Kei te ahua kore ora tō tinana? Ko te Myasthenia Gravis (MG) tēnā? Me kōrero tāua!

I ētahi wā ka tino ngenge koe, ka kore ora hoki i te roanga o te rā? Ina koa ka rite ō kanohi ki te katia, ā, he uaua ki te kōrero, ki te kai, ki te hiki rānei i te ringa, i te waewae rānei? Ehara i te ngenge noa iho ēnei mea. I tēnei rā ka kōrero tātou mō te Myasthenia Gravis , (MG) rānei, he mate uaua, engari ka taea te whakahaere pai mēnā ka whakahaerea tika .

He aha te Myasthenia Gravis? He māmā noa iho...

He mate pūnaha ārai mate te myasthenia gravis. He aha te mea? He tino māmā noa iho. He pūnaha ārai mate kei roto i ō tātou tinana. He rite ki tētahi ope taua kei roto i ō tātou tinana. Ko tāna mahi he tiaki i a tātou mā te whawhai ki ngā iroriki me ngā mate e puta mai ana i waho. Engari, i ētahi wā ka hē te ope taua nei. E whakaaro ana ia ko ngā pūtau hauora o roto i ō tātou tinana te hoariri. Kātahi ka tīmata te whakaeke i aua pūtau hauora. Koinei te mea e tupu ana i roto i te myasthenia gravis.

Ko te nuinga o tēnei ka pā ki ngā uaua angaanga . Arā, ko ngā uaua e piri ana ki ō tātou wheua, e āwhina ana i a tātou ki te neke. Whakaarohia, ka ara ake tō ringa, ka kimo ō kanohi, ka kōrero, ka kata, ka kai, ka hikoi... Ka āwhina ēnei uaua i ēnei mea katoa. I roto i te tangata e pāngia ana e te myasthenia gravis, ka ngoikore ēnei uaua, ka kore he ora.

Ko te mea nui , ka piki ake te ngoikore o te uaua ina mahi ana koe, ā, ka heke iho ina okioki koe . Ahakoa kei te pai koe i te oho ake i te ata, i te roanga atu o te rā, me te mahi i tāu mahi, ka ngenge haere koe, ka ngoikore haere ō uaua.

He mate pūmau tēnei, arā, kāore e memeha i roto i te wā poto. Kaua e manukanuka, he pai ngā maimoatanga hei āwhina i a koe ki te whakahaere i ō tohumate me te noho i te oranga noa .

He aha tēnei e tupu ana? He aha ngā mea e tupu ana i roto i ō tātou tinana?

Hei mārama ki tēnei, me tango he tauira iti. Whakaarohia kei te mātaki koe i tētahi whakataetae kirikiti.

Ko ō tātou io te kaiwhiu. Ko rātou te hunga e tuku karere ana ki ngā uaua.

Ko ō tātou uaua te kaihopu. Ko rātou te hunga e hopu ana i te karere.

Ko te wāhi e hono ai ēnei karere e rua ko te hononga io-uaua . Koinei te papa tākaro.

Ināianei, ina hiahia te io ki te tuku karere ki te uaua, ka tukuna e te io he matū e kiia nei ko te acetylcholine (koinei te pōro). He wāhi motuhake kei ngā uaua hei hopu i tēnei acetylcholine, e kiia nei ko ngā kaiwhakawhiwhi acetylcholine (koinei te karapu o te kaitiaki).

Pērā i te pānga o te pōro ki te karapu, ka kōpiri te uaua, arā, ka whakahohe, ina haere te acetylcholine ka herea ki aua kaiwhakawhiwhi. Ka tino tere te tupu o tēnei, kāore he aukati, i roto i te tinana o te tangata hauora.

Engari, ko te mea ka tupu i roto i te tangata e pāngia ana e te myasthenia gravis, ko te pūnaha ārai mate i kōrerohia e tātou i mua ake nei ka whakangaro, ka aukati rānei i ēnei kaiwhakawhiwhi acetylcholine (karapu hopu) . Kātahi ka kore e taea e te uaua (te kaitiaki) te hopu tika i te karere (te pōro) e puta mai ana i te io. Ka tino puhoi te whakawhitiwhiti karere, kāore rānei. Koia te take ka ngoikore ai ngā uaua. Kei te mārama koe?

He rerekē ngā momo myasthenia gravis?

Ae, he maha ngā momo matua:

• Te mate pūkahukahu ā-tinana: Koinei te momo tino noa. E ai ki tā tātou i kōrero ai i mua ake nei, nā te ngoikore o te pūnaha ārai mate i puta ai. Ahakoa kāore i te mōhiotia te tino take o tēnei, e whakaponohia ana nā te whakaputanga o ētahi momo paturopi .
• Myasthenia pēpi hou: Ka puta tēnei ina whiwhi te pēpi i ētahi paturopi mai i te whaea he myasthenia gravis tōna i te wā e hapu ana. I muri i te whānautanga, tera pea ka paku mārō ake te tangi a te pēpi, ā, ka uaua ki te ngote. Heoi, he wā poto noa iho tēnei, ā, ka pai ake i muri i te toru marama pea.
• Myasthenia whānau: Ehara tēnei i te mate pūnaha ārai mate. He momo onge tēnei e hua mai ana i te huringa ira .

E rua ngā momo matua o te myasthenia gravis autoimmune:

1. Te mate kanohi myasthenia: I tēnei, ka ngoikore ngā uaua e neke ana i ngā kanohi, e whakaara ake ana hoki i ngā kamo. Ka piko pea ngā kamo (ptosis) , ka uaua rānei te pupuri i ngā kanohi kia tuwhera. Ka kite pea ētahi tāngata i ngā mea e rua (tirohanga takirua). He maha ngā wā, ko te tohu tuatahi o te mate kanohi myasthenia ko te ngoikore o ngā kanohi . Tata ki te haurua o te hunga whai tēnei momo mate kanohi myasthenia ka pāngia e te momo tuarua i muri mai.

2. Te myasthenia whānui: I roto i tēnei, haunga ngā uaua o ngā kanohi, ka ngoikore hoki ngā uaua o te mata, te kaki, ngā ringa, ngā waewae, me te korokoro. He uaua pea te kōrero, te horomi kai, te hiki i ō ringa, te whakatika i te tūru, te hikoi tawhiti, me te piki arawhata.

He aha ngā tohu o te myasthenia gravis?

Ahakoa he rerekē ngā tohu, ko ngā mea tino kitea ko:

• Te ngoikore o ngā uaua o ngā ringa, o ngā maihao, o ngā waewae, me te kaki.
• Ngenge rawa (fatigue) .
• Te kamo e takoto kau ana (ptosis) .
• Te tirohanga pōuri, te tirohanga takirua rānei .
• Te uaua ki te whakaatu i ngā āhua o te kanohi (pēnei i te kore e taea te menemene tika, te hanga kanohi).
• Te uaua ki te kōrero, te horomi, te ngaungau rānei . Hei tauira, ka huri haere pea tō reo i a koe e kōrero ana, ka rite tō reo ki te reo pōturi.
• Te uaua ki te hikoi .

Ka puta ohorere pea ngā tohu tuatahi o te myasthenia gravis. E ai ki tā mātou i kōrero ai i mua ake nei, ka ngoikore ō uaua i a koe e mahi ana, ā, ka hoki mai te kaha ina okioki koe . Ka rerekē te kaha o tēnei ngoikore uaua i ia rā, i ia rā. He maha ngā tāngata ka pai ake te ahua i te tīmatanga o te rā, ā, ka ngoikore rawa atu i te mutunga.

He tino onge, ka pāngia hoki ngā uaua o te pūnaha manawa e te myasthenia gravis. Ka taea e tēnei te whakapoto i te manawa, te whakararuraru rānei i te manawa. Ki te mea kei te raru koe i te manawa, he āhuatanga ohorere tēnei. Me haere tonu koe ki te hōhipera tata. Kāore tēnei e puta i te wā kotahi.

Ko wai te mea tino mōrearea mō tēnei?

Ahakoa ka taea te whakawhanake i te myasthenia gravis i ngā tau katoa, he nui ake te kitea i roto i ngā wāhine kei raro iho i te 40 tau te pakeke me ngā tāne neke atu i te 60 tau te pakeke .

Tērā pea ka nui ake tō tūponotanga ki te whakawhanake i tēnei mate nā ēnei take e whai ake nei:

• Mena kei a koe ētahi atu mate pūnaha ārai mate (hei tauira, te rumatiki rheumatoid, te lupus).
• Mena he mate tairoi tōu .

Mena kei a koe te myasthenia gravis, ka kino ake pea ō tohumate i ētahi āhuatanga:

• Ko ētahi rongoā mō te malaria me ngā mate manawataki o te ngakau.
• Kei te pokangahia .
• He mate urutā .

He aha te whanaungatanga i waenga i te repe thymus me te myasthenia gravis?

He maha ngā tāngata e pāngia ana e te myasthenia gravis, he raruraru tō rātou repe thymus . He okana iti te repe thymus i roto i te uma o runga, i raro noa i te wheua uma. He wāhanga ia o te pūnaha lymphatic. Koinei te okana e hanga ana i ngā toto mā, e āwhina ana hoki ki te whawhai ki ngā mate.

Tata ki te rua hautoru o te hunga whai myasthenia gravis he thymic hyperplasia , he āhuatanga e kaha rawa ai te mahi a te repe thymus. Hei tāpiri, tata ki te kotahi i roto i te tekau o te tangata ka puta he pukupuku i roto i te repe thymus e kiia nei ko ngā thymomas . Ka taea e ēnei te mate pukupuku, te kore rānei e kino. E whakaarohia ana ko ēnei āhuatanga rerekē i roto i te repe thymus ka whai wāhi ki te kore mahi a te pūnaha ārai mate.

He aha ngā raruraru ka pā mai i te myasthenia gravis?

Ko te mea matua he āhuatanga e kiia nei ko te myasthenic crisis . I roto i tēnei, ka ngoikore rawa ngā uaua e āwhina ana i a koe ki te manawa. Kātahi, ka hiahia pea koe ki tētahi mea pēnei i te mīhini (manawa/whakahaunga mīhini) hei āwhina i a koe ki te manawa. He āhuatanga ohorere hauora tēnei ka tūpono ki te ora.E kiia ana ko te kotahi i roto i te rima o ngā tāngata e pāngia ana e te myasthenia gravis ka pāngia e tēnei mate i te iti rawa kotahi i roto i ō rātou oranga.

Hei tāpiritanga, ka taea e tēnei ngoikore me te ngenge o ngā uaua te aukati i a koe ki te whai wāhi atu ki ngā mahi e pai ana ki a koe. Ka taea hoki e ia te arahi ki te ahotea me te pouri . Heoi, kua whakaatuhia e ngā rangahau he maha ngā tāngata whai myasthenia gravis ka taea te mahi i ngā mahi māmā me te whakakori tinana i ia rā.

Me pēhea te tautuhi a ngā tākuta i te myasthenia gravis?

Mena kei te whakapae tō tākuta i tēnei i muri i te whakarongo ki ō tohu me te whakahaere i tētahi whakamātautau tinana, ka mahia e rātou ētahi whakamātautau hei whakaū i tēnei:

• Ngā whakamātautau paturopi toto: Tata ki te 85% o te hunga whai myasthenia gravis he nui rawa ngā taumata o ngā paturopi acetylcholine receptor i roto i ō rātou toto. Ko tētahi atu 6% he paturopi ki te muscle-specific kinase (MuSK) .
• Ngā matawai whakaahua: Ka mahia he matawai MRI (Magnetic Resonance Imaging) he matawai CT rānei (Computed Tomography scan) hei tirotiro mō ngā raruraru pēnei i ngā pukupuku i roto i te repe thymus.
• Te Electromyography (EMG): Ka ine tēnei whakamātautau i te ngohe hiko o ngā uaua me ngā io. Ka taea e ia te kite i ngā raruraru o te whakawhitiwhiti kōrero i waenga i ngā io me ngā uaua.

Ka whakarōpūhia e ngā tākuta te myasthenia gravis i runga i te kaha o te mate. E rima ngā momo (Aso I - V). He mate ngawari te Aso I e pā ana ki ngā kanohi anake, ko te Aso V ia he mate kino e pā ana ki te manawa, i ētahi wā me whakauru he ngongo , he manawa mīhini rānei.

He aha ngā maimoatanga mō te myasthenia gravis?

Kāore he rongoā mō te myasthenia gravis, engari he maimoatanga whai hua hei āwhina i a koe ki te whakahaere i ō tohumate me te noho i te oranga pai.

• Ngā rongoā:
• Ngā aukati cholinesterase / anticholinesterase: Ko te mahi a ēnei rongoā mā te whakapai ake i te whakawhitiwhiti kōrero i waenga i ngā io me ngā uaua, ka whakanui ake i te kaha o te uaua.
• Ngā rongoā ārai mate: Ka mahi ngā rongoā pēnei i te corticosteroids mā te whakaiti i te kaha rawa o te pūnaha ārai mate me te whakaiti i te hanga o aua paturopi hē.
• Ngā paturopi monoclonal: He pūmua hangarau koiora ēnei. Ka hoatu hei werohanga ā-uaua (IV) hei werohanga ā-kiri rānei (SQ) . Ka whakahaere i te kaha rawa o te pūnaha ārai mate.
• Whakawhiti plasma / plasmapheresis: Ka tangohia e te mīhini te plasma mai i te toto, kei roto nei ngā paturopi kino, ka whakakapia ki te plasma, ki te otinga plasma rānei mai i te kaituku.
• Immunoglobulin ā-uaua, ā-kiri rānei (IV, SQ Immunoglobulin rānei - IVIG, SCIG rānei): Ka tukuna ngā paturopi mai i ngā kaituku mā te werohanga ā-uaua (IV) mō te wā e rua ki te rima ngā rā. He maimoatanga tēnei mō te myasthenic crisis me te myasthenia gravis whānui.
• Pokanga: Ko te thymectomy te tango pokanga i te repe thymus. E taunakihia ana tēnei pokanga mō te hunga whai thymoma, me te hunga kāore he pukupuku thymus.

Tērā pea ka pā mai ētahi pānga taha ki ēnei maimoatanga katoa, nō reira me kōrero ki tō tākuta i mua i te tīmatanga o tētahi rongoā hou.

He aha taku e taea ai te mahi i te kāinga hei whakaiti i ngā tohu?

Mena kei a koe te myasthenia gravis, ngana ki te whakaiti i te ngenge me te whakanui ake i te kaha o te uaua:

• Whakakorikori tinana i ngā wā katoa: Engari i muri i te kōrero ki tō tākuta, tīmatahia he kaupapa whakakorikori tinana haumaru e pai ana ki a koe. Ka whakapakari te whakakorikori i ngā uaua, ka whakapai ake i te wairua, ā, ka hoatu he kaha ki tō tinana.
• Kaua e haere ki waho i te wā tino wera: Ka taea e te wera te whakararu i ngā tohu. Ki te tino wera koe, whakatakotoria he tauera kua rumakina ki te wai matao ki tō kaki me tō rae.
• Tāpirihia he nui o te pūmua me te warowaihā ki roto i ō kai: Ka whakaratohia e ēnei he pūngao tāpiri ki te tinana.
• Mahia ngā mahi e tino hoha ana koe i te tīmatanga o te rā: koinei te wā e tino kaha ana koe.
• Moe poto, okioki rānei i te awatea: Mā tēnei ka whai okiokinga tō tinana.

He aha te heke mai o te myasthenia gravis? (Tirohanga)

He mate ka taea te rongoā i te myasthenia gravis. Ka rerekē ngā tohu mai i te ngawari ki te kino. Ko te tikanga ka eke ngā tohu ki tōna taumata teitei i roto i te kotahi ki te toru tau o te tautuhi tuatahi.

He tokomaha te hunga e ora ora ana, e ora kaha ana i roto i te maimoatanga.

I ētahi wā ka memeha haere te mate. Ko te tikanga ka ngaro ngā tohu mō tētahi wā. He wā poto, he wā pumau rānei tēnei. Ki te puta tēnei, ka whakarerekē tō tākuta i tō mahere maimoatanga.

He maha ngā tāngata e pāngia ana e te myasthenia gravis e ora noa ana . Ka puta noa ngā pānga morearea ki te ora ina pāngia te manawa, pērā i te myasthenic crisis i kōrerohia e tātou.

Myasthenia gravis me te haputanga

He onge noa iho te puta tuatahi mai o ngā tohu myasthenia gravis i te wā e hapu ana. Mena kei a koe tēnei mate, ka kino ake pea ō tohu i te toru marama tuatahi o te haputanga, i muri rānei i te whānautanga o tō pēpi. Heoi, i ētahi wā, ka pai ake pea ō tohu i te wā e hapu ana.

Kāore ētahi maimoatanga i te haumaru i te wā e hapu ana, e whāngai ana hoki. Nō reira, he mea nui kia rapu tohutohu a tō tākuta i tēnei wā kia pai ai te hauora o te hāputanga.

Āhea ahau me toro atu ki te tākuta?

Tirohia te tākuta mēnā kei a koe ēnei tohu:

• Te tirohanga pōuri, te tirohanga takirua rānei.
• He uaua ki te haere, ki te kōrero, ki te kai rānei.
• Te ngenge nui, te ngoikore rānei o te uaua.
• Te uaua ki te manawa.

Kia maumahara, ki te uaua tō manawa, he āhuatanga ohorere tēnei! Waea atu ki te 911 (tō nama ohorere ā-rohe) tonu atu, haere rānei ki te hōhipera tata.

He aha ngā pātai me pātai atu e au ki taku tākuta?

Ka taea e koe te pātai atu ki te tākuta i ngā pātai penei:

• He aha ngā pūtake o ēnei tohu?
• He aha te kōwhiringa maimoatanga pai rawa atu mōku?
• He aha ngā pānga taha o ngā maimoatanga?
• He aha ngā huringa āhua noho me mahi e au?
• He aha ngā tohu me tirotiro e au mō ngā raruraru?
• Ka taea e au te tīmata haumaru i tētahi kaupapa whakakori tinana?
• He rōpū tautoko tūroro kei reira ka taea e au te whakauru atu?

Hei whakamutunga, ngā mea hei maumahara (Karere hei tango ki te kāinga)

He uaua te mate Myasthenia Gravis. Ahakoa e hiahia ana koe kia noho kaha tonu, tera pea ka tino ngenge koe, ka ngoikore hoki i ētahi wā. Ka pā pea tēnei ki tō hauora hinengaro me tō hauora tinana i roto i te wā.

Engari kia maumahara, ahakoa kāore he rongoā, mā te maimoatanga, he tokomaha te hunga ka taea te noho ora tonu, te ora kaha. He onge te hauātanga nui mai i te myasthenia gravis. Ka taea e tō tākuta te tohutohu i ngā huarahi hei whakahaere i ō tohumate kia ora tonu ai koe. Kaua e mataku, kaua hoki e ngana ki te whakatau i tēnei ko koe anake. Whaia ngā tohutohu a tō tākuta, ā, tikina te āwhina e hiahiatia ana e koe. Kei te hiahia ahau kia tere tō ora!

Myasthenia Gravis, Myasthenia Gravis, Ngā ngoikore o te uaua, Ngā mate pūnaha ārai mate, Acetylcholine, Repe Thymus, Hononga io-uaua