I fa te hian hetiang hian thawk harsatna a nei em? "Double Aortic Arch" chungchang hi han sawi ila!

I fate hian a chang chuan thawk harsa ang maiin a inhria em? Chaw pek emaw, hnute pek emaw laiin a chok em? A nih loh leh a thawk lai hian thawm mak tak tak a siam em? Chûngte chu naupan lai natna tlanglawn tak tak an ni thei a, mahse, hei hi a hnuaiah hian dinhmun pawi zâwk, mahse enkawl theih a awm thei a ni. Chutiang dinhmun hmuh tur awm lo mahse hriat tur pawimawh tak pakhat chu "Double Aortic Arch" tih a ni. Vawiin hian chipchiar takin sawi ila.

A awlsam zawngin, i naute thinlung aṭanga a taksa dang thlenga thisen phurtu thisen kalna kawngpui ber chu aorta . A tlangpuiin lawng pakhat, lian tak a ni. He thisen kalna kawngkhar ( vessel ) hi thinlung chunga a curved part hi aortic arch an ti a .

Mahse, naute "Double Aortic Arch" neiah chuan he "aortic arch" hi pahnih ah a lo piang ta a ni. Chu chu, thisen kalna kawng dang pakhat chu he "aortic arch" lian ber nen hian a inzawm a, arch pahnihna a siam tihna a ni. Heng arch pahnih hi an inzawm khawm a, naute thlipui (trachea) leh ei tur pipe (esophagus) vel chu ring an siam a ni . Ngaihtuah teh, he ring hi a block a nih chuan eng nge thleng ang? Chutah chuan naute hian natna lanchhuahna na tak tak a nei tan a, chu chu thawk harsa, thawk laiin thawm a chhuah, ei tur ei harsa tih te hi a ni.

He "aortic arch" hi naupai tirh lamah, kar hnih atanga kar sarih inkar ah a lo awm thin. Hemi hun chhung hian thinlung leh thisen kalna kawngte hi a buaithlak hle a. A hmun thenkhat chu a lo insiam a, rei vak lo hnuah chuan a mamawh tawh lo va, a bo ta vek a ni. Hetiang thil avang hian "double aortic arch" hi a lo piang a ni. Naupai kar ngana vel khan thisen kalna kawng pakhat, a chhan hriat loh avanga bo tur chu a bo lo va, he "double aortic arch" hi a lo piang ta a ni. Hei hi congenital heart defect , chu chu naute chu a pianpui tihna a ni.

He natna hi "double aortic arch" tia koh a ni a, pianpui heart defects pawl pakhat , "vascular rings" tia koh zinga mi a ni. Chungte chuan naute thlipui leh chaw kawng (esophagus) chu a ti compress a ni.

Heng "vascular rings" te hi eng nge ni?

Okay, "Vascular Rings" hi ka sawi tawh ang khan "aortic arch" a lo awm dan pangngai lo, naute thlipui (trachea), ei tur pipe (esophagus), emaw, a pahnih emaw a compress theihna tur condition a ni. Hengte hi congenital heart defects a awm lo hle a ni . Ngaihtuah teh, naute 100 zinga pakhat vel chu pianpui thinlung natna chi khat neiin an piang a ni. Mahse "vascular ring" hian naute 10,000 zinga pakhat chauh a nghawng a ni. Chutiang khawpa rare chu a ni.

"Vascular Rings" chi hrang hrang lian ber berte chu engte nge ni?

Heng "vascular rings" te hi chi hrang hrang lian tak tak a awm. Eng nge an nih i en ang u:

• Double Aortic Arch: Hetah hian "aortic arches" pahnih (khawi leh dinglam) chuan trachea leh esophagus te chu an hual vel a. Hei hi kan thupui ber a ni.
• Right aortic arch with aberrant left subclavian artery and left ligamentum: Hetah hian aortic arch pakhat a awm a, mahse trachea dinglam (a tlangpuiin veilam)-ah a awm thung. Chutiang a nih chuan naute kut atanga thisen pe thin left subclavian artery chu aorta atanga tan niin trachea leh esophagus hnung lamah a kal thin. He vascular ring hi nausen dam chhunga thisen kalna hmun la awm, a bo vek tawh , left ligamentum arteriosus nena inzawm hian a ti famkim a ni.
• Left aortic arch with aberrant right subclavian artery: Hetah hian dinglam subclavian artery chu trachea leh esophagus hnung lamah a kal a, a compress a ni.
• Innominate artery compression: Innominate (brachiocephalic) artery hi aorta peng pakhat a ni a. Chutiang a nih chuan trachea veilam atanga tan a ni a, chutah chuan trachea hmalam atanga dinglamah a kal leh thin. Hei hian trachea-ah pressure a siam a ni.
• Pulmonary artery sling: Left pulmonary artery hi dinglam pulmonary artery atanga tan niin, trachea leh esophagus inkarah a kal a.

Chung zawng zawnga thil thleng chu boruak kawng emaw, chaw kawng emaw chu eng emaw ti takin a nghawng a ni.

"Double Aortic Arch" chi hrang hrang a awm em?

Ni e, "double aortic arch" hi chi thum lian tak a awm. Chungte chu eng arch nge lian zawk tih leh chu arch lian zawk chu trachea dinglam emaw veilam emaw a awm leh awm loh hmangin an thliar hrang a ni.

• Dominant right arch with a small left arch: Hei hi a tam ber a ni a, zaa 80 velin a thleng thin.
• Dominant left arch with a small right arch: Hei hi zaa 10 velin hmuh tur a awm.
• Balanced arches: Hei hi za zela 10 vel ah pawh hmuh tur a awm bawk.

Eng chi "vascular ring" nge hmuh tam ber?

Doctor-te chuan "double aortic arch" hi "vascular ring" chi khat zingah chuan a tam ber niin an ngai thin. Mahse zirchianna thar chuan "right aortic arch" hi a takah chuan a tam zawk tih hmuhchhuah a ni.

Mahse, thil dang a awm. Naute "right aortic arch" nei te hian "double aortic arch" nei naute aiin congenital heart defects dang an nei tam zawk. Amaherawhchu, an pian tirh atanga hriatchhuah an tlem zawk. Hei hi a chhan chu "right aortic arch" hian a tir lamah symptom a thlen lo thei a ni. Chuvangin, he harsatna hi thla 6 leh thla 18 inkarah operation neih a ngai mai thei.

``Double Aortic Arch'' an tih hi vascular ring chi khat a ni ber . Chuvangin, i naute doctor-in a harsatna chu a hriat hmasak theih a ni. Vascular ring chi dang nei naute nena khaikhin chuan ``Double Aortic Arch'' nei naute chu an pian hnu rei vak lovah operation neih a ngai mai thei.

"Double Aortic Arch" tih hi engte nge ni?

"Double aortic arch" symptoms hi naute thlipui, esophagus emaw, a pahnih emaw a compress hian a awm tlangpui. He compression hian naute thawk dan, chaw pek dan emaw, thinlung hnathawh dan emaw a nghawng thei a ni.

A tam zawkah chuan heng symptoms te hi naupan lai (a bik takin natna a nasat chuan) a lo lang thin a, mahse a chang chuan kum thum atang pawhin a lang thei a, tleirawl lai pawhin a lang thei bawk.

Naupang thenkhat chu asthma vei nia hriat sual an ni thei a, a chhan chu a natna lan chhuah dan a inang vek a ni. Asthma enkawlna a hlawhchham a, test dang neih belh a nih chauhvin he natna hi hriat theih a ni.

Thluak lam natna lanchhuahna

Naute leh naupang "double aortic arch" nei zinga zaa 91 vel chuan heng thawkna nena inzawm natna hi an nei thin. Anni chu:

• Thâwk chhuah laiin aw mak tak (`stridor` tia koh ri sang tak emaw, `wheezing` tia koh thawm ri nasa tak) .
• "Seal barking" ang maia ri chhuak khuh. Hei hi "croup" an tih dinhmunah khuh (cough) nen a inang a ni.
• Thluak hnuai lam natna vei fo thin .

Gastrointestinal natna lan chhuah dan

Naute leh naupang "double aortic arch" nei zinga zaa 40 vel chuan heng ei leh in lama natna hi an nei thin. Chung zingah chuan:

• Naupai lai emaw, hnute pek lai emawa choking .
• Chaw ei harsa (dysphagia) . Hei hi nautein ei tur solid a ei tan hnuah a lang fo thin.
• Thil thau tihpun harsatna .
• Chaw ei tur chu rilruah a rawn chho leh (`Regurgitation/reflux`) .

Lung lam natna lan chhuah dan

Nausen leh naupang "double aortic arch" nei zinga zaa 30 vel chuan thinlung lam natna an nei a ni. Chung zingah chuan:

• A rilru a na .
• Thinlung ri danglam tak (`Thinlung murmur`) .
• Vun sen (cyanosis) .

Eng thilin nge "Double Aortic Arch" hi a thlen?

"Double otic arch" awm chhan dik tak hi hmuhchhuah a la ni lo . Hetiang dinhmun hi "in-vitro fertilization" (IVF) hmanga nau pai zingah hmuh tur awm fo mahse, a chhan dik tak erawh hriat a la ni lo.

Double aortic arch hi damdawi lam thil dang nen pawh a inzawm thei bawk. Double aortic arch nei naute zaa 12 vel chuan pianpui heart defect dang an nei a, chu chu ventricular septal defect (VSD) leh tetralogy of Fallot te hi a ni. Chu bakah, naute double aortic arch nei zinga zaa 20 vel chuan chromosome 22q11 deletion leh trisomy 21 (Down syndrome) te ang chi genetic condition an nei bawk.

"Double Aortic Arch" hi engtin nge kan hriat theih ang?

Double aortic arch hi thil thleng mai mai emaw, a lan chhuah tan tirh emaw a ni. A châng chuan, naupai lai emaw, nau neih hnuah emaw, chhan dang vanga imaging test an tih lai emaw pawhin a lo lang chhuak ṭhin. Kum 2004 atang khan naupai laiin scan hmanga he natna hi hmuhchhuah an pung chho ta a ni. Hei hi a \angkai hle a, naute pian veleh enkawl dan tur ruahman theih a nih avangin.

A nih loh leh, naute pian hnua symptoms a lan chuan hriat theih a ni. I naute doctor chuan a natna lan chhuah dan a sawipui ang che a, chutah chuan test engemaw zat a nei ang.

"Double Aortic Arch" tih hriat theihna tur test neih a ni.

He natna hriat theihna atana test hman ber berte chu:

• Chest X-ray: Hei hi test hmasa ber a ni fo thin.
• CT scan a ni.
• Echocardiogram (Echo) test: Hei hi thinlung lama harsatna dang a awm leh awm loh hriat nan a \angkai ber.
• MRI (MRI) hmanga enfiah a ni.

A chang chuan naute thlipui (windpipe) enfiah nan bronchoscopy tih a ni thei bawk. Hei hi double aortic arch hmuhchhuah hmaa thawk harsatna chhanna atan tih theih a ni. A nih loh leh, surgeon-in harsatna thlentu a hriat theih nân operation hmaa tih a ni thei bawk.

Genetic testing hian genetic conditions hriat theihna a pui a ni.

"Double Aortic Arch" hi engtin nge kan tihdam theih ang?

"Double aortic arch" dinhmun siamthat nan operation neih a ngai a ni. Nausen natna lanchhuahna nei lo tan pawh thla 6 leh thla 9 inkarah surgery tih a tha ber. Nausen symptomatic nei, a bik takin symptoms a nasat chuan surgery hmasa zawk a ngai mai thei.

Ngaihtuah teh, "double aortic arch" tih hi kum 1737 khan hmuhchhuah hmasak ber a ni a, a tan surgery hmasa ber chu kum 1947 khan an ti a, chuta tang chuan eng chen nge kan thleng tawh! Hetiang piansualna nei naute hi surgery hmanga enkawlna avang hian dam rei tak, hrisel takin an nung thei a ni.

"Double Aortic Arch" tih hmanga operation tih a ni

"Double Aortic Arch" surgery hi a him hle a, a result pawh a hlawhtling hle . I naute chu "cardiopulmonary bypass" (heart-lung machine) nena inzawm a ngai dawn lo .

Surgery hi "lateral thoracotomy" tih hmanga tih a ni. Chumi awmzia chu surgeon chuan naute rilru sir khatah, ruh pahnih inkarah incision a siam tihna a ni. Hei hi veilam lamah tih a ni fo thin a, a chhan chu chutah chuan naute tam zawk chuan chu "extra" little rib cage chu an nei thin. Surgery hmaa imaging test an tih hian surgeon chuan naute taksa chhung lam chu a en tha thei a, chutiang chuan surgery chu a ruahman thei bawk.

Surgeon hian "ligating and dividing" technique a hmang a . Chumi awmzia chu arch te tak te chu a kal tlanga thisen chhuak tur tihtawp nan an khih tihna a ni. Tichuan an tan a, an suture leh thin. Hetiang hian arch chu a inthen vek a, thlipui leh chaw kawng (esophagus)-a pressure a awm loh thlengin tih leh a ni.

I naute chu kar khat vel damdawi inah a awm ang a, chutah chuan a dam leh ang a, a lo haw leh ang.

"Kommerell diverticulum" (`Kommerell diverticulum - KD`) enkawl dan tur a ni.

A tlem berah chuan naute thenkhat "double aortic arch" nei te pawhin "Kommerell diverticulum (KD)" tih ang chi an nei thei bawk. Hei hi naute "right aortic arch" neiah a tam zawk a, mahse "double aortic arch" neiah chuan a tlem hle bawk.

He `KD` hi `aneurysm` a ni a, thisen kalna kawng chu `aortic arch` bula `aorta` hnuai lam atanga lo piang chhuak a ni. He bulge hian hmun a luah thei a, naute thlipui leh ei tur pipe-ah a press thei bawk. Harsatna a thlen nghal lo mai thei. Mahse, surgeon-te chuan a hnua harsatna awm lo turin `double aortic arch` an siam hian hei pawh hi paih chhuah an duh hle.

Lung lam harsatna dang enkawl dan

I naute hian thinlung lama harsatna dang, operation ngai a neih chuan double aortic arch nen a rualin enkawl theih a ni. Hei hian ``median sternotomy'' tih procedure a mamawh thei a, chu chu rilru lai takah incision siam a ni. I naute surgeon chuan i tan a tha ber tur a sawipui ang a, chu chu enkawl ngai thil awm dan azirin a ni.

Surgery avanga harsatna awm thei te chu engte nge ni?

Double aortic arch surgery atanga harsatna awm thei hi a tlem hle . A tlem berah chuan naute hian chaw pek harsatna emaw, thawk lama harsatna awm reng emaw a nei thei. Thâwk lama harsatna awm reng a awm chuan operation hnu kum khat chhungin a bo tlangpui.

Double aortic arch leh heart defect dang siamthatna atana surgery neih avanga harsatna awm thei chu a inang lo thei hle. Heng hlauhawm leh harsatna zawng zawng hi i naute surgeon nen sawiho rawh.

"Double Aortic Arch" hi a veng thei ang em?

Ni lo, "double aortic arch" tih dinhmun chu ven theih a ni lo . Naupai tirh atanga lo piang chhuak, pian tirh atanga awm thin thil a ni.

"Double Aortic Arch" vei te hmalam hun eng nge ni?

Naute leh naupang "Double Aortic Arch" surgery nei tawhte chuan hmalam hun duhawm tak an nei a ni . Engmah khapna awm lovin an khawsa thei a, thil pangngaiah an inhmang thei bawk.

Operation hnuah pawh i naute hian kum khat chhung chu thawk ri nasa takin a nei chhunzawm thei a ni . Hei hi naute thlipui (windpipe) chu "double aortic arch" vangin a lo thanglian kim loh vang a ni. Chuvangin, thlipui a chak zawk theih nan hun engemaw chen a la ngai dawn a ni.

A tlem hle a, naute leh naupangte hian operation an neih hnu kum khat aia tam pawh thawkna lama natna an la nei thei tho.

A pawimawh ber chu i naute chu checkup fo turin hruai la , symptoms kal zel i neih chuan doctor hnenah hrilh rawh. Naupang thinlung surgery nei tawh zawng zawng tan hun rei tak chhunga enkawlna hi a pawimawh hle.

Engtikah nge ka naute doctor ka biak ang?

Symptom thar i hmuh chuan, emaw, symptom awmsa chu a zual deuh niin a lang a nih chuan, i naute doctor nen inbia nghal rawh. Nausen leh naupang te te hi an inthlak nasa em em a, a chang chuan thil pangngai leh thil pangngai lo hriat a harsa thei hle. Mahse i naute chuan chu "seal ang chi" khuh emaw, thawk hah ri emaw a neih chuan i doctor hnenah hrilh nghal rawh. Naupan lai natna pangngai a ni thei. Mahse, a tlem berah chuan i naute thawk theihna tichhe thei thinlung lam harsatna chhinchhiahna a ni thei.

Engtikah nge 911 (emergency number) i biak ang?

"Double aortic arch" hian i naute thlipui (windpipe)-ah nunna atana hlauhawm tak pressure a siam thei a ni. I naute vun chu a sen (cyanosis) , emaw, i naute thawk harsatna nasa tak a neih chuan 911 call nghal rawh.

Ka naute doctor hnenah eng zawhna nge ka zawh ang?

I naute chu "double aortic arch" a ni tih hmuhchhuah a nih chuan zawhna tam tak i neih hi thil pangngai a ni. I naute dinhmun hriat a pawimawh a, engtikah nge operation a ngai tih te, i naute hian hriselna lama harsatna dang a neih leh neih loh hriat a pawimawh bawk. Zawhna i zawt duh mai thei:

• Engtikah nge ka naute hian operation a neih ang?
• Khawiah nge surgery hi tih a nih? Tuin nge perform?
• In lamah eng symptom nge ka fimkhur tur?
• Ka naute in lama awm a awlsam zawk nan eng nge ka tih theih ang?
• Ka naute hian thinlung lama harsatna dang a nei em?
• Ka naute tan nge ka chhungkaw dangte tan genetic testing ka neih tur em ni?
• Ka naute hmalam hun chu eng ang nge ni ang?

"Aortic Arch Syndrome" tih hi eng nge ni? "Double Aortic Arch" nen hian a danglam em?

Ni e, an pahnih hi tibuai suh. "Aortic Arch Syndrome" hi "Vasculitis" chi khat hmuh tur awm lo tak a ni. "Takayasu's arteritis" tia hriat a ni bawk.

"Vasculitis" tih hi i thisen kalna kawng bang a inflammation a ni. Thisen kalna kawng eng pawhah a awm thei a, thisen kalna kawng te ber, capillaries-ah pawh a awm thei. "Takayasu's arteritis" tih hi thisen kalna kawng lian lo leh lian lo tak takte inflammation a ni. "aortic arch" leh a branch lian ber berteah a awm tam ber. Chuvangin "aortic arch syndrome" an ti bawk.

Takayasu's arteritis ("aortic arch syndrome" tia hriat bawk) hi puitling naupang leh puitling naupangte zingah a awm thin . Hei hi a hmaa kan sawi tawh congenital "double aortic arch" aiin harsatna danglam tak a ni a , enkawlna mamawh pawh a danglam hle.

Nausen piang hi lawmna leh lawmna hun a ni tlangpui. Mahse, i naute hian thinlung natna a nei tih i hriat chuan, naupai lai emaw, a pian hnuah emaw, chu hlimna chu lungkhamna leh rinhlelhnain a thlak a ni. I naute hian "double aortic arch" a nei tih i hriat chauh a nih chuan eng nge lo thleng dawn tih i ngaihtuah mai thei.

Lungngai suh. I medical team chuan heng zawng zawng hi step by step in an pui ang che. A hmasa ber chu i la tawh a, chu chu i naute dinhmun hriat belh a ni. Thu lawmawm tak chu double aortic arch surgery hi a him hle a, a hlawhtling hle bawk. I naute hian thinlung lama harsatna dang emaw, genetic condition emaw a neih chuan enkawlna chu a buaithlak deuh thei. Mahse, nau piang thar enkawlna lama hmasawnna a awm avangin i naute chu a mamawh enkawlna dik tak a neih theih nan i pui thei a, a dam leh thei a, naupan lai hun hlimawm tak a neih theih nan i pui thei bawk.

Chuti a nih chuan, kan sawi tawh atang hian eng thil nge hriat reng tur pawimawh ber? (In lama hruai tur thuchah)

Okay, he "Double Aortic Arch" chungchanga kan sawi tawh atanga i hriat reng tur thenkhat kha han khaikhawm ila:

• "Double aortic arch" hi pianpui thinlung natna a ni . Naute aorta hi arch pahnih ah a inthen a, chu chuan trachea leh esophagus compression a thlen thin.
• A lan chhuah dan ber chu thawk harsa, thawk hah, ei harsa, leh thawkna lama natna hrik awm fo te hi a ni .
• He natna hi test hmanga hriat theih a ni a, chungte chu `CT scan`, `MRI`, `Echocardiogram` te hi a ni . A châng chuan naupai lai pawhin hriat theih a ni.
• Enkawlna chu surgery a ni . He surgery hi a him hle a, a hlawhtling hle bawk.
• Operation hnua naute tanNun pangngai, hrisel takin i nung thei a ni.
• I naute hian thawk harsa emaw, thawk hah emaw ang chi natna lan chhuahna a neih chuan doctor thurawn zawng nghal rawh .
• Lungngai suh . Tunlai damdawi lam hmasawnna avang hian he natna hi hlawhtling taka enkawl theih a ni. I medical team chuan i mamawh tur support an pe ang che.

` Double Aortic Arch, Congenital Heart Disease, Vascular Rings, Nausen Asphyxia, Nausen hriselna, Lung Surgery