Nu emaw, pa emawin nausen piang thar an en huna an hlimna chu sawifiah theih loh a ni. Mahse, a châng chuan chu hlimna rual chuan hlauhna leh manganna nasa tak i neih hun a awm ṭhin. Chu chu doctor rawn kal a, i fain pianpui harsatna a neih thu a hrilh che chuan i rilru put hmang chu a ni. Cloacal Malformation hi chutiang natna hlauhawm tak a ni a, mahse nu leh pate tithinur thei tak a ni. Vawiin hian he thu hi awlsam takin, i hriatthiam theih dan tur angin kan sawi dawn a ni.
A awlsam zawngin Cloacal Malformation chu eng nge ni?
Hei hi thil awm lo tak a ni a, hmeichhe naupang chauh a nghawng a, pian tirh atanga hmuhchhuah a ni. A tlangpuiin hmeichhe naupang perineum hian kawngkhar pathum a nei tur a ni: urethra, vagina leh anus.
Mahse, Cloacal Malformation nei naupang chuan heng opening pathumte hi a nei vek lo. Chu ai chuan, hawnna pakhat chauh a awm . He natna hi natna pawl pakhat, anorectal malformation an tih zingah a tel a ni.
Ngaihtuah teh, naute chu a pum chhunga a lo seilian lai hian naute intestinal tract, genital tract leh urinary tract te chu unit pakhat angin an inzawm khawm vek a ni. Hei hi "cloaca" kan ti a. Naute a lo seilian chhoh zel chuan he unit pakhat hi zawi zawiin hmun thumah a inthen a, kawngkhar hrang hrang pathum a siam a ni.
A châng chuan, he inṭhenna kalphung hi a thleng dik lo. Tichuan system pathumte chu an inzawm khawm a, common channel pakhatah an inzawm khawm a, pawn lam hawiin kawngkhar pakhat chauh hmangin an inhawng ta a ni. Chu chu Cloacal Malformation kan tih chu a ni.
Hetiang dinhmun enkawlna chu operation pakhat chauh ni lovin opening hrang hrang pathum siam a ni. He surgery hi naupang dam kum khatna chhungin tih a ni tlangpui.
Hetiang dinhmun hi chi hrang hrang a awm em?
Ni e, he dinhmun hi naupang tinah hian danglamna tlemte nen hmuh theih a ni. Mahse naupang zawng zawngte tana thil awm dan chu pathum ni lovin hawnna pakhat an nei hi a ni. He hawnna hi a hmaa kan sawi tawh "common channel" nen hian a chhungril lamah a inzawm tlat a ni. He common channel sei zawng hian natna nasat dan leh naupangin eng enkawlna nge a mamawh tih a hril a ni. He channel hi khawi hmunah pawh centimetre 1 atanga 10 thleng a sei thei a ni.
Hei hi tlem han sawifiah leh ila.
| Channel chi hrang hrang hman tlanglawn tak | Hrilhfiahna |
|---|---|
| Common Channel tawi tak a ni | Chutiang a nih chuan system pathum inzawmna chu taksa pawn lama hawnna nen a inhnaih hle a ni. Chu chu common duct a tawi tihna a ni. Chumi awmzia chu naupang chuan taksa atanga bawlhhlawh leh zun paih chhuah kawngah harsatna a nei vak lo tihna a ni. Chutiang naupangte dam lehna rate leh hmalam hun tur chu a tha hle tlangpui. |
| Long Common Channel a ni | Hei hi thil buaithlak deuh a ni. System pathum inzawmna hi taksa chhungah a thuk hle. Chuvangin common duct chu a sei hle. He duct sei tak hian naupang chu ek leh zun chhuah a ti harsa a, a tikhawlo bawk. Surgery pawh a buaithlak deuh thei bawk. |
Hetiang dinhmun hi engtiang chiahin nge a awm?
Hei hi thil awm lo tak a ni a, nau piang thar 25,000 atanga 50,000 zinga pakhat vel ah a thleng thin.
Hei hi eng symptoms nge ni?
A zia ber leh langsar ber chu pian tirh lamah hawnna pathum ni lovin pakhat chauh hmuh theih a ni.
Tin, heng naupangte hian hriselna lama harsatna dang an nei thei bawk.
- Clitoris hi mipa penis angin a awm a.
- Anal area-a thil awm dan pangngai lo.
- Vagina, uterus emaw cervix-ah hmun khat aia tam.
- Kidney, ureter, emaw urinary system-a harsatna dang (urological problems).
- Lung emaw ruhro emaw lama harsatna nei.
- Chaw ei leh in lama harsatna dang (Gastrointestinal problems).
Engvangin nge hetiang hi a lo awm? Eng nge a chhan?
Doctor-te chuan hei hi chhan chiang tak an la hmu lo. Random occurrence, a nih loh leh chhan bik nei lo thil thleng anga ngaih a ni.
Hei hi nu leh pa i nihna anga i thil tih leh i sawi vang a ni lo tih hriatthiam hi a pawimawh ber a ni. Hei hi i sualna a ni lo.
Engtin nge he dinhmun hi kan hriat theih ang?
He dinhmun hi kawng hnih in hriat theih a ni.
1. Naute pian hma (naupai lai) .
A châng chuan, naupai kar 20 vêlah anomaly scan emaw ultrasound emaw hmangin hei hi hriat theih a ni. Hei hi naute serh (vagina) a hring a, tuiin a khat angin kan hmu tlangpui. Hei hi finfiah a ngai a nih chuan naupai laiin MRI scan theih a ni.
2. Naute a pian hnuah
Hei hi naute pian hnuah naupang enkawltu doctor-in naute a enfiah hian a hriat chhuah fo thin. He dinhmun hi pathum ni lovin hawnna pakhat a awm chuan hriat theih a ni. Naute pum pawh a hring thei bawk. Chumi hnuah doctor chuan taksa chhunga thil thleng dik tak hriat theih nan test eng emaw zat a ti ang.
- Ultrasound examination: Naute kal (kidney), bladder leh ruhro te enfiah thin ang che.
- X-ray test: I fa zun kawng hnathawh dan hriat nan X-ray technology bik, fluoroscopy ang chi hmang la.
- Echocardiogram: Thinlung lama harsatna awm leh awm loh enfiahna test a ni.
Engtin nge enkawl a nih? Surgery chungchang i zir dawn teh ang
Hetiang dinhmun enkawlna awmchhun chu operation a ni. Surgery tum ber chu hawnna pakhat ni lovin hawnna hrang hrang pathum siam a ni a, chu chuan naupang chu a pangngaiin a zun leh a chhuah theih nan leh heng thilte hi a thunun thei a ni.
Hetiang enkawlna hi a tlangpuiin stage engemaw zatah a thleng thin.
A hmasa ber: Naute a pian veleh
Hei hi naute pian atanga darkar 48 chhungin tih thin a ni. Hetah hian a tum ber chu naute hriselna tihngheh leh taksa atanga bawlhhlawh leh zun chhuahna kawng siam a ni.
- Colostomy: Hetiang tih danah hian surgeon chuan naupang intestine lian tak thenkhat chu a pum chhunga vun chung lamah a rawn hruai a, hawnna a siam thin. Chumi hnuah chuan stool chu a hawnna atang chuan a chhuak a, a chhunga bag bik dahkhawmah a khawl khawm ta a ni. Hei hi naupangin operation lian tak a neih hma loh chuan hun eng emaw chen atana tih tur a ni.
- Catheterization: Naupang zun chhuah pui turin catheter dah a ni a, a chhan chu bladder a hring emaw a block emaw vang a ni.
- Vaginal drainage: Nausen vaginal drainage a hring a, tui a awm khawm chuan surgery hmangin a chhuak thei bawk.
Stage hnihna: Major Reconstructive Surgery tih a ni
He surgery lian tak hi thla 6 leh thla 12 inkar, naupang hriselna a nghet lai hian tih a ni. Hei hi system pathum inzawmkhawmte chu inthen a, hawnna hrang hrang pathum (anus, vagina, leh urethra) siamna hmun a ni.
- Common fallopian tube hi a tawi (cm 4 aia tlem) a nih chuan he surgery hi a awlsam hle.
- Common duct a sei chuan surgery chu a buaithlak deuh deuh thin.
Chutiang surgery atan chuan naupang surgeon leh naupang urologist, he lam hawia hriatna leh tawnhriat bik nei te hi an pawimawh hle.
Stage Pathumna: Colostomy tihdanglam
Naupang chu main surgery atanga a dam kim hnuah chuan original colostomy chu tihdanglam a ni. Chu chu, pum chhunga hawnna siam chu khar a ni a, ek chu hnute siam thar atang chuan a pangngaiin a kal theih nan a phalsak tihna a ni.
Ka fa hian eng ang hmalam hun nge a neih ang?
Hei hi nu leh pa zawng zawng rilrua zawhna lian ber a ni. A tlangpuiin result a tha hle.
- Naupang common duct tawi, a complex lo zawk tihna a ni a, 90% zetin zun chhuah dan pangngai leh bowel control theihna chance 90% an nei a ni.
- Naupang common duct sei tak, i.e., complex condition nei te pawhin zun leh bawlhhlawh paih danah thuneihna tha tak an neih theihna chance 70% an nei a ni.
Naupang tam zawk hi chu a pangngaiin an ek chhuak thei a ni. Amaherawhchu, naupang thenkhat chuan zun insum theih lohna an nei thei a, chu chu duh loh vanga zun tlakchhamna a ni. Naupang thenkhat chuan ni khatah vawi tam tak catheter hmangin an bladder an tihthianghlim a ngai mai thei.
Sex nun leh naupai chungchang
Hetiang natna nei naupangte hian an lo puitlin hunah sex nun hlimawm tak an nei thei a ni. Naupai hi a pangngai aia harsa zawk mah se, fa neih theih loh tihna erawh a ni lo. Nakin lawka fa i beisei a nih chuan hemi chungchangah hian doctor thurawn i la thei ang. Nau neih dawnin C-section neih a tha fo thin.
Nu leh pa angin eng nge ka tih theih ang?
He zinkawng hi naupang leh nang tan pawh a harsa hle.
- I fa tana thurawn pe rawh: I fa healthcare team te nen inbiakna neih fo thin ang che. I ngaihtuahna emaw hlauhna emaw i neih chuan anmahni hnenah hrilh rawh.
- Schedued clinic leh test te chu tlawh loh tur: Surgery hnuah naupang system te a thawk tha em tih enfiah chhunzawm zel a ngai a ni.
- Symptoms fimkhur rawh: I fate a lo seilian chhoh zel chuan zun emaw, bowel control-na lama harsatna i hmuh chuan i doctor hnenah hrilh nghal rawh.
I doctor zawh tur zawhna thenkhat:
- Engtin nge he surgery hi tih a nih? Kum engzat nge tih a nih?
- Ka fa hian hrehawm a ti ang em? Tunah hian a na em?
- Operation hnua dam leh hunah eng nge ka beisei ang?
- Naupang chu a lo puitlin chuan operation tam zawk a mamawh dawn em?
- Nakin lawkah ka rectum, urethra, emaw vagina emaw-ah harsatna ka nei dawn em?
- Ka fanu hian nakin lawkah him takin fa a nei thei dawn em ni?
Hetiang thil i zir hian thinlung a na tih hi thil pangngai tak a ni. Mahse, tunlai hian medical science hi a hmasawn hle tih hre reng ang che. Surgery hian he dinhmun hi hlawhtling takin a siam tha thei a, i fa chu nun pangngaiin a hmang thei a ni. I doctor leh healthcare team te hian he zinkawngah hian nang leh i fate tanpuitu tha tak an ni ang.
Take-Home Thuchah a ni
- Cloacal Malformation hi natna hlauhawm tak a ni a, naute hmeichhia chauh a nghawng a, an pian tirh atanga hmuhchhuah a ni.
- Hetah hian urethra, vagina leh anus tan hawnna hrang hrang awm lovin, hawnna tlangpui pakhat chauh a awm a ni.
- Hei hi a chhan bik a awm lo va, nu leh pa te tihsual vang pawh a ni lo.
- Enkawlna hi a pumpuiin surgery hmanga enkawl a ni a, stage hrang hrang a awm a ni.
- Surgery hlawhtling tak an neih hnuah naupang tam zawk chuan an bowel leh bladder function te an control thei a, nun pangngai leh hlim takin an nung thei a ni.
- Chumi atan chuan specialist pediatric surgeon te puihna leh hun rei tak chhunga medical supervision neih a pawimawh hle.











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