ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛ ꯅꯠꯠꯔꯒꯥ ꯅꯍꯥꯛꯀꯤ ꯏꯃꯨꯡꯒꯤ ꯃꯤꯑꯣꯏ ꯑꯃꯅꯥ ꯀꯣꯟꯖꯤꯅꯤꯑꯦꯜ ꯑꯦꯗ꯭ꯔꯤꯅꯜ ꯍꯥꯏꯄꯔꯞꯂꯥꯁꯤꯌꯥ (CAH) ꯀꯧꯕꯥ ꯀꯟꯗꯤꯁꯟ ꯑꯃꯥ ꯂꯩꯔꯕꯗꯤ, ꯃꯁꯤ ꯅꯍꯥꯛꯀꯤꯗꯃꯛꯇꯥ ꯌꯥꯝꯅꯥ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯄꯥꯎ ꯑꯃꯥ ꯑꯣꯏꯒꯅꯤ꯫ ꯆꯍꯤ ꯷꯰ꯒꯤ ꯃꯇꯨꯡꯗꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤꯒꯤꯗꯃꯛꯇꯥ ꯑꯈꯟꯅꯅꯥ ꯑꯅꯧꯕꯥ ꯂꯥꯌꯦꯡ ꯑꯃꯥ ꯍꯧꯖꯤꯛ ꯑꯌꯥꯕꯥ ꯄꯤꯈ꯭ꯔꯦ꯫ ꯃꯁꯤ ꯇꯁꯦꯡꯅꯥ ꯁꯤ.ꯑꯦ.ꯑꯩꯆ.ꯒꯥ ꯂꯣꯌꯅꯅꯥ ꯍꯤꯡꯂꯤꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡꯒꯤꯗꯃꯛ ꯑꯆꯧꯕꯥ ꯑꯥꯁꯥ ꯑꯃꯅꯤ꯫ ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯑꯅꯧꯕꯥ ꯍꯤꯗꯥꯛ ꯑꯁꯤ ꯀꯔꯤꯅꯣ, ꯃꯁꯤꯅꯥ ꯀꯔꯝꯅꯥ ꯊꯕꯛ ꯇꯧꯕꯒꯦ ꯑꯃꯁꯨꯡ ꯃꯁꯤꯒꯤ ꯀꯥꯟꯅꯕꯁꯤꯡ ꯑꯁꯤ ꯀꯔꯤꯅꯣ ꯍꯥꯌꯕꯗꯨ ꯌꯦꯡꯁꯤ꯫
ꯑꯍꯥꯅꯕꯗꯥ, ꯈꯉꯂꯁꯤ, ꯁꯤ.ꯑꯦ.ꯑꯩꯆ.
ꯌꯥꯝꯅꯥ ꯂꯥꯏꯅꯥ ꯍꯥꯌꯔꯕꯗꯥ, ꯁꯤ.ꯑꯦ.ꯑꯩꯆ.ꯅꯥ ꯑꯩꯈꯣꯌꯒꯤ ꯑꯦꯗ꯭ꯔꯤꯅꯜ ꯒ꯭ꯜꯌꯥꯟꯗꯁꯤꯡꯗꯥ ꯁꯣꯀꯍꯜꯂꯤꯕꯥ ꯖꯦꯅꯦꯇꯤꯛ ꯂꯥꯌꯅꯥ ꯑꯃꯅꯤ꯫ ꯍꯥꯌꯔꯤꯕꯥ ꯒ꯭ꯜꯌꯥꯟꯗꯁꯤꯡ ꯑꯁꯤ ꯑꯩꯈꯣꯌꯒꯤ ꯀꯤꯗꯅꯤꯒꯤ ꯃꯊꯛꯇꯥ ꯂꯩ꯫ ꯃꯈꯣꯌꯅꯥ ꯑꯩꯈꯣꯌꯒꯤ ꯍꯀꯆꯥꯡꯗꯥ ꯇꯉꯥꯏꯐꯗꯕꯥ ꯍꯣꯔꯃꯣꯟ ꯀꯌꯥ ꯄꯨꯊꯣꯀꯏ꯫
ꯑꯦꯗ꯭ꯔꯤꯅꯜ ꯒ꯭ꯜꯌꯥꯟꯗ ꯑꯁꯤ ꯐꯦꯛꯇꯔꯤ ꯑꯃꯥ ꯑꯣꯏꯅꯥ ꯈꯅꯕꯤꯌꯨ꯫ ꯐꯦꯛꯇꯔꯤ ꯑꯁꯤꯒꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯄꯣꯠꯊꯣꯛ ꯑꯁꯤ ꯀꯣꯔꯇꯤꯁꯣꯜ ꯀꯧꯕꯥ ꯍꯣꯔꯃꯣꯟ ꯑꯃꯅꯤ꯫ ꯃꯁꯤ ꯑꯩꯈꯣꯌꯒꯤ ꯍꯀꯆꯥꯡꯗꯥ ꯁ꯭ꯠꯔꯦꯁ, ꯑꯅꯥꯕꯥ ꯑꯃꯁꯨꯡ ꯈꯨꯗꯣꯡꯊꯤꯕꯥ ꯊꯦꯡꯅꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯂꯤꯕꯥ ꯌꯥꯝꯅꯥ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯍꯣꯔꯃꯣꯟ ꯑꯃꯅꯤ꯫
ꯍꯀꯁꯦꯜ ꯐꯕꯥ ꯃꯤꯑꯣꯏ ꯑꯃꯗꯥ ꯀꯣꯔꯇꯤꯁꯣꯂꯒꯤ ꯆꯥꯡ ꯍꯟꯊꯔꯀꯄꯥ ꯃꯇꯃꯗꯥ, ꯕ꯭ꯔꯦꯟ (ꯐꯦꯛꯇꯔꯤ ꯃꯦꯅꯦꯖꯔ ꯑꯃꯒꯨꯝꯅꯥ)ꯅꯥ "ꯀꯣꯔꯇꯤꯁꯣꯜ ꯁꯦꯝꯅꯕꯥ" ꯑꯦꯗ꯭ꯔꯤꯅꯜ ꯒ꯭ꯜꯌꯥꯟꯗꯇꯥ ACTH ꯀꯧꯕꯥ ꯁꯤꯒꯅꯦꯜ (ꯑꯣꯔꯗꯔ) ꯑꯃꯥ ꯊꯥꯏ꯫ ꯑꯗꯨꯕꯨ CAH ꯂꯩꯕꯥ ꯃꯤꯑꯣꯏ ꯑꯃꯗꯥ, ꯑꯦꯗ꯭ꯔꯤꯅꯜ ꯒ꯭ꯜꯌꯥꯟꯗꯇꯥ ꯀꯣꯔꯇꯤꯁꯣꯜ ꯁꯦꯝꯕꯗꯥ ꯃꯊꯧ ꯇꯥꯕꯥ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯑꯦꯅꯖꯥꯏꯝ ꯑꯃꯥ ꯅꯠꯠꯔꯒꯥ ‘ꯋꯥꯔꯀꯔ’ ꯑꯃꯥ ꯂꯩꯇꯦ꯫ ꯑꯗꯨꯅꯥ ꯕ꯭ꯔꯦꯅꯅꯥ ꯀꯌꯥ ꯌꯥꯝꯅꯥ ACTH ꯊꯥꯔꯕꯁꯨ ꯐꯦꯛꯇꯔꯤ ꯑꯁꯤꯅꯥ ꯀꯣꯔꯇꯤꯁꯣꯜ ꯁꯦꯝꯕꯥ ꯉꯃꯗꯦ꯫
ꯃꯁꯤꯅꯥ ꯋꯥꯍꯪ ꯑꯅꯤ ꯊꯣꯔꯀꯏ:
1. ꯍꯀꯆꯥꯡꯅꯥ ꯃꯊꯧ ꯇꯥꯕꯥ ꯀꯣꯔꯇꯤꯁꯣꯜ ꯄꯨꯊꯣꯀꯄꯥ ꯉꯃꯗꯦ .
2. ꯕ꯭ꯔꯦꯅꯗꯒꯤ ACTH ꯁꯤꯒꯅꯦꯂꯁꯤꯡ ꯃꯈꯥ ꯇꯥꯅꯥ ꯆꯠꯊꯔꯀꯄꯒꯥ ꯂꯣꯌꯅꯅꯥ, ꯑꯦꯗ꯭ꯔꯤꯅꯜ ꯒ꯭ꯜꯌꯥꯟꯗꯅꯥ ꯄꯨꯊꯣꯀꯄꯥ ꯑꯇꯣꯞꯄꯥ ꯃꯈꯜ ꯑꯃꯒꯤ ꯍꯣꯔꯃꯣꯟ , ꯑꯦꯟꯗ꯭ꯔꯣꯖꯦꯟ ꯀꯧꯕꯥ, ꯑꯍꯦꯅꯕꯥ ꯄꯨꯊꯣꯀꯏ꯫
ꯍꯥꯌꯔꯤꯕꯥ ꯑꯦꯟꯗ꯭ꯔꯣꯖꯦꯅꯁꯤꯡ ꯑꯁꯤ (ꯈꯨꯗꯝ ꯑꯣꯏꯅꯥ ꯇꯦꯁ꯭ꯇꯣꯁ꯭ꯇꯦꯔꯣꯟ) ꯑꯁꯤ ꯅꯨꯄꯥꯒꯤ ꯍꯣꯔꯃꯣꯅꯁꯤꯡꯅꯤ꯫ ꯅꯨꯄꯥ ꯑꯃꯁꯨꯡ ꯅꯨꯄꯤ ꯑꯅꯤꯃꯛꯅꯥ ꯃꯈꯣꯌ ꯈꯔꯗꯤ ꯃꯊꯧ ꯇꯥꯏ, ꯑꯗꯨꯕꯨ ꯁꯤ.ꯑꯦ.ꯑꯩꯆ.ꯗꯥ ꯃꯈꯣꯌ ꯌꯥꯝꯅꯥ ꯋꯥꯡꯏ꯫ ꯃꯁꯤꯅꯥ ꯑꯉꯥꯡ ꯑꯃꯒꯤ ꯗꯤꯚꯦꯂꯄꯃꯦꯟꯇꯗꯥ ꯉꯟꯅꯥ ꯃꯤꯔꯣꯅꯕꯥ, ꯃꯤꯔꯣꯅꯕꯥ ꯑꯃꯁꯨꯡ ꯑꯇꯩ ꯄ꯭ꯔꯣꯕ꯭ꯂꯦꯃꯁꯤꯡ ꯊꯣꯀꯍꯅꯕꯥ ꯌꯥꯏ .
ꯆꯍꯤ ꯇꯔꯥꯒꯤ ꯈꯨꯖꯤꯡ ꯀꯌꯥꯗꯒꯤ ꯃꯁꯤꯒꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯂꯥꯏꯌꯦꯡ ꯑꯁꯤ ꯃꯄꯥꯟꯗꯥ ꯀꯣꯔꯇꯤꯁꯣꯂꯒꯨꯝꯅꯥ ꯊꯕꯛ ꯇꯧꯕꯥ ꯁ꯭ꯇꯦꯔꯣꯏꯗꯁꯤꯡ (ꯒ꯭ꯂꯨꯀꯣꯀꯣꯔꯇꯤꯀꯣꯏꯗꯁꯤꯡ) ꯄꯤꯕꯅꯤ꯫ ꯃꯁꯤꯅꯥ ꯍꯀꯆꯥꯡꯗꯥ ꯂꯩꯇꯕꯥ ꯀꯣꯔꯇꯤꯁꯣꯂꯒꯤ ꯃꯍꯨꯠ ꯁꯤꯅꯕꯇꯥ ꯅꯠꯇꯅꯥ ꯕ꯭ꯔꯦꯅꯗꯒꯤ ꯂꯥꯀꯄꯥ ACTH ꯁꯤꯒꯅꯦꯜ ꯑꯗꯨꯁꯨ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯗꯨꯅꯥ ꯑꯦꯟꯗ꯭ꯔꯣꯖꯦꯅꯁꯤꯡ ꯄꯨꯊꯣꯀꯄꯥ ꯍꯟꯊꯍꯜꯂꯤ꯫ ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ, ꯄ꯭ꯔꯣꯕ꯭ꯂꯦꯝ ꯑꯁꯤꯗꯤ ꯃꯁꯤꯅꯥ ꯃꯇꯝ ꯁꯥꯡꯅꯥ ꯅꯣꯔꯃꯦꯂꯗꯒꯤ ꯍꯦꯟꯅꯥ ꯁ꯭ꯇꯦꯔꯣꯏꯗꯀꯤ ꯗꯣꯖ ꯍꯦꯟꯅꯥ ꯂꯧꯕꯥ ꯃꯊꯧ ꯇꯥꯏ꯫ ꯃꯁꯤꯅꯥ ꯁꯥꯏꯗ ꯏꯐꯦꯛꯇ ꯀꯌꯥ ꯊꯣꯀꯍꯅꯕꯥ ꯌꯥꯏ, ꯃꯈꯣꯌ ꯑꯗꯨꯗꯤ ꯑꯔꯨꯝꯕꯥ ꯍꯦꯅꯒꯠꯂꯀꯄꯥ, ꯁꯔꯨ ꯇꯥꯡꯁꯤꯡ ꯁꯣꯀꯄꯥ, ꯑꯃꯁꯨꯡ ꯇꯨꯝꯕꯥ ꯉꯃꯗꯕꯥ .
ꯑꯅꯧꯕꯥ ꯍꯤꯗꯥꯛ ꯑꯁꯤ ꯀꯔꯝꯅꯥ ꯐꯪꯈꯤꯕꯒꯦ?
ꯁꯥꯏꯟꯇꯤꯁ꯭ꯇꯁꯤꯡꯅꯥ ꯁ꯭ꯇꯦꯔꯣꯏꯗꯀꯤ ꯁꯃꯁ꯭ꯌꯥ ꯑꯁꯤꯒꯤ ꯑꯇꯣꯞꯄꯥ ꯁꯣꯂꯨꯁꯟ ꯑꯃꯥ ꯂꯩꯕꯔꯥ ꯍꯥꯌꯅꯥ ꯈꯅꯈꯤ꯫ ꯃꯄꯥꯟꯗꯥ ꯁ꯭ꯇꯦꯔꯣꯏꯗ ꯀꯌꯥ ꯄꯤꯕꯒꯤ ꯃꯍꯨꯠꯇꯥ, ꯀꯔꯤꯒꯨꯝꯕꯥ ꯑꯩꯈꯣꯌꯅꯥ ꯕ꯭ꯔꯦꯅꯗꯒꯤ ꯂꯥꯀꯄꯥ ꯑꯦ.ꯁꯤ.ꯇꯤ.ꯑꯩꯆ.
ꯃꯐꯝ ꯑꯗꯨꯗꯥ ꯃꯈꯣꯌꯅꯥ ꯑꯅꯧꯕꯥ ꯄꯥꯟꯗꯝ ꯑꯃꯥ ꯐꯪꯈꯤ꯫ ꯃꯁꯤ ꯕ꯭ꯔꯦꯅꯗꯥ ꯂꯩꯕꯥ ꯁꯤ.ꯑꯥꯔ.ꯑꯦꯐ.꯱ ꯀꯧꯕꯥ ꯔꯤꯁꯦꯄꯇꯔ ꯑꯃꯅꯤ꯫ ꯀꯣꯔꯇꯤꯁꯣꯂꯒꯤ ꯆꯥꯡ ꯍꯟꯊꯔꯀꯄꯥ ꯃꯇꯃꯗꯥ, ACTH ꯁꯤꯒꯅꯦꯜ ꯑꯁꯤ CRF1ꯅꯥ ꯊꯣꯀꯍꯜꯂꯤ꯫ ꯁꯤ.ꯑꯦ.ꯑꯩꯆ.ꯗꯥ ꯃꯁꯤꯒꯤ ꯊꯧꯑꯣꯡ ꯑꯁꯤ ꯁꯣꯀꯍꯜꯂꯤ꯫
ꯑꯗꯨꯅꯥ ꯁꯥꯏꯟꯇꯤꯁ꯭ꯇꯁꯤꯡꯅꯥ ꯈꯜꯂꯃꯈꯤ, ꯀꯔꯤꯒꯨꯝꯕꯥ ꯑꯩꯈꯣꯌꯅꯥ ꯁꯤ.ꯑꯥꯔ.ꯑꯦꯐ.꯱ ꯑꯁꯤ ꯕ꯭ꯂꯣꯛ ꯇꯧꯔꯕꯗꯤ ꯑꯩꯈꯣꯌꯅꯥ ꯑꯦ.ꯁꯤ.ꯇꯤ.ꯑꯩꯆ. ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯗꯨ ꯑꯣꯏꯔꯕꯗꯤ ꯑꯦꯟꯗ꯭ꯔꯣꯖꯦꯅꯁꯤꯡ ꯄꯨꯊꯣꯀꯄꯁꯨ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯒꯅꯤ, ꯑꯃꯁꯨꯡ ꯑꯅꯥꯕꯥ ꯑꯗꯨꯅꯥ ꯂꯧꯕꯥ ꯃꯊꯧ ꯇꯥꯕꯥ ꯁ꯭ꯇꯦꯔꯣꯏꯗꯀꯤ ꯗꯣꯖꯁꯨ ꯍꯟꯊꯔꯒꯅꯤ꯫
ꯃꯁꯤꯒꯤ ꯑꯅꯧꯕꯥ ꯋꯥꯈꯜꯂꯣꯟ ꯑꯁꯤꯅꯥ ꯀ꯭ꯔꯤꯅꯦꯁꯦꯔꯐꯣꯟꯇ ꯀꯧꯕꯥ ꯑꯅꯧꯕꯥ ꯗ꯭ꯔꯒ ꯑꯃꯥ ꯄꯨꯊꯣꯀꯄꯅꯤ꯫ ꯃꯁꯤ ꯁꯤ.ꯑꯥꯔ.ꯑꯦꯐ.꯱ ꯕ꯭ꯂꯣꯛ ꯇꯧꯗꯨꯅꯥ ꯁꯤ.ꯑꯦ.ꯑꯩꯆ.ꯒꯤ ꯐꯟꯗꯥꯃꯦꯟꯇꯦꯜ ꯄ꯭ꯔꯣꯕ꯭ꯂꯦꯝ ꯑꯃꯥ ꯀꯣꯀꯍꯟꯅꯕꯥ ꯗꯤꯖꯥꯏꯟ ꯇꯧꯕꯥ ꯗ꯭ꯔꯒ ꯑꯃꯅꯤ꯫
ꯃꯤꯑꯣꯏꯕꯗꯥ ꯍꯤꯗꯥꯛ ꯑꯃꯥ ꯄꯤꯗ꯭ꯔꯤꯉꯩꯗꯥ ꯇꯧꯕꯥ ꯇꯦꯁ꯭ꯇꯁꯤꯡ꯫
ꯑꯅꯧꯕꯥ ꯍꯤꯗꯥꯛ ꯑꯃꯥ ꯈꯉꯗꯣꯀꯄꯥ ꯃꯇꯃꯗꯥ ꯃꯤꯑꯣꯏꯕꯗꯥ ꯄꯤꯕꯥ ꯉꯃꯗꯦ꯫ ꯃꯁꯤ ꯁꯥꯐꯕꯥ ꯑꯃꯁꯨꯡ ꯏꯐꯦꯛꯇꯤꯕ ꯑꯣꯏꯕꯔꯥ ꯍꯥꯌꯕꯗꯨ ꯀꯅꯐꯔꯝ ꯇꯧꯅꯕꯥ ꯇꯦꯁ꯭ꯠ ꯀꯌꯥ ꯑꯃꯥ ꯄꯥꯡꯊꯣꯀꯄꯥ ꯃꯊꯧ ꯇꯥꯏ꯫ ꯀ꯭ꯔꯤꯅꯦꯁꯔꯐꯣꯟꯇ ꯗ꯭ꯔꯒ ꯑꯁꯤꯅꯥ ꯈꯣꯡꯊꯥꯡ ꯄꯨꯝꯅꯃꯛ ꯑꯁꯤ ꯆꯠꯈꯤ꯫
1. ꯂꯦꯕꯣꯔꯦꯇꯔꯤ ꯑꯃꯁꯨꯡ ꯑꯦꯅꯤꯃꯦꯜ ꯇꯦꯁ꯭ꯠ ꯇꯧꯕꯥ: ꯑꯍꯥꯅꯕꯥ ꯈꯣꯡꯊꯥꯡꯗꯤ ꯂꯦꯕꯣꯔꯦꯇꯔꯤꯗꯥ ꯂꯩꯕꯥ ꯁꯦꯂꯁꯤꯡ ꯑꯃꯁꯨꯡ ꯁꯥꯁꯤꯡꯗꯥ ꯗ꯭ꯔꯒ ꯑꯁꯤ ꯇꯦꯁ꯭ꯠ ꯇꯧꯕꯅꯤ꯫ ꯃꯁꯤ ꯗ꯭ꯔꯒ ꯑꯗꯨ ꯇꯣꯛꯁꯤꯀꯦꯜ ꯑꯣꯏꯕ꯭ꯔꯥ ꯅꯠꯠꯔꯒꯥ ꯑꯣꯔꯒꯥꯅꯁꯤꯡꯗꯥ ꯑꯀꯥꯌꯕꯥ ꯄꯤꯕ꯭ꯔꯥ ꯍꯥꯌꯕꯗꯨ ꯈꯪꯗꯣꯛꯅꯕꯒꯤꯗꯃꯛꯇꯅꯤ꯫ ꯈꯟꯗꯨꯅꯥ ꯌꯦꯡꯕꯤꯌꯨ, ꯑꯅꯧꯕꯥ ꯗ꯭ꯔꯒ ꯱꯰,꯰꯰꯰ꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯆꯥꯎꯔꯥꯛꯅꯥ ꯑꯃꯈꯛꯇꯅꯥ ꯑꯋꯥꯠꯄꯥ ꯄꯨꯝꯅꯃꯛ ꯑꯁꯤ ꯂꯥꯟꯊꯣꯀꯏ ꯑꯃꯁꯨꯡ ꯑꯌꯥꯕꯥ ꯄꯤꯔꯤ꯫
2. ꯀ꯭ꯂꯤꯅꯤꯀꯦꯜ ꯇ꯭ꯔꯥꯏꯑꯦꯜ: ꯑꯦꯅꯤꯃꯦꯜ ꯇꯦꯁ꯭ꯠ ꯇꯧꯕꯥ ꯃꯥꯌ ꯄꯥꯛꯂꯕꯥ ꯃꯇꯨꯡꯗꯥ ꯃꯤꯑꯣꯏꯕꯒꯤ ꯇ꯭ꯔꯥꯏꯑꯦꯜ ꯑꯁꯤ ꯁ꯭ꯇꯦꯖ ꯀꯌꯥꯗꯥ ꯄꯥꯡꯊꯣꯀꯏ꯫
ꯀ꯭ꯔꯤꯅꯦꯁꯔꯐꯣꯟꯇꯀꯤ ꯇꯦꯁ꯭ꯇꯀꯤ ꯔꯤꯖꯜꯇꯁꯤꯡ ꯑꯁꯤ ꯀꯔꯝꯅꯥ ꯑꯣꯏꯔꯤꯕꯒꯦ?
ꯗ꯭ꯔꯒ ꯑꯁꯤꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯄꯥꯡꯊꯣꯀꯈꯤꯕꯥ ꯇ꯭ꯔꯥꯏꯑꯦꯂꯁꯤꯡ ꯑꯁꯤꯅꯥ ꯌꯥꯝꯅꯥ ꯐꯕꯥ ꯐꯂꯁꯤꯡ ꯐꯪꯂꯦ꯫ ꯃꯔꯨꯑꯣꯏꯅꯥ ꯐꯦꯖ II & ꯐꯦꯖ III ꯇ꯭ꯔꯥꯏꯑꯦꯂꯁꯤꯡ ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯃꯔꯨꯑꯣꯏ꯫
ꯐꯦꯖ II - ꯅꯍꯥ ꯑꯣꯏꯔꯤꯕꯥ ꯑꯉꯥꯡꯁꯤꯡꯒꯤ ꯔꯤꯖꯜꯇ꯫
ꯃꯐꯝ ꯑꯁꯤꯗꯥ, ꯁꯤ.ꯑꯦ.ꯑꯩꯆ.ꯅꯥ ꯅꯥꯕꯥ ꯅꯍꯥ ꯑꯣꯏꯔꯤꯕꯥ ꯑꯉꯥꯡꯁꯤꯡ (ꯆꯍꯤ ꯱꯴-꯱꯷)ꯒꯤ ꯑꯄꯤꯀꯄꯥ ꯀꯥꯡꯂꯨꯞ ꯑꯃꯗꯥ ꯅꯨꯃꯤꯠ ꯱꯴ꯅꯤꯒꯤ ꯑꯣꯏꯅꯥ ꯗ꯭ꯔꯒ ꯑꯁꯤ ꯄꯤꯈꯤ ꯑꯃꯁꯨꯡ ꯃꯈꯣꯌꯒꯤ ꯍꯣꯔꯃꯣꯅꯒꯤ ꯆꯥꯡꯗꯥ ꯑꯍꯣꯡꯕꯥ ꯂꯥꯀꯄꯥ ꯎꯕꯥ ꯐꯪꯈꯤ꯫ ꯃꯁꯤꯒꯤ ꯐꯂꯁꯤꯡ ꯑꯁꯤ ꯑꯉꯀꯄꯥ ꯑꯣꯏꯈꯤ꯫
- ꯑꯦ.ꯁꯤ.ꯇꯤ.ꯑꯩꯆ.(ꯕ꯭ꯔꯦꯟ ꯁꯤꯒꯅꯦꯜ) ꯑꯁꯤ ꯵꯷% ꯍꯟꯊꯈꯤ꯫
- ꯱꯷-ꯑꯣ.ꯑꯩꯆ.ꯄꯤ.(ꯑꯦꯟꯗ꯭ꯔꯣꯖꯦꯟ ꯄꯨꯊꯣꯀꯄꯒꯤ ꯏꯟꯗꯤꯀꯦꯇꯔ ꯑꯃꯥ) ꯑꯁꯤ ꯶꯹% ꯍꯟꯊꯈꯤ .
- ꯑꯦꯟꯗ꯭ꯔꯣꯁ꯭ꯇꯦꯅꯗꯤꯑꯣꯟ (ꯑꯦꯟꯗ꯭ꯔꯣꯖꯦꯟ ꯃꯈꯜ ꯑꯃꯥ) ꯑꯁꯤ ꯵꯸% ꯍꯟꯊꯈꯤ .
ꯐꯦꯖ III - ꯑꯆꯧꯕꯥ ꯀꯥꯡꯂꯨꯄꯁꯤꯡꯒꯤ ꯔꯤꯖꯜꯇꯁꯤꯡ꯫
ꯃꯁꯤꯒꯤ ꯐꯂꯁꯤꯡ ꯑꯁꯤꯅꯥ ꯄꯨꯛꯅꯤꯡ ꯊꯧꯒꯠꯂꯗꯨꯅꯥ ꯁꯥꯏꯟꯇꯤꯁ꯭ꯇꯁꯤꯡꯅꯥ ꯑꯍꯂꯁꯤꯡ ꯑꯃꯁꯨꯡ ꯑꯉꯥꯡꯁꯤꯡ ꯁꯤꯖꯤꯟꯅꯗꯨꯅꯥ ꯑꯆꯧꯕꯥ ꯇ꯭ꯔꯥꯏꯑꯦꯜ ꯑꯅꯤ ꯄꯥꯡꯊꯣꯀꯈꯤ, ꯃꯐꯝ ꯑꯗꯨꯗꯥ ꯈꯔꯗꯥ ꯗ꯭ꯔꯒ ꯀ꯭ꯔꯤꯅꯦꯁꯔꯐꯣꯟꯇ ꯄꯤꯈꯤ ꯑꯃꯁꯨꯡ ꯑꯇꯣꯞꯄꯥ ꯈꯔꯗꯥ ꯗ꯭ꯔꯒ ꯑꯃꯥ ꯑꯣꯏꯅꯥ ꯎꯕꯥ ꯑꯗꯨꯕꯨ ꯏꯐꯦꯛꯇ ꯑꯃꯠꯇꯥ ꯂꯩꯇꯕꯥ ꯄ꯭ꯂꯦꯁꯦꯕꯣ ꯑꯃꯥ ꯄꯤꯈꯤ꯫
| ꯀꯥꯉꯕꯨ | ꯃꯔꯨꯑꯣꯏꯕꯥ ꯐꯜ꯫ | ꯋꯥꯔꯣꯜ |
|---|---|---|
| ꯑꯍꯜ ꯑꯣꯏꯔꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡ (ꯀ꯭ꯔꯤꯅꯦꯁꯔꯐꯣꯟꯇ ꯂꯧꯕꯥ) | ꯁ꯭ꯇꯦꯔꯣꯏꯗꯀꯤ ꯗꯣꯖ ꯍꯟꯊꯍꯅꯕꯥ꯫ | ꯍꯣꯔꯃꯣꯅꯒꯤ ꯆꯥꯡ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯗꯨꯅꯥ ꯅꯣꯡꯃꯗꯥ ꯁ꯭ꯇꯦꯔꯣꯏꯗꯀꯤ ꯗꯣꯖ ꯲꯷% ꯍꯟꯊꯍꯅꯕꯥ ꯉꯃꯈꯤ꯫ |
| ꯑꯦꯗꯜꯇ (ꯄ꯭ꯂꯦꯁꯦꯕꯣ ꯂꯧꯈꯤꯕꯥ) | ꯁ꯭ꯇꯦꯔꯣꯏꯗꯀꯤ ꯗꯣꯖ ꯍꯟꯊꯍꯅꯕꯥ꯫ | ꯁ꯭ꯇꯦꯔꯣꯏꯗꯀꯤ ꯗꯣꯖ ꯑꯁꯤ ꯱꯰% ꯈꯛꯇꯃꯛ ꯍꯟꯊꯈꯤ꯫ |
| ꯑꯉꯥꯡꯁꯤꯡ (ꯀ꯭ꯔꯤꯅꯦꯁꯔꯐꯣꯟꯇ ꯂꯧꯕꯥ) | ꯑꯦꯟꯗ꯭ꯔꯣꯖꯦꯅꯒꯤ ꯆꯥꯡ ꯑꯃꯁꯨꯡ ꯁ꯭ꯇꯦꯔꯣꯏꯗꯀꯤ ꯆꯥꯡ꯫ | ꯅꯨꯃꯤꯠ 4ꯅꯤꯒꯤ ꯃꯇꯨꯡꯗꯥ ꯑꯦꯟꯗ꯭ꯔꯣꯖꯦꯅꯒꯤ ꯆꯥꯡ ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯍꯟꯊꯈꯤ꯫ ꯇ꯭ꯔꯥꯏꯑꯦꯜ ꯑꯁꯤꯒꯤ ꯑꯔꯣꯏꯕꯗꯥ ꯁ꯭ꯇꯦꯔꯣꯏꯗꯀꯤ ꯗꯣꯖ ꯑꯁꯤ ꯱꯸% ꯍꯟꯊꯍꯅꯈꯤ . |
| ꯑꯉꯥꯡꯁꯤꯡ (ꯄ꯭ꯂꯦꯁꯦꯕꯣ ꯂꯧꯈꯤ) | ꯑꯦꯟꯗ꯭ꯔꯣꯖꯦꯅꯒꯤ ꯆꯥꯡ ꯑꯃꯁꯨꯡ ꯁ꯭ꯇꯦꯔꯣꯏꯗꯀꯤ ꯆꯥꯡ꯫ | ꯑꯦꯟꯗ꯭ꯔꯣꯖꯦꯅꯒꯤ ꯆꯥꯡ ꯍꯦꯅꯒꯠꯂꯀꯈꯤ꯫ ꯁ꯭ꯇꯦꯔꯣꯏꯗꯀꯤ ꯗꯣꯖ ꯑꯁꯤ ꯆꯥꯎꯔꯥꯛꯅꯥ ꯶% ꯍꯦꯅꯒꯠꯍꯅꯕꯥ ꯃꯊꯧ ꯇꯥꯈꯤ꯫ |
ꯃꯁꯤꯒꯤ ꯔꯤꯖꯜꯇꯁꯤꯡ ꯑꯁꯤꯅꯥ ꯃꯌꯦꯛ ꯁꯦꯡꯅꯥ ꯇꯥꯛꯂꯤ ꯃꯗꯨꯗꯤ ꯀ꯭ꯔꯤꯅꯦꯁꯔꯐꯣꯟꯇꯅꯥ ꯑꯦꯟꯗ꯭ꯔꯣꯖꯦꯅꯒꯤ ꯆꯥꯡ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯏ, ꯃꯁꯤꯒꯥ ꯂꯣꯌꯅꯅꯥ ꯑꯅꯥꯕꯁꯤꯡꯗꯥ ꯃꯇꯝ ꯁꯥꯡꯅꯥ ꯈꯨꯗꯣꯡꯊꯤꯕꯥ ꯊꯣꯀꯍꯅꯕꯥ ꯌꯥꯕꯥ ꯁ꯭ꯇꯦꯔꯣꯏꯗꯁꯤꯡꯒꯤ ꯗꯣꯖꯁꯨ ꯍꯟꯊꯍꯜꯂꯤ꯫
ꯍꯤꯗꯥꯛ ꯑꯁꯤ ꯀꯌꯥ ꯌꯥꯝꯅꯥ ꯁꯥꯐꯕꯒꯦ?
ꯁ꯭ꯇꯗꯤꯁꯤꯡꯅꯥ ꯇꯥꯛꯂꯤ ꯃꯗꯨꯗꯤ ꯗ꯭ꯔꯒ ꯑꯁꯤꯅꯥ ꯑꯀꯅꯕꯥ ꯁꯥꯏꯗ ꯏꯐꯦꯛꯇ ꯈꯔꯥ ꯂꯩ꯫ ꯔꯤꯄꯣꯔꯠ ꯇꯧꯔꯀꯄꯥ ꯁꯥꯏꯗ ꯏꯐꯦꯛꯇ ꯑꯌꯥꯝꯕꯗꯤ ꯑꯄꯤꯀꯄꯥ ꯑꯃꯁꯨꯡ ꯃꯇꯝ ꯈꯔꯒꯤ ꯑꯣꯏꯕꯥ ꯑꯣꯏ꯫
- ꯋꯥꯕ
- ꯀꯣꯛ ꯆꯤꯛꯄ
- ꯀꯣꯜꯗ ꯅꯠꯠꯔꯒꯥ ꯁ꯭ꯇꯣꯐ ꯑꯣꯏꯕꯥ ꯅꯥꯀꯣꯡ꯫
- ꯃꯁꯜ ꯅꯠꯠꯔꯒꯥ ꯈꯣꯡꯗꯥ ꯁꯣꯀꯄꯥ꯫
- ꯁꯔꯨ ꯇꯥꯡꯒꯤ ꯑꯅꯥꯕꯥ꯫
ꯍꯤꯗꯥꯛ ꯑꯁꯤꯒꯥ ꯂꯣꯌꯅꯅꯥ ꯂꯥꯀꯄꯥ ꯑꯃꯠꯇꯥ ꯉꯥꯏꯔꯕꯥ ꯑꯆꯧꯕꯥ ꯆꯦꯀꯁꯤꯅꯋꯥꯗꯤ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯅꯥ ꯄꯤꯕꯥ ꯁ꯭ꯇꯦꯔꯣꯏꯗꯀꯤ ꯑꯀꯛꯅꯕꯥ ꯗꯣꯖ ꯑꯗꯨ ꯂꯧꯗ꯭ꯔꯕꯗꯤ , ꯅꯍꯥꯛꯀꯤ ꯀꯣꯔꯇꯤꯁꯣꯂꯒꯤ ꯆꯥꯡ ꯑꯁꯤ ꯈꯨꯗꯣꯡꯊꯤꯅꯤꯉꯥꯏ ꯑꯣꯏꯅꯥ ꯍꯟꯊꯔꯀꯄꯥ ꯌꯥꯏ, ꯃꯗꯨꯅꯥ ꯑꯦꯗ꯭ꯔꯤꯅꯜ ꯏꯅꯁꯨꯐꯤꯁꯤꯑꯦꯟꯁꯤ ꯀꯧꯕꯥ ꯄꯨꯟꯁꯤꯗꯥ ꯈꯨꯗꯣꯡꯊꯤꯅꯤꯉꯥꯏ ꯑꯣꯏꯕꯥ ꯀꯟꯗꯤꯁꯟ ꯑꯃꯥ ꯊꯣꯀꯍꯜꯂꯤ꯫ ꯑꯗꯨꯕꯨ ꯁ꯭ꯇꯗꯤꯁꯤꯡꯗꯥ ꯍꯤꯗꯥꯛ ꯑꯁꯤ ꯃꯑꯣꯡ ꯆꯨꯝꯅꯥ ꯂꯧꯈꯤꯕꯥ ꯀꯅꯥꯒꯨꯝꯕꯥ ꯑꯃꯠꯇꯅꯥ ꯃꯁꯤꯒꯤ ꯐꯤꯚꯝ ꯑꯁꯤ ꯊꯦꯡꯅꯈꯤꯗ꯭ꯔꯤ . ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯒꯤ ꯏꯅꯁ꯭ꯠꯔꯛꯁꯅꯁꯤꯡ ꯉꯥꯛꯅꯥ ꯆꯠꯄꯥ ꯍꯥꯌꯕꯁꯤ ꯌꯥꯝꯅꯥ ꯃꯔꯨꯑꯣꯏ꯫
ꯁꯤ.ꯑꯦ.ꯑꯩꯆ.ꯒꯤ ꯂꯥꯌꯦꯡꯕꯒꯤ ꯑꯅꯧꯕꯥ ꯑꯥꯁꯥ꯫
ꯃꯥꯌ ꯄꯥꯛꯂꯕꯥ ꯐꯂꯁꯤꯡ ꯑꯁꯤꯅꯥ ꯃꯔꯝ ꯑꯣꯏꯗꯨꯅꯥ ꯑꯃꯦꯔꯤꯀꯥꯗꯥ ꯂꯩꯕꯥ ꯑꯦꯐ.ꯗꯤ.ꯑꯦ.(ꯗ꯭ꯔꯒꯁꯤꯡ ꯑꯌꯥꯕꯥ ꯄꯤꯔꯤꯕꯥ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯑꯦꯖꯦꯟꯁꯤ)ꯅꯥ ꯗ꯭ꯔꯒ ꯑꯁꯤꯒꯤ ꯑꯈꯟꯅꯕꯥ ꯑꯌꯥꯕꯥ ꯄꯤꯈ꯭ꯔꯦ꯫ ꯀ꯭ꯔꯤꯅꯦꯁꯔꯐꯣꯟꯇ (ꯕ꯭ꯔꯦꯟꯗ ꯅꯦꯝ ꯀ꯭ꯔꯦꯅꯦꯁꯤꯇꯤ) ꯑꯁꯤ ꯁꯤ.ꯑꯦ.ꯑꯩꯆ. ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ ꯃꯁꯤ ꯁꯤ.ꯑꯦ.ꯑꯩꯆ.ꯒꯤ ꯂꯥꯌꯦꯡꯕꯗꯥ ꯑꯆꯧꯕꯥ ꯈꯣꯉꯊꯥꯡ ꯑꯃꯅꯤ꯫
ꯍꯧꯖꯤꯛꯇꯤ ꯗꯣꯛꯇꯔꯁꯤꯡꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯍꯧꯖꯤꯛ ꯂꯩꯔꯤꯕꯥ ꯁ꯭ꯇꯦꯔꯣꯏꯗ ꯂꯥꯌꯦꯡ (ꯑꯦꯗ-ꯑꯣꯟ ꯊꯦꯔꯥꯄꯤ)ꯒꯤ ꯃꯊꯛꯇꯥ ꯍꯤꯗꯥꯛ ꯑꯁꯤ ꯄꯤꯕꯥ ꯌꯥꯔꯦ . ꯃꯁꯤꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯁ꯭ꯇꯦꯔꯣꯏꯗꯀꯤ ꯗꯣꯖ ꯍꯟꯊꯍꯅꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯏ꯫ ꯃꯁꯤꯅꯥ ꯇꯥꯀꯄꯗꯤ ꯅꯍꯥꯛꯅꯥ ꯁ꯭ꯇꯦꯔꯣꯏꯗꯁꯤꯡꯗꯒꯤ ꯁꯥꯏꯗ ꯏꯐꯦꯛꯇ ꯍꯟꯊꯔꯀꯄꯥ ꯌꯥꯏ, ꯅꯍꯥꯛꯀꯤ ꯍꯣꯔꯃꯣꯅꯒꯤ ꯆꯥꯡ ꯑꯗꯨ ꯍꯦꯟꯅꯥ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯕꯥ ꯌꯥꯏ ꯑꯃꯁꯨꯡ ꯄꯨꯟꯁꯤꯒꯤ ꯃꯒꯨꯟ ꯍꯦꯟꯅꯥ ꯂꯩꯕꯥ ꯌꯥꯏ꯫
ꯇꯦꯛ-ꯍꯣꯝ ꯃꯦꯁꯦꯖ ꯇꯧꯕꯥ꯫
- CAH (Congenital Adrenal Hyperplasia) ꯍꯥꯌꯕꯁꯤ ꯑꯦꯗ꯭ꯔꯤꯅꯜ ꯒ꯭ꯜꯌꯥꯟꯗꯁꯤꯡꯗꯥ ꯁꯣꯀꯍꯜꯂꯤꯕꯥ ꯑꯃꯁꯨꯡ ꯍꯣꯔꯃꯣꯅꯒꯤ ꯏꯃꯕꯦꯂꯦꯟꯁ ꯊꯣꯀꯍꯜꯂꯤꯕꯥ ꯖꯦꯅꯦꯇꯤꯛ ꯂꯥꯌꯅꯥ ꯑꯃꯅꯤ꯫
- ꯀ꯭ꯔꯤꯅꯦꯁꯔꯐꯣꯟꯇ (ꯀ꯭ꯔꯦꯅꯦꯁꯤꯇꯤ) ꯑꯁꯤ ꯁꯤ.ꯑꯦ.ꯑꯩꯆ.ꯒꯤꯗꯃꯛ ꯅꯧꯅꯥ ꯑꯌꯥꯕꯥ ꯄꯤꯔꯕꯥ ꯗ꯭ꯔꯒ ꯑꯃꯅꯤ, ꯃꯁꯤ ꯁ꯭ꯇꯦꯔꯣꯏꯗ ꯂꯥꯌꯦꯡꯕꯒꯤ ꯃꯊꯛꯇꯥ ꯄꯤꯔꯤ꯫
- ꯃꯁꯤꯅꯥ ꯍꯀꯆꯥꯡꯗꯥ ꯑꯦꯟꯗ꯭ꯔꯣꯖꯦꯟ ꯍꯣꯔꯃꯣꯅꯒꯤ ꯆꯥꯡ ꯋꯥꯡꯅꯥ ꯍꯟꯊꯍꯜꯂꯤ ꯑꯃꯁꯨꯡ ꯅꯣꯡꯃꯗꯥ ꯁ꯭ꯇꯦꯔꯣꯏꯗꯀꯤ ꯗꯣꯖ ꯍꯟꯊꯍꯅꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯕꯥ ꯉꯝꯃꯤ꯫
- ꯁ꯭ꯇꯦꯔꯣꯏꯗꯁꯤꯡꯒꯤ ꯗꯣꯖ ꯍꯟꯊꯍꯟꯗꯨꯅꯥ ꯃꯇꯝ ꯁꯥꯡꯅꯥ ꯁ꯭ꯇꯦꯔꯣꯏꯗ ꯁꯤꯖꯤꯟꯅꯕꯒꯥ ꯃꯔꯤ ꯂꯩꯅꯕꯥ ꯁꯥꯏꯗ ꯏꯐꯦꯛꯇꯁꯤꯡ ꯍꯟꯊꯍꯟꯅꯕꯒꯤ ꯈꯨꯗꯣꯡꯆꯥꯕꯥ ꯑꯃꯥ ꯂꯩ꯫
- ꯃꯁꯤ ꯂꯥꯌꯅꯥ ꯑꯁꯤꯒꯤ ꯍꯤꯗꯥꯛ ꯑꯃꯥ ꯑꯣꯏꯗ꯭ꯔꯕꯁꯨ, ꯃꯁꯤꯅꯥ ꯁꯤ.ꯑꯦ.ꯑꯩꯆ.ꯒꯤ ꯑꯅꯥꯕꯁꯤꯡꯒꯤ ꯄꯨꯟꯁꯤ ꯃꯍꯤꯡ ꯐꯒꯠꯍꯅꯕꯗꯥ ꯑꯆꯧꯕꯥ ꯈꯣꯉꯊꯥꯡ ꯑꯃꯅꯤ꯫
- ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛ ꯅꯠꯠꯔꯒꯥ ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯗꯥ CAH ꯂꯩꯔꯕꯗꯤ, ꯑꯅꯧꯕꯥ ꯂꯥꯏꯌꯦꯡ ꯑꯁꯤ ꯅꯍꯥꯛꯀꯤꯗꯃꯛꯇꯥ ꯆꯨꯝꯃꯤꯕ꯭ꯔꯥ ꯍꯥꯌꯕꯗꯨ ꯌꯦꯡꯅꯕꯒꯤꯗꯃꯛ ꯅꯍꯥꯛꯀꯤ ꯑꯦꯟꯗꯣꯛꯔꯥꯏꯅꯣꯂꯣꯖꯤꯁ꯭ꯠ ꯅꯠꯠꯔꯒꯥ ꯐꯦꯃꯤꯂꯤ ꯗꯣꯛꯇꯔꯒꯥ ꯋꯥꯔꯤ ꯁꯥꯅꯕꯥ ꯍꯥꯌꯕꯁꯤ ꯌꯥꯝꯅꯥ ꯃꯔꯨꯑꯣꯏ .











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