I fa naupang chu thinlung lama harsatna khirh tak neiin a piang em? A châng chuan doctor-te chuan i naute thinlung hian main pump pakhat chauh a nei tih an hrilh che a, chu chu ventricle a ni. Chutiang thila doctor-te’n an rawt special surgery chu ‘Fontan procedure’ an ti a. A nihna takah chuan he hming i hriat hian hlauhna leh rinhlelhna i neih hi thil pangngai tak a ni. Mahse hei hi kan hriat chian tawk chuan he zinkawng zawh tur hian chakna leh chakna nasa tak i nei ang. Hemi chungchang hi awlsam takin kan sawi dawn em ni?
Fontan Procedure hi a awlsam zawngin eng nge ni?
Hei hi hrethiam tur chuan thinlung hrisel hnathawh dan hi han thlir hmasa ila. Thinlung hrisel chuan chamber lian pali a nei a. A chung lamah pahnih (atria) leh a hnuai lamah pahnih (ventricles). Heng chamber pahnih hi thinlung pump lian ber pahnih an ni. Pakhat chuan oxygen tlachham, thisen thianghlim lo chu lungah oxygen la turin a thawn thin. A dang chuan oxygen tamna, thisen thianghlim tak chu taksa peng dang zawng zawngah a pump lut a ni.
Amaherawhchu, nausen thenkhat chu heng cell pahnih zinga pakhat hi mumal taka siam lohvin an piang thin. Tichuan hna thawktu cell pakhat chuan heng hna pahnih hi a thawk tur a ni. Mi pakhat tan hna pahnih thawh a ngai hi a hahthlak zia han ngaihtuah teh. Chutiang chiah chuan he cell pakhat hian a chau nghal thei a, a chhan chu lung leh taksaah thisen a pump a ngai a ni.
Fontan procedure hian a tih chu chu cell pakhata hnathawh tur tihtlem a ni. Hna thawkrim tura pui turin midang pek ang mai a ni.
Hetiang tih danah hian surgeon-te chuan taksa hnuai lam atanga oxygen tlachham thisen chu pulmonary artery-ah an thlunzawm a, thinlung chu an bypass a ni. Hei hi ‘shortcut’ thar siam ang mai a ni. A tlangpuiin, he tih hma hian tih dan dang Glenn procedure an tih chu taksa chunglam atanga thisen oxygen tlakchhamna chu lung lam pan turin an ti thin. He kalphung hrang hrangah hian Fontan kalphung hi a tawp ber a ni.
Chutianga kawng thar siam a nih chuan, chu cell pakhat hna awm chhun chu taksa pum puia thisen thianghlim, oxygen tamna pump chhuah hi a ni. Hei hi chu thinlung te tak te tan chuan thlamuanna ropui tak a ni.
He surgery hi tute nge mamawh a, engvangin nge?
He surgery hi naupang ventricle pakhat neia piangte chungah tih a ni ber. Kum 2 leh 5 inkar ah tih thin a ni .
Mahse he surgery hi mi zawng zawng tan a ni lo. Doctor chuan i fa chu uluk takin a enfiah ang a, hemi atan hian a inhmeh em tih a en ang. Entir nan:
- Naupang hnathawhna cell hi a chak em em a ngai a ni.
- Lung hi a hrisel tawk tur a ni a, chu chuan lungah thisen lo lut nghal a dawng thei ang.
A hnuaia table-ah hian he surgery hmanga enkawl thinlung natna lian ber ber thenkhat tarlan a ni.
| Dinhmun | Hrilhfiahna awlsam tak |
|---|---|
| Hypoplastic Left Heart Syndrome (HLHS) a awm a, a rilru a hah lutuk a, a rilru a buai em em bawk a. | Thinlung veilam (left ventricle telin) hi a thang tha lo hle. (Hei hi Fontan hnathawh chhan ber a ni) |
| Tricuspid Atresia a awm thin | Thinlung dinglama tricuspid valve hi a lo thang tha lo hle. |
| Pulmonary Atresia a awm thin | Lung chhunga thisen phurtu pulmonary valve block. |
| Double Inlet Left Ventricle ah a awm a | Heart chhunga thisen kalna kawng lian ber pahnih hi left ventricle nen an inzawm a ni. |
Surgery hma leh operation neih chhung hian eng nge thleng?
I fa chu operation atan a tha tih a rel hnuah doctor chuan test eng emaw zat a ti ang.
- Transthoracic Echocardiogram (TTE): Hei hi thinlunga ultrasound scan a ni. Thinlung insiam dan te, a valve te, a hnathawh dan te a tarlang tha hle.
- Electrocardiogram (EKG): Thinlung electric hnathawh dan tehna a ni.
- Heart Catheterization: Tube te tak te (catheter) chu thisen kalna kawng khat kaltlangin thinlung chhungah a lut a, chu chuan thinlung chhunga pressure leh oxygen level a teh thin.
- CT emaw MRI Scan: A then phei chuan hei hi thinlung leh a chhehvel thisen kalna kawng (3D)-a thlalak lak nan a tul a ni.
Surgery ni hian naupang chu mut tir turin anesthesia pek a ni. Chumi awmzia chu naupangin engmah hrehawm a nei lovang tihna a ni. Surgery neih chhung hian naupang chu hun eng emaw chen atana thinlung leh lung machine (heart-lung machine) hna thawk thei machine bik nen an inzawm ang . He machine hian surgeon-in connection thar (inferior vena cava atanga pulmonary artery thleng) a siam hma loh chuan taksaah thisen a pe ang.
A châng chuan surgeon chuan he kawngpui tharah hian khur te tak te (fenestration) a siam ṭhin.Surgery zawh hnua thinlunga pressure tihziaawmna tura tih a ni. Surgery pumpui hi darkar 4-5 vel a ni thei .
Surgery hnuah eng nge thleng? Risk a awm em?
Surgery zawhah naupang chu intensive care unit (ICU)-ah uluk taka enfiah turin dah a ni. Ni engemaw zat hnuah regular ward-ah sawn an ni. Damdawi ina awm zat chu ni 7 leh ni 13 inkar a ni .
He surgery hian a hlawkna bakah a hlauhawmna leh harsatna a nei a, chu chu hriat chian a pawimawh hle.
| Risk chi hrang hrang | Harsatna awm thei te |
|---|---|
| Hun rei lote chhunga risk awm thei (Operation hnuah) . | Pleural effusions, kal lama harsatna, thinlung tha lo, thinlung thawk dan pangngai lo, thin natna. |
| Hun rei tak chhunga risk awm thei (hun nen) . | Protein hloh enteropathy, thisen zam (thromboembolism), Fontan-associated liver disease (FALD), leh plastic bronchitis te a awm bawk. |
Hun a kal zel a, damlo thenkhat chuan he surgery hi a thatna a tlahniam thei a ni. Hei hi ‘failed Fontan’ an ti a. Chutih hunah chuan thinlung thlak a ngai mai thei. Doctor-te chuan hei hi zinkawngah an ngai a ni.
Naupangin eng ang hmalam hun nge a beisei theih?
Tun hma chuan cell pakhat neia piang naupang hmalam hun tur chu a chiang lo hle. Mahse tunlai hian medical science hmasawnna avang hian Fontan operation hian heng naupangte hi naupan lai atanga kal pelin, thalai lam pan leh puitling lam pan theihna hun remchang a siamsak ta a ni.
Statistics atanga a lan dan chuan Fontan operation nei tawh zingah hian:
- 90% vel chu kum 10 hnuah an dam tawh a ni.
- 85% vel chu kum 30 hnuah an dam tawh a ni.
Tunah hian mi tam tak chuan kum 50 pel tawhin nun hrisel takin an hmang mek a, mahse a pawimawh ber chu, heng naupangte hi a niI dam chhung zawngin cardiologist enkawlna hnuaia awm hi a pawimawh hle. Test leh check-up neih fo a ngai a ni.
Engtikah nge Doctor i hmuh a ngaih?
Operation hnua in lama i haw hunah a hnuaia symptoms te hi i neih chuan doctor hnenah hriattir nghal tur a ni:
- Surgery hliam atanga thisen emaw tui dang emaw a luang chhuak a nih chuan.
- Khawsik emaw, hri kai chhinchhiahna dang (khuh, khawsik) i neih chuan.
I fa dinhmun hi a buaithlak em avangin i hriatthiam loh zawng zawng doctor hnenah zawh hreh suh. I fa dinhmun hriatthiamna tha tak neih chuan i fa enkawl tha turin a pui ang che.
Take-Home Thuchah a ni
- Fontan procedure hi single-cell heart disease tihdamna famkim a ni lo. Thisen kal dan tidanglamtu, thinlunga pressure tihziaawmna, nun ti awlsamtu procedure pawimawh tak a ni.
- He surgery hian naupang cell pakhata hnathawh tur a tihtlem bakah taksaa oxygen level nasa takin a tisang bawk.
- Hun rei tak chhunga harsatna awm thei, thin natna ang chi, hun kal zelah lo awm thei te hriat a pawimawh hle.
- A pawimawh ber: Cardiologist hmuh a pawimawh a, operation hnuah i dam chhung zawngin checkup neih fo a pawimawh hle.
- I doctor nen zalen takin inbiakna nei rawh. Zawhna emaw, ngaihtuahna emaw i neih chuan anmahni nen sawiho rawh. I fate hriselna atan i awareness hi a pawimawh hle.











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