MRKH syndrome (Mayer-Rokitansky-Küster-Hauser Syndrome) hi eng nge ni? Hemi chungchang hi kan sawi dawn em ni?

I fanu, emaw, i hriat naupang tê tê emaw hian kum tling chinah a period a la tan lo em ni? A nih loh leh, mipat hmeichhiatna hman a tum hian a châng chuan hrehawmna emaw, lungawi lohna emaw a nei em? Vawiin hian hriselna lama harsatna bik, heng thil thleng thei, mahse a hluar vak loh leh mi tam takin an hriat loh chungchang kan sawi dawn a ni. Hei hi Meyer-Rokitansky-Küster-Hauser syndrome , a tawi zawngin ``MRKH syndrome'' an ti a. A hming hi sei deuhin lang mahse, hei hi hmeichhiate natna vei, genetic condition hmuh tur awm lo tak a ni. A awlsam zawngin, i hriatthiam theih dan tur angin sawi ila.

MRKH syndrome hi eng nge ni tak tak?

A awlsam zawngin sawi ila, MRKH syndrome hi hmeichhe serh leh nausen (uterus) a lo thang tha lo emaw, a pian tirh atanga a insiam kim loh emaw a ni. In sak ang maiin pindan thenkhat chu mumal taka siam loh angin han ngaihtuah teh. Mahse, a tam zawkah chuan he natna vei te ovary leh fallopian tube te hi a pangngaiin hna a thawk thin . Tin, pawn lam mipat hmeichhiatna (external genitalia), chu chu vagina hnuai lam, vaginal opening, labia, clitoris leh an chhehvela sam sei te hi a pangngai a ni. Urethra a nghawng loh avangin zun kawngah harsatna a awm lo.

Mahse, MRKH syndrome chi thenkhatah chuan taksa peng dang, kal leh ruhroah te hmasawnna lama harsatna engemaw zat a awm thei.

A tam zawkah chuan he natna hi kum naupang takah hmuhchhuah a ni a, chu chu kum 15-16 inkar, thlasik a intan loh lai a ni. Hei hi a chhan chu nausen pum hi a lo thang kim lo a, chuvang chuan thlasik a awm lo. A châng chuan, sex hman tum hian a serh chu a tawi a, a zim avangin a na emaw, a harsa emaw a ni thei.

Nausen pum hi a lo thang kim lo emaw, a awm loh avangin, hetiang dinhmunah hian damdawi lam puihna tel lo chuan nau pai leh phurh theih a ni lo. Mahse, ovary te chu a thawk tha a, egg siam a nih chuan , ``IVF - in vitro fertilization`` leh ``surrogacy`` tih ang chi option te ngaihtuah theih a ni. Fa neih i beisei a nih chuan i doctor nen sawiho a pawimawh hle. Chumi hnuah chuan i tana ṭha tur duhthlan tur chungchangah thurawn an pe thei che a ni.

`(MRKH syndrome)` tih hming dang engemaw zat hman a ni bawk:

• Nausen pum leh nausen pianpui (CAUV) .
• Vaginal atanga chhuak (vaginal agenesis) a awm
• Müllerian agenesis a ni
• Müllerian aplasia (MA) natna a ni.
• Genital renal ear syndrome (GRES) a awm a, a rilru a hah lutuk a, a rilru a buai em em bawk a.

MRKH syndrome chi hrang hrang a awm em?

Ni e, `(MRKH syndrome)` hi chi hnih lian tak a awm a:

• Type 1-na chu:Hetiang chi ah hian ovary leh fallopian tube te hi a pangngaiin hna a thawk a, mahse vagina chunglam, cervix leh uterus te chu a block emaw, a hmunah a awm lo emaw a ni. Mahse, hei hian taksa peng dang engmah a nghawng lo.

• Type 2: Hetiang chi ah hian vagina, cervix leh uterus chunglam a block emaw, a hmuna awm loh emaw bakah hian fallopian tube, ovaries, spine, kidney emaw organ dang emaw ah pawh harsatna engemaw zat a awm thei bawk.

Hetiang dinhmun hi engtiang chiahin nge a awm?

MRKH syndrome hi a awm lo hle a ni . Hmeichhe naupang 4,500 zinga pakhat vel chauh a nghawng a ni. Chuvangin kan la hre tam lo hi thil mak a ni lo.

MRKH natna lanchhuahna chu engte nge ni?

MRKH syndrome symptoms hi i neih chi hrang hrang a zirin a danglam thei.

A tam zawkah chuan a lan chhuahna ber chu kum 16 an tlin hmaa thlasik (amenorrhea) a awm loh vang a ni a, hei hian nausen pum emaw, nausen emaw a lo thang tha lo tihna a ni. Amaherawhchu, Ovary te hi a thawk dan pangngai a nih avangin thlasik nena inzawm symptom dang, bloating leh mood swing te hi thisen chhuak lo pawhin a awm thei a ni.

Hmeichhe chromosome leh hormone i neih avangin mipat hmeichhiatna lama hmasawnna pangngai i tawng a, chu chu hnute than leh armpit leh genital area-a sam sei te hi a ni. Mahse, vaginal sex hman i tum hmasak ber ṭumin natna emaw, lungawi lohna emaw i nei thei. Hei hi a chhan chu i vagina chu a tlangpui aia a hring, a tawi zawk leh a tawi zawk vang a ni.

Type 2 MRKH i neih chuan symptom dang i nei thei bawk a, chungte chu:

• Kidney complication, emaw, kidney pakhat emaw, a pahnih emaw a hlawhchham vang emaw.
• Spine vertebrae-a harsatna emaw, skeletal system deformity dang emaw a awm.
• Hriatna lama harsatna nei.
• Lung lam harsatna thenkhat.

MRKH hi eng thilin nge a thlen?

MRKH syndrome hi a chhan dik tak hi zirchiangtute chuan an la hre lo . Mahse, gene leh chromosome-a harsatna engemaw zat a keng tel tih an hria a ni. Mahse, gene bik pakhatah an pin down thei lo. A pawimawh ber chu nuin naupai lai a tih leh tih loh thil a ni lo . Chuvangin ngaihtuah buai suh.

Hmeichhia naupai kar hmasa berah hian a chi thlah dan a lo thang tan thin. Fallopian tube, uterus, cervix, leh vagina chunglam chu Müllerian ducts tih hming pu thil a\anga siam a ni. MRKH syndrome vei teah chuan heng Müllerian duct te hi a lo thang kim lo. Mi thenkhatah hetiang thil hi a thlen chhan hriat a la ni lo. Mahse, Ovary te hi reproductive system dang atanga a hranin an lo thanglian avangin ovary te hi a nghawng lo tlangpui.

Engtin nge MRKH i nei tih chiang taka i hriat theih ang?

Doctor-te chuan hmeichhe naupang pakhatin a period hmasa ber a neih loh chuan MRKH syndrome an hmuchhuak fo thin.

Hetiang dinhmun hi hriat chian hmasak ber tur chu taksa enfiahna a ni . I doctor chuan i vagina chhungah gloved finger a dah ang a, a thuk leh zau zawng a teh ang. He test hian MRKH a hriat theih a, a chhan chu vagina a tawi vang a ni. Tichuan, i uterus, fallopian tube, kidney, a nih loh leh taksa peng dang a nghawng em tih en turin ultrasound scan emaw MRI (magnetic resonance imaging) scan emaw ang chi imaging test ti turin an ti thei che a ni. A châng chuan, i hormone level enfiah nân thisen test pawh a awm thei bawk.

MRKH enkawl dan tur chu engte nge ni?

MRKH syndrome enkawl dan hi i thil tum leh i natna lan chhuah dan azirin a inang lo. Surgery leh non-surgical treatment a awm bawk. Chung zinga ṭhenkhat chu vaginoplasty, vaginal dilation, leh uterine transplant te a ni.

Vaginal tihzauh a ni

Doctor ten vagina an tihzauh dan pakhat chu vaginal dilators an tih hmanrua hmangin a ni . Hengte hi plastic emaw silicone emaw atanga siam niin, a sei leh zau zawng hrang hrang a awm. Heng tube ang chi hmanrua te hian a chhung atang hian vagina chu a tizau a, a tizau thei bawk. I doctor chuan i dinhmun atana vaginal dilator hman dan tha ber a hrilhfiah ang che.

Vaginoplasty (surgical hmanga hnute siam thar leh) .

Vaginoplasty hi surgery hmanga vagina siam a ni a . Surgeon te hian he procedure hi tih dan hrang hrang an nei a. A tam zawkah chuan khur an siam a, i taksa peng dang atanga lak chhuah tissue hmangin an khuh thin. Hei hian mipat hmeichhiatna pangngai i neih theih phah a ni.

Nausen pum thlak (uterus transplant) a ni

Uterine transplant hian MRKH syndrome nei hmeichhia chu nau neih theihna hun a pe thei a ni. Hei hi operation lian tak a ni. Donor atanga uterus nei lo hmeichhiaah transplant a ni. Hei hian MRKH vei te chu mahni fa phur leh hrin theihna hun a pe a ni. Khawvel hmun hrang hrangah uterine transplant hi nasa taka tih a la ni lo a, mahse nakin lawkah chuan enkawlna hlawhtling tak a ni thei ang.

Hetiang dinhmun hi ven theih a ni em?

Ni lo, MRKH syndrome hi ven theih a ni lo . Tun hmaa la nei ngai loteah a awm thei a, a nih loh leh genetic a ni thei bawk. Sawi tawh ang khan gene bik pakhat chauh avanga lo awm a ni lo.

MRKH vei te hian naute an nei thei ang em?

Ni e, `(MRKH syndrome)` vei te hian naute an nei thei!I ovaries a thawk tha a nih chuan i egg te chu sperm nen inzawmkhawmin in vitro fertilization (IVF) hmangin fertilized theih a ni. Chumi hnuah chuan embryo chu gestational carrier/surrogate mother hnenah an transfer leh thin . Chumi awmzia chu nangmah ngeiin genes nei, hmeichhe hrisel dang pum chhungah lo seilian fa i nei dawn tihna a ni.

MRKH hian hriselna lama harsatna dang eng nge a thlen theih?

Tun hmain ``Type 2`` MRKH vei te hian taksa peng dang, kal, ruhro, thinlung emaw ah pawh harsatna an nei thei tih kan sawi tawh a. Tin, ``Type 2`` MRKH vei te zingah hriselna lama harsatna dang awm fo chu:

• Spine vertebrae nena inzawm harsatna.
• Scoliosis natna (Scoliosis) a ni.
• Kidney malformations, kal inzawmkhawm emaw, kal pakhat emaw pahnih emaw awm lohna (renal agenesis).
• Kidney stone, urinary tract infection, leh urinary tract obstruction awm theihna a sang.
• Hriatna lama harsatna nei.
• Lung natna.

MRKH vei zingah hian reproductive system complication hi a awm fo thin. Nau pai theih lohna emaw, mahni fa neih theih lohna bakah hian nausen pum huap lo nei te pawhin endometriosis ang chi natna an nei thei bawk.

Heng zawng zawng nen hian emotional stress engemaw zat neih hi thil pangngai a ni . I doctor chuan support group-a tel emaw, psychological counseling service, cognitive-behavioral therapy (CBT) ang chi, chu dinhmun hmachhawn tûra ṭanpui tûrin a rawt thei che a ni. Heng thilte hi a \angkai hle thei a ni.

Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome i vei tih i hriat chuan thil mak tak a ni thei tih hi thil mak a ni lo. Uterus emaw vagina emaw a lo thang lian lo a piang i nih chuan i naupan lai leh thlasik i neih tan tirh thlengin i hre lo mai thei. Nunna atana hlauhawm tak a nih loh laiin, stress nasa tak a thlen thei a, hmeichhe naupai theihna leh sex hman theihna a nghawng thei bawk. A then phei chuan taksa peng dang a nghawng thei a, hriselna lama harsatna thenkhat a thlen theihna a tipung thei bawk.

Thil pawimawh tak tak hriat reng tur (Take-Home Message) .

Okay, chuti a nih chuan tunah chuan kan sawi thin, ``MRKH syndrome'' hi i hrethiam zawk tawh a, hriat reng tur pawimawh ber chu nangmah chauh i ni lo tih hi a ni Khawvelah hian hetiang dinhmun neia khawsa mi dang pawh an awm bawk.

• Hetiang symptoms i neih chuan doctor tha tak pan a, diagnosis dik tak neih a pawimawh hle .
• Enkawlna hrang hrang a awm. Doctor nen inbia la, i tana tha ber tur chu thlang rawh.
• Naupangte tan beiseina bansan suh. `(IVF)` leh `(surrogacy)` ang chi technology hmang hian chu duhthusam chu tihhlawhtlin theihna hun remchang a awm a ni.
• I rilru hriselna pawh uluk hle ang che.A tul chuan counseling zawng la, chutiang thil tawn tawhte nen support group-ah tel ve rawh. Hei hian chakna nasa tak a pe ang che.
• Hei hi i sualna a ni lo. Hei hi tu chungah pawh thleng thei natural condition a ni.

I doctor, leh specialist team pawhin he `(MRKH syndrome)` hi hmasawn zel turin i mamawh tanpuina leh kaihhruaina a pe ang che. Anni chu ring rawh. Hemi chungchanga zawhna dang i neih chuan zawh hreh suh. Hrisel takin awm rawh!

` MRKH syndrome, Mayer-Rokitansky-Küster-Hauser Syndrome, vaginal agenesis, uterine agenesis, hmeichhe hriselna, nau neih hriselna, amenorrhea