I hmai sir khat chu a rawn sen nghal a, a thawmhnaw a chhuak nghal a, a sir lehlamah chu a pangngai vek tih i hmu ngai em? Mi ṭhenkhat tân chuan hei hi thil mak tak, nuam lo tak pawh a ni thei. Hei hi damdawi lam hawi chuan Harlequin Syndrome kan tih chu a ni. A hming hi thil lian tak angin a lang thei a, mahse hlauh tur a ni lo a, mahse hriat chian a pawimawh hle.
Hei hi eng nge ni tak tak (Harlequin Syndrome)?
A awlsam zawngin, Harlequin Syndrome hi i hmai, i kawr, leh a châng chuan i rilru chunglam sir khat chauh a sen a, a thawmhnaw a chhuak ṭhin . Mak tak maiin heng zawng zawng hi i taksa sir lehlamah a thleng lo va, chu chu a pangngai reng a ni.
Hetiang dinhmun hi kan taksa sympathetic nervous system hnathawh dan a inthlak vang a ni . Tunah chuan he sympathetic nervous system hi eng nge ni tih i ngaihtuah mai thei. Kan taksa hian control system mak tak mai a nei a, chu chu autonomic nervous system an ti a ni. Hei hian thil tam tak, kan ngaihtuah ngai lovin "automatic"-a thil thleng, kan thinlung chakna, thisen sang, thawk dan, leh chaw ei dan te chu a thunun a ni.
He autonomic nervous system-a tel ve chu sympathetic nervous system hi a ni. Kan taksa ‘alert’ system ang mai a ni . He system hi kan tlan lai te, kan hlauh lai te, emaw, hlimna nasa tak emaw, lungngaihna nasa tak emaw ang chi emotion chak tak kan neih hian a activate thin. Hei hi ‘fight-or-flight’ response an ti a ni. He sympathetic nervous system hi kan taksa lumna control turin kan taksa chu thawk hah turin signal petu a ni a, chu chu kan taksa lum leh vawt tura exercise kan tih ang bawkin. (Harlequin Syndrome) He sympathetic nervous system hi a thawh chuan symptoms a lo lang thin.
(Harlequin Syndrome) leh (Harlequin Sign) hi thil hrang hrang pahnih a ni em?
Ni e, a danglamna tlem a awm. (Harlequin Syndrome) tih hian a hmaa ka sawi tawh neurological condition a kawk a ni. (Harlequin Sign) tih hian natna lan chhuahna ber a kawk a ni. Chu chu taksa sir khata vun rawng a inthlak (redness or darkening) a, a sir lehlamah vun chu a dum emaw, a normal emaw a awm reng tihna a ni. Hei (Harlequin Sign) hi (Harlequin Syndrome)-ah chauh ni lovin hriselna lama harsatna dang thenkhat chhinchhiahna angin kan hmu thei bawk.
Hei hi dinhmun tlanglawn tak a ni em? Nunna atana hlauhawm a ni em?
Harlequin Syndrome hi a takah chuan a awm lo hle . Khawvel pumah hri kai tlemte chauh hmuhchhuah a ni. Chuvangin i la hre lo a nih chuan thil mak a ni lo.
A pawimawh ber chu he dinhmun hi nunna atana hlauhawm a ni lo . Tin, i dam chhung pawh a nghawng dawn lo bawk. Chuvangin ṭul lova hlauh chhan tur a awm lo.
Hei hi eng symptoms nge ni?
Harlequin Syndrome-ah chuan i taksa sir lehlamah i hmuh dan a inang lo.
A natna vei lam atanga hmuh theih symptoms:
- I vun rawng pangngai aia vun sen emaw dum emaw.
- Thawmhnaw a chhuak nasa hle.
- Chu lai hmuna vun chu khawih chuan a lum hle.
A nghawng lo lam atanga hmuh chhuah symptoms:
- Vun dum (pale skin) a ni.
- Thawmhnaw hak lo tak tak.
- Chu lai hmuna vun chu khawih chuan a vawt hle.
Chutiang chuan heng features te hi taksa sir lam chu a chanvea then ang maiin a lang. I hmai lai tak a\anga, i hnar hnuai lam, leh i rilru thlenga dinglam line siam chu han mitthla teh.
Heng symptom lian ber berte bakah hian symptom dang langsar lo deuh thenkhat pawh hmuh tur a awm thei bawk:
- Hmun thenkhatah chuan vun a vawt a, a hring ang maiin a hring chhuak thin.
- Lu na.
- Hnar luang chhuak .
- Mit atang chuan mittui a rawn chhuak a.
- Mitmeng sir khata tlak leh/ emaw mitmeng inthlak danglamna ( Horner Syndrome tia koh bawk, chu chu natna hran nen a inzawm thei).
Engtikah nge heng symptoms te hi a lo lan?
Harlequin Syndrome chhinchhiahnate hi i nei thei a, a bik takin a hnuaia thil awmteah hian:
- Exercise i tih laiin: Gym-a tlan, zuang, inkhelh emaw, workout emaw lai.
- Emotion chak tak emaw rilru lama harsatna i neih lai: exam emaw interview emaw ang chi thil pakhat hmaa i hlim em em lai, i lungngaih em em lai, i hlauhthawn lai emaw, pressure i neih lai emaw.
- Khaw lum laiah: ni chhuahna hmuna chhuah lai te, room lum chhunga awm lai te.
- Chaw tui tak ei hunah: Chili tam tak nena siam chaw ei hian.
I ṭhiante nen cricket inkhelh laiin i thawmhnaw a chhuak nasa hle tih han ngaihtuah teh, i hmai dinglam chauh chu a sen a, a thawmhnaw a chhuak a, mahse veilam erawh a tha a, a hma ang bawkin. Chu chu he thil tawnah hian a thleng a ni.
Harlequin Syndrome hi engte nge ni?
A tam zawkah chuan Harlequin Syndrome awm chhan chiang tak hmuh a harsa thin . Chu chu a chhan a chiang lo tihna a ni. Mahse, zirchianna chuan kan autonomic nervous system dinglam leh veilam a cell te inbiakpawhna a tihchhiat vang a ni thei tih hmuhchhuah a ni.
A châng chuan, he inbiakpawhna kawngah hian tihbuai a awm thei bawk. He inbiakpawhna thuchah hi kan thluaka hypothalamus atanga kan rilru chunglam thoracic spinal cord thlengin a kal a ni. Chutah chuan sympathetic nerve te hian hmai leh taksa chunglam a supply a ni. He pathway hian thawmhnaw leh thisen kalna kawngte a control a ni.
Hetianga inthlak danglamna hi a awm theih chhan hrang hrang a awm a:
- Nerve pathway-a lo awm tumor a ni.
- Infection emaw inflammation emaw avanga hliam emaw chhiatna emaw .
- Chest chunglam operation avanga accident, ruhro operation ang chi .
Hetiang hi tuin nge nei tam zawk? (Risk factor hrang hrang) 1.1.
He natna, Harlequin Syndrome tia koh hian kum eng pawh ni se, naute, naupang, leh puitlingte pawh a nghawng thei a ni . Mahse, he natna hi i vei theihna a sang zawk thei a, chu chu:
- Endoscopic thoracic sympathectomy (surgical procedure hmanga thawk hah lutuk enkawlna atana hman thin) i neih tawh chuan.
- Anesthesia i dawng tawh a nih chuan.
- I sympathetic nervous system tichhe thei accident i tawk tawh a nih chuan.
- Horner Syndrome ang chi damdawi lam natna dang a awm chuan .
Hei hian eng harsatna nge a thlen theih?
Hei hi a tlem hle nachungin Harlequin Syndrome vangin harsatna thenkhat a awm thei. Chungte chu:
- Taksa lum leh vawt control harsat.
- Hmêl rawng (a sir khatah) inthlak danglam reng a ni.
- Mahni hmel lan dan ngaihtuah avanga lungngaihna, lungkhamna emaw, mahni inngaihsakna hniam emaw . A chhan chu, midangte’n khawtlang nunah hetiang hi an hmuh hian mi thenkhat tan chuan a zahthlak deuh thei a ni.
Engtin nge dik taka (Harlequin Syndrome) hi kan hriat theih ang? (Diagnosis) tih a ni.
Doctor chuan Harlequin Syndrome i neih leh neih loh chu i symptoms enfiahin a hre thei ang. A hmasa ber chu taksa enfiahna a ni . Tichuan, natna dang, chutiang bawka chhinchhiahna awm thei chu paih chhuah a, a chhan bulpui a awm leh awm loh hriat nân test hrang hrang an nei a ni.
Harlequin Syndrome hriat theihna tur test hrang hrang a awm a:
- Stress test: He test-ah hian doctor chuan exercise a pe ang che a, taksa chakna hian symptom a thlen em tih a en ang che. Exercise neih laiin Harlequin Syndrome symptoms hi a langsar zawk thei.
- Imaging test: Heng test te hian doctor chuan i taksa chhungril a hmu thei a. Hengte hi painless test a ni. Entirnan , rilru X-ray, CT scan (Computed Tomography), leh MRI (Magnetic Resonance Imaging) te hi a ni.
Hei hi eng enkawlna nge ni?
Thu lawmawm tak chu Harlequin Syndrome hi enkawl a ngai ngai lo . A châng chuan a dinhmun chu a mah chauhin a ṭha chho thei bawk. Doctor-in enkawlna a rawt leh rawt loh chu i natna lan chhuah chhanah a innghat a ni. Enkawlna kawng hrang hrangte chu:
- Therapy emaw counseling emaw hian he natna avanga khawtlang nun hrehawmna leh rilru hahna hi a tihziaawm thei a ni.
- Hmai sen emaw vun rawng danglam emaw control nana vaccine pek thin`(stellate ganglion block)` tih a ni.
- Botulinum toxin injection hmangin thawk hah leh a lan chhuah dan dangte control.
- A chhan chu tumor emaw lesion emaw a nih chuan surgery emaw radiation therapy emaw hmanga paih chhuah a ngai dawn a ni.
Harlequin Syndrome i neih chuan eng nge i beisei theih ang?
Harlequin Syndrome hian i taksaah harsatna lian tham a thlen lo tlangpui. Hun kal zelah i symptoms te chu a mah chauhin a bo thei. A nih loh leh, exercise i tih emaw, chaw tui tak i ei emaw chauhvin symptoms i nei thei bawk. Mi zawng zawng hian enkawlna an mamawh vek lo. I doctor chuan i dinhmun leh nakin lawka i beisei turte a hrilh belh ang che.
Heng symptoms te hi eng chen nge a awm?
Symptoms hi minute tlemte atanga darkar tlemte chauh a ni tlangpui . Chumi awmzia chu, natna lan chhuahna thlentu thiltih i tihtawp hnuah chuan hun rei lote chhungin vun chu a pangngaiin a awm leh ang. Entirnan, exercise i tih laiin symptoms a lo lang a nih chuan vawi khat exercise i chawlhsan a, i lum a, i chawlh hnuah vun chu a pangngaiin a awm leh ang.
Harlequin Syndrome hi a veng thei ang em?
Tun thlenga hmuhchhuah a nih angin Harlequin Syndrome hi ven dan tur a awm lo .
Engtikah nge doctor i hmuh ang?
Harlequin Syndrome symptoms i neih chuan taksa sir khat chauh a thawmhnaw hak leh vun rawng inthlak danglam te hi doctor pan a pawimawh . Harlequin Syndrome hi a tlangpuiin ngaihtuah tur a awm lo. Mahse, a tlem berah chuan damdawi lam dinhmun hnuaia awm, tumor ang chi chhinchhiahna a ni thei a, chuvangin a chhan dik tak hriat chian nan doctor pan a pawimawh hle.
Doctor hnenah eng zawhna nge i zawh tur?
Doctor hmu tura i kal dawnin heng zawhnate hi zawh a tha ang:
- Eng thil nge ka natna lan chhuah chhan?
- Enkawlna emaw, zai emaw ka mamawh em?
- Enkawlna hian side effect a nei em?
- Ka natna lan chhuah dan avanga mualpho emaw, nuam lo emaw ka tih chuan eng enkawlna nge awm?
(Harlequin Syndrome) leh (Harlequin Ichthyosis) te hi thil inang an ni em?
Ni lo, hengte hi dinhmun hrang hrang pahnih a ni. Hei hi mi tam tak tibuai thei thil a nih avangin chiang taka sawi a tha.
Harlequin Syndrome hi taksa sir khata thawk hah leh vun rawng tidanglamtu a ni. Nunna atana hlauhawm a ni lo va, genetic condition a ni lo (mahse, a then phei chuan congenital a ni thei).
A lehlamah Harlequin Ichthyosis hi genetic skin disease a ni a, nunna atana hlauhawm thei a ni.. Hetiang natna nei naute hi vun thim tak, hring hring tak neiin a piang thin. Harlequin Ichthyosis vei naute hian diamond ang maia vun an nei a, chu chu fissure thuk tak takin a then a ni. A châng chuan doctor-te chuan he natna hi "Harlequin Baby Syndrome" an ti ṭhin. "Harlequin Syndrome" angin a ri thei a, mahse hengte hi natna hrang hrang pahnih a ni.
Take-Home Thuchah a ni
Harlequin Syndrome (i taksa sir khatah hun engemaw chen thawk hah leh vun rawng tidanglam thei natna) hian i taksa sir khat chauh a nghawng a ni. I vun chu a hma aia danglamin a lan laiin nuam lo tih hi thil pangngai a ni. Mahse, hei hi dinhmun hlauhawm tak a ni lo tih hre reng ang che.
A pawimawh ber chu heng symptoms te hi i neih chuan doctor pan la , a chhan dik tak chu zawn chhuah a ni . A châng chuan, a chhan chu a lang chiang lo thei bawk. Enkawlna i mamawh lo tih i sawi a nih pawhin, he hmel danglamna avang hian rilru lama harsatna i tawk a nih chuan, chu chu rilru lam hriselna counselor hnenah i sawipui thei a, mahni inngaihhlutna siam dan tur leh mahni inngaihsakna tha tak siam dan tur i sawi thei bawk. Nangmah chauh i ni lo va, tanpuina dawn pawh i hreh ngai lo.
` Harlequin Syndrome, nervous system, thawk hah, luang chhuak, autonomic nervous system, Horner Syndrome, natna hmuh tur awm lo











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