I kawppui emaw, i in chhûnga mi tu emaw chuan i mut laiin mi i au chhuak a, i flail a, a châng chuan mi i beih pawh a hrilh che em? I taksaah hliam tuar chungin i harh a, "Eng nge ka chungah thleng?" Hei hi mumang tha lo mai a ni lo mai thei. Vawiin hian he mut dan mak tak, REM Sleep Behavior Disorder, emaw RBD an tih hi kan sawi dawn a ni.
`REM Sleep Behavior Disorder (RBD)` tih hi eng nge ni?
A awlsam zawngin, `REM Sleep Behavior Disorder (RBD)` chu `REM (Rapid Eye Movement)` stage-a i mut lai a ni a, i mumang chu i act tak tak a, chu chu taksa lamah i mumang a i thil tih te, i mumang a i thusawi te i ti a ni. Heng thil i tih lai hian i hre lo. He `RBD` dinhmun hi `parasomnia` category-ah a tla a ni. `Parasomnia` hi mutna lama harsatna, taksa lama thil thleng danglam leh duh loh tak tak emaw, mut tibuaitu thil tawn emaw a ni.
Kan mut hian mut dan hrang hrang a awm a. Chutiang stage pakhat chu `REM sleep` tih a ni. `REM` tih hi `Rapid Eye Movement` tihna a ni. Hei hi mit a che chak lai a ni. Hei hi mumang chiang tak, fing tak tak kan neih fo hun hi a ni. Heng `REM` cycle te hi zan khatah vawi eng emaw zat kan paltlang thin. `REM` cycle hmasa ber hi kan mut atanga minute 90 vel atanga tan a ni a, minute 10 vel a ni. `REM` cycle lo awm apiang chu a rei deuh vek.
`RBD` hi chi hnih a awm a, chungte chu:
1. `Isolated (idiopathic) RBD`: Chumi awmzia chu a chhan bik awm lovin a awm tihna a ni. Vanduaithlak takin `isolated RBD` vei tam tak chuan a tawpah chuan `neurodegenerative condition` (nervous system tichak lo zauh zauhtu) an nei thei a ni. A bik takin natna chi hrang hrang `Parkinson natna` (Parkinson natna), `Lewy body dementia` (Lewy body dementia) emaw `multiple system atrophy (MSA)` (multiple system atrophy) te hi a ni. Heng natnate hi `alpha-synucleinopathies` an ti bawk.
2. Symptomatic (secondary) RBD: Hei hi a hnuaia awm natna dang avanga lo awm a ni. Entirnan, mut lama harsatna nei Type 1 narcolepsy -ah a awm thei. Miin a chunga kan sawi tak alpha-synucleinopathy leh RBD te hi a neih ve ve chuan secondary RBD anga ngaih a ni bawk.
Tin, antidepressant thenkhat ei thinte pawhin RBD an nei thei bawk. Hei hi drug-induced RBD an ti a.
He `RBD` hian nangmah emaw, i mutpui tu emaw tan pawh tum loh takin a tichhe thei a, chuvangin hei hi hriat chian a, a tul chuan inenkawlna zawn a pawimawh hle.
Tute nge RBD vei tam zawk?
REM Sleep Behavior Disorder (RBD) hian kum 50 chunglam a vei tam ber.He natna vei tan kum zat chu kum 61 vel a ni. Mahse, a tlem hle a, he natna hi naupang tê leh puitling naupangteah pawh a awm thei a ni.
Kum 50 chunglam zingah hmeichhia aiin mipa hian RBD vei an tam zawk a, a let 9 velin an tam zawk .
RBD hi neurodegenerative disorder thenkhat nen a inzawm tlat a ni. A hmaa kan sawi tawh ang khan, isolated (idiopathic) RBD (i.e. RBD chhan dang awm lo) vei zinga a tam zawk chuan Parkinson’s disease, Lewy body dementia, emaw multiple system atrophy (MSA) an vei tih hmuhchhuah a nih atanga kum 14 chhungin an vei tih hmuhchhuah a ni
`Type 1 narcolepsy` vei zinga 36% vel chuan secondary `RBD` an nei thei. Tin, antidepressant ei thin zinga 6% vel chuan `drug-induced RBD` an nei thei bawk.
RBD hi engtiang chiahin nge a awm?
REM Sleep Behavior Disorder (RBD) hi a takah chuan a awm lo hle a ni . Mipui zahawm zinga 1% vel a nghawng a ni. Kum 50 chunglam ah chuan 2% vel a ni.
Mahse heng zat hi a nihna tak aiin a hniam zawk mai thei, a chhan chu RBD hi hriat a harsa thei a, chutiang natna vei zinga a chanve vel chuan an nei tih pawh an hre lo
`RBD` natna lan chhuah dan chu engte nge ni?
`RBD` symptoms hi mi hrang hrangah a inang lo thei. Mi thenkhat chuan an tawng fo thin a, thenkhat erawh chuan an tawng tlem hle thung. Mi a mut lai hian mumang tha lo tak nei ang maiin a awm thei. Thil thleng thei thenkhat chu hetiang hi a ni:
- Ka taksa chunga sa chu zawi zawiin a che a, ka ke leh ke te chu a inher chhuak.
- Thusawi te, au thawm te, a chang chuan tawngkam tha lo tak tak sawi a ni.
- Mi vuak emaw, man emaw ang maiin an insiam a, khumah pawh an vuak emaw, an vuak emaw pawh a ni thei.
- Khum atanga zuang chhuak, leiah a tla thla.
Ngaihtuah teh, i thiannu Nilanthi leh a pasal Sugat te chu zanah an mu a, rang takin "Hold on! Hold on!" leh mi vuak tum ang maiin an kut an phar chhuak bawk. A chang chuan Sugat hi khum atangin a tlu a, a inhliam bawk. Zing lama an han harh chuan Sugat-a chuan engmah a hrechhuak lova, mahse a mumang a neih kha a hre reng a ni. Hei hi `RBDs` nihna chu a ni.
RBD vei mi sawm zinga pariat chuan mutnaah hliam an tuar niin an sawi .
Heng thil thlengte hi mut khat chhungin vawi khat emaw vawi tam tak emaw a thleng thei a ni. Mi thenkhat chuan zan tin an tawng a, thenkhat erawh chuan an tawng tlem hle thung. Miin mumang na tak, tharum thawhna a neih hian symptoms a na ber.
A pawimawh ber chu, heng thilte hi engtikah nge a thlen tih i hre lo. Mi tam zawk chuan khumah mi pakhatin a hrilh hian emaw, in lama mi pakhatin a hmuh emaw, zing lama an taksaa hliam tuar chunga an thawh hian emaw chauh an hre thin.
Hetih lai hian miin a kaitho che a nih chuan awlsam takin i harh chhuak thei a ni. I harh chuan i fimkhur a, i mumang i hre reng bawk. Hei hi `zan lama hlauhawm` an ti a.`Zan lama hlauhawm` nen a danglam. Mi kaihthawh a harsa a, a harh pawhin an buai hle a, an buai hle niin a lang.
A châng chuan `Obstructive sleep apnea (OSA)` (mut laiin thawk hah) vei te pawhin heng symptoms te hi an lantir thei bawk. Hei hi `pseudo RBD` an ti a. Chutiang miteah chuan `OSA` enkawl a nih chuan nungchangte chu a bo vek thin.
`RBD` awm chhante chu engte nge ni?
A tlangpuiin `REM` muthilh lai te, mumang kan neih lai te hian kan taksa ruh tam tak (a bik takin ruh ruh) te hian rei lo te chhungin an hnathawh an hloh thin. Hei hi `muscle atonia` an ti a. Hei hi kan mumang a kan thil tih tak tak te hi ti tak tak lovin him taka kan mumang kan neih theih nan a thleng thin. Chu chu kan neih loh chuan eng nge thleng ang tih han ngaihtuah teh! Kan mumang ah kan tlan tak tak a, kan mumang ah kan zuang tak tak a nih chuan accident kan tawk thei a ni lawm ni?
Mahse RBD vei te hian he taksa ruh hnathawh hloh rei lo te, muscle atonia an tih hi an tawng lo. Chuvang chuan hriat lohvin an act out a, an mumang a an thil tih te an sawi chhuak thin. Hetiang thil a thlen chhan hi zirchiangtute chuan an la hre chiang lo hle. REM mutnaah hian neural pathway complex tak tak tam tak a awm a.
`Isolated (idiopathic) RBD` awm chhan te
Theory lian tak pakhat chu isolated (idiopathic) RBD hi thluak bul peng pakhat pons-a harsatna awm vang a ni a, chu chuan REM mut laiin muscle atonia a thlen a ni. Pons chhunga cell thenkhat chuan REM mut laiin muscle contraction an control thin. Pons-a hliam hi Parkinson natna, Lewy body dementia leh MSA te nen pawh a inzawm tih an sawi bawk. Isolated RBD leh heng natnate hi inzawmna nghet tak a neih avangin zirchiangtute chuan pons-a harsatna awm hi a chhan a ni thei niin an ngai.
Zirchianna pakhatah chuan `isolated RBD` vei zinga 97% chuan `RBD` an hmuhchhuah atanga kum 14 chhungin heng thluak lam natna zinga pakhat hi an nei a, `Parkinson's disease` hi a tam ber a ni.
`Secondary (symptomatic) RBD` awm chhan
Narcolepsy vei te hian thluaka chemical pakhat orexin emaw hypocretin emaw an tih chu an nei tlem hle a ni . He chemical hian mut, harh leh ei duhna a thunun a ni. He chemical hi a tlem chuan REM mut a tibuai thei a, RBD a thlen thei a ni.
`Drug-induced RBD` awm chhan
Researcher te chuan antidepressant thenkhat avanga RBD lo awm hi REM mutnaah hian neurotransmitters dopamine leh serotonin te inthlauhna vang a ni thei niin an ngai.
`RBD` hi engtin nge kan hriat theih ang? (Diagnosis) tih a ni.
`RBD` symptoms i neih chuan doctor pan ngei ngei tur a ni.Doctor chuan i symptoms leh i medical history te a zawt ang che. I mutpui emaw, i chhungte emaw i neih chuan doctor chuan i mut dan chungchang pawh a zawt thei bawk.
Doctor chuan taksa a enfiah ang che a, neurological exam a ti ang che. Mut lama mithiam hnenah pawh refer i ni thei bawk.
RBD i vei em tih chiang taka hriat theih nan in-lab video sleep study neih a ngai a, hei hi polysomnogram (PSG) tia hriat bawk a ni . Hei hi damdawi in emaw, mutna hmunah emaw tih a ni tlangpui a, camera monitoring hnuaiah zan khat chhung i awm thin. He test hian i mut laiin i taksa chungchang a hnuaia thilte hi a record a ni:
- Lungphun na tak.
- Thâwk chakna leh boruak kal dan.
- Brain wave hnathawh dan.
- Mit chet dan.
- I chin leh upper extremities-a muscle movement te.
International Classification of Sleep Disorders, Third Edition (ICSD-3)-in a tarlan dan chuan RBD vei hriat theih nan a hnuaia mi zawng zawng hi a awm vek tur a ni:
- I mut laiin i thusawi leh/ emaw, complex movement i tihna episode i nei fo thin.
- Heng thiltih te hi polysomnography (PSG) test hmanga finfiah a ngai a, REM mut laiin a thleng tur a ni. A nih loh leh, i clinical history atanga thlir chuan REM mut a nih thu an sawi chhuak tur a ni.
- `PSG` test hian `REM` mut laiin `muscle atonia` (muscle life hloh) i nei tih a lantir tur a ni. (`REM mut atonia tel lo` - RWA).
- REM mut lai hian seizure-related activity a bo tur a ni.
- Heng mut harsatnate hi mutna lama harsatna dang emaw, natna dang emaw, rilru lam natna emaw, damdawi ei avanga nghawng tha lo emaw, ruihhlo hmansualna emaw hian a sawifiah tha tur a ni lo.
RBD hi engtin nge enkawl a nih?
He `RBD` enkawl hian tum ber chu nang leh i kawppui tan mut him siamsak hi a ni . Hei atan hian strategy hrang hrang a awm a, a chang chuan damdawi pawh a awm bawk.
Hriselna atana hmalakna tur
Mut theihna hmun him siamna atana i tih theih thenkhat chu hetiang hi a ni:
- Khum chhehvel atang hian thil hrual, glass leh rit tak tak te chu paih chhuak rawh .
- Nangmah leh headboard emaw nightstand emaw inkarah thil nêm tak, pillow ang chi dah rawh.
- Khum atanga i tlak palh hlauh chuan khum bulah khum dah la , a nih loh leh khum sir lehlamah padded bedside rail dah bawk ang che.
- Mi thenkhat tan chuan mutna bag chhunga mut hian a pui thei bawk.
I natna lan chhuah dan a na hle a nih chuan i mutpui tur himna atan pindan hranah nangmah chauha mut chu a tha ber mai thei.
Tin, zu in hi a theih ang anga in loh tur a ni , zu hian `RBD` vei a tipung thei a, a natna a tizual thei bawk.
`RBD` atana damdawi hman tur
I natna lan chhuah dan a nasat a, himna dan ringawt pawh hian hliam a veng thei lo a nih chuan i doctor chuan i natna lan chhuah dan control nan damdawi a pe thei ang. RBD atana hman tur bik FDA-in a pawmpui damdawi awm lo mah se, zirchianna atanga a lan dan chuan melatonin, clonazepam, leh pramipexole te hian a chang chuan natna lanchhuahna a tihziaawm thei a ni.
- Melatonin: Hei hi kan thluaka pineal gland atanga pianphung atanga siam hormone a ni. Kan mut leh harh cycle tihreh nan a pawimawh hle. Synthetic melatonin hi damdawi atan a awm a. Hei hi RBD enkawlna atana first-line treatment anga ngaih a ni a, a chhan chu side effect a nei tlem hle. Doctor chuan dose tlem a\angin a tan ang a, zawi zawiin a natna lan chhuah dan a reh hma loh chuan a tipung ang.
- Clonazepam: Hei hi sedative a ni. RBD-ah hian engtin nge a puih tih zirchiangtute chuan an la hre chiang lo. Mahse, RBD vei tam tak chuan mut hmaa clonazepam dose tlem ei hian mumang chhia, au thawm leh mutthilh te a tihziaawm emaw, a ti bo emaw tih an hmuchhuak. Mahse, clonazepam hian side effect nuam lo tak tak a nei thei a ni. Hei vang hian i doctor chuan melatonin hian hahdamna a pe tawk lo a nih chuan a pe mai thei.
- Pramipexole: Hei hi dopamine agonist a ni. Doctor-te chuan Parkinson natna leh restless leg syndrome tan an pe ber a ni. Mahse tun hnaia zirchianna atanga a lan dan chuan RBD symptoms a tihziaawm thei bawk. Researcher te chuan he damdawi hian hna a thawk niin an ngai a, a chhan chu RBD hi dopamine tlakchhamna (dopaminergic deficiency disorder) avanga lo awm a nih vang a ni.
RBD hi ven theih a ni em?
A tam zawkah chuan RBD venna tur hian engmah tih theih a awm lo. Hei hi kan ven theih loh leh kan thlak danglam theih loh risk factor a awm vang a ni. Entirnan, i kum, emaw, narcolepsy emaw, neurodegenerative condition emaw i neih leh neih loh.
Mahse RBD hi zu ang chi thil avanga lo awm a nih chuan, a natna lan chhuah dan a pun chuan chutiang thil i hman tawh loh chuan RBD chu a bo mai thei.
RBD hi eng prognosis nge ni?
RBD hmalam hun tur, chu chu natna hi khawiah nge a kal dawn tih hi thil engemaw zatah a innghat a ni:
- A chhan bulpui a awm leh awm loh. Chu chu `narcolepsy` (secondary `RBD`), antidepressant (`drug-induced RBD`) vang nge, a lo thleng mai mai (spontaneously - `isolated RBD`) vang emaw tihna a ni.
- I symptoms te hi engtiang chiahin nge a nasat tih leh chhiatna a thlen che em tih te.
- Enkawlna zawng emaw zawng lo emaw.
- RBD nen hian nervous system natna i nei em tih pawh.
RBD thil pawimawh leh pawi ber chu thluak lam natna, a bik takin Parkinson’s disease, multiple system atrophy, leh Lewy body dementia te nena a inzawmna hi a ni. Evidence pung zel chuan RBD hi heng natnate hriattirna hmasa ber a ni thei tih a tarlang. Hei hi RBD hi a takin a lo awm a, chhan dang awm lovin, narcolepsy emaw damdawi emaw avanga lo awm a nih loh chuan a dik hle.
RBD hian nangmah leh/ emaw i mutpui kawppui tan harsatna nasa tak a thlen thei a, chuvangin enkawlna zawn a pawimawh hle.
RBD nei leh neurological condition nei tan chuan prognosis hi a tlangpuiin a tha lo. Entirnan, Parkinson natna hmasa ber leh RBD nei te hian Parkinson natna hmasa ber nei mahse RBD nei lote aiin nunphung a hniam zawk tih hmuhchhuah a ni.
RBD avanga harsatna awm thei te chu engte nge ni?
Heng mite hi an mut laiin a chang chuan tharum thawha an che avangin khumah emaw midang emaw hliam an tuar theihna a sang hle. Tin, mut hi tihtawp a nih fo avangin hei hian mut quality zawng zawng a nghawng thei bawk.
Hliam chi hrang hrang awm thei:
- A hliam (Bruises) a awm.
- Cuts a ni.
- Sprains a awm.
- Ruh tliak.
- Lu hliam leh subdural hematomas (luruh chhunga thisen chhuak) ang chi natna khirh tak tak .
A châng chuan heng hliamte hi nunna atana hlauhawm tak a ni thei .
RBD vei partner zinga 90% chuan mut harsatna an nei tih an sawi a , 60% aia tam chuan taksa hliam an tuar bawk .
Chuvangin RBD enkawlna zawng a, a tlem berah mut him theihna tur boruak siam a pawimawh hle.
Engtikah nge `RBD` chungchangah doctor i hmuh ang?
- `Isolated RBD` (RBD chhan dang nei lo) i vei tih hmuhchhuah i nih chuan, a nena inzawm tlat thei thluak lam natna (`Parkinson’s`, `Lewy body dementia`, `MSA`) `signs` awm leh awm loh enfiah turin doctor i pan fo a ngai ang.
- Symptom thar i neih chuan, chetna lama harsatna emaw, hriatna lama inthlak danglamna emaw i neih chuan doctor pan nghal rawh.
- Nangmah emaw, i mutpui tu emaw hian RBD vangin hliam i tuar a nih chuan damdawi lam thurawn zawng nghal rawh.
`RBD` hi rilru lam natna a ni em?
Ni lo, `REM Sleep Behavior Disorder (RBD)` hi `rilru natna` a ni lo. `Mood disorder` emaw `anxiety disorder` ang a ni lo. `RBD` hi `mutna lama harsatna` – a bik takin `parasomnia` chi khat a ni.
Nangmah emaw, i mutpui tu emaw i hliam palh chuan lungngaihna leh lungchhiatthlak tak a ni thei. I kawppuiin i mut laiin i bei emaw, i au emaw tih a hrilh che a nih chuan ngaihthah suh. Doctor nen inbia ang che. RBD an neih leh neih loh enfiah turin mut zirchianna an rawt thei a, a tul chuan enkawl an rawt thei bawk. Hliam tuar lo tura mutna hmun him siam hi a pawimawh ber tih hre reng ang che.
A tawp berah chuan hei hi hre reng ang che (Take-Home Message) .
Chuvangin, nangmah emaw i hriat mi emaw chu an mut laiin mak tak maia an awm a nih chuan – au chhuahpui, an kut an thlak, khum atanga tlu, etc. – mumang tha lo anga ngaih mai suh. REM Sleep Behavior Disorder (RBD) a ni thei bawk.
A bik takin nangmah emaw midang emaw hliam a thlen chuan doctor thurawn la ngei ang che. Hei hi thluak lam natna khirh tak tak thenkhat chhinchhiahna hmasa ber a ni thei bawk tih hre reng ang che. Chuvangin a hmaa hriatchhuah a, a tul anga hmalak a pawimawh hle. I mutna te, i kawppui mut dan te, an pahnih himna te hi a pawimawh hle. Chuvangin hei hi uluk takin enkawl rawh.
` REM mut nungchang lama harsatna, RBD, mut harsatna, mutthilh, mut au, mut harsatna, thluak lam harsatna











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