I fa hian a chang chuan thawk a ti harsa thin em? A nih loh leh hun engemaw chen a khelh hnuah pawh a chau thuai em? Naupang tê ṭhenkhat chuan pianpui thinlung natna an nei thei bawk. Vawiin hian chutiang pakhat, a tlem deuh, mahse hriat tur pawimawh tak thinlung natna pakhat kan sawi dawn a ni. Hei hi `(Pulmonary Artery Stenosis)` kan ti a. A awlsam zawngin, lung chhunga thisen phurtu main artery blockage a ni.
Pulmonary Artery Stenosis hi eng nge ni?
A awlsam zawngin sawi ila, kan thinlung dinglam (``right ventricle`` kan tih) atanga thisen phurtu thisen kalna kawng lian tak a awm a. Hei hi ``pulmonary artery`` an ti a. Lung a thlen chuan he thisen hi oxygen pek a ni a, chu thisen oxygen nei chu taksa pum puiah a phur chhuak ta a ni.
Tunah chuan he `(Pulmonary Artery Stenosis)` an tih dinhmunah hian lung chhunga thisen phurtu thisen kalna kawng chu hmun khatah emaw, a peng pakhatah emaw a inkhar emaw, a tawi emaw a ni . Tui pipe a laiah a block ang mai a ni. Chuti a nih chuan eng nge thleng? Chu chu lungah thisen kal a harsa ta hle mai. Thisen a luang tha lo a nih chuan taksain oxygen a mamawh zat a hmu lo. Chumi avang chuan naupang thinlung leh taksa pum puiin hna a thawk tha thei lo.
He blockage hi main pulmonary artery (`(main pulmonary artery)`), emaw a branch veilam emaw dinglam emaw (`(left or right branches)`) ah a awm thei bawk. Hetiang blockage a awm hian thinlung dinglam (`(right ventricle)`) hian blockage kal pelh turin thisen pump turin nasa takin hna a thawk a ngai a ni . Pipe block atanga tui nawr chhuah nan chakna nasa tak hman a ngai ang mai a ni. Hun a kal zel a, he beih chhunzawm zel hian thinlung ruh a tichhe thei a ni.
Hetiang dinhmun atang hian eng harsatna nge lo awm thei?
Hei hi uluk taka enkawl a nih loh chuan hun kal zelah thinlung dinglam chu a thawk tha lo thei a ni. Chu chu ``Right-sided heart failure'' tih ang chi natna lo awm theihna a awm tihna a ni. Chuvang chuan hei hi uluk taka enkawl a pawimawh hle a ni.
He dinhmun hian tute nge a nghawng ber?
He natna `(Pulmonary Artery Stenosis)` an tih hi a takah chuan a tlem hle . Chu chu mi zawng zawngah a thleng lo tihna a ni. Naupang thenkhat chuan thinlung natna dang (`(congenital heart disease)` - chu chu an pian tirh atanga lo awm thin thinlung natna te nen an nei thei bawk. A châng chuan thinlung lam harsatna dang nei lovin a awmchhun a ni thei bawk. Tin, he natna hi thinlung operation thenkhat hnuah pawh a awm thei bawk.
Hei hi eng symptoms nge ni? I fa pawhin hengte hi a nei em tih en rawh.
Heng symptoms te hi tube a narrow danah a innghat a ni. A châng chuan, stenosis hi a na lo hle (`mild stenosis`) a nih chuan, symptoms a awm lo thei . Mahse stenosis a na zual zel chuan i fa chuan hetiang hi a lantir thei a ni:
- Thâwk harsa ang maia inhriatna (`(Shortness of breath)`).
- Chau tih hriat reng (`(Fatigue)`).
- It sounds like you’re breathing very fast , a nih loh leh i thawk nasa hle mai thei.Hetiang hian a lang em? (`(Thawk rit emaw, thawk rang emaw)`).
- I heart rate chu a na lutuk ang maiin i hria em ? (Thinlung chak tak).
- I ke, i ke ruh, i hmai, i mitmeng emaw, i pum chhungah emaw a hring a awm em? (`(A hring)`).
- A chang chuan i lu a buai emaw, i pass out emaw ? (`(Lung chhuak emaw, rilru hahna emaw)`).
- I hmui, i kut zungtang leh i ke ruhte chu a sen vek em ? Hei hi damdawi lam chuan ``Cyanosis'' kan tih chu a ni.
- Naupang dang nena infiam hian i chau vat em ? Naupang dang ang bawkin tlan leh zuang thei lo i ni em? (`(Exercise tuar theihna tihtlem)`).
Heng symptoms zinga pakhat emaw pahnih emaw i neih chauh hian natna i nei tihna a ni lo tih hre reng ang che. Mahse i fain heng zinga pakhat tal a neih chuan damdawi lam thurawn lak a tha ber.
Engvangin nge he pulmonary artery hi a block? A chhante chu engte nge ni?
Naupang thenkhat chu he natna (Pulmonary Artery Stenosis) neia piang an ni a, chubakah chuan valve, wall emaw, thinlung hmun dangah emaw harsatna an nei thei bawk. Mi dangte chu he natna neia piang ni mah se, thinlung lama harsatna dang nei lo an ni thei bawk. Chu bâkah, he natna hi thinlung operation hnuah emaw, thil dang, hmuh tur awm lo tak tak, avânga lo awm thei a ni.
Pianpui atanga lo chhuak a ni
A pum puiin mi 40% vel chu he natna (Pulmonary Artery Stenosis) neia piang an ni a, mahse thinlung lama harsatna dang an nei lo.
Mahse, pianpui thinlung natna dang nei zinga 2% leh 3% inkar pawhin he natna hi an nei thei bawk (Pulmonary Artery Stenosis). Hetih lai hian thinlung lam natna langsar zual thenkhat chu hetiang hi a ni:
- (Tetralogy of Fallot): Hemiah hian naupang hian thinlung lamah harsatna pali a nei a, chu chuan thisen kal dan a tibuai a ni.
- (Pulmonary atresia): Hetah hian thinlung ventricle dinglam leh pulmonary artery (pulmonary artery) inkar valve (pulmonary valve) a lo awm lo. Chuvang chuan thisen chu lungah a luang lo.
- (Truncus arteriosus): A tlangpuiin thisen kalna kawng lian pahnih aiah pakhat. Hei hian oxygen nei thisen chu deoxygenated thisen nen a inhmeh tir thin.
- Aortic valve stenosis: Thinlung atanga taksa thlenga thisen phurtu main artery-a valve-a harsatna awm a, chu chuan taksaa thisen kal zat a tihtlem phah a ni.
- Atrial septal defect: Thinlung chunglam chamber pahnih (atria) inkar bang chhunga khur awm. Hei hian oxygenated leh deoxygenated thisen a inhmeh tir thei a ni.
- Ventricular septal defect: Thinlung hnuai lam chamber pahnih (ventricles) inthenna bang chhunga khur awm. Hei hian thisen tam lutuk chu lungah a luang lut thei a ni.
- (Transposition of the great vessels): Thinlung atanga thisen phurtu thisen kalna kawng lian pahnih chu a inher a. Hei hian thisen kal dan pangngai a tibuai a, taksa cell-a oxygen lut zat a tikhawtlai bawk.
- (Patent ductus thisen kalna kawng): 1.1.Hei hi naute pulmonary artery leh taksaa thisen phurtu main artery (aorta) inzawmna a ni. Hei hi pian hnuah khar tur a ni a, mahse a khar loh chuan thisen tam lutuk chu lungah a luang lut ang.
Chhan dang
Hei bakah hian chhan dang engemaw zat a awm thei bawk:
- Rubella syndrome: Naupai laiin rubella i vei chuan i naute hian thinlung leh hriselna lama harsatna dang a nei thei.
- (Williams syndrome): Hei hian naupang thinlung leh taksa peng dangteah thil danglam chi hrang hrang a thlen a.
- (Alagille syndrome): Hei hian thin lam harsatna a thlen a, lung natna a thlen bawk.
- Takayasu’s arteritis: Hei hi inflammation a ni a, thisen kalna kawng lian tak tak a tichhe thin.
- Naupang pulmonary artery pawn lam hawia nawr dan chungchangah buaina thenkhat.
Surgery avanga thil thleng
Mi thenkhat chuan operation hnuah he natna hi an nei thei a ni. Entir nan:
- A lung transplant a ni.
- Naupang pianpui heart defect siamthatna tur emaw, heart kaltlanga thisen kal dan tur tihchangtlunna tur emaw surgery.
- Surgery pakhat ``Pulmonary artery banding'' tih a ni. Hei hian thisen chu lung chhunga kal zat tihtlem nan tumruh takin artery chu tihtlem a ni.
He natna hi engtin nge kan hriat theih ang?
I fa chu doctor-in a enfiah chuan thinlung ri danglam tak (``murmur'') an hre thei. Chutiang a nih chuan test eng emaw zat an order leh ang. Chung zinga ṭhenkhat chu:
- Electrocardiogram - ECG emaw EKG: Hei hian thinlung a thawk laia electric inthlak danglamna a record a. Heartbeat mumal lo (arrhythmias) leh heart muscle-a stress a hriat theih.
- Chest X-ray: Hei hian thinlung, lung leh pulmonary arteries te lian leh te, a pianzia a tarlang thei a ni.
- Echocardiogram: Hei hi thinlung thlalak che thei ang mai a ni. Sound wave hmangin heart muscle leh valve te a en thin.
- Cardiac magnetic resonance imaging (MRI): Hei hi three-dimensional (3D) imaging technique a ni a, i fa thinlung leh thisen kalna kawng hrang hranga thisen kal dan a en thei a ni.
- (CT scan): Hei hi `(X-ray)` test a ni bawk. Computer chuan naupang thinlung thlalak `(X-ray)` hrang hrang hmangin cross-sectional view a siam thin. Thinlung insiam dan leh thisen kal dan en turin thinlungah hian dye bik (`(IV contrast)`) an inject a.
- Cardiac catheterization: Hetiang tih danah hian vein emaw artery emaw-ah tube te tak te (catheter) dahin thinlung chhungah kaihhruai a ni. Hei hian doctor chuan oxygen level te, pressure inthlak dan te a enfiah thei a, thinlung X-ray a la thei bawk.
- Pulmonary angiography: Pulmonary arteries leh veins te X-ray chu Dye hmanga lak a ni.
- (Perfusion scan): Hetah hian radioactive material tlemte an inject a. Tichuan, khawl bik hmangin lung tinah thisen a kal tha em tih enfiah a ni.
I doctor chuan i fain Pulmonary Artery Stenosis a nei tih a hriat chuan congenital heart specialist hnenah an refer ang che. Hetiang doctor chi hian i fate thinlung harsatna dik taka hriat theihna tur, test tul apiang tih theihna tur, damdawi lam enkawlna pe thei tur, thinlung surgery tih theihna tur leh follow-up checkups pe thei tur khawpa thiamna leh training a nei a ni. A tul chuan test tam zawk an ti thei bawk.
He natna chungchang i sawi hian i doctor chuan Type I, II, III, emaw IV tiin a sawi thei a ni. Hei hi artery hmun engzat nge block tih leh engzat nge block tih atanga classification a ni.
Hei hi eng enkawlna nge ni? (Tihdamna)
Enkawlna tha ber chu i fa natna lan chhuah dan leh thil dang dangah a innghat a ni. Pulmonary artery branch pakhat emaw, a aia tam emaw chu a narrowing narrowing to moderate a awm chuan enkawl a ngai lo mai thei . Mahse, a narrowing nasat chuan enkawl a ngai a ni .
`(Pulmonary Artery Stenosis)` enkawl dan tur chu:
Balloon tihzauh / Angioplasty tih a ni
Hemi kawngah hian doctor chuan:
- Balloon ang chi catheter (balloon dilation catheter) chu blocked duct chhungah dah a ni.
- Tichuan fimkhur takin balloon chu pressure hniam atanga pressure sang takah an inflated a.
- Tichuan chu blocked duct chu a zau ta a ni.
- Tichuan balloon atanga boruak chu la chhuakin an la chhuak leh thin.
Balloon dilation leh stent dah (hei hi tih tam ber a ni) .
Hemi kawngah hian doctor chuan:
- Balloon-a tihzauh theih stent (stent chu mesh tube te tak te) hmangin thisen kalna kawng khar chu hawn a ni.
- He stent hi balloon angioplasty catheter chungah dahin, sheath hmanga khuh a ni.
- Stent chu hmun dik takah an sawn mek a ni.
- Stent-balloon chunga khuhna chu a la chhuak ta a.
- Tichuan balloon chu pressure dik takah an inflate a, stent chu a tizau a, chutah chuan a awm reng a ni.
Balloon bik ``(The Cutting BalloonTM)`` tih hming pu
He balloon hi balloon pangngai ang mai a ni. Mahse, a sei zawngah chuan blade te te engemaw zat a nei a. Doctor chuan balloon a inflate chuan heng blade te hian activate in blocked area chu an cut thin. Hei hian tube chu a tizau a, hawnna lian zawk a siam a ni.
Congenital heart disease dang nei lo tam zawk chuan he procedure hmang hian result tha tak an nei thin. Mahse, mi 21% vel chuan thla engemaw zat hnuah an thisen kalna kawng a block leh thei a ni.
Inzai
Surgeon-te chuan pulmonary artery stenosis enkawl nan hian kawng hrang hrang an hmang a. Duhthlan tur chu blockage awm dan, a chhehvela thisen kalna kawng leh thil dang awm danah a innghat a ni.
Enkawlnaah hian harsatna a awm em?
Balloon dilation hian mi tam zawkah blockage a ti tlem a ni. Mahse, hun kal zelah chuan thisen kalna chu 15% atanga 20% velin a block leh thei a, chu chu tih leh a ngai a ni. Tunah hian zirchiangtute chuan balloon chi hrang hrang, result tha zawk, rei zawk daih thei tur an chhui mek a ni.
Balloon dilation laiin harsatna awm thei:
- Pulmonary artery-a thisen kalna (aneurysm) a awm.
- Pulmonary artery dissection (Pulmonary artery dissection) tih a ni.
- Pulmonary artery rupture (`(Pulmonary artery rupture)`) a ni a, a rilru a hah lutuk a, a rilru a buai em em bawk a.
- Pulmonary edema (`(Pulmonary edema)`) tih a ni.
- A tlem hle a, thihna a awm thei.
Stent hman avanga harsatna awm thei te:
- Thisen a chhuak thin.
- Lungphun a mumal lo (`(Ventricular arrhythmias)`).
- Stent hi a hmun dik lo emaw, a chhuah loh emaw pawh a ni thei.
- Artery tihzauh leh a ngai (hei hi a thleng tlem hle).
Enkawlnain eng hlawkna nge a neih?
Doctor-te chuan Pulmonary Artery Stenosis tan stent dah hi hengte avang hian an duh zawk a ni:
- Anni hi 96% velin an thawk nghal vek a ni .
- Artery hawn reng tur chuan hun rei tak a ngai a ni .
- A zau zawng chu a let hnih velin a zau thei a ni .
- Balloon dah mai emaw, operation tih mai emaw aiin a man a tlawm zawk a, a hlawk zawk bawk .
- Balloon angioplasty aiin a hlawhtling zawk.
Doctor-te chuan a hnuaia thil thlengah hian stent ai chuan balloon angioplasty an thlang thei ang:
- Naupang dinhmun a nasat em em chuan .
- Naupang taksa chhungril lam insiam dan chu a buaithlak (`(complex anatomy)`) a nih chuan .
- Naupang chu a te lutuk a nih chuan .
Surgery hnuah eng nge thleng?
I fain stent a neih chuan antibiotics leh thisen tithianghlimtu pawh hun engemaw chen a ei a ngai dawn a ni. Heng damdawi te hi infection laka invenna atan leh thisen zam titawp turin pek thin a ni.
Engtiang chiahin nge naupang chu enkawl a nih hnuah a dam leh thuai ang?
I naute pulmonary artery tihzauh dan hian hna a thawk nghal a ni. Hei hian i naute tan chuan an lung chhunga thisen luh a awlsam zawk tihna a ni a, oxygen a dawng thei bawk.
Ka fa hian hetiang dinhmun hi a nei a nih chuan hmalam hun chu eng ang nge ni ang? (Prognosis) tih a ni.
Tunlai damdawi hmanraw changkang tak takte nen hian he natna vei tam tak hi puitling thlengin an nung a ni. Mahse, ``Williams syndrome'' leh ``Alagille syndrome'' ang chi natna nei te chuan enkawlna an dawng tha lo mai thei.
Engtikah nge i fa chu doctor hnenah i hruai ang?
I fate chu an dinhmun hriat nan regular checkup turin i hruai a ngai dawn a ni . Nakin lawkah artery hi tihzauh leh a ngai em tih hriat nan echocardiograms neih fo a ngai bawk ang.
Doctor hnenah eng nge ka zawh ang?
Doctor hnenah hetiang zawhna hi i zawt thei ang:
- Engvangin nge ka fa hian `(Pulmonary Artery Stenosis)` a neih?
- Ka fa tan hian eng enkawlna tha ber nge ni ang?
- Hemi avanga ka fa hi enkawl leh a ngai leh theihna chance engzat nge awm?
I fain Pulmonary Artery Stenosis natna a enkawl a ngai a nih chuan doctor chuan i fa dinhmun enkawlna tha ber a ngaihtuah ang. I fa kalphung chungchanga i hriatthiam loh zawng zawng zawhna zawt hreh suh.
Take-Home Thuchah a ni
He natna `(Pulmonary Artery Stenosis)` tih hi sawi dawn chuan a pawimawh ber chu a natna lan chhuah dan hriat hmasak a, damdawi lam thurawn lak hi a ni . `(congenital heart specialist)` thurawn lak a pawimawh hle a, a bik takin naupangte hian he natna hi an nei a nih chuan.
Ngaihtuah buai suh, hei hi enkawlna a awm . Hetiang dinhmun hi balloon dilation, stent dah, leh a tul chuan operation tih ang chi thil hmangin control theih a ni. Enkawlna hnuah pawh naupang hriselna atan chuan damdawi lam checkup neih fo a, doctor thupek zawm a pawimawh hle . Zawhna emaw, ngaihtuahna emaw i neih chuan doctor nen sawiho rawh.
` Pulmonary Artery Stenosis, Naupang Lung natna, Pianpui Lung chhiatna, Thâwk harsa, Lung zai, Stent











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