Kua kōrerotia atu rānei e tō tākuta kua paku whānui ake tō pakiaka aorta, ā, me pokanga koe? He mea noa te mataku me te manukanuka ina rongo koe i tēnā. Ko wai kāore e pai ki te kupu "pokanga ngākau"? Kaua e manukanuka. He tino matatau te hangarau i ēnei rā. I tēnei rā, ka kōrero tātou mō tētahi pokanga tino angitu, motuhake e whakaoti ana i tēnei raruraru me te kore e tango i te wāhanga tino nui o tō ngākau, arā, ko tō ake 'valve' tūturu.
He aha te whakakapinga o te pakiaka aorta e tiaki ana i te takirere?
Hei mārama ki tēnei, me titiro tuatahi tātou ki te mahi a te ngākau. Whakaarohia tō ngākau he papu wai i roto i tō whare. Ka pupuhihia e tēnei papu te toto puta noa i tō tinana.
- Aorta: Koinei te ngongo matua, te ngongo nui rawa atu e puta ana i te ngākau. Ka haria te toto ki te tinana katoa.
- Pūtake Aorta: Koinei te wāhanga tuatahi o te uaua matua e hono ana ki te ngākau. He rite ki te wāhi e hono ai koe i te ngongo ki te motuka.
- Takirere Aorta: Koinei te wāhanga tino nui o te kōrero. I te wāhi e hono ana ki te ngākau, kei reira tētahi wāhanga e mahi ana pērā i te tatau. Ina pupuhi te ngākau i te toto, ka tuwhera tēnei tatau, ka tukuna te toto ki waho. Kātahi ka kati tēnei tatau hei aukati i te toto kei hoki mai ki roto i te ngākau. Koinei te mea e kiia nei e tātou ko te `(Takirere Aorta)`.
I roto i ētahi tāngata, ka ngoikore te pūtake o tēnei uaua nui e hono ana ki te ngākau, te `(Aortic Root),` ka tīmata te pupuhi me te nui haere pērā i te poihau. Ka kiia tēnei he `(Aortic Root Aneurysm)`. Ina nui haere pēnei, kāore taua tatau, taua takirere, e kati tika. Kātahi ka tīmata te toto ki te turuturu whakamuri, `(Aortic Regurgitation)`.
I ngā wā o mua, i te wā i puta ai tēnei momo raruraru, ka tangohia e ngā taote te pūtake aorta me te takirere aorta, ā, ka whakakapia ki te pūtake aorta horihori me te takirere. Ka kiia tēnei pokanga ko te tikanga Bentall .
Inaianei, ki te mea kei te pai te āhua o tō takirere, arā, kāore i tino pakaru, hei utu mō te tango i taua takirere tūturu utu nui, ko te `(Pūtake Aorta)` kua pakaru anake ka tangohia, ka whakauruhia he ngongo horihori hou (`graft`), ā, ka honoa anō tō ake takirere ki reira. He māmā noa iho, ka kiia tēnei ko te Whakakapinga Pūtake Aorta Tiaki-Takirere .
He aha ngā āhuatanga e rongoatia ana e tēnei pokanga?
Ko te tikanga o tēnei pokanga he `(Aortic Root Aneurysm)`. Ko te tikanga tēnei ina pupuhi te pakiaka o te aorta pērā i te poihau. He mea morearea tēnei, nā te mea ki te nui atu i tētahi rohe, ka pakū (pakaru) ka haehae rānei (aortic dissection).
He mate ira honohono tō ētahi tāngata, pērā i te Marfan syndrome. He nui ake te tūponotanga o te hunga whai i ēnei mate ki te whakawhanake i te aneurysm pakiaka aorta.
Ko wai te tangata e tika ana mō tēnei pokanga?
Ka whakahaerehia e tō tākuta ngā whakamātautau maha hei whakatau mēnā he pai koe mō tēnei pokanga. I te nuinga o te wā, he pai pea koe mō tēnei pokanga.
- Mena he iti noa iho, he kore rānei he whakapūkara o tō takirere Aorta.
- Ki te kore te takirere e tino pakaru.
- Mena kei te pai te mahi a te takirere, ka taea rānei te whakatika mā te whakatikatika iti.
- He tino taunaki tēnei pokanga mō te hunga kei raro iho i te 75 tau te pakeke me te hunga he mate ira tō rātou.
Me pēhea te whakarite i mua i te pokanga?
He pokanga nui tēnei, he mea tino nui kia pai te whakarite mōna. Mā tō taote pokanga koe e hoatu he huinga tohutohu mārama mō tēnei.
- Ngā Rongoā: Me kōrero koe ki tō tākuta mō ngā rongoā katoa e tangohia ana e koe i tēnei wā. Tērā pea ka tono ia kia mutu, kia whakarerekē rānei koe i ētahi rongoā (ina koa ko ngā rongoā whakaiti toto) i mua i te pokanga.
- Nohopuku: Ka tonoa koe kia kaua e kai, e inu rānei i tetahi mea i muri i te waenganui pō i te pō i mua i te pokanga. Kaua rawa e inu wai.
- Ngā whakamātautau: Ka whakahau te tākuta i ētahi whakamātautau hei whakamahere i te pokanga.
- Echocardiogram (he matawai o te ngākau)
- Ngā whakamātautau toto
- Matawai CT kua āraia e te EKG
- MRI o te ngākau
- Angiogram Coronary
- Momi hikareti: Mena he kaipaipa koe, he mea nui kia mutu rawa te kaipaipa i te iti rawa i te kotahi marama i mua i te pokanga.
- Pātai atu: Kōrerohia mā te mahorahora ki tō tākuta mō ō āwangawanga, ō wehi rānei. He tino whakamarie te mōhio mārama ki ngā mea katoa.
Me pēhea te mahi i te pokanga?
E 4 ki te 6 hāora te roa o tēnei pokanga. Ina mahia ā-ringa e te taote pokanga mātau, ka mutu te manawa mō te wā poto, tata ki te kotahi hāora. Ko ngā mahi e whai wāhi ana ki tēnei tukanga koia ēnei.
1. Rongoā Whakamoe: Tuatahi, ka hoatu he rongoā whakamoe ki a koe kia moe hohonu ai koe. Kia kore ai koe e mamae.
2. Te whakatuwhera i te uma: Ka tapahia e te tākuta te waenganui o te uma (median sternotomy) hei uru atu ki te ngākau.
3. Mīhini ngākau-pūkahukahu: Muri iho, ka honoa koe ki tētahi mīhini ngākau-pūkahukahu (mīhini karo manawa). Mā tēnei mīhini e mahi te mahi a tō ngākau me ō pūkahukahu i te wā o te pokanga. Ka hoatu hoki he rongoā ki a koe hei aukati i tō ngākau mō tētahi wā poto.
4. Te wehenga o te takirere: Ka wehea marietia e te taote tō takirere aorta mai i te kiko e karapoti ana.
5. Whakatikatika:Mena he iti noa te pakaru o ngā taupoki takirere, ka whakatikahia tonutia.
6. Te tango i te wāhanga pakaru: Ka tapahia, ka tangohia te wāhanga pupuhi me te pakaru o te `(Aortic Root)`.
7. Te whakatō ngongo horihori: Engari, ka tangohia he "tāpiri" ngongo horihori i hangaia ki tētahi papanga motuhake, ka hangaia ki te rahi e tika ana māu, kātahi ka whakatōkia ki taua wāhi.
8. Te tāpiri anō i te takirere: Kātahi ka whakanohoia tō ake takirere tūturu , i tangohia marietia, ki roto i te ngongo hou kua whakatōkia, ā, ka tuia anō kia honoa (whakatōngia anō).
9. Te Tirotiro: Tirohia mēnā kei te pai ngā mea katoa, mēnā kei te tika te whakatuwheratanga me te kati o te takirere, me mēnā kei te turuturu.
10. Te Katinga: Kātahi ka honoa ngā uaua o te ngakau e tuku toto ana ki te ngākau ki te poka hou. Ka tangohia koe i te mīhini ngākau-pūkahukahu, ā, ina tīmata anō te mahi a tō ngākau, ka katia te tapahi i tō uma.
11. Tirotiro whakamutunga: I mua i te tangohia i te rūma pokanga, ka mahia he "transesophageal echocardiogram" hei whakaū i te angitu o te pokanga.
Ngā whakapainga hou i roto i te pokanga
I roto i ngā wā, kua tāpirihia e ngā tākuta ētahi tikanga hou kia angitu ake ai tēnei pokanga.
- Te whakaiti i te annulus: Ki te kī māmā, ka pēhia te turanga e pupuri ana i te takirere (aortic annulus) kia uru ki tō tinana. Mā tēnei ka ārai i te toto kei turuturu mai i te takirere ā muri ake nei.
- Te Waihanga i ngā Sinuse Aorta Hou (Nēosinus): He iti noa ngā wiri o te pūtake o te aorta tūturu. Nā te mea he ngongo tika te hononga hou, ka hangaia hoki he wiri iti. Mā tēnei ka rere noa te toto, ka whakaitihia hoki te kino ki ngā rau takirere.
He aha ngā painga o tēnei pokanga?
He maha ngā painga nui o tēnei pokanga i runga i te pokanga Bentall tuku iho (arā, me whakakapi te takirere me te takirere).
| Painga | Pokanga Tiaki-Taurere | Pokanga Bentall (me te takirere miihini) |
|---|---|---|
| Ngā rongoā whakaheke toto mō te wā roa | Kāore koe e hiahia ki te tango. | Me tango ngā rongoā pēnei i te Coumadin (Warfarin) mō te wā katoa. |
| Ngā toto totoka, te mōrearea o te whiu | Tino iti . | He nui ake te hiranga . |
| Te mōrearea o te mate takirere (endocarditis) | Tino iti . | Nui rawa . |
| Te hiahia mō te pokanga whakakapinga takirere | He tino iti . Kāore e hiahiatia ana e te 95% o te tangata mō ngā tau 10. | Tērā pea ka hiahiatia i roto i te wā. |
Kia pēhea te roa o te wā e ora ai i muri i te pokanga?
I muri i te pokanga, ka puritia koe ki te wāhanga tiaki nui (ICU) mō te rā kotahi, e rua rānei, kātahi ka whakawhitia ki te wāhanga noa. I te nuinga o te wā ka taea e koe te hoki ki te kāinga i te hōhipera i roto i ngā rā e 4 ki te 7.
E ono wiki pea te roa hei whakaora katoa i a koe, hei hoki anō ki ngā mahi o ia rā.
I tēnei wā,
- He whakaaro pai te whai wāhi atu ki tētahi kaupapa whakaora ngākau . Ka āwhina i a koe kia tere ake te ora, kia kaha ake hoki.
- E ai ki te tākuta kia kaua e mahi i tetahi mea pēnei i te hiki taumaha, te taraiwa rānei mō te ono wiki.
- Ngā wā tirotiro ā muri ake nei: Kāore pea koe e whakaaro me toro atu anō koe ki tō tākuta i muri i tō oranga ake. Engari he mea nui kia pērā tonu . He mea nui kia tirotirohia tonutia tō āhua ngākau.
Āhea te waea atu ki te tākuta tonu
I muri i te hokinga ki te kāinga, ki te puta mai tētahi o ngā tohu e whai ake nei i a koe, waea atu ki tō tākuta tonu atu , haere rānei ki te Tari Ohotata (ETU) o te hōhipera tata.
| Tohu | He aha ngā mea hei aro atu |
|---|---|
| Ngā huringa o te ara tapahi | Te whero, te pupuhi, te mamae nui, te mahana, me te pupuhi kōwhai, kākāriki rānei huri noa i te wāhi i tapahia. |
| Mamae o te uma | Te mamae ohorere, te mamae nui rānei o te uma. |
| Te uaua ki te manawa | Te poto ohorere o te manawa. |
| Pupuhi waewae | Te pupuhi o ngā waewae, te kore rānei e taea te neke i ngā waewae. |
| Pōuriuri, ngoikore rānei | Te whanoke nui, te ngoikore, te ngenge nui rānei. |
| Te kirika, te makariri rānei | He kirika me te makariri, he rerenga hūpē kōwhai, kākāriki rānei. |
He mea noa te mataku i mua i tētahi pokanga nui. Engari kia mahara, ko tēnei pokanga e mahia ana hei whakaora i tō oranga, hei āwhina hoki i a koe kia noho hauora mō te wā roa. Kōrero ki tō whānau me ō hoa mō tēnei. He kaha nui tō rātou tautoko ki a koe i tēnei wā.
Karere Tangohia ki te Kāinga
- Ko te Whakakapinga Pūtake Aorta e Tiaki Ana i te Valve he pokanga matatau e whakaora ana i tō takirere aorta tūturu, e rongoā ana hoki i te whakawhānui o te pūtake aorta.
- Ko te painga nui o tēnei, kāore koe e hiahia ki te tango i ngā rongoā whakaiti toto mō te toenga o tō oranga, pērā i tāu e mahi ai me te takirere miihini.
- Ka taea te mahi i tēnei pokanga i raro i te tirotiro a tētahi taote pokanga mātau i roto i tētahi hōhipera he pai ngā ratonga, ā, he tino teitei te angitu (neke atu i te 99%).
- E ono wiki pea te roa hei whakaora katoa i te pokanga. I taua wā, he mea tino nui te whai i ngā tohutohu a te tākuta.
- Kaua e wehi ki te kōrero ki tō tākuta mō ngā pātai, ngā āwangawanga rānei kei a koe. He kaha nui tēnei māu kia tino mōhio koe i mua i te haerenga ki te pokanga.











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