I naute thinlungah hian he natna hmuh tur awm lo tak hi i hria em? (Double Inlet veilam Ventricle) a ni.

Doctor-in i naute hian thinlung lam harsatna a nei tih a hrilh che chuan nangmah, nu leh pa angin hlauhna leh lungkhamna nasa tak i neih hi thil pangngai a ni. A bik takin ‘Double Inlet Left Ventricle’ tih ang hming buaithlak tak nei dinhmun a nih a, a tlem hle a nih chuan chu hlauhna chu a nasa zawk thei. Mahse, lungngai suh. Hemi chungchang hi awlsam takin, i hriatthiam theih dan tur angin sawi ila. He thu hriatna hian he zinkawng hmachhawn turin chakna nasa tak a pe ang che.

He Double Inlet Left Ventricle hi eng nge ni tak tak?

A awlsam zawngin, hei hi pianpui thinlung natna a ni . Chu chu naute nu pum chhunga a la awm laia thinlung a lo pian huna inthlak danglamna a ni. Kan thinlung hian lower chamber (chamber) lian pahnih a nei a. Ventricle dinglam leh ventricle veilam a ni. Mahse, he natna vei naute thinlungah hian heng hnuai lam chamber pahnih zinga pakhat chauh hian hna a thawk tha hle . Chu chu left ventricle a ni.

A tlangpuiin thinlung (atria) chunglam chamber pahnih chu a hnuai lam chamber pahnih nen a hranin an inzawm a ni. Mahse hetiang a nih chuan upper chamber pahnih hi working chamber pakhat, left ventricle -ah an inzawm a ni . Hei hi thil awm lo tak, `single ventricle defect` an tih a ni.

Hetiang dinhmun hian naute taksa hi engtin nge a nghawng?

Hei hi hrethiam tur chuan thinlung hrisel hnathawh dan hi han thlir hmasa ila. Kan thinlung hi in te tak te, pindan pali nei ang mai hi han ngaihtuah teh.

1. Thinlung hrisel: Taksa thisen oxygen tlachham, "bawlhhlawh" chu atrium dinglamah a lut a. Chuta tang chuan ventricle dinglamah a kal a, chu chuan lungah a pump lut a, oxygen a la thei a ni. Thisen "thianghlim", lung atanga oxygen pek tawh chu thinlung veilam atrium-ah a kir leh thin. Chuta tang chuan veilam ventricle-ah a kal a, chu chuan thisen thianghlim chu taksa pum puiah a pump lut a ni. Hetiang hian thisen thianghlim leh bawlhhlawh chu a inhmeh ngai lo.

2. DILV condition: Hetiang natna nei naute hian oxygen tlachham thisen leh oxygen tamna thisen pahnih hi working chamber khatah (left ventricle) ah an khawlkhawm thin Thil thleng chu heng thisen pahnih hi an inzawm khawm ta a ni. Tichuan he thisen inzawmkhawm hi naute lungah leh taksa pum puiah a kal ta a ni. Chuvang chuan naute taksa peng hrang hrangah oxygen a dawng tlem hle.

Hetiang natna lan chhuah dan hi engte nge ni?

Heng symptoms te hi naute pian hnu ni engemaw zat emaw, kar tlemte chhungin a lang tlangpui. A chang chuan heng symptoms te hi rang takin a na thei hle.

Eng thilin nge hei hi a thlen? Lung natna dang pawh a awm thei em?

Hei hi a chhan dik tak hi hriat a la ni lo . Naupai kar 8 hmasa berah naute thinlung a lo thang lian lai hian a thleng fo thin. Genetic influence leh environment factors inzawmkhawm niin an ngai.

Vawi tam tak chu he `Double Inlet Left Ventricle` natna vei naute hian thinlung lama harsatna dang an nei bawk. Chungte chuan lung lama thisen kalna a tibuai thei a ni.

• Aortic Coarctation a awm chuan:Taksa lama thisen phurtu main artery (aorta) a tawi.
• Pulmonary Atresia: Pulmonary valve, lung chhunga thisen phurtu chu a siam tha tawk lo.
• Pulmonary Valve Stenosis: Lung chhunga thisen phurtu valve a tawi.

He natna hi engtin nge kan hriat theih ang?

Naupai laia natna hriatchhuah

A châng chuan i naute dinhmun chu a pian hmain hriat theih a ni . Hei hi scan bik, fetal echocardiogram an tih hmanga tih a ni. Hei hi naupai kar 18 leh kar 24 inkarah tih a ni tlangpui. I doctor chuan he test hi a rawt thei ang:

• Routine scan neih laiin naute thinlungah rhythm pangngai lo ang chi thil hmuh a nih chuan.
• Chhungkaw zingah tu pawhin congenital heart disease an neih chuan.
• Nuin lung natna, zunthlum ang chi damdawi lam natna a neih chuan.

Naute pian hnua hriat chian

Vawi tam tak chu he natna hi naute pian hnuah hmuhchhuah a ni.

• Pulse Oximetry (Pulse Ox) test: He test hi naute pian atanga darkar 24 chhungin tih thin a ni. Naute thisena oxygen level a teh thin. Oxygen level a hniam chuan thinlung lam harsatna a ni thei.
• Damdawi lam enfiahna: Doctor-in naute a enfiah hian thinlung ri pangngai lo (murmur) a hriat emaw, naute chu a sen hring a hmuh emaw hmangin a ringhlel thei a ni.

Test hmangin a dinhmun finfiah a ni

Vawikhat rinhlelhna a lo awm chuan test eng emaw zat an nei a, chu chu finfiah nan leh thinlung dinhmun hriatthiamna tha zawk an nei thin.

Hei hi eng enkawlna nge ni?

He natna hi surgery hrang hrang hmanga enkawl a ni a , chu chu stage hrang hrangah tih a ni . Heng surgery te hian thinlung chu "normal" a siam lo va, mahse naute chu hun rei tak chhunga a dam theih nan thinlung chhunga thisen kal dan chu a siam thar leh a ni.

Operation hmasa ber: Blalock-Taussig Shunt a ni

Hei hi naute pian hnu ni engemaw zat emaw, kar hmasa berah emaw tih thin a ni. Hei hian thisen kal tlem a nih chuan lung-a thisen kal zat vawng reng tura pui turin tube te tak te (shunt) dah a ni. Hei hian naute chu operation vawi hnihna thlengin a lo thanglian tha thei a ni.

Surgery pahnihna: Glenn Shunt Procedure tih a ni

He surgery hi naute thla 4-6 vel a nih laiin tih thin a ni . Heta tih tur chu taksa chunglam atanga thisen oxygen tlachham lo chhuak chu lungah thlunzawm a, thinlung chu bypass a ni. Hei hian thinlunga harsatna awm chu nasa takin a tihziaawm a ni.

Surgery pathumna leh hnuhnung ber: Fontan Procedure

Hei hi naupang kum 2-3 vel a nih chuan tih thin a ni . Hetah hian taksa hnuai lam atanga oxygen tlachham thisen lo chhuak chu lung nen direct-in a inzawm a ni. He operation hnu hian oxygen tlachham leh oxygen tamna thisen inzawmkhawm chu a tawp vek tawh mai. Naupang taksaa oxygen level chu naupang hrisel tak nen a inhnaih hle.

Surgery bakah damdawi pek thin

Naupang chu operation hma leh operation hnuah damdawi chi hrang hrang pek a ngai dawn a ni.

• Digoxin: Thinlung inzawmna (contraction) a tichak.
• ACE inhibitors: Thisen sang tihhniam.
• Anticoagulants: Thisen zam (e.g. Aspirin) a veng thei.
• Diuretics: Taksa atanga tui tam lutuk paih chhuak thin.

Naute hmalam hun tur chu engtin nge i ngaihtuah ang?

Hei hi zawhna zawh harsa tak a ni a, mahse hriat a pawimawh hle. Kum sawmhnih tlemte kalta khan he natna vei naute hi an dam rei lo hle. MahseTunlai surgery hmasawn tak tak a awm tawh avangin thil awmdan chu a danglam hle.

Tunah chuan naupang 70% - 80% aia tam, he surgery series zawh hian kum 10 hnuai lam an dam a, tam tak chuan hlawhtling takin puitling an thleng hial a ni.

Mahse, heng naupangte hi an dam chhung zawnga cardiologist nen enkawl an ngai a ni . Harsatna thenkhat pawh a awm thei a, chu chu heart rhythm lama harsatna leh pneumonia awm fo te hi a ni. Infiamna hahthlak tak tak lakah pawh khap an ni thei bawk. Mahse, naupang tam zawk chuan sikul nun pangngai an nei thei a ni.