Naupang thenkhat chuan kawng khata an mit an hawi harsa tih i hmu ngai em? A nih loh leh mit pakhat chu hnar lam hawi a, mit dang chu beng lam hawi ang mai a ni. Nu leh pate hian hetiang thil an hmuh hian an lungkham nasa hle a, a bik takin an fate chunga thil thleng hi thil awmdan pangngai a ni. Vawiin a kan sawi tur Duane Syndrome hi pianpui natna a ni a, mit chetna nena lo awm a ni. A awlsam zawngin hei hi strabismus chi khat a ni.
Duane Syndrome hi eng nge ni? Tlemin i hrilhfiah thei ang em?
Okay, hei hi tlem a awlsam zawkin han sawifiah ila. Duane Syndrome vei chuan a mit chu a sir lam, chu chu hnar sir leh beng sir lam hawi a harsat thin. Mit pakhat a ni thei a, mit pahnih a ni thei bawk. Heng mitte hi a sir lam hawi harsat bakah hian mi thenkhat chuan chung leh hnuai lam en harsa an ti thei bawk.
Thil dang pakhat chu mit hi a inmil lo va, a sir lamah an en a, mit chet tum hian mitmeng pawh a che danglam thei hle. A chhan ber chu kan mit chhunga thau (muscles) control tu nerve (cranial nerves) te hian hna an thawk tha lo a ni. Ngaihtuah teh, motor steering wheel chu a sir lehlamah a herh theih loh ang mai a ni.
A tam zawkah chuan 80% leh 90% inkar ah hian he natna hian mit pakhat (unilateral) chauh a nghawng a ni. Tin , mit veilam hi a nghawng nasa zawk tih hmuhchhuah a ni bawk .
Hei hi hming dang a awm em?
Ni e, Duane Syndrome hming atan hian hming dang engemaw zat hman a awm bawk. I doctor-in heng hming zinga pakhat a sawi chuan lungngai suh, an dinhmun inang vek an ni.
- Duane retraction natna a ni
- Mit lak let theihna syndrome
- Retraction syndrome emaw, pianpui atanga inhnukdawk (congenital retraction syndrome) emaw a ni thei
- Duane radial ray natna a ni
- Still-Turk-Duane natna a ni
Heng hmingte hi hriat a tha, a chhan chu a chang chuan heng hmingte hi medical record-ah a lang thei a ni.
Duane Syndrome chi hrang hrang a awm em?
Ni e, ei tur kan sawi ang bawkin Duane syndrome hi chi thum a awm a. Type 1, type 2, leh type 3 an ti a, tunah chuan type tin hi a hranin i en ang u.
Type 1 Duane syndrome a ni
This is the most common type , Duane syndrome vei zawng zawng zinga 78% vel a ni.
Nangmah emaw, i fa emaw hian chi khatna i neih chuan pawn lam, chu chu beng lam hawia hawi a harsa hle.. Mahse i mit chu i hnar sir lamah i hawi thei. Mahse chutianga i tih chuan mit awmna hmun hawnna chu a te zawk a, mitmeng chu ``retract'' angin a lang thei bawk. A châng chuan mit hi i hnar sir lamah hrual ang maiin a lang thei bawk (esotropia).
Type 2 Duane syndrome a ni
This is the least common type , he natna vei zinga 7% vel an ni.
A chi hnihna nei chuan mit chu chhung lam hawiin, chu chu hnar lam hawiin a hawi thei lo . Mahse, mit chu beng lam hawiin an hawi thei a ni. Mahse, chutianga an tih chuan mit hawnna chu a chi hmasa ang bawkin a te zawk a, mitmeng chu chhung lam pan ang maiin a lang thei. Heng mite hian an mit chu pawn lam, beng lam hawi (exotropia) an ni thei.
Type 3 Duane syndrome a ni
Hetiang chi hian damlo zawng zawng zinga 15% vel a nghawng a ni.
Type 3 vei chuan a mit chu a sir lehlamah, chhung lam leh pawn lam hawia hawi theihna a nei tlem hle . Tin, angle hrang hrang atanga thlir chuan mitmeng chu a zim ang maiin a lang thei a, mitmeng chu chhung lam pan angin a lang thei bawk.
He classification hi doctor-te tan chuan enkawl dan tur ruahmanna siam nan leh natna awm dan hriatthiamna atan a pawimawh hle.
Duane Syndrome hi engtiang chiahin nge a awm?
United States-a statistics atanga a lan dan chuan mipui 4% vel, a nih loh leh mi maktaduai 13 vel chuan strabismus chi khat emaw an nei a ni. Hetiang natna vei zinga 1% leh 5% inkar hian Duane syndrome an nei nia chhut a ni.
Thil dang pakhat chu he natna hi hmeichhiaah hian a tam zawk deuh a ni .
Hei hi eng symptoms nge ni? Naupang tê tête pawhin hengte hi an hmu em?
Ni e, Duane syndrome symptom thenkhat chu naute naupang takah pawh hmuh theih a ni. A lan chhuah dan ber chu eng nge ni tih i lo en ang u:
- Lu tilt pangngai lo: Duane syndrome vei thenkhat chuan an mit dinglam reng tumna atan an lu chu a sir khatah an tilt thin. Bang chunga thlalak tar i en hian i lu i ti nghing ang maiin ngaihtuah rawh.
- Strabismus: A châng chuan, mahse a ni lo, mit pahnih hian kawng khata an kawhhmuh lo niin a lang .
- Amblyopia emaw mit lazy: Hei hi "lazy eye" an ti bawk. Thluak hian mit tha zawk a hman thiam deuh deuh chuan mit natna atanga signal lo lut chu a ngaihthah tan ta a ni. Hei hian hun kal zelah chu mitah chuan mit hmuhna a tichhe thei a ni .
- Mit pakhat chu a dang aiin a te zawka lang: Hei hi mitmeng a zim vang a ni.
- Kawng khata en laiin mit chu a chung emaw a hnuai emaw a sawn: Hei hi ``up-shooting'' emaw ``down-shooting'' emaw an ti a. Mit chu a zuang chho emaw, a hnuai emaw a zuang nghal vat ang maiin a lang thei.
I fate zingah heng symptoms te hi i hmuh chuan mit lam doctor hnenah thurawn dil ngei ngei tur a ni.
Duane Syndrome vei te hian damdawi lam natna dang an nei thei em?
Engtik lai pawhin ni lo mah se, Duane syndrome hi a chang chuan hriselna lama harsatna dang nen a inzawm thei bawk. Chung zinga ṭhenkhat chu:
- Hriatna lama harsatna nei
- Goldenhar syndrome: Hei hi hmai, beng leh ruhroah thil dik lo awm thei a ni.
- I ruhro emaw, i vertebrae emaw a harsatna
Tin, mit natna dang pawh Duane syndrome nen hian a awm thei bawk. Entir nan:
- Cataract: Hei hian mit lens a clouding tihna a ni.
- Microphthalmos: Hetiang a nih chuan mit chu a tlangpuiin a te a ni.
- Nystagmus: Hei hi mit chu rang tak leh thunun theih loha a kal lai a ni.
- Crocodile tears syndrome: Hei hi hmai nerve dysfunction condition Bell’s palsy an tih nen a inzawm a ni. Hetiang dinhmunah hian thil ei emaw in emaw hian mittui a lo lang thin.
Chuvangin Duane syndrome an hriat chuan doctor-te pawhin hetiang ang chi dang a awm leh awm loh an enfiah bawk.
Duane Syndrome hi engte nge ni?
Duane syndrome hi genetic condition a ni a, mahse a tlangpuiin rochun a ni lo . Heng mit chetna lama harsatnate hi kan sawi tawh ang khan kan mit chetna control tu cranial nerve-a harsatna avanga lo awm a ni.
A bik takin, naupai laiin thalidomide damdawi ei tawh nu fate chu Duane syndrome (he damdawi hi hman a ni tawh lo) an vei tam zawk tih hmuhchhuah a ni.
Duane syndrome vei zinga 10% vel chuan chhungkaw member dang an nei a, anni pawhin he natna hi an nei ve bawk. Chutiang chhungkaw dinhmunah chuan mit pahnih hi a nghawng tlangpui (bilaterally).
Duane syndrome hi rochun a nih chuan naupangin an nu leh pate hnen atanga genes `CHN1`, `MAFB`, emaw `SALL4` chi hrang hrang a rochun vang a ni. Hetiang rochan dan hi `autosomal dominant` an ti a. Chumi awmzia chu mipa leh hmeichhia thliar lovin a thleng thei tihna a ni a, nu leh pa pakhat chauhvin he natna hi nei mahse naupangin a rochun thei tihna a ni.
Duane Syndrome hi a kai theih em?
Ni lo, a ni lo tak zet. Duane syndrome hi natna hrik kai theih a ni lo. Chu chu khawsik emaw, flu emaw angin mi pakhat atanga mi dangah a darh lo tihna a ni. Chuvangin hlauhna tur a awm lo.
Engtin nge Duane Syndrome hi hmuhchhuah a nih?
I doctor, a bik takin mit lam doctor chuan medical history kimchang a la ang a, i mit chu uluk takin a enfiah ang. I mit a tui awm zat leh a sir lehlamah i hawi kual theih dan te an teh ang.
Doctor chuan Duane syndrome nena inzawm thil dang awm leh awm loh enfiah turin test a ti thei bawk.
Condition dang sixth cranial nerve palsy tih a awm a, hei hi Duane syndrome nen a inang hle a, mahse chutiang chuan a awm lo. Doctor pawhin heng natna pahnih hi thliar hran a tum bawk ang.
Duane Syndrome hi engtin nge enkawl a nih?
Enkawl dan tur chu i kum, natna nasat dan leh damdawi lam harsatna dang i neih theih danah a innghat a ni.
- Mi thenkhat chuan enkawl an ngai lo mai thei: Duane syndrome vei thenkhat chuan enkawlna bik an mamawh lo. Mit doctor pan chhunzawm zel leh mit enfiah chhunzawm zel a ngai chauh a ni.
- Lazy Eye (Amblyopia) enkawlna): Mit lazy i neih ve bawk a nih chuan, chu mit chu mit tha tak chu patch hmanga khuh a, mit chak lo chu hna thawkrim zawka siamin, chu mit hmuhna tichak turin i bei thei ang. Hei hi class-a naupang fing tak chu hun engemaw chen a sir lama ding tura ngen a, naupang dang chu hun pek ang mai a ni.
- Surgery: Duane syndrome a nasat chuan mit ruh siam that nan surgery neih a ngai mai thei. He surgery hian nerve problem hi a tifel thei lo a, mahse mit ruhte chu a insiamrem leh thei a, lu tilt pangngai lo a tihziaawm thei a, hmalam hawia mit a ding nghet thei a, up-shoot/down-shoot a control thei bawk.
Mi zawng zawng hian operation an mamawh vek lo tih hre reng ang che. Chu chu i doctor-in a rel tur a ni.
Duane Syndrome hi a veng thei ang em?
Hetih lai hian Duane syndrome laka inven dan tur a awm lo. Duane syndrome (piangsual dang tam tak zingah) thlen thei damdawi thalidomide hi hman a ni tawh lo. Chuvangin hlauh a ngai lo.
Duane Syndrome ka neih chuan eng nge ka beisei ang?
Duane syndrome vei thenkhat chuan an lu chu tlem an herh thei a, an mit an ti tha thei a, nun pangngaiin an hmang thei bawk. Thil engemaw takah chuan a hmaa kan sawi tawh ang khan zai a ngai mai thei.
Duane syndrome nen hian natna dang i neih chuan i doctor pawhin chu natna chu a enkawl ve bawk ang.
Mit hmuh that nan leh/ emaw, i mit dinhmun siamthat nan glasses vuah turin a fuih thei bawk.
Doctor hnenah eng zawhna nge ka zawh ang?
I doctor hnenah hetiang zawhna hi i zawt thei ang:
- Genetic counselor ka hmu tur em ni? (A bik takin chhungkuaa mi tu emaw hian hetiang dinhmun hi a nei a nih chuan, emaw, fa tam zawk ka beisei a nih chuan).
- Mit hmuhna atana pui thei tur assistive devices a awm em?
Doctor chuan naupang chu a dam chhung kum 10 chhungin Duane syndrome a nei tih a hmuchhuak tlangpui ang. I mit hmuhna chungchangah emaw, i fate mit hmuh danah emaw ngaihtuahna i neih chuan doctor pan nghal rawh. I doctor chuan Duane syndrome enkawlna tha ber tur ngaihtuah turin a pui thei che a, amblyopia a awm chuan a enkawl thei bawk.
A tawp berah chuan thil hriat reng tur (Take-Home Message) .
Okay, chuvangin, kan sawi tawh Duane Syndrome kha a tawi zawngin sawi ila, heng thilte hi hre reng ang che:
- Duane syndrome hi pianpui natna a ni a, mit chu a sir lehlamah hawitir a harsa hle.
- Hei hi natna hrik kai theih a ni lo.
- A lan chhuah dan chu lu chu a sir khata hawitir, mit khap, mit pakhata mit hmuhna tlahniam te a ni.
- Hei hi chi thum a awm a, a chang chuan hriselna lama harsatna dang nen pawh a thleng thei bawk.
- Enkawlnaah chuan enfiahna, mit lazy patch emaw, operation emaw pawh a tel thei. Mi zawng zawng hian operation an mamawh vek lo.
- A pawimawh ber chu nangmah emaw, i fa emaw hian heng symptoms te hi i nei a nih chuan hlauthawng suh la, mit lam doctor hnenah thurawn leh enkawlna dik tak dil rawh.
He thu hi in tan a tangkai ngei ka beisei. Zawhna dang i neih chuan i doctor zawt hreh suh!
Duane syndrome, strabismus, pianpui mit natna, mit chetna, mit lazy, amblyopia, mit lama harsatna te











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