I mit vel ah dark circle i nei em? Kayser-Fleischer Rings chungchang hi han sawi ila.

Mi mitmeng (iris) vel a hmun thim, ring ang maia awm i hmu ngai em? Hemi chungchang hi doctor pakhatin a hrilh che pawh a ni mai thei. Mi thenkhat chuan hei hian an mit a tichhe dawn tih an hlau mai thei. Mahse hei hi a takah chuan mit tichhe thei thil a ni lo. Mahse, hei hi kan taksa chhunga natna khirh tak dang lo thleng mek chhinchhiahna pawimawh tak a ni thei. Vawiin hian he thu hi awlsam takin han sawi ila.

Kayser-Fleischer Rings (KF ring) te hi eng nge ni?

A awlsam zawngin, Kayser-Fleischer ring hi kan mit rawng hrang hrang, iris vel a lo awm ring dum a ni. Heng ring te hi kan taksaa copper tam lutuk mit a awm khawm vang a ni . Green, gold, brown emaw angin an lang thei.

A tha ber chu heng ring te hian i mit a tichhe dawn lo .

He ring hi mit chunglam atanga arc angin a intan thin. Chumi hnuah chuan zawi zawiin a darh a, full ring a lo ni ta a ni. Heng ring te hi mit hmun dum (sclera) leh mit rawng nei (cornea) chunglam hmun chiang tak inzawmna hmunah an awm a.

Engtin nge hengte hi mit natna dang nen an danglam?

Hetiang mit zungbun chi hrang hrang awmna hmun dang pawh a awm bawk. Chuvangin hengte hi inthliarna leh inhriatthiam tawn a pawimawh hle. A danglamna ber chu eng nge ni tih i lo en ang u.

Heng KF rings te hi enfiah turin mit lam doctor chuan microscope bik slit-lamp examination . A châng chuan, gonioscopy an tih hi thuk zawka enfiah a ngai bawk. Hei hian mit tiharh a, mit chungah lens bik dah a huam a ni.

Kayser-Fleischer Rings siam chhan ber chu eng nge ni?

Hei hi a chhan ber leh a tam ber chu Wilson natna a ni .

Wilson natna hi genetic condition a ni a, taksain a mamawh aia tam copper a khawlkhawm thin. A tlangpuiin kan thin hian copper tam lutuk chu a paih chhuak thin. Mahse Wilson natna vei mi pakhatah chuan chu kalphung chu a thawk tha lo hle. Tichuan, he copper hi liver, thluak, mit leh taksa peng dangteah a lo awm tan ta a ni.

• Liver natna: Copper buildup hian thin a tichhe thei a, thin natna a thlen thei bawk.
• Nervous system leh rilru lama harsatna: Thluaka copper a lo awm tan chuan thluak lam natna chi hrang hrang leh rilru lam harsatna a lo awm thin. Entir nan:
• Movement disorder te, ke ruh leh ke ruh tliak leh kal harsatna te
• Thusawi harsa
• Lungkhamna leh lungngaihna
• Nungchang leh mize inthlak danglamna

Ngaihtuah teh, Wilson natna avanga thluak lam natna nei mite hnen atanginHeng KF ring te hi mi 100 zinga 95 velin an hmu thei a ni. Hei hi liver symptoms chauh nei mi 50% vel ah hmuh a ni.

Chhan dang

Wilson natna bakah hian KF ring awm chhan dang eng emaw zat a awm bawk. Hengte hi thin (liver) kaihhnawih natna te pawh an ni.

• Primary biliary cholangitis (PBC): Hei hi natna khirh tak a ni a, liver chhunga bile ducts tichhe thei a ni.
• Neonatal cholestasis: Nausen piang tharte liver-a bile flow tihchhiat.

Hei hi engtin nge enkawl a nih?

Hetah hian kan hriatthiam tur pawimawh ber chu Doctor-te hian ringworm ngei hi an enkawl lo tih hi a ni. Anni hian ringworm thlentu damdawi lam dinhmun hnuaia awm chu an enkawl a ni.

Wilson natna enkawl dan

Enkawlna kawngah hian tum lian tak pahnih a awm a.

1. Taksa atanga copper tam lutuk lakchhuah: Hei hi copper chelation therapy an ti a. Chumi awmzia chu damdawi bik (chelating agents) pek a ni a, chu chuan taksaa copper chu a binding a, zun hmangin a paih chhuak thin. Chung entirnan penicillamine leh trientine ang chi damdawi te hi a ni.

2. Chaw atanga copper lakluh tihtlem: Hei hi zinc supplement pek hmanga tih a ni . Zinc hian intestine atanga copper chu taksaa lakluh a veng a ni.

Thin natna dang enkawl dan

Primary biliary cholangitis (PBC) ang natna hi a dam kim thei lo. Amaherawhchu, natna lan chhuah dan thunun nan leh natna zual zel tur venna atan damdawi pek a ni. Nausen piang thar cholestasis tan chuan special formula milk, anti-itch damdawi pek thin a ni a, a nasat chuan liver transplant surgery neih a ngai thei bawk.

Heng Kayser-Fleischer Rings siam chhuah hi kan dang thei lo em ni?

A nihna takah chuan heng ring te hi direct-a siam theih a ni lo, a chhan chu Wilson natna ang chi natna thlentu hi thlahtute atanga lo piang a nih avangin ven theih a ni lo.

Mahse, i tih theih ṭha ber chu a hmaa hriat chhuah hi a ni .

Heng ring te hi a awm reng em?

Ni lo, hei hi chanchin tha ber a ni. Kayser-Fleischer ring hi a awm reng lo . Natna hnuaia awm, entirnan Wilson natna chu uluk taka enkawl a nih chuan taksaa copper tam lutuk chu a bo vek ang. Tichuan mit chhunga heng ring te hi zawi zawiin a bo vek ang a , a bo vek ang .

Chuvangin hei hi hmuh hlauh a ngai lo. A pawimawh ber chu symptom anga hriat a, a hnuaia awm chu a rang thei ang bera enkawl tan hi a ni. I mit enfiahnaah mit lam doctor-in hei hi a sawi a nih chuan, enkawlna dang nei turin specialist \ha tak hnenah a refer ang che.