Nu ni tur i nih angin, khawsik i neih pawhin a chang chuan hlauhna leh lungkhamna tlem i nei em? A pangngai hle mai. I pum chhunga i naute hlu tak kha i ngaihtuah nasa em avangin. Chuvang chuan, vawiinah hian naupai laiin nuin rubella a vei a nih chuan pum chhunga naute a nghawng theih dan tur kan sawi dawn a ni. Hei hi doctor-te’n Congenital Rubella Syndrome (CRS) an tih chu a ni. A hming hi sei deuh mah se, awlsam takin i hrethiam ang u.
Congenital Rubella Syndrome hi eng nge ni?
A awlsam zawngin sawi ila, congenital rubella syndrome (CRS) hi nu naupaiin rubella (German measles tia hriat bawk) a vei hian naute hriselna lama harsatna awm thin a ni. Hetah hian "congenital" tih thumal hi "pian tirh laia awm" tihna a ni.
Rubella virus hi naute taksaa a luh chuan nausen pianphungah kawng hrang hrangin a nghawng thei a ni. Heng nghawngte hian naute a pian hnuah pawh harsatna a thlen thei a ni. Entirnan, mitdel emaw, pianpui thinlung natna emaw. CRS nasat dan hi mi hrang hrangah a inang lo thei. A tam zawkah chuan nuin naupai tirh lamah rubella a vei a, a bik takin kar 13 hmaa rubella a vei chuan a na zawk.
Hetiang dinhmun hi engtiang chiahin nge a awm?
America ang ramah chuan congenital rubella syndrome (CRS) vei an tlem hle a, a chhan chu rubella vaccine hi an hmang nasa hle a ni. Mahse, khawvel pum kan en chuan kum tin CRS vei 100,000 vel an awm thin tih hi ngaihtuahawm tak a ni. Kan ramah pawh rubella vaccine hi ram pum huapa vaccination program-ah telh a nih avangin he dinhmun hi control a ni ta. Mahse, awareness hi a pawimawh hle.
Congenital rubella syndrome natna lan chhuah dan chu engte nge ni?
He CRS natna lan chhuah dan leh a nasat dan hi mi hrang hrangah a inang lo thei hle a, ka sawi tawh ang khan. Naupai laiin nuin rubella a vei hma chuan naute hian natna lan chhuahna na tak a nei tam zawk thin. A châng chuan CRS natna hi a na lo a nih chuan pian tirh lamah chhinchhiahna langsar tak a awm lo thei bawk.
Hengte hi naute pian hnua hmuh nghal theih chhinchhiahna hmasa ber thenkhat chu an ni:
- Nau piang rit lo.
- A châng chuan i naute vunah hian blue-purple circular spot emaw blister emaw i hmu thei bawk. Mi thenkhat chuan hei hi "blueberry muffin rash" an ti a, a chhan chu blueberry muffin-a spot awm ang mai a nih vang a ni.
- Vun (Purpura)-ah hian purple, red, emaw brown emaw a awm a, a hring (Purpura) a awm bawk.
- Naute lu chu a pangngai aia te zawk (Microcephaly) a ni.
Naute pian hnu lawka lo lang thei symptom dangte chu hengte hi a ni:
- Congenital cataract leh mit pressure sang (Glaucoma) a awm bawk.
- Pianpui Lung natna. Hengte hi chi hrang hrang a awm a. Entirnan, thinlung chamber inkara khur (Ventricular Septal Defects, Atrial Septal Defects), thinlung chhunga thisen kalna kawng hrang hranga harsatna (Patent Ductus Arteriosus, Peripheral Pulmonary Artery Stenosis) etc. Hengte hi Doctor ten chipchiar zawkin an hrilhfiah ang che.
- Developmental Delay: Chumi awmzia chu naute chu an kum nena inmil takin, a kekawrte, a thut, a kal leh a thusawiah a tlai tihna a ni.
- Liver emaw spleen emaw a lian (Hepatosplenomegaly).
- Hriatna hloh. A châng chuan hei hi bengchheng famkim thlengin a kal thei a ni.
- Hemolytic anemia hi thisen sen (red blood cells) a chhiat vang a ni.
- Thil hriatna lama harsatna nei.
- Pneumonia natna (Pneumonia) a ni.
- Thluak leh meninges-a natna (Meningoencephalitis) a awm.
- Pigmentary Retinopathy natna a ni.
- Ruh natna te.
- Lymph node a lo hring chhuak.
Pawimawh: Nausen Congenital Rubella Syndrome (CRS) neia piangte chu an naupan laiin insulin-dependent diabetes leh thyroid natna vei theihna a sang hle.
Hei hi eng nge a chhan?
Congenital rubella syndrome (CRS) awm chhan ber chu naupai laiin rubella i vei vang a ni. Chumi hnuah rubella virus chu nu hnen atangin nausen (placenta) kaltlangin a kal a, nausen pum chhunga naute chu a kai ta a ni. He virus hian nausen cell te a tichhe thei a, naute taksa peng hrang hrang hmasawnna a nghawng thei bawk. Hei vang hian nau piang laia hriselna lama harsatna awm thin a awm thin.
He hlauhawmna hi eng ang nge a nih tih han ngaihtuah teh:
- Nuin naupai kar 12 hmasa berah rubella a vei a nih chuan CRS hian nau piang thar 85% vel a nghawng thei a ni.
- Naupai kar 13 leh kar 16 inkar a kai chuan nau piang thar 50% thleng a nghawng thei.
- Second trimester second half-a kai chuan nau piang thar 25% vel a nghawng thei a ni.
Rubella hi natna hrik `(RuV)` an tih atanga lo chhuak a ni. A lan chhuah dan ber chu vun sen, itchy rash a ni a, a tlangpuiin hmaiah a intan a, taksa pum puiah a darh thin. Hei hi tunah chuan ram tam takah vaccine pek a nih avangin a tlem tawh hle. Mahse, khawvel hmun thenkhatah chuan rubella hi a la awm reng a ni.
CRS vei naute hian natna hi an thehdarh thei em?
Ni e, chu chu a pawimawh. Doctor-te chuan naute pianpui rubella syndrome nei chu kum khat tal chu kai theih niin an ngai. Mahse, naute chu thla 3 mi a nih a, rubella test pahnih, thla khat inkar a nih chuan `negative` (virus a awm lo tihna) a lo let leh a nih chuan, a kai thei tawh lo tihna a ni. Chuvangin chumi hun chhung chuan midangte venhimna kawngah a bik takin fimkhur a tul hle.
Engtin nge he CRS natna hi hriat chhuah a nih?
Congenital rubella syndrome hi hriat theih dan kawng hrang hrang a awm a:
- Naupai screening: Ram tam takah chuan naupai tirh lamah rubella leh natna dang engemaw zat screening hi standard practice a ni. Naupai laiin rubella symptoms i neih chuan i doctor chuan i natna hriat chian nan test a ti ang. Chumi hnuah chuan i nautein CRS a vei theih dan tur an hrilhfiah ang che.
- Naupai laiin nausen (fetal diagnosis): Naupai laiin rubella i vei a nih chuan i doctor chuan i nauteah hri hi a darh tawh em tih enfiah turin special test engemaw zat neih a rawt thei ang. Entirnan, amniocentesis, chorionic villus sample lak te, nausen thisen lak te. Hengte hi test buaithlak zawk a ni a, i doctor chuan a tul chuan a ti mai ang.
- Pian hnua natna hriatchhuah dan: Naute pian hnuah thisen test (ELISA test) hmangin naute thisenah rubella virus laka antibody a awm leh awm loh enfiah theih a ni. Naute hian rubella virus a vei em tih enfiah nan zun sample, saliva sample emaw, hnar swab emaw pawh test theih a ni bawk. Doctor chuan heng test hi a ti thei a, naupai laiin nuin rubella a vei tih hriat a nih chuan, emaw, naute hian CRS chhinchhiahna a lantir a nih chuan.
I naute chu rubella a vei tih finfiah a nih chuan, medical team chuan naute hriselna zawng zawng enfiah nan leh CRS avanga hriselna lama harsatna dang eng nge awm thei tih hriat nan test dang eng emaw zat neih belh an rawt ang.
Hei hi eng enkawlna nge ni?
Vanduaithlak takin congenital rubella syndrome (CRS) hi damdawi leh direct treatment a awm lo. Tin, a nghawng thenkhat, hriatna hloh leh rilru lama harsatna te hi a awm reng a, chu chu dam chhung zawng a daih tihna a ni. Mahse, a lan chhuah dan thenkhat, hemolytic anemia leh interstitial pneumonia te hi enkawl emaw, enkawl emaw theih a ni. Lung lam natna thenkhat chu operation hmanga enkawl theih a ni bawk.
I naute damdawi lam team chuan i naute natna lan chhuah dan leh a mamawh dan azirin enkawlna tur ruahmanna bik an siam ang. Hei hian specialist tam tak puihna a ngai mai thei.
Ka naute hian CRS a vei a nih chuan eng nge ka beisei ang?
Congenital rubella syndrome hian naute zawng zawng hi a nghawng dan inang vek lo va, a nasat dan pawh a inang lo thei hle. CRS hian i naute a nghawng dan kimchang taka hriat theih nan test leh assessment engemawzat a ngai dawn a ni. Hun tikhawtlai tak a ni thei. Mahse he zinkawngah hian nangmah chauh i ni lo. I naute medical team chuan i kalna apiangah an awmpui ang che, CRS chu eng nge a nih tih leh i naute hmalam hun leh i chhungte a nghawng dan tur an hrilhfiah ang che.
He CRS condition hi ka veng thei ang em?
Awle! Hei hi a pawimawh ber a ni. Congenital Rubella Syndrome (CRS) hi a tam zawkah chuan ven theih a ni!
Chutianga tih dan tha ber chu naupai hmaa rubella virus laka invenna pek hi a ni. Chu chu rubella vaccine lak tihna a ni.
Sri Lanka-ah chuan naupangte chu MMR vaccine kan pe a, chu chuan measles, mumps leh rubella lakah a veng a ni. Dose hmasa ber hi thla 9-12 inkarah pek a ni tlangpui a, a pahnihna chu kum 3 inkarah pek thin a ni (heng hun hi ram pum huapa vaccination schedule a zirin a danglam deuh thei a, chuvangin i awmna hmuna health officer hnenah zawt rawh).
Naupan laia vaccine i la lo a nih chuan, a nih loh leh i chiang lo a nih chuan, tunah hian i doctor nen inbiakna neih a pawimawh. Puitling anga vaccine i lak chuan vaccine i lak hnu ni 28 (thla khat vel) chhung chu naupai loh tur a ni tih hre reng ang che. Hei hi thurawn pawimawh tak a ni.
CRS vei ka naute hi engtin nge ka enkawl ang?
I naute hian CRS natna a neih hriselna lama harsatna a neih dan azirin, a lo upat deuh deuh chuan damdawi lam enkawlna leh enkawl chhunzawm zel a ngai mai thei. I naute tan i advocate a, an mamawh damdawi lam enkawlna leh puihna tha ber an hmuh ngei ngei a pawimawh. Hei hian i naute chu nun tha ber a neih theih nan a pui ang.
Congenital rubella syndrome hi naute hriselnaah nghawng na tak a nei thei a ni. Mahse thu lawmawm tak chu rubella vaccine (MMR vaccine) hmang hian a tam zawkah chuan ven theih a ni. A theih phawt chuan naupai hmain doctor pan hmasa phawt la, rubella leh natna hrik kai dangte laka i him em tih enfiah hmasa phawt ang che. Nang leh i naute tan pawh tanpuina tha tak a ni.
Thil pawimawh tak tak hriat reng tur (Take-Home Message) .
Kan sawi tawh atang hian thil engemaw zat hriat reng tur a awm a:
- Congenital rubella syndrome (CRS) hi natna khirh tak a ni a, naupai nuin rubella a vei chuan nausen a vei thei a ni.
- Hei hian naute chu a pian tirh atangin hriselna lama harsatna hrang hrang (mit, beng, thinlung, thluak) a neih tir thei a ni.
- A pawimawh ber chu MMR vaccine hmang hian hei hi a tam zawkah chuan ven theih a ni.
- Naute i beisei a nih chuan i naupai hmain rubella laka i him em tih doctor zawt rawh . A tul chuan vaccine lak thin ang che.
- MMR vaccine i lak chuan thla khat tal naupai loh tur a ni.
- Naupai tawh a, rubella i rinhlelh chuan damdawi lam thurawn la nghal rawh.
He thu hi i tan a tangkai ngei kan beisei. Chhungkaw hrisel chu hlimna ropui ber a ni!
` Congenital Rubella Syndrome, CRS, Rubella, German Measles, Naupai, Rubella vaccine, MMR vaccine, Naupang hriselna, Pianpui natna











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