I naute thinlung veilam chu a chak lo em? Hypoplastic Left Heart Syndrome (HLHS) chungchang hi han sawi ila

I doctor-in i naute piang thar hian thinlung natna khirh tak a nei tih a hrilh che hian i rilru put hmang chu sawifiah a harsa hle. Hlauhna, mangang leh lungngaihna nen chuan zawhna "Kan naute hi engtin nge a awm ang?" i rilruah a rawn ri chhuak. Hun harsa tak a ni. Mahse hetiang hun lai hian a pawimawh ber chu he dinhmun hi hriat chian vek hi a ni. Vawiin hian kan sawi dawn a, Hypoplastic Left Heart Syndrome (HLHS) chungchang kan sawi dawn a, hei hi thinlung natna khirh tak leh hmuh tur awm lo tak, nau piang avanga lo awm thin a ni. He thuziakah hian he thu hi awlsam takin, i hriatthiam theih angin kan sawi dawn a ni.

Hypoplastic Left Heart Syndrome (HLHS) hi eng nge ni tak tak?

A awlsam zawngin sawi ila, Hypoplastic Left Heart Syndrome (HLHS) hi naute pum chhunga a seilian laiin thinlung veilam a lo thang tha lo a nih chuan a lo awm thin a ni. Hei hi pianpui thinlung natna a ni. "Hypoplastic" tih thumal hi "underdeveloped" tihna a ni.

Kan thinlung hi in te tak te, pindan pali nei ang mai a ni. Chhawng chung lamah pindan pahnih leh a hnuai lamah pindan pahnih a awm. HLHS vei naute thinlung veilam sir thenkhat, a bik takin:

• Left ventricle: Hei hi thinlung pumping chamber ber a ni. Thisen thianghlim, oxygen awmna taksa pum puiah a pump chhuak thin. HLHS-ah chuan a tlem hle a, a hmasawn lo hle bawk.
• Aorta: Thisen kalna kawngpui ber, veilam ventricle atanga taksa peng dang thlenga thisen phurtu a ni. Hei pawh hi a tawi leh te deuh fo bawk.
• Mitral leh aortic valve: Hengte hi kawngkhar ang a ni. Thisen chu kawng khatah chauh a luang chhuak thei a ni. HLHS-ah chuan heng valve te hi a lo thang tha lo thei a, a khar vek thei bawk.

Heng a peng lian ber berte hi an thang tha tawk lo a, chuvang chuan thinlung veilam hian taksa peng dang zawng zawngah oxygenated thisen a pump tling thei lo. Hei hi dinhmun pawi tak a ni. A châng chuan, thinlung chung lam pindan pahnih inkârah chuan bangah khur tê tak tê a awm thei a, chu chu atrial septal defect an ti a ni.

Hei leh thinlung hrisel hi eng nge a danglamna?

Thinlung hrisel takah chuan dinglam leh veilam pahnih hian hna an thawk dun a ni. A dinglam chuan taksa atanga oxygen tlachham thisen chu la chhuakin, oxygen la turin lungah a thawn chhuak ang tih han ngaihtuah teh. Lung atanga oxygen tamna thisen chu thinlung veilam lamah a kir leh thin. Tichuan veilam (left ventricle) a pump chak tak chuan chu thisen chu taksa dang zawng zawngah a pump chhuak ta a ni.

Mahse HLHS vei nauteah chuan thinlung veilam chu a chak lo hle. Chuvangin chu hna chu a thawk thei lo. Chuti a nih chuan eng nge thleng? Thinlung dinglam chuan hna pahnih hi a mah chauhin a thawk tur a ni . Chumi awmzia chu ventricle dinglam hian lungah thisen a pump a ngai a, chutih rualin taksa dang zawng zawngah thisen a pump chhuak bawk.

Engtin nge hetiang hi a lo thlen? Nausen pum chhunga a awm chuan thinlung chhunga thisen kalna kawng lian pahnih inkarah hian hun eng emaw chen inzawmna a awm a. Ductus arteriosus an ti a.'Shortcut' ang mai a ni. He ‘shortcut’ hi HLHS vei naute pian hnua dam khawchhuahna atan a pawimawh hle. A chhan chu thisen hi he tube kaltlangin taksaah a luang lut a ni. A tlangpuiin he tube hi naute pian hnu ni engemaw zat hnuah a khar thin. Mahse he tube hi HLHS vei nauteah a khar a nih chuan taksaah thisen kal theihna tur kawng a awm lo. Chuvangin, he natna hi enkawl a nih loh chuan naute hian ni tlemte chauh dam a nei ang.

Engtin nge i naute hian he natna hi a nei tih i hriat theih ang? Eng nge a lan chhuah dan?

Nausen piang tharin HLHS a neih chuan a chang chuan a lan dan chu a tir lamah hmuh tur a awm lo. Mahse heng symptoms te hi darkar tlemte emaw ni engemaw zat chhungin a lo lang thei a ni. Hei hi nu leh pa ten kan hriat chian a pawimawh hle.

Engvangin nge naute chungah hetiang hi a thlen? Eng nge a chhan?

He zawhna hi nu leh pa tin rilruah a awm reng a ni. "Engvangin nge kan naute chungah hetiang thil hi a lo thlen? Thil dik lo kan ti em?"

Mahse thudik tak chu, a tam zawkah chuan HLHS awm chhan chiang tak a awm lo . Chu chu nu emaw, pa emaw avanga lo awm thil a ni lo tihna a ni. A châng chuan, genetic factors hian hmun a chang thei bawk. Chu chu, chhûngkuaa genetic change ṭhenkhat chuan a hlauhawmna a tipung thei tihna a ni. Naute, genetic condition dang, Turner syndrome emaw trisomy 18 emaw nei te pawh HLHS vei an hlauhawm hle.

Engtin nge doctor-te hian he natna hi dik taka an hriat theih?

Vanneihthlak takin tûn laia technology hmasawn tak hmang hian he natna hi naute pian hmain, chu chu naupai laiin hriat theih a ni . Nau neih hmaa ultrasound scan pangngai neih laiin thinlungah thil danglam a awm a nih chuan i doctor chuan specialist hnenah a refer ang che a, nausen echocardiogram tihsak turin a ti ang che. Hei hian naute thinlung insiam dan leh a hnathawh dan chiang takin a hmu thei a ni.

Naute pian hnua a dinhmun hriat chian nan doctor chuan naute natna lan chhuah dan a en ang a, a rilru chu stethoscope hmangin a ngaithla ang a, thinlung ri (heart murmur) pangngai lo a awm leh awm loh a en ang. Tichuan, a natna hriat chian nan test eng emaw zat tih a ni ang a, chungte chu:

• Chest X-ray: Chest X-ray hian thinlung leh lung lian leh te, a pianzia a enfiah thei a.
• Echocardiogram: Hei hi test pawimawh ber a ni. Thinlung video scan ang mai a ni. Thinlung pindan, valve leh thisen kalna kawngte chu chiang takin a lang vek a. Hei hian HLHS a awm tih a nemnghet a ni.
• Electrocardiogram (EKG): Thinlung electric hnathawh dan tehna test a ni.
• Pulse oximetry screening: Naute kut zungtang emaw beng emaw-ah clip ang chi hmanraw te tak te dahin thisena oxygen awm zat tehna a ni. He value hi HLHS vei naute tan chuan a hniam hle.

Hetiang dinhmun hi enkawlna tur a awm em? Naute hi chhandam theih a ni em?

Ni e, hei hi natna khirh tak a ni a, mahse enkawl dan erawh a awm. Mahse hei hi damdawi hmanga tihdam theih natna a ni lo. Naute nunna chhanhim nan chuan stage hrang hranga surgery complex tak tak tih a ngai a ni.

Step khatna: Naute dinhmun nghet taka siam

Operation hma hian naute chu stabilized a ngai a ni. A hmasa ber chu ductus arteriosus , kan sawi tawh thisen kalna ‘shortcut’ kha hawn reng hi a ni. Damdawi pakhat prostaglandin an tih chu thisenah pek a ni. Damdawi dang pawh nausen thinlung thawkna atan hman theih a ni a, ventilator pawh nausen thawk thei turin hman theih a ni bawk.

Step hnihna: Stage thum nei Surgical Series

He surgery series-a thil tum ber chu veilam chak lo tak chu bypass vek a, thinlung dinglam (right ventricle) chak zawk chu taksa pum puia thisen pump hna pek a ni. Thisen kal dan chu kawng danglam takah redirect ang mai a ni.

1. Norwood procedure: Hei hi naute pian atanga kar hnih hmasa berah tih thin a ni. Hei hi surgery buaithlak tak, serious tak a ni. Hetah hian surgeon-te chuan:

• Aorta lo thanglian lo chu siam thar leh a ni.
• Ventricle dinglam atanga thisen chu lung lam pan nghal turin special tube (shunt) dah a ni.
• Chutiang chuan thinlung "tubular system" chu siam danglam a ni a, chutiang chuan ventricle dinglam chuan taksa pum leh lungah thisen a pump thei a ni.

2. Glenn surgery (Bidirectional Glenn shunt operation): Hei hi naute thla 4 leh thla 6 inkar a nih chuan tih thin a ni . Hetah:

• Surgery hmasa berah tube (shunt) dah chu lakchhuah a ni.
• Taksa chunglam (superior vena cava an tih vein atanga lo chhuak) oxygen tlachham thisen chu lung nen direct-in a inzawm a ni.
• Hei hian ventricle dinglam chunga phurrit chu nasa takin a tihziaawm a, a chhan chu tunah chuan taksa chunglam atanga thisen pump a ngai tawh lo va, lungah a kal nghal a ni.

3. Fontan kalphung: Hei hi a tawp ber a ni. Thla 18 atanga kum 4 inkar ah tih thin a ni . Hetah:

• Taksa hnuai lam (inferior vena cava an tih vein atanga lo chhuak) oxygen tlachham thisen chu lung nen direct-in a inzawm a ni.
• He surgery zawh hian taksa atanga thisen oxygen tlachham zawng zawng chu lungah a kal nghal vek a ni. Thinlung ventricle dinglam hian thisen thianghlim, oxygen tamna chu lung atanga taksa pum puiah a pump chhuak chauh a ngai a ni.

Heng surgery pathumte hi an tih zawh hnu hian naute thisen kalna kawng chu kawng thar takin a thawk tan ta a ni.

Enkawlna avanga harsatna awmte chu engte nge ni?

Heng surgery te hi nunna chhanhim thei mahse, a buaithlak hle a, hlauhawm leh harsatna a keng tel thei bawk. Surgery neih chhung leh operation hnuah pawh harsatna a awm thei.

• Ventricle dinglam chu a phurrit rit tak avangin a chak lo hle.
• Heart valve atanga thisen chhuak.
• Liver natna te.
• Thinlung rhythm pangngai lo.
• Thisen a chhuak.
• Infection awm thei te.
• Chaw ei harsat.
• Seizures a awm thin.
• Kidney-a nghawng a neih dan.

Doctor chuan heng hlauhawm zawng zawng hi chipchiar takin a sawipui ang che. He zinkawng an zawh lai hian medical team te chuan naute hi uluk takin an enfiah dawn a ni.

Heart transplant hi duhthlan tur tha tak a ni em?

Ṭhenkhatah chuan naute thinlung dinhmun a buaithlâk hle emaw, doctor-te chuan naute chu operation aṭanga dam chhuak lo tûra an ngaih emaw chuan, thinlung thlak an rawt thei a ni . Mahse thinlung inmil tak a awm hma chu an nghah a ngai a ni. Tin, heart transplant hnuah naute hian a dam chhung zawngin immunosuppressive drugs a ei a ngai dawn bawk.

Naute hian he natna hi a nei a nih chuan nu leh pa kan nih angin eng nge kan hriat tur?

He zinkawng hi a harsa hle a, mahse damdawi lam enkawlna leh enkawlna mumal a awm chuan HLHS vei naupangte chuan nun tha tak an nei thei a ni.

• Lifelong medical supervision: Operation hnuah naupang chu a dam chhung zawng cardiologist pan a ngai dawn a ni. Kum khatah vawi khat tal check-up an nei tur a ni.
• Damdawi: Naupang tam tak chuan an dam chhungin thinlung damdawi an ei a ngai dawn a ni.
• Surgery dang hmaa antibiotics: Surgery dang eng pawh, ha lakchhuah hma hian thinlung natna (endocarditis) laka inven nan antibiotics i ei hmasak phawt a ngai a ni.
• Taksa tihchak: I fate taksa tihchakna hi tihkhawtlai a ngai mai thei. Thil hahthlak tak tak, inelna infiamna ang chi hi a tlangpuiin a tha lo. Hemi chungchangah hian doctor hnenah thurawn zawt rawh.
• I rilru hriselna: He zinkawng hi nu leh pate tan chuan a hahthlak hle. A stressful thei hle. Chuvangin, i pasal/nupui leh chhungte nen i rilru put hmang sawi rawh. A tul chuan counseling zawng rawh. I chak hunah chauh i fa chu i enkawl tha thei ang.