Susac Syndrome hi eng nge ni? A awlsam zawngin sawi ila.

Lu na, hriatrengna hloh, leh i mit leh hriatna lama inthlak danglamna tlemte i nei nghal em? Heng thilte hi a rualin a thleng thei mai thei. Chutiang chhinchhiahna a lo lang thut chuan kan hlauthawng hi thil pangngai a ni. Vawiin hian kan sawi dawn a, hetiang symptoms thlen thei, mahse kan ramah hian hriat lar vak lo, rare condition kan sawi dawn a ni. Chu chu Susac Syndrome a ni.

Susac Syndrome hi eng nge ni mai?

A awlsam zawngin sawi ila, Susac Syndrome hi autoimmune condition a ni. Kan taksa invenna (immune system) hi kan ram sipai ang maiin han ngaihtuah teh. A hna ber chu natna thlentu hrik laka min humhim hi a ni. Mahse a chang chuan he system hian tihsual tlemte a nei thin. Tichuan, pawn lam atanga hmelma te beih ai chuan kan taksa cell tha tak tak te chu a rawn bei tan ta zawk a ni. Hei hi autoimmune diseases kan tih chu a ni.

Susac Syndrome-ah hian kan taksa chakna (immune system) hian thluak, mit leh mit (cochlea)-a thisen kalna kawng te tak te te chu a bei thin a ni . He attack hian chu thisen kalna kawngte chu a ti hring a, chuta thisen kal chu a tihtlem emaw, a tikhawlo vek emaw a ni. Chu chu he natna lanchhuahna thlentu a ni.

Khawiah nge he natna hi a tuar ber?

He natna hian taksa peng pathum a nghawng ber a, chungte chu thluak, mit leh beng te an ni.

Hei hi thil awm lo tak a ni. Chuvangin mi engzat nge lo thanglian tih chiang taka sawi a har hle. A chang chuan, natna dang Multiple Sclerosis (MS) an tih nen hian a lan chhuah dan a inang a, chuvangin doctor-te pawhin a chang chuan natna pahnih hi an tibuai thei a ni. Chuvangin, a chang chuan diagnosis dik tak hmuh theih nan hun rei tak a la ngai thei.

Susac Syndrome natna lan chhuah dan chu engte nge ni?

Mi hrang hrangah symptoms a inang lo thei a, mahse a hmaa kan sawi tawh component lian pathum nen hian a inzawm tlat a ni. Eng nge an nih i en ang u.

Engtin nge heng miziate hian a nghawng che?

Heng symptoms te hi mi zawng zawng tan a inang vek lo. Mi thenkhat chuan an dam chhungin vawi khat chauh hetiang hi an nei thin. Midang tan chuan symptoms a lo thleng a, a kal leh a, a lo let leh thin... leh a dangte. Vawi tam tak chu kum engemaw zat chhungin a natna lan chhuah dan chu a wax thei a, a reh thei bawk. Mi tlemte chauh hian natna hmuhchhuah a nih hian a rualin an pathum hian symptom an nei vek a ni.

Engvangin nge Susac Syndrome hi a lo awm?

Hei hi a chhan dik tak erawh hriat a la ni lo. Mahse autoimmune condition a ni tih kan hria. A hmaa kan sawi tawh ang khan keimahni immune system hian kan thluak, retina leh inner ear-a thisen kalna kawng te tak te chhunga cell awmte chu a bei a. He attack hian chu cell te chu a ti hring chhuak thin. Tichuan, chu thisen kalna kawngte chu a then emaw, a pumin emaw a inkhar thei a ni. Chutiang a nih chuan chu taksa peng hrang hrangte chuan an mamawh oxygen leh nutrients an hmu lo. Chu chu a hmaa kan sawi tawh ang chi natna lan chhuah zawng zawng hi a ni.

Hei hi thlahtu natna a ni em? Tute nge risk sang zawk?

Ni lo, hei hi thlahtu natna a ni tih finfiahna a awm lo. Mahse , hmeichhia hian mipa aiin he natna hi a let thum velin an vei tam zawk. Kum 20 leh 40 inkar atanga a lan chhuah dan a ni tlangpui.

He natna hian eng harsatna nge a thlen theih?

Thisen kalna kawng khar vanga mit leh beng chhiatna hi a chang chuan a awm reng thei a ni.Chumi awmzia chu mit leh hriatna hloh reng theihna a awm tihna a ni. Tin, a tlem hle nachungin, dementia an tih, hriatrengna a bo vek tawhna pawh a awm thei bawk.

He natna hi engtin nge doctor hian a hriat theih ang? (Diagnosis) tih a ni.

I doctor chuan he natna hi a hriat theih nan test eng emaw zat a ti ang.

• Taksa enfiahna
• Neurological exam a ni
• Mit lam enfiahna (Ophthalmological exam) a ni

Chu bakah, i natna lan chhuah dan hriat belh duh chuan hetiang test hi i ti thei bawk:

• Magnetic Resonance Imaging (MRI) of the brain: Hei hian doctor chuan thluak hemisphere pahnih inzawmna hmun (corpus callosum)-ah ‘snowball lesions’ an tih hmun dum a zawng thei a ni. Hengte hi Susac Syndrome chhinchhiahna chiang tak a ni.
• Fluorescein Angiography: Hei hi test bik a ni a, mit retina-a thisen kalna kawngte enfiahna a ni. Thisen kalna kawngkhar a block eng pawh a hmuchhuak thei.
• Audiogram: Hei hi hriatna test a ni. Low-frequency sound i hriat theih leh hriat loh leh thusawi hriatthiam harsa i neih leh neih loh a enfiah thin.

Hei hi eng enkawlna nge ni?

Enkawlna tum ber chu kan taksa hriselna (immune system) control hi a ni a, chu chu a thawk tha lo hle. Chumi atan chuan immunosuppressants hman a ni. Entirna thenkhat chu:

• Corticosteroid (e.g. prednisone) te hi a tha hle.
• Immunoglobulin (IVIG) hmanga thisen kal tlanga hman thin.
• Mycophenolate a ni
• Azathioprine a ni
• Cyclophosphamide hmanga siam a ni
• Rituximab a ni

Heng damdawi te hi taksaah kawng hrang hrangin pek theih a ni. Ṭhenkhat chu pill emaw capsule emaw angin an ei ṭhin. Ṭhenkhat chu injection angin pek an ni. A dangte chu saline hmangin thisenah (IV) pek an ni. Heng damdawi te hian overactive immune system tihziaawmna hmangin hna an thawk a ni.

Enkawlna, dam lehna leh hmalam hun tur zir rawh

Enkawlna hian side effect a nei em?

Ni e, damdawi zawng zawng ang bawkin he damdawi hian side effect hrang hrang a nei thei. Chuvangin, enkawlna i tan hmain he thu hi i doctor nen sawiho rawh. Side effect i neih chuan doctor hnenah hrilh la.

Enkawlna hnuah a dam leh theih nan eng chen nge a duh ang?

Hei hi hriat hmasak a nih a, enkawl tan a nih chuan a natna lan chhuah dan chu a reh thuai thei a ni. Mi thenkhat chu vawi khat chauh an damlo thin. Mi dangte chuan kum tam tak chhung chu episode lo lang leh ṭhin an nei thei bawk. Mahse , immunosuppressant therapy dik tak hman chuan a lo lang leh theihna chu nasa takin a tlahniam a ni.

He natna nen hian nun hi eng ang nge ni ang? (Hmuh dan tur) .

Symptoms a lan veleh enkawl nghaltute tan hmalam hun a tha hle. Hei hian thluak, mit leh bengte a tichhe vek tur a veng thei a ni. Mitdelna leh hriatna hloh ang chi harsatna awm reng chu a tlem hle. Hei hi nunna atana hlauhawm a ni lo, a tlem hle tih loh chu. I nunphung tichhe thei mah se, i dam chhung chu direct-in a nghawng lo.

Natna laka inven dan tur leh engtikah nge Doctor pan tur?

Susac Syndrome hi ven dan tur bik a awm lo. Mahse, i doctor-in treatment plan a pek dik tak zawm chuan symptoms (flare-ups) lo lang leh tur chu i ti tlem thei ang.

Heng inthlak danglamna te hi i tawn chuan doctor pan nghal rawh:

• Mit hmuh dan inthlak danglam
• Hriatna hloh
• Ngaihtuahna emaw, hriatrengna emaw lama inthlak danglamna
• Nungchang emaw, mize emaw inthlak danglamna

Natna hriat chian hma chuan hrisel takin i awm thei a, chhiatna awm reng tur i veng thei bawk.

I doctor zawh tur zawhna

• "Ka symptoms a reh hnuah ka rawn let leh thei ang em?"
• "Eng ang enkawlna nge min rawt?"
• "He damdawi hi eng chen nge ka hman ang a, engtin nge ka hman ang?"
• "He damdawi hian eng side effect nge a neih?"
• "Hearing aids nge cochlear implant ka mamawh ang?"

Susac Syndrome hian nitin nun a nghawng thei a ni. I rin fo tawh thil, i mit emaw, i hriatna emaw a lo inthlak thut chuan hlauhna leh lungkhamna i neih hi thil pangngai a ni. A châng chuan mental health counselor biak pawh hi hahdamna nasa tak a ni thei. Hriat reng tur chu, natna lan chhuah dan i hriat veleh doctor hnenah hrilh vat a tha ber a, harsatna a awm thei a ni. Enkawl vat chuan chhiatna awm reng tur a veng thei a ni.