Sneddon Syndrome hi eng nge ni? I vunah hian hetiang spot hi i nei em? Kan sawi dun teh ang!

Mi thenkhat chuan an vunah, a bik takin an ke ruhah, net ang maia rawng dum (purple spot) an nei tih i hmu tawh em? A chang chuan luak chhuak leh lu na vangin an phunnawi bawk. Vawiin hian natna hlauhawm tak, a lan chhuah dan inang tak tak kan sawi dawn a, mahse tumahin an sawi tam lo. Hei hi Sneddon Syndrome an ti a.

Sneddon Syndrome hi eng nge ni? A awlsam zawngin...

A awlsam zawngin sawi ila, Sneddon Syndrome hi i taksaa thisen kalna kawng te tak te leh lian lo te a nghawng a ni. Heng thisen kalna kawngte hi tui phurtu pipe angin ngaihtuah rawh. He natnaah hian i thisen kalna kawng chhunga cell smooth layer, damdawi lama endothelium tia koh chu a thang chak zawkin a thang chak zawkin a thang lian zawk thin. Chuti a nih chuan eng nge thleng? Heng extra cells te hian thisen kalna kawng chhunga hmun awm chu a ti tlem a, pipe chhunga bawlhhlawh a tlakbuak chuan tui luang a harsat ang bawkin. Hei hian thisen kal dan a tikhawlo thin.

Hei hi hun engemaw chen enkawl ngai a ni a, hun kal zelah a zual zel thei a ni. Hetiang natna vei te hi thisen zam (blood clots) an nei nasa hle. Tin, vun lama harsatna leh thluak lam harsatna an nei thei bawk. A chang chuan Sneddon-Champion syndrome an ti bawk. A hming dang chu livedo reticularis racemosa a ni. Hetiang dinhmun hian mi thenkhatah stroke leh transient ischemic attack (TIA) a thlen thei a ni.

Hetiang dinhmun hi engtiang chiahin nge a awm? Tu zingah nge a tam ber?

Dik tak chuan Sneddon Syndrome hi natna hmuh tur awm lo tak a ni. Statistics-ah chuan kum tin mi maktaduai khat zinga mi pali chauhvin an vei nia chhut a ni. Chu chu mi sang hnih leh a chanve zinga pakhat vel a ni.

Chubakah, he natna hi mipa aiin hmeichhiaah a tam zawk. Sneddon syndrome vei zinga 80% vel chu hmeichhia an ni. Kum 40 vel an nih veleh he natna hi an vei tih hmuhchhuah a ni tlangpui.

Hei hi eng symptoms nge ni? Engtin nge i hriat chian?

Sneddon Syndrome vei chuan symptom hrang hrang a nei thei a. Mahse, heng symptoms zawng zawng hi vawi khatah a lang vek lo. Symptom thenkhat chu neurological problems a lo awm atanga kum tam tak hnuah a lo lang thei bawk. A nih loh leh mi ṭhenkhat chuan mit lama harsatna emaw, lu na emaw an nei hmasa thei bawk. A lan chhuah dan thenkhat chu hetiang hi a ni:

• Vun chunga mesh ang chi pattern:Hei hi mi tam takin an hriat chian hmasak ber a ni. Vun hian fishnet emaw rul thenkhata pattern ang chi, reddish-purple spot hrang hrang a nei a. Hei hi a pawi lo. Heng hmul te hi i kut leh keah a lo lang a, khaw lum laiin a lo lang a, i lum laiin a bo a nih chuan livedo reticularis an ti a ni. Mahse, he pattern hi i rilru, i pum emaw, i hnute emaw-ah a lo lang a, i lum lai pawhin a bo lo a nih chuan livedo racemosa an ti a ni.
• Lu na: Lu na fo, a chang chuan na tak tak a awm thei.
• Luak chhuak: A inher chhuak tih hriatna.
• Stroke leh TIA: A hmaa kan sawi tawh ang khan hengte hi a pawi ber pawl an ni.
• Nungchang leh ngaihtuahna inthlâk danglamna: I mizia te, i ngaihtuahna te, leh i hriat reng theihnaah te inthlâk danglamna a awm thei a.
• Kal lama harsatna: Hei hi a tlem deuh a, mahse mi thenkhat chuan kal lama harsatna an nei thei bawk.

A pawimawh ber chu heng symptoms zinga pakhat emaw pahnih emaw i neih chuan, a bik takin lu na leh luak chhuak leh mesh ang chi vun pattern i neih chuan doctor hnenah thurawn dil ngei ngei tur a ni.

Engvangin nge Sneddon Syndrome hi a lo awm? A chhan chu eng nge ni?

Hei hi a takah chuan doctor-te’n an la chhui chhuah theih loh thil a ni. Sneddon Syndrome awm chhan dik tak hi hriat chian a la ni lo. Chuvangin idiopathic an ti a, a chhan hriat loh tihna a ni. Mahse, he natna hi chhungkaw ṭhenkhatah a kal tih hmuh a nih avangin, genetic component a awm thei nia rinhlelh a ni .

Tin, a then phei chuan Sneddon syndrome hi autoimmune condition dang nen a awm dun thei bawk . Autoimmune disease chu kan taksa immune system-in kan taksa cell-te a beih dan mai a ni. Sneddon syndrome i neih chuan a hnuaia natna pakhat nen hian a inzawm thei a ni:

• Lupus a ni
• Antiphospholipid natna a ni
• Behçet natna a ni
• Mixed connective tissue natna a ni

Engtin nge hei hi hriat chhuah a nih? Eng test nge tih thin?

I doctor chuan i symptoms atanga Sneddon Syndrome i vei nia a rinhlelh chuan test hrang hrang engemawzat an order ang. Heng test-te hian:

• I thisen: Autoimmune disease chhinchhiahna leh thisen zam chungchanga harsatna awm leh awm loh enfiah rawh.
• I thinlung: I thinlung leh thisen kalna kawng hrang hranga thisen a kal dan enfiah thin ang che.
• I thluak chu:Thluak a chhiat leh chhiat loh enfiah thin ang che. Stroke vang pawh a ni thei.
• I vun: Vun te tak te lak a, enfiah (skin biopsy) a, he natna ziarang cell inthlak danglamna a awm em tih enfiah a ni.

Heng test te hian specialized imaging test te pawh a huam thei . Entir nan:

• MRI scan (magnetic resonance imaging - MRI scan) hmanga enfiah a ni.
• CT scan `(computed tomography - CT scans)` hmanga tih a ni
• Angiograms (thisen kalna kawng dinhmun enfiahna atana X-ray bik) .

Doctor ten heng test zawng zawng an tih zawh hnuah chauh he natna hi dik takin an finfiah thei a ni.

Engtin nge enkawl a nih? (Enkawlna) Eng nge duhthlan tur awm?

Sneddon Syndrome enkawl dan tha ber chu tun thlengin hriat chian a la ni lo. Hei hi a chhan pakhat chu he natna vei hi an tlem em avangin clinical trial lian tak tak nei thei tur mi tling hmuh a harsat vang a ni.

Mahse, natna lan chhuah dan azirin enkawl dan hrang hrang a awm. Entirnan, i doctor chuan damdawi a pe thei a, chungte chu:

• Anticoagulant emaw antiplatelet damdawi: Hengte hian thisen zam a veng a, thisen kal a ti awlsam bawk.
• Vasodilators: Entirnan, nifedipine. Chungte chuan thisen kalna kawng a tizau a, thisen kalna a tipung bawk. Hei hian vun natna lanchhuahna atanga hahdamna a pe tlangpui.
• Angiotensin-converting enzyme inhibitors (ACE inhibitors): Hengte hian a hmaa kan sawi tawh endothelial cells te lo thang dan pangngai lo chu a titawp thei a ni.

Pawimawh: Sneddon syndrome i neih chuan meizuk leh estrogen awmna birth control pill hman loh vek tur a ni. Chûngte chuan natna chu a tizual thei a ni.

He natna laka inven dan tur a awm em?

Vanduaithlak takin tunlai thuthang atanga thlir chuan Sneddon Syndrome hi ven dan tur a awm lo. A chhan dik tak hriat a nih loh avangin a ven dan tur sawi a har hle.

Hetiang dinhmun hi a awm reng chuan eng nge thleng ang? (Prognosis) Nakin hun atan eng nge kan beisei theih ang?

Thil tam takah chuan Sneddon Syndrome hian nervous system a tidanglam thin. Entirnan , hriatrengna hloh leh thusawi harsatna chu hun kal zelah a lo awm zauh zauh thei. A then phei chuan Sneddon Syndrome vei te pawh hi early-onset dementia vei an ni thei bawk. Chuvang chuan heng symptoms te hi hriat chian a pawimawh hle.

Damdawi famkim a awm em?

Tuna damdawi lam chanchin atanga a lan dan chuan Sneddon Syndrome``Damdawi'' kimchang tak chu hmuh a la ni lo. Enkawlna hian symptoms control a tum a, natna a zual zel loh nan ven tum a ni.

Engtikah nge damdawi lam thurawn i lak ang?

Sneddon Syndrome symptoms i neih chuan mesh ang maia vun pattern, lu na leh luak chhuak te hi doctor pan nghal rawh. A bik takin vun rawng nen hian symptom dang i neih chuan tihkhawtlai suh.

Sneddon syndrome i vei tih hriatchhuah tawh i nih chuan, symptom thar i neih chuan emaw, i symptoms a zual zel nia i hriat chuan doctor hnenah hriattir nghal rawh.

Tin, stroke symptoms i neih chuan tihkhawtlai suh. 911 call nghal rawh (Sri Lanka-ah chuan 1990 Suwaseriya Ambulance Service) emaw, damdawi in emergency department hnai ber pan rawh. Stroke natna lan chhuah dan chu:

• Lu na tak tak a lo awm nghal.
• Mit lama harsatna (mit pakhata mit hmuh lohna, a pahnih a fiah lo ang chi).
• Taksa sir lehlamah emaw, a sir lehlamah emaw, rilru hahna emaw, chak lohna emaw.
• Kal harsat.
• Midang thusawi emaw hriatthiam harsat .

A tawp berah chuan thil hriat reng tur (Take-Home Message) .

Sneddon Syndrome hi natna hlauhawm tak a ni a, natna khirh tak a ni thei bawk. Mahse, he natna hi i vei tih hmuhchhuah a nih chuan i doctor thupek chu uluk takin zawm tur a ni. I damdawi ei tur chu a hun takah ei la, i follow-up appointment te chu vawng reng la, testing schedule engmah ti lo.

Thinlung hrisel nunphung i hman hian i in tanpui thei a ni. Chu chu ei leh in inthlau tak ei te, exercise lak te, leh meizuk leh estrogen awmna naupai venna pumpelh tihna a ni. Heng thilte hian i dinhmun thunun kawngah kawng thui tak a zawh thei a ni. Ngaihtuah buai suh, damdawi lam enkawlna dik leh nunphung thlak danglamna nen hian he dinhmun hi i nung thei a ni.

` Sneddon syndrome, thisen kalna kawng natna, vun natna, stroke, neuropathy, livedo reticularis, thisen zam