Hliam te tak te atang pawhin thisen a chhuak nasa em? Hei hi von Willebrand Disease vang pawh a ni thei.

Thisen chhuak tura beisei aia rei cut tenau i nei tawh em? A nih loh leh i taksa pum puiah hnar thisen emaw, hliam emaw i nei tawh em? "Aw... chutiang chiah chu ka ni," tiin i ngaihtuah mai thei. Mahse heng thilte hnuaiah hian damdawi lam chhan i hriat loh a awm thei. Vawiin hian thisen zam (blotting process) tichhe thei dinhmun kan sawi dawn a, chu chu mi tam takin an la hriat ngai loh, mahse chutiang khawpa tlem a ni lo. Chu chu von Willebrand Natna a ni.

A awlsam zawngin, von Willebrand natna chu eng nge ni?

von Willebrand natna hi genetic blood disorder a ni a, chu chuan kan thisen a clot tha thei tih a tichhe a ni.

Kan taksaah hliam kan neih hian thisen chhuah titawptu hnathawk pawl tlemte an awm tih han ngaihtuah teh. Heng hnathawkte hian an thawk ho a, hliam chu khar nan an pui a, plaster ang maiin. Chu "manager" chu protein pakhat von Willebrand factor (VWF) tih a ni. He VWF protein hian thisen chhunga platelet te chu a inzawm khawm a, thisen zam a siam a, chu chuan hliam chu a seal a ni.

Tunah chuan von Willebrand natna vei tan chuan taksain he VWF protein hi a siam chhuak tawk lo. A nih loh leh protein siam chhuah hian hna a thawk tha lo. Chuvangin chu "manager" chu a awm loh avangin platelet te chu an inzawm khawm a, thisen zam a siam theih nan hun rei tak a ngai a ni. Chuvang chuan hliam te tak te pawhin thisen a chhuah chhunzawm zel a ni.

Hetiang dinhmun hi a nasat chuan ruh chhung emaw soft tissue emaw chhungah thisen a chhuak thei a, natna nasa tak leh hliam na tak a thlen thei a ni. Mi thenkhatah chuan hei hian thisen tlakchhamna (anemia ) a thlen thei bawk a, chu chu taksaa thisen awm zat tlahniamna a ni.

He natna chi hrang hrang lian ber ber a awm em?

Ni e, von Willebrand natna hi mi zawng zawng tan a inang vek lo. A chi thum a awm a. A lan chhuah dan nasat dan hi a chi hrang hrang a zirin a inang lo.

Von Willebrand natna lan chhuah dan chu engte nge ni?

Mi tam tak, a bik takin Type 1 vei tan chuan a natna lan chhuah dan chu chutiang chuan a na lo. Natna an vei tih pawh hre loin an nung mai thei. Mahse, a nasat chuan a hnuaia chhinchhiahna te hi a awm thei a ni:

• Hnar thisen chhuak fo: I hnar atanga thisen chhuak tlemte pawh a chhuak a, tihtawp a harsat chuan.
• Hliam tenau atanga rei tak thisen chhuak: Cut emaw scrape emaw atanga minute 10 aia tam thisen chhuak a nih chuan.
• Bruising easily: Bump tenau tak i neih hnuah pawh bruise lian tak tak, hring dup i neih chuan.
• Hmeichhiaah thlasik lai thisen chhuak nasa: I period laiin a tlangpui aia tam thisen i chhuah chuan. Entirnan, darkar khat emaw darkar hnih emaw a ral hmaa i pad thlak a ngai a nih chuan, thisen zam lian tak tak i paltlang a nih chuan, emaw, ni 7 aia tam thisen i chhuah chuan i ngaihtuah tur a ni.
• Operation hnua thisen chhuak tam lutuk: Ha lak chhuah ang chi thil awlsam tak hnuah pawh a pangngai aia tam thisen i chhuah chuan.
• Nau neih hnua thisen chhuak nasa emaw, nau pai emaw.
• Thisen chu bawlhhlawh emaw zun emaw ah a awm.

Engvangin nge he natna hi a lo awm? Engtin nge rochun a nih?

von Willebrand natna hi genetic disorder a ni a . A awlsam zawngin sawi ila, VWF protein siam chhuahna control tu gene-a chhiatna avanga lo awm a ni. He gene chhia hi kan nu leh pate hnen atangin kan rochun a ni.

Hei hi rochun theih dan kawng hnih a awm a:

1. Autosomal dominant inheritance: Hei hi nu emaw pa emaw atanga lo chhuak a ni.Mi pakhat chauhvin gene chhia chu rochun mah se, natna hi a lo awm thei a ni. Hetiang hian Type 1 leh Type 2 hi kan rochun fo thin.

2. Autosomal recessive inheritance: Hetiang a nih chuan natna lo vei tur chuan nu leh pa pahnihin gene chhia chu an rochun a ngai a ni. Type 3, a na ber chi hi hetiang hian rochun a tam ber.

A tlem berah chuan cancer thenkhat, autoimmune disorder, leh thinlung natna te pawhin nakin lawkah he natna hi a thlen thei bawk. A hming chu acquired von Willebrand syndrome an ti a ni .

He natna hi engtin nge doctor hian a hriat theih ang?

I doctor hnenah i natna lan chhuah dan i hrilh chuan a enfiah hmasa ang che a, i hliam emaw, thisen chhuahna chhinchhiahna dang emaw a zawng ang. Tichuan i chhungkuaah hian hetiang thisen chhuahna lama harsatna nei an awm em tih an zawt ang.

Natna dik tak hriat theih nan thisen test eng emaw zat neih a ngai a ni.

• Complete blood count (CBC): Hei hian i thisena red cell, white cell leh platelet awm zat a enfiah thin. I platelet count a hniam a nih chuan, emaw, thisen tlakchham vanga i hemoglobin a hniam chuan he dinhmun hi rinhlelh theih a ni.
• Clotting test: Hei hi i thisen a clotting hun chhung tehna a ni.
• von Willebrand factor (VWF) test: Heng test bikte hian i thisena VWF protein level leh a thawk tha em tih an enfiah thin.
• Factor VIII test: VWF protein hian Factor VIII a venghim a, hei hi thisen zam tura puitu protein pawimawh dang a ni. Chuvangin VWF a hniam chuan Factor VIII level pawh a hniam thei bawk. He test hian chu chu a zawng a ni.

Hei hi eng enkawlna nge ni?

Enkawlna chu i natna chi hrang hrang leh i natna lanchhuahna nasat danah a innghat a ni. Mi tam zawk chuan operation hma emaw, hliam an neih hnuah emaw chauh enkawlna an mamawh a ni.

Enkawl dan tlangpui engemaw zat a awm a:

• Desmopressin (DDAVP): Hei hi damdawi hman tam ber a ni. Hormone a ni. Hnar spray angin emaw, injection angin emaw pek thin a ni. Kan taksaa VWF proteins dahkhawmte thisenah a chhuah chak zawk avangin hna a thawk a ni.
• von Willebrand factor infusions: A nasat chuan VWF concentrated form chu injection hmangin taksaah pek a ni. Hei hi taksa tana VWF protein tlakchham tawh pek ang a ni.
• Antifibrinolytics: Heng damdawi te hian thisen zam chu a hmin rang lutuk loh nan a titawp a ni. Ha lakchhuah ang chi thila thisen chhuahna control nan pek an ni.
• Birth control pills: Hengte hi thlasik laia thisen chhuak nasa tak nei tan chuan a tangkai hle. Heng pill-a estrogen hormone hian VWF level a tisang a ni.

Engtikah nge Doctor ka hmuh ang?

Thisen chhuah awlsam, hliam awlsam, emaw, period na tak i neih chuan chhungkaw doctor pan ngei ngei tur a ni. Thisen chhuak nasa chhan dang pawh a awm thei a, chuvangin diagnosis dik tak neih a pawimawh.

He natna nen hian eng nge ka tih theih ang?

Von Willebrand natna i neih chuan thisen chhuah loh nan tlem tal fimkhur a ngai tihna a ni. Hemi chungchangah hian i doctor chuan thurawn a pe ang che. A tlangpuiin a hnuaia mite hi pumpelh a tha ber:

• Hliam thlen thei infiamna pumpelh tur: Infiamna tam tak inhnaih tak tak, rugby leh boxing te hi a inhmeh lo hle.
• Thisen tihthianghlimna damdawi ei loh tur: Doctor phalna la hmasa lovin natna tidamtu aspirin emaw NSAID emaw (e.g., Ibuprofen, Diclofenac) ei loh tur a ni.
• Supplement thenkhat ei loh tur: Vitamin E leh fish oil ang chi thil hian thisen a ti thim thei. Eng thil pawh i hman hmain doctor zawt hmasa phawt ang che.

I doctor zawng zawng (i ha enkawltu pawh tel) hnenah he natna hi i nei tih hrilh la , chutiang chuan engmah an tih hmain thisen chhuahna control turin hma an la thei ang, surgery ang chi. Tin, emergency a awm chuan medical staff te hriattirna atan medical alert bracelet bun a tha bawk.