Mi thenkhat ha chu a rawng mak deuh deuh, blue-gray rawng emaw, yellow-brown rawng emaw a ni tih i hmu ngai em? A nih loh leh, thil te tak te i ei pawhin a chhe emaw, a chhe emaw thei khawpa ha chak lo i nei em? Chu chu thil pangngaiah i ngai mai thei. Mahse, hei hi ha lo pian chhuah laia thil awm lo tak `(Dentinogenesis Imperfecta)` tih vang pawh a ni thei. Vawiin hian he thu hi tlem han sawi ila, a tha em?
`(Dentinogenesis Imperfecta)` tih hi eng nge ni? A awlsam zawngin hrethiam ila, kan hrethiam ang em?
A awlsam zawngin sawi ila, `(Dentinogenesis Imperfecta)` hi ha a lo pian lai, chu chu ha a lo thang lai a lo awm thin a ni. Hetiang a nih chuan i ha a chak lo hle a , a chhe awlsam hle . Biscuit ang maiin tlemte pawh i tikehsawm chuan a chhe vek ang. Tin, he natna vei te ha hi a translucent deuh a ni . A rawng pawh, ka sawi tawh ang khan , blue-gray emaw yellow-brown emaw a ni.
He natna, ``Dentinogenesis Imperfecta,'' tia koh hian i ha hmasa ber leh i ha awm rengte pawh a nghawng thei a ni . Chumi awmzia chu naupan lai atang tawhin symptoms hi a intan thei a, a nih loh leh nakin lawkah a lo lang thei tihna a ni.
Tunah chuan en teh, ha kan lak hian layer engemaw zat a nei a. A chung lama eng mawi leh chak tak chu `(Enamel)` an ti a. Chu `(Enamel)` hnuaiah chuan layer dang a awm a, chu chu `(Dentin)` an ti a. He `(Dentin)` part hi ha chakna leh rawng petu ber a ni. `(Dentinogenesis Imperfecta)`-a thil thleng chu `(Dentin)` part hi a lo thanglian tha lo a ni. Chuti a nih chuan eng nge thleng? `(Dentin)` a chak loh avangin a chunga `(Enamel)` chu ha ah a inbun tha tawk lo. Chuvangin `(Enamel)` chu awlsam takin a flake a, a chhe vek bawk.
Pawimawh: `(Dentinogenesis Imperfecta)` hi `(Amelogenesis Imperfecta)` nen a danglam. `(Amelogenesis Imperfecta)` ah chuan ha `(Enamel)` chu direct-in a nghawng a ni. `(Dentinogenesis Imperfecta)`-ah chuan buaina chu `(Dentin)`-ah a awm a ni.
Hei hi thil awm lo tak niin an sawi . A tlangpuiin he natna hi mi 6,000 atanga 8,000 zinga pakhat vel ah a awm thin.
`(Dentinogenesis Imperfecta)` chi hrang hrang a awm em?
Ni e, `(Dentinogenesis Imperfecta)` chi thum kan sawi a ni. Eng nge an nih i en ang u.
1. `(Dentinogenesis Imperfecta)` Type 1 (Type I): Hei hi a bik tak a ni. A chhan chu he chi hi natna `(Osteogenesis Imperfecta)` tih nen a lo awm thin a ni. `(Osteogenesis Imperfecta)` hi ruh a ti chhe hle (brittle bone disease) natna mai a ni. Chuvangin, ha lam harsatna bakah hian heng mite hian ruh lama harsatna an nei bawk. A chhan chu `(COL1A1)` emaw `(COL1A2)` genes `(Genes)` ah hian inthlak danglamna engemaw zat a awm vang a ni. Heng gene pahnihte hian kan taksaa protein `(Collagen)` siam turin a pui a ni.
2. `(Dentinogenesis Imperfecta)` Type 2 (Type II): Hetiang chi hi ha nghet aiin a tam zawk.Nausen ha ah a tam ber. Heng mite hian rochan dang natna dang an nei tlem zawk tlangpui. Mahse, a châng chuan kum upat vanga hriatna hloh theihna a awm tih hmuhchhuah a ni .
3. `(Dentinogenesis Imperfecta)` Type 3 (Type III): Hei hi chi tlem ber a ni . Nausen ha aiin ha nghet tak a nghawng nasa zawk. Zirchiangtute chuan he chi hi Juda hnam chhuak `(Ashkenazi Jewish)` tia koh zingah an report tam ber a, Maryland khawthlang lama cheng chhungkaw engemaw zatah an report bawk.
`(Dentinogenesis Imperfecta)` natna lan chhuah dan chu engte nge ni? Engtin nge kan hriat theih ang?
Ka sawi tawh ang khan, a lan chhuah dan ber chu ha rawng danglam leh ha chak lo, hring hring . Ha chu a tlangpuiin a hring (translucent) a, a rawng chu a sen hring emaw, a sen hring emaw a ni .
Chu bakah chuan symptom dang pawh i hmu thei a, chungte chu:
- Naute ha hloh tlai: Naute ha chu a tlangpui aia tlain a tla.
- Enamel Hypoplasia: Hei hian ha chunglam enamel layer chu a bo tawk tihna a ni.
- Joint Hypermobility: Mi thenkhat chuan an ruh, an kut zungtang leh kekawrte chu hma leh hnung lamah an ben nasa lutuk thei.
- Tooth Agenesis: Hei hian ha engemaw zat nei lo piang tihna a ni.
- Ha enamel chak lo: Ha enamel hi a chak lo va, a chhe nghal vat thin.
Ngaihtuah teh, naupang tê naute ha chu rawng mak tak a nih a, bluish tint a neih emaw, a chhe awlsam emaw a nih chuan i ngaihtuah ngei ngei tur a ni.
Engvangin nge hetiang `(Dentinogenesis Imperfecta)` hi a lo awm? A chhan chu eng nge ni?
Hei hi a chhan ber chu kan genes inthlak danglam vang a ni. A bik takin, `(DSPP) ` an tih gene a inthlak danglam chuan `(Dentinogenesis Imperfecta) a thlen thin. He `(DSPP)` gene hian kan ha layer lai tak `(Dentin)` siam dan tur thupek a pe a ni. Chuvangin he gene-ah hian harsatna a awm chuan `(Dentin)` hi a insiam tha lo.
He genetic variation hi nu leh pa atanga rochun a ni thei a , a nih loh leh randomly a thleng thei bawk .
Dentinogenesis Imperfecta type 1 nei te hian ka sawi tawh ang khan COL1A1 emaw COL1A2 emaw genes ah mutations an nei a. Hengte hi Osteogenesis Imperfecta (ruh hring (brittle bones) thlentu natna) vei te pawhin an hmuh thin genetic mutations ang chiah kha an ni.
Engtin nge doctor-te hian hei hi an hriat chian?
Nangmah emaw i fa emaw hian heng chhinchhiahnate hi i neih chuan ha enkawltu i pan hmasa tur a ni . A taksa enfiah hmasa phawt ang a, i chhungkuaah hian heng natna hi an nei tawh em tih a zawt ang..
Tin, Dentinogenesis Imperfecta i vei nia i rinhlelh chuan a hnuaia test te hi tih theih a ni bawk.
- Ha X-ray lak.
- CT scan pawh i ti thei maithei .
Heng thlalakte hi a en hian doctor chuan ha chhung lam dinhmun, ``Dentin'' awm dan te chu a hre chiang thei a ni.
A châng chuan, i doctor chuan i DNA-a inthlâk danglamnain dentinogenesis imperfecta a thlen tih chiang taka hriat theih nân genetic test neih a rawt thei bawk.
Hei hi eng enkawlna nge ni? (Tihdamna)
Dentinogenesis Imperfecta enkawlna atana ngaih pawimawh ber chu ha chak lote tihchak hi a ni . Hemi atan hian dentist te hian restorative procedure hrang hrang an hmang thin.
Entir nan:
- Fillings: Ha gap leh crack awm te chu fill up thin ang che.
- Veneers: Hengte hi ha hmalam a dah thin shell te tak te a ni. Tin, ha hmel a titha thei bawk.
- Lallukhum: Lallukhum chu ha chunga kawr dah ang a ni. Ha pumpui a khuh a, a tichak bawk.
Heng enkawlnaah hian ha rawng chi hrang hrang an hmang a, chuvangin i nuihzatthlak chu i vawng mawi thei a ni.
Dentinogenesis Imperfecta i neih chuan i tar chhoh zel chuan ha i hloh tam zawk. Ha i hloh chuan ha dahna emaw, ha lem emaw hmangin i thlak thei a ni .
Hetiang dinhmun nena nun dun lai hian eng ang beiseina nge i neih theih ang? (Hmuh dan tur) .
I thlirna chu thil engemaw zatah a innghat a ni:
- I natna hmuhchhuah a nih lai khan i kum.
- Engtiang chiahin nge enkawlna i tan tirh.
- Eng ang Dentinogenesis Imperfecta nge i neih?
A pawimawh ber chu Dentinogenesis Imperfecta hi tihdam theih a ni lo . Mahse, ha enkawl dan dik leh hmui faina tha tak i neih chuan i ha tihchhiat belh zel tur venna leh chak taka awm reng turin i pui thei a ni. He natna hi hriatchhuah leh enkawl a nih hma chuan a rah chhuah a tha zawk.
Dentinogenesis Imperfecta hi ven theih a ni em?
Vanduaithlak takin Dentinogenesis Imperfecta hi kan thunun theih loh genetic changes avanga lo awm a nih avangin ven theih a ni lo. Mahse, a rang thei ang bera enkawl tan chuan hun rei tak chhunga ha tihchhiat a ti tlem thei.
Engtin nge ka ha ka enkawl ang? (Mahni Inenkawlna) .
`(Dentinogenesis Imperfecta)` i neih chuan hmui faina tha a pawimawh.Maintenance hi a pawimawh hle. Ha ro leh chhiatna tihziaawm nan a hnuaia mi ang hian ti rawh:
- I ha tichak turin fluoride hmanga enkawlna chungchang i ha enkawltu hnenah zawt la.
- Ni khatah vawi hnih emaw vawi thum emaw ha chu soft-bristled toothbrush leh fluoride toothpaste hmangin silfai thin ang che .
- Chaw sugary, acidic ei kha tihtlem rawh.
- Ni khatah vawi khat fluoride hmangin i hmui silfai thin ang che .
- Checkup leh tihfai nan hunbi neiin dentist tlawh thin ang che .
`(Dentinogenesis Imperfecta)` i neih lai hian eng nge ei leh in tur tha?
A tha ber chu ei leh in tur sugar leh acid tlem te thlan hi a ni . Hei hian soda ang chi in tur, limes ang chi citrus fruit, leh tomato sauce te chu a theih ang anga tihtlem tihna a ni. Tin, ei tur chi hrang hrang ei ngai leh khauh emaw, a hmin emaw ei tlem pawh a tha hle .
Dentinogenesis Imperfecta vei tan ei tur tha thenkhat chu hetiang hi a ni:
- Nga baked a ni
- Casseroles chi hrang hrang
- Thlai chawhmeh siam
- Oatmeal a ni
- Pasta chu cream hmanga siam sauce nen
- Scrambled egg a ni
- Smoothies te pawh a awm
Hengte hi ei leh in awl tak tak leh ha tichhe vak lo a ni.
Engtikah nge Doctor ka hmuh ang?
Nangmah emaw, i fa emaw chuan an ha chungchânga thil danglam emaw, danglam emaw i hmuh chuan i doctor hnênah hrilh nghâl a ṭha ber . DGI symptoms hi kum eng pawhah a lang thei tih hre reng ang che. I naute ha hmasa ber chu blue, gray, or brown -a a lan chuan , naupang ha enkawltu hnenah thurawn dil ngei ang che.
Doctor hnenah eng zawhna nge i zawh tur?
Dentinogenesis Imperfecta i vei tih hmuhchhuah i nih chuan i doctor hnenah zawhna i zawt mai thei a, chungte chu:
- Eng chi `(DGI)` nge ka neih?
- Eng ang enkawlna nge ka mamawh?
- Enkawlnate hian eng chen nge a daih ang? Eng chen nge enkawlna te hi a awm ang?
- Engzat nge ka ha ka tihfai tur?
- Ha hring leh chhiatna tihziaawmna turin eng invenna nge ka tih theih ang?
A tawpah chuan thil pakhat... (Take-Home Message)
Ha chak lo, awlsam taka chhe thei neih hi a tithinur tak zet a ni. Chaw ei apianga fimkhur a ngai hi a hahthlak hle bawk. `(Dentinogenesis Imperfecta)` i neih chuan i ha lan danah i mualpho mai thei. Hemi avang hian khawtlang hmachhawn i duh lo mai thei.
Mahse, nangmah chauh i ni lo tih hre reng ang che.. Doctor tanpui thei che an awm. I ha tihchakna tur, i nuihza siam thatna tur leh i inrintawkna tihpunna tur enkawlna an rawt thei a ni. Chuvangin, engmah ngaihtuah buai suh la, i doctor thurawn zawm rawh.
Natna hi a tir atanga hriatchhuah a, enkawlna dik tak dawng a, hmui faina tha tak zawm hian `(Dentinogenesis Imperfecta) tih natna nei pawhin nun hrisel, hlim takin i nung thei ang.
` dentinogenesis imperfecta, ha natna, ha chak lo, ha rawng danglam, genetic natna, ha hriselna, nausen ha
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