Kan fate thenkhat, chutiang bawkin puitlingte pawhin Thalassemia ang natna avangin thisen an lak fo a ngai thin. Hetianga thisen kan pek chhunzawm zel hian kan taksain a tuar theih loh thir a khawlkhawm thei a ni. Hei hi ‘Iron Overload’ kan ti a. Chuvangin, doctor-te’n hetiang taka taksa atanga iron tam lutuk lo khawlkhawmte paih chhuah nan damdawi bik an pek chu Deferasirox an ti a. He damdawi hi brand name Jadenu hmangin i hre mai thei. Chuvangin, vawiinah hian he damdawi chungchang hi han sawi ila.
Deferasirox chu eng nge ni?
A awlsam zawngin sawi ila, Deferasirox hi damdawi chi khat ‘iron chelator’ a ni. Hei hian a awmzia chu he damdawi hian i thisena iron particle tam lutuk chu a man a, a binding a, i taksa atanga i bawlhhlawh a paih chhuakin hna a thawk tihna a ni. Magnet angin ngaihtuah la, thir duh loh chu a la chhuak a. Hetianga iron tam lutuk paih hi a pawimawh hle. A chhan chu iron tam lutuk taksaah a awm khawm chuan taksa peng pawimawh, thin leh thinlung ang chite a tichhe thei a ni.
Damdawi ei hmaa doctor hnena i hrilh tur thilte
He damdawi hi i ei tan hmain doctor hnenah i hriselna dinhmun kimchang tak i hrilh hmasak phawt a pawimawh hle . He damdawi hi damdawi lam harsatna thenkhat nei te hnena pek tur a nih avangin a hnuaia natna hrang hrang i neih chuan hrilh a pawimawh hle:
- Cancer i vei emaw, cancer enkawl mek i nih chuan.
- Liver emaw kidney emaw natna i neih chuan.
- Mit hmuh that loh emaw, mit natna (e.g. cataracts) i neih chuan.
- Hriatna lama harsatna i neih chuan .
- Thisen natna history i neih chuan . Entîr nân, thisenah thisen var, thisen sen, a nih loh leh platelet a tlem theihna dinhmun.
- He Deferasirox damdawi emaw damdawi dang emaw, ei tur emaw, dye dang emaw allergy i neih chuan.
- Naupai i nih chuan, naupai tum i nih chuan, nau hnute i pe a nih chuan .
Heng thilte hi thup lova doctor hnena hrilh hi i himna atan a pawimawh hle.
Engtin nge damdawi hi ka hman ang?
I doctor chuan he damdawi hman dan tur chiang takin a hrilhfiah ang che. Chu thupekte chu dik taka zawm a pawimawh hle.
- Timing: He damdawi hi chaw ei loh laiin ei fo tur a ni . Chu chu chaw ei hma minute 30 tal emaw ei zawh hnu darkar 2 emaw tal tihna a ni . Chaw ei ruala ei hian damdawi thatna a ti tlem thei. Nitin hun khata ei thin hi tih thiam a tha ber.
- A lak dan: 1.1.Hei hi damdawi a ni a, granule form-a lo awm a ni. Tui, apple tui, emaw orange tui ang chi thila hnim a, in a pek thin a ni. I doctor-in a hrilh che angin ti rawh.
- Titawp: Doctor thurawn tel lo chuan he damdawi hi ei nghal vat ngai suh. Chutianga i tih chuan i iron level chu a tisang nghal vat thei a ni.
- Naupang hnena pek a nih chuan: He damdawi hi naupang kum 2 chunglam hnena pek theih a awm. Mahse doctor enkawlna bik hnuaia tih tur a ni. Naupang hnena pek dan tur leh pek dan tur chu hre reng ang che.
- Dose i miss a nih chuan: Dose i ei theihnghilh chuan i hriatreng veleh ei nghal rawh. Mahse, i dose leh tur hun a lo thleng tawh a nih chuan missed dose kha skip la, i dose leh tur chu a hun ruatah ei rawh. Double dose ei ngai suh.
Pawimawh: Damdawi i ei tam palh a nih chuan ngaihthah suh. Colombo National Hospital a National Poisons Information Center ah phone nghal rawh . A nih loh leh damdawi in hnai ber Emergency Treatment Unit (ETU)-ah kal rawh.
Damdawi ei huna fimkhur tur thil
He damdawi i ei lai hian i doctor chuan i thisen test te, mit hmuh dan te, leh hriatna te a enfiah fo ang. Heng test te hi skip suh. Tin, heng symptoms te hi fimkhur hle ang che.
- Vun natna nasa tak: Mi thenkhat chuan he damdawi hi an ei tan atanga kar engemaw zat hnuah vun natna khirh tak tak an nei thei. I vunah khawsik, taksa na, leh i vunah a sen emaw, a sen emaw a awm a, a hnuah a hring leh a hring chhuak a nih chuan doctor hnenah i hrilh nghal tur a ni. Tin, i vunah a sen hring a awm a, i hmai, hmui, emaw i kawng/kawngkhar ah lymph node a hring a nih chuan chu pawh chu chhinchhiahna pawi tak a ni.
- Pum thisen chhuak: I bawlhhlawh chu tarry black a nih emaw, coffee grounds ang maia i luak emaw chuan i pum emaw, i intestines emaw a ulcer avanga thisen chhuak a ni thei. Hei hi emergency a nih avangin doctor pan nghal rawh.
- Luak chhuak: He damdawi hian mi thenkhatah luak chhuak a thlen thei. Chuvangin, damdawi in a nghawng dan i hriat hma chuan lirthei khalh emaw, machinery hman emaw ang chi thil hlauhawm tak takte chu pumpelh rawh. A bik takin tar i nih chuan thut atanga tho thut suh.
- Naupangte tui tlakchhamna: I fain luak chhuak nasa tak, luak chhuak emaw, thawkrim lutuk emaw a neih chuan an taksa atanga tui tam tak a hloh a ni thei. Hei hi he damdawi ei lai hian a hlauhawm thei hle. Chuvangin chutiang hunah chuan i doctor hnenah hrilh rawh.
A side effects te chu engte nge ni?
Damdawi dang ang bawkin Deferasirox hian side effect a nei thei a ni. Mi zawng zawngin kan hmu vek lo a, mahse fimkhur a pawimawh.
| Side effect a awm thei | Hrilhfiahna |
|---|---|
| Side effects te chu doctor hnenah hriattir nghal tur a ni | |
| Allergic Reaction na tak tak a awm thei | Skin rash, itching, hmai/ hmui/lei hring, thawk harsa. |
| Mit emaw hriatna lama inthlak danglamna | Mit a fiah lo, mit a rawng a danglam a, hriatna a tlahniam bawk. |
| Liver chhiatna chhinchhiahna | Dark yellow/brown urine, mit emaw vun emaw yellowing, pum dinglam chunglam na, luak chhuak, hah lutuk. |
| Kidney-a nghawng a neih dan | Zun chhuah tlem emaw zun harsatna emaw. |
| Thisen chhuak | Tar ang maia bawlhhlawh dum, coffee ground ang maia luak chhuak, taksaah random bruise awm. |
| A awm reng emaw, a buaithlak emaw chuan doctor hnenah hrilh rawh. | |
| Digestive system lama harsatna awm thei | Pum na, luak chhuak, luak chhuak, luak chhuak. |
| Mut harsatna a awm | Mut theih lohna emaw mut buai emaw. |
Hei hian damdawi dang nen a inzawm thei em?
Ni e, hei hi a pawimawh hle. Deferasirox hi damdawi dang thenkhat nena ei hian harsatna a thlen thei a ni. Chuvangin i damdawi, vitamin, herbal remedy, emaw supplement i ei zawng zawng chu i doctor hnenah hrilh rawh.
Deferasirox hi heng damdawi te nen hian i ei hian fimkhur hle tur a ni:
- Iron awmna pill emaw supplement dang: He damdawi hi iron tam lutuk paih chhuahna atana ei a nih avangin iron pill ei hian a pui dawn lo.
- Antacids: Aluminum awmna antacids gas leh heartburn atana hman thin hian Deferasirox hi a lakluhna a ti tlem thei a ni.
- Cholesterol damdawi thenkhat: Cholestyramine leh Colestipol ang chi damdawi.
- Natna tidamtu thenkhat: NSAID-type natna tidamtu (e.g. Ibuprofen, Naproxen).
- Naupai venna damdawi.
- Thisen zam lohna damdawi, Warfarin .
- Steroid damdawi Prednisone ang chi te hi a ni.
He list hi a kim lo va, chuvangin i damdawi ei zawng zawng doctor hnenah hrilh vek a him ber .
Take-Home Thuchah a ni
- Deferasirox hi thalassemia ang chi natna avanga taksa atanga iron tam lutuk paih chhuahna atana pek thin damdawi pawimawh tak a ni.
- He damdawi hi pum ruak, i doctor-in a pek hun leh a dose-ah ei fo ang che.
- Damdawi dang, vitamin leh supplement i ei zawng zawngte chu i doctor hnenah hriattir a pawimawh hle.
- Vun natna nasa tak, coffee ground ang maia luak chhuak, tarry stools, mitdelna ang chi natna khirh tak tak i hmuh chuan ngaihthah suh la, doctor lam pan nghal rawh.
- Doctor thurawn tel lo chuan damdawi ei kha bansan ngai suh la, a dose pawh thlak ngai suh.











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