang leh i naute tanpui turin an inpeih reng a ni. I naute hian a pian hnu lawkah operation vawi engemaw zat a mamawh ang a, chutah chuan a taksa peng hrang hrangte siam danglam turin operation tam zawk a mamawh ang.

Mahse a ṭha ber chu, enkawl ṭhat a nih chuan, he natna neia piang naupang tam zâwkte chu nun pangngai leh hlim takin an nung ṭhîn . Zawhna emaw, ngaihtuahna emaw i neih chuan i doctor nen sawiho rawh. Engkim an hrilhfiah ang che.

` Cloacal Exstrophy, Nau piangsual, OEIS Complex, Omphalocele, Bladder Exstrophy, Naupang enkawlna