I nau piang thar hian bawnghnute a in veleh khuh leh gagging a tan em? A hmuiah a foam em? Nge a vun chu a sen hmel em? Nu leh pa angin heng thilte hi i hmuh hian hlauhna leh lungkhamna nei hi thil pangngai tak a ni. Hetiang symptoms hi a chang chuan nau piangsualna awm lo tak, mahse na tak , Esophageal Atresia (EA) tih chhinchhiahna a ni thei bawk. He hming i hriat hian hlau suh. Vawiin hian a zawng zawng hi i hriatthiam theih tur awlsam takin kan sawi dawn a ni.
Esophageal Atresia (EA) hi eng nge ni?
A awlsam zawngin sawi ila, Esophageal Atresia hi piansualna a ni. I naute esophagus, ka atanga chaw ei tur phurtu tube a siam kim loh chuan a thleng thin. "Atresia" tih thumal hian taksa chhunga kalkawng pakhat chu a inkhar emaw, a inkhar emaw tihna a ni. Hetiang dinhmunah hian chaw kawng (esophagus) chu pum nena inzawm tur hmunah a block a ni. Chuvang chuan naute chuan a pangngaia ei leh in tur a nei tawh lo.
Hei hi han ngaihtuah teh, a laiah tui pipe a chhe a, hmun hnih a inthen ang mai a ni.
Hetiang dinhmun hi a buaithlak deuh thei. EA vei naute 90% vel pawhin harsatna dang an nei bawk. Tracheoesophageal fistula (TEF) an ti a ni. Hei hi chaw kawng (esophagus) siam \ha lo chu thlipui, thlipui (windpipe) nen a inzawm hian a ni. Hei hi a hlauhawm hle a ni, a chhan chu naute ei tur thil, hmui pawh hi pum chhungah ni lovin lung chhungah a lut thei a ni. Chutiang a nih chuan naute chuan thawk a harsat ang a, a chok ang a, lung infection pawh a nei thei bawk.
Hetiang dinhmun hi eng chi hrang hrang nge ni ber?
Esophageal atresia hi chi hrang hrangah then a ni a. Chungte chu chaw kawng (esophagus) kha khawiah nge a block tih leh thlipui (windpipe) nena a inzawm leh inzawm loh leh a inzawm dan a zirin an thliar hrang thin. Hei hi a buaithlak deuh thei a, mahse hriatthiam awlsam zawk nan a hnuaia table hi en la.
| Lampang | A awlsam zawngin sawifiah a ni |
|---|---|
| Type A tih a ni | Chutiang a nih chuan trachea chu trachea nen a inzawm lo. Mahse, trachea chunglam leh hnuai lam chu a inthen a, a tawp chu a inkhar a ni. A hmun pahnih inkarah hian inthlauhna lian tak a awm a. |
| Type B tih a ni | Hei hi a tlem hle. Trachea chunglam chu trachea nen a inzawm a ni. A hnuai lam chu a hranin khar a ni. |
| Type C. tih a ni | Hei hi a tam ber chi (85% vel) a ni. Trachea chunglam chu khar a ni a, a hnuai lam erawh chu thlipui (windpipe) nen a inzawm tlat thung. |
| Type D tih a ni | Hei hi a tlem ber leh a na ber chi a ni. Trachea chunglam leh hnuai lam pahnih hi thlipui (windpipe) nen a hranin an inzawm a ni. |
Doctor ten heng chi hrang hrang zingah hian i naute hian eng chi nge a neih tih hriat nan test hrang hrang an nei ang. Chumi ang chuan enkawl dan tur ruahman a ni.
Naute hian he natna hi a nei tih hriat theihna tur symptoms engte nge ni?
He natna hi rang taka hriat theihna tura doctor leh nurse-te hman thin chhinchhiahna lian pathum a awm a. "Three Cs" an ti bawk.
- Khuh a awm
- Choking (a tlakbuak) .
- Cyanosis (vun rawng dum danglam) .
Cyanosis hi taksain oxygen a dawn tlem chuan vun, a bik takin hmui leh kut zungtang te chu a sen a nih chuan a ni.
Heng thil pawimawh tak takte bakah hian thil dang pawh i hmu thei ang:
- Naute hmui chu foamy mucus tam takin a khuh a.
- A pangngai aia tam drooling emaw, bawnghnute riltam emaw.
- Duhthusamin bawnghnute pek ka tum hian a rilru a na a, a chok bawk.
- Thâwk a harsa chho zel a, i thawh lai hian thawm mak tak mai a awm bawk.
Natna chi hrang hrang, ei harsatna thlentu tam tak awm mahse, ei leh in hi thawk harsatna nen a inzawm chuan Esophageal Atresia leh Tracheoesophageal Fistula te hi a awm tih chhinchhiahna chak tak a ni fo thin.
Engvangin nge naute chungah hetiang hi a thlen? A chhan ber chu eng nge ni?
Hei hi piansualna kan ti a. Nausen pum chhunga a seilian laia inthlak danglamna avanga lo awm a ni. A tlangpuiin nausen pian tirh lamah chuan esophagus leh trachea te hi tube pakhat an ni vek a. A hnuah chuan hmun hnih ah a inthen a, tube hrang hrang pahnih ah a lo thang lian ta a ni. Esophageal Atresia lo awm chhan ber chu tube pakhat ni thin structure chu a inthen a, a lo thang chak tawh lo vek a ni.
Mahse, scientist-te chuan, "Engvangin nge chu thanna chu a chanve velah a tawp?" Hemi kawngah hian genetic factor leh environment factor pahnih hian nghawng a nei thei niin an ngai. Chu chu naute DNA-a inthlak danglamna thenkhat leh naupai laiin nuin a hmachhawn tur boruak inthlak danglamna thenkhat chu a chhan a ni thei tihna a ni.
Risk factors a awm em?
He natna hi a thlen chhan dik tak finfiah ni lo mah se, zirchiangtute chuan EA vei naute piangte mizia tlangpui engemaw zat an hmuchhuak a ni. Chungte chuan a hlauhawmna chu tlem a tipung thei a ni:
- Nu kum 35 chunglam leh/ emaw pa kum 40 aia tam a ni.
- Artificial insemination hmanga fa neih (IVF, IUI ang chi).
- Twins emaw triplet emaw neih.
Tin, EA hi piansualna dang leh genetic syndromes te nen pawh inzawm anga hmuh a ni fo bawk. Entir nan:
- Trisomy (kum 13, 18 emaw 21 emaw) .
- VACTERL pawl a ni
- CHARGE syndrome tih hi a ni
- Pianpui thinlung natna
- Digestive system tibuaitu dangte (GI atresias) .
- Kidney leh genitourinary system lama chhiatna
Engtin nge doctor-te hian he natna hi an hriat theih? (Diagnosis) tih a ni.
A tam zawkah chuan he natna hi naute pian hnuah hmuhchhuah a ni. Mahse, a châng chuan nau neih hmaa scan hian clues a pe thei a ni.
- Naute pian hma: Kar 20 vel a i anatomy scan laiin naute chhehvela amniotic fluid awm zat chu a tlangpui aia tam a nih chuan (hei hi polyhydramnios an ti a), doctor chuan a ringhlel mai thei. Hei hi a chhan chu naute hian a tlangpuiin hetiang tui hi a ei thin vang a ni. Naute hian a ei thei lo a nih chuan a tui chu a pung zel a ni. Tin, scan laiin naute pum chu a hring (a pum bubble tlem emaw awm lo emaw) a lang a nih chuan chu chu chhinchhiahna dang a ni.
- Naute pian hnuah: Naute hian a pian hnu lawka kan sawi tawh ang chi natna lan chhuah dan (khuh, khuh, blueness) a lantir chuan doctor-te chuan hei hi an ringhlel nghal a ni. Hei hi finfiah nan test awlsam ber chu naute hnar emaw hmui emaw atanga tube te tak te (nasogastric tube) dah a, pum chhunga luh tum hi a ni. Esophagus a block chuan tube chu pum chhungah a lut thei lo. A chanve vel chu a ding ta a.
Tichuan, X-ray hmangin chu chu finfiah a ni a, eitur kawng (esophagus) hian eng chi defect nge a neih tih chiang taka hriat a ni. X-ray hmang hian lung chhungah tui a lut em tih emaw, pum chhungah boruak a lut em tih emaw a hriat theih bawk. He diagnosis a nih hnuah hian doctor chuan naute chu a kaihhnawih piansualna dang a neih leh neih loh a enfiah bawk ang.
Engtin nge enkawl a nih? Hei hi tihdam theih a ni em?
Awle! Hei hi dam theih dinhmun a ni ngei ang. Hei hi enkawlna awm chhun chu surgery a ni.A tam zawkah chuan he surgery hi naute pian hnu lawkah tih thin a ni.
Operation hmaa enkawl dan tur
Surgery an tih hmain doctor-te chuan naute dinhmun tihngheh nan hma eng emaw zat an nei ṭhin.
- Stabilizing breathing: Thlawhnaa mucus leh phlegm awm khawmte chu lung a thlen loh nan tube (suction) hmangin an la chhuak fo thin. Nausen thaw a harsat chuan ventilator-ah an thlunzawm thin.
- Ei leh in him pek: Naute chu ka hmanga chaw pek theih a nih loh avangin ei tur mamawh chu vein ( parenteral nutrition ) emaw, pum chhunga dah nghal tube emaw ( enteral nutrition ) hmangin pek a ni.
- Infection ven dan: Lung infection (pneumonia) laka inven nan IV antibiotics pek thin a ni.
Naute chu a pian hma, a thau lo emaw, harsatna lian tham dang, thinlung lama harsatna nei emaw a neih chuan, naute chu operation hmaa chutiang dinhmun a lo nghet hma loh chuan neonatal intensive care unit (NICU)-ah a awm a ngai dawn a ni.
Surgery (Surgical Repair) tih a ni.
Naute chu operation atan a inpeih tawh tih a hriat chuan surgeon chuan surgery chu a ti ta a ni. Surgery hian thil tum lian tak pahnih a nei a, chungte chu:
1. Esophagus hmun hrang hrang pahnih inzawmkhawm (hei hi anastomosis an ti a ni ).
2. Pharynx leh trachea inzawmna tul lo (fistula) khar.
Tunlai technology hmasawn tak tak hmang hian he surgery hi rilru hawn lohvin tih a ni fo va, camera leh instruments te chu incision tenau tak tak tlemte hmanga dah a ni zawk (thoracoscopic surgery). Hei hian naute tan natna a ti tlem a, a dam thuai bawk.
Surgery hnuah eng nge thleng?
Surgery zawhah naute chu NICU-ah uluk taka enkawl turin hruai kir leh a ni. Ni engemaw zat hnuah chuan special X-ray esophagram an tih chu an incision chu a dam tha em tih leh leak a awm em tih enfiah thin a ni. Engkim finfiah a nih hnuah naute chu zawi zawiin oral feeding system-ah dah a ni. Naute hian a ei dan a thiam theih nan hun engemaw chen a mamawh a ni.
Operation hnua hun rei tak chhunga harsatna awm thei te chu engte nge ni?
Nausen tam zawk chu an dam chhuak vek a, nun pangngaiin an hmang thin. Mahse, naupang thenkhat chuan operation an neih hnuah hun engemaw chen chu harsatna engemaw zat an tawk thei a ni. Hengte hi fimkhur a pawimawh hle.
- Chaw ei harsatna: Naupang thenkhat chuan an kawr chhunga thau (muscles) te hian hna an thawk tha lo mai thei. Hei hian solid foods an ei tan hian an choke thei a ni. Chaw ei tur chu a hmin tha tur a ni a, tui nen pek tur a ni.
- Gastroesophageal Reflux Disease (GERD): Hei hi pum acid chu chaw kawng atanga a luang leh a ni. Hei hian heartburn leh indigestion a thlen thei a ni. Enkawl loh chuan chaw kawng a tichhe thei a ni. Hetiang dinhmun hi naupang EA surgery nei zinga a chanve vel ah a awm thin.
- Tracheomalacia natna (Tracheomalacia) a ni.Hei hi thawkna kawng chhunga cartilage chak lohna a ni. Hei hian thawk hah, khuh fo, leh lung infection (bronchitis, pneumonia) a thlen fo thei a ni.
Heng harsatnate hi i neih chuan hlauthawng suh. Chung zawng zawng tan chuan enkawlna a awm vek. A pawimawh ber chu i doctor nen inbiakna neih fo a, a thupek zawm hi a ni. Speech-Language Pathologist (SLP) hnen atangin tanpuina i dil a ngai thei bawk.
Take-Home Thuchah a ni
- Esophageal atresia (EA) hi nau piangsual na tak, mahse tihdam theih vek tawh mai a ni.
- I naute piang thar chu chaw i pek hnuah a tap chhunzawm zel a, a chok chhunzawm zel a, a blue a nih chuan doctor hnenah hruai nghal rawh. Hengte hi EA chhinchhiahna a ni thei.
- He natna hi operation hmanga enkawl a ni. Surgery result pawh a hlawhtling hle.
- Surgery an neih hnuah naupang thenkhat chuan hun rei tak chhung harsatna an tawk thei a, chu chu ei harsa leh GERD te hi a ni a, mahse hengte hi damdawi lam thurawn nen uluk taka enkawl theih a ni.
- Zawhna, hlauhthawnna, rinhlelhna i neih apiang chu i doctor nen zalen takin sawipui rawh. I tanpui turin an inpeih reng a ni.











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