ꯅꯍꯥꯛꯀꯤ ꯏꯆꯥꯅꯨꯄꯤ ꯑꯗꯨ ꯈꯣꯡꯅꯥ ꯆꯠꯄꯗꯥ ꯂꯦꯞꯂꯤꯕ꯭ꯔꯥ? ꯅꯠꯔꯒꯥ ꯃꯈꯣꯌꯒꯤ ꯈꯣꯉꯅꯥ ꯈꯔꯥ ꯀꯨꯄꯁꯤꯜꯂꯕꯥ ꯎꯕꯥ ꯐꯪꯕꯔꯥ? ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯇꯃꯗꯥ ꯍꯥꯌꯔꯤꯕꯁꯤꯡ ꯑꯁꯤ ꯅꯣꯔꯃꯦꯜ ꯑꯣꯏꯕꯥ ꯌꯥꯏ꯫ ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ, ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯇꯃꯗꯥ ꯃꯈꯣꯌꯒꯤ ꯃꯇꯨꯡꯗꯥ XLH (X-Linked Hypophosphatemia) ꯒꯨꯝꯕꯥ ꯀꯟꯗꯤꯁꯟ ꯑꯃꯥ ꯂꯩꯕꯥ ꯌꯥꯏ꯫ ꯉꯁꯤ ꯃꯁꯤꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯈꯔꯥ ꯋꯥꯔꯤ ꯁꯥꯟꯅꯔꯁꯤ, ꯅꯠꯇꯦ? ꯋꯥꯈꯜ ꯋꯥꯕꯥ ꯂꯩꯔꯣꯏꯗꯕꯅꯤ, ꯃꯁꯤ ꯄꯨꯝꯅꯃꯛ ꯑꯁꯤ ꯈꯉꯕꯗꯥ ꯑꯩꯅꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯒꯅꯤ꯫
XLH ꯍꯥꯌꯕꯁꯤ ꯀꯔꯤꯅꯣ? ꯃꯁꯤ ꯌꯥꯝꯅꯥ ꯂꯥꯏꯅꯥ ꯂꯧꯁꯤꯅꯁꯤ!
ꯌꯥꯝꯅꯥ ꯂꯥꯏꯅꯥ ꯍꯥꯌꯔꯕꯗꯥ, XLH (X-Linked Hypophosphatemia) ꯑꯁꯤ ꯖꯦꯅꯦꯇꯤꯛ ꯑꯣꯏꯕꯥ ꯂꯥꯌꯅꯥ ꯑꯃꯅꯤ꯫ ꯍꯥꯌꯕꯗꯤ ꯑꯩꯈꯣꯌꯒꯤ ꯍꯀꯆꯥꯡꯗꯥ ꯂꯩꯔꯤꯕꯥ ꯖꯤꯅꯁꯤꯡꯗꯥ ꯑꯄꯤꯀꯄꯥ ꯑꯍꯣꯡꯕꯥ ꯑꯃꯅꯥ ꯊꯣꯀꯍꯅꯕꯥ ꯀꯟꯗꯤꯁꯟ ꯑꯃꯅꯤ꯫ ꯃꯁꯤꯅꯥ ꯃꯔꯨꯑꯣꯏꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯁꯔꯨ ꯑꯃꯁꯨꯡ ꯍꯀꯆꯥꯡꯗꯥ ꯁꯣꯀꯍꯜꯂꯤ . ``ꯔꯤꯀꯦꯠꯁ`` ꯀꯧꯕꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤꯒꯤ ꯃꯔꯃꯗꯥ ꯅꯍꯥꯛꯅꯥ ꯇꯥꯕꯤꯔꯝꯂꯒꯅꯤ? ꯋꯥꯐꯝ ꯑꯁꯤ, ꯑꯦꯛꯁ.ꯑꯦꯜ.ꯑꯩꯆ.ꯅꯥ ꯔꯤꯀꯦꯠ ꯃꯈꯜ ꯑꯃꯅꯤ꯫ ꯀꯟꯗꯤꯁꯟ ꯑꯁꯤ ꯂꯩꯕꯥ ꯅꯍꯥ ꯑꯣꯏꯔꯤꯕꯥ ꯑꯉꯥꯡꯁꯤꯡꯅꯥ ꯈꯣꯡꯅꯥ ꯆꯠꯄꯗꯥ ꯑꯋꯥꯕꯥ ꯃꯥꯌꯣꯛꯅꯔꯀꯄꯥ ꯌꯥꯏ, ꯃꯈꯣꯌꯒꯤ ꯈꯣꯡ ꯑꯗꯨ ꯀꯨꯄꯁꯤꯅꯕꯥ ꯌꯥꯏ꯫ ꯃꯁꯤ ꯈꯛꯇꯥ ꯅꯠꯇꯅꯥ ꯃꯈꯣꯌꯗꯥ ꯃꯁꯜ ꯁꯣꯟꯊꯕꯥ ꯑꯃꯁꯨꯡ ꯇꯥꯕꯥ ꯉꯃꯗꯕꯥ ꯑꯁꯤꯅꯆꯤꯡꯕꯥ ꯑꯇꯩ ꯄ꯭ꯔꯣꯕ꯭ꯂꯦꯃꯁꯤꯡꯁꯨ ꯂꯩꯕꯥ ꯌꯥꯏ꯫
XLHꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯗꯨ ꯀꯔꯤꯅꯣ? ꯈꯔꯥ ꯆꯦꯀꯁꯤꯅꯁꯤ!
XLHꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯁꯤ ꯃꯍꯧꯁꯥꯅꯥ ꯑꯉꯥꯡ ꯑꯣꯏꯔꯤꯉꯩꯗꯥ ꯎꯕꯥ ꯐꯪꯏ꯫ ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ, ꯂꯥꯏꯑꯣꯡ ꯈꯔꯗꯤ ꯃꯄꯨꯡ-ꯃꯔꯩ ꯐꯥꯔꯕꯥ ꯃꯇꯃꯗꯁꯨ ꯎꯕꯥ ꯐꯪꯏ꯫
ꯅꯍꯥ ꯑꯣꯏꯔꯤꯕꯥ ꯑꯉꯥꯡꯁꯤꯡꯗꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ:
ꯃꯈꯥꯗꯥ ꯅꯍꯥꯛꯅꯥ ꯄꯨꯛꯅꯤꯡ ꯆꯪꯒꯗꯕꯥ ꯋꯥꯐꯝ ꯈꯔꯗꯤ ꯃꯈꯥꯗꯥ ꯄꯤꯔꯤ:
- ꯈꯣꯡꯅꯥ ꯆꯠꯄꯗꯥ ꯑꯋꯥꯕꯥ ꯅꯠꯠꯔꯒꯥ ꯈꯣꯡꯅꯥ ꯆꯠꯄꯥ ꯍꯧꯕꯗꯥ ꯊꯦꯡꯊꯕꯥ꯫
- ꯈꯣꯡ ꯀꯀꯄꯥ ꯅꯠꯠꯔꯒꯥ ꯈꯣꯡ ꯍꯥꯝꯂꯕꯥ, ꯈꯣꯡꯒꯤ ꯃꯔꯛꯇꯥ ꯑꯆꯧꯕꯥ ꯕꯣꯜ ꯑꯃꯥ ꯄꯥꯁ ꯇꯧꯔꯀꯄꯒꯨꯝꯅꯥ꯫
- ꯁꯔꯨ ꯑꯃꯁꯨꯡ ꯃꯁꯂꯁꯤꯡꯗꯥ ꯑꯁꯣꯛ-ꯑꯄꯟ ꯊꯣꯀꯄꯥ꯫ ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯅꯥ ꯑꯌꯥꯝꯕꯅꯥ "ꯑꯣꯍ, ꯑꯩꯒꯤ ꯈꯣꯉꯅꯥ ꯁꯣꯀꯄꯥ" ꯍꯥꯌꯕꯔꯥ?
- ꯋꯥꯡꯈꯠꯄꯥ (short stature) ꯍꯟꯊꯔꯀꯄꯥ꯫
- ꯃꯇꯝ ꯄꯨꯝꯅꯃꯛꯇꯥ ꯄꯨꯟꯁꯤ ꯂꯩꯇꯕꯥ ꯑꯃꯁꯨꯡ ꯋꯥꯈꯜ ꯅꯨꯡꯉꯥꯏꯇꯕꯥ ꯐꯥꯎꯕꯥ꯫
- ꯃꯁꯜ ꯁꯣꯟꯊꯕꯥ꯫
- ꯍꯥꯀꯆꯥꯡꯒꯤ ꯄ꯭ꯔꯣꯕ꯭ꯂꯦꯃꯁꯤꯡ: ꯑꯉꯥꯡꯒꯤ ꯍꯥꯀꯆꯥꯡ ꯑꯗꯨ ꯃꯇꯝ ꯆꯥꯗꯅꯥ ꯃꯥꯡꯈꯤꯕꯥ, ꯍꯥꯀꯆꯥꯡ ꯁꯣꯀꯄꯥ, ꯈꯣꯡ ꯍꯥꯝꯕꯥ ꯌꯥꯗꯕꯥ, ꯑꯃꯁꯨꯡ ꯈꯣꯡ ꯍꯥꯝꯂꯀꯄꯥ ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯇꯣꯏꯅꯥ ꯊꯣꯀꯄꯥ꯫
- ꯃꯀꯣꯛ ꯅꯠꯠꯔꯒꯥ ꯃꯥꯌꯒꯤ ꯃꯑꯣꯡ-ꯃꯇꯧꯗꯥ ꯑꯍꯣꯡꯕꯥ ꯂꯥꯀꯄꯥ꯫ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯇꯃꯗꯥ ꯃꯁꯤ ꯁ꯭ꯀꯨꯂꯒꯤ ꯁꯔꯨ ꯇꯥꯡꯁꯤꯡ ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯊꯨꯅꯥ ꯌꯥꯡꯅꯥ ꯐ꯭ꯌꯨꯖ ꯇꯧꯕꯅꯥ (`ꯀ꯭ꯔꯦꯅꯤꯑꯣꯁꯥꯏꯅꯣꯁ꯭ꯇꯣꯁꯤꯁ` ꯍꯥꯌꯅꯥ ꯀꯧꯏ) ꯊꯣꯀꯍꯅꯕꯥ ꯌꯥꯏ꯫
ꯃꯤꯔꯣꯜꯂꯤꯉꯩ ꯃꯇꯃꯗꯥ ꯂꯥꯀꯄꯥ ꯑꯍꯦꯅꯕꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ:
XLHꯅꯥ ꯅꯥꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡꯅꯥ ꯆꯍꯤ ꯌꯥꯃꯈꯠꯂꯀꯄꯒꯥ ꯂꯣꯌꯅꯅꯥ ꯑꯍꯦꯅꯕꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯂꯥꯀꯄꯥ ꯌꯥꯏ꯫ ꯃꯁꯤꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯃꯈꯥꯗꯥ ꯄꯤꯔꯤꯕꯁꯤꯡ ꯑꯁꯤ ꯌꯥꯑꯣꯔꯤ:
- ꯇꯥꯕꯥ ꯉꯃꯗꯕꯥ꯫
- ꯀꯣꯛ ꯆꯤꯛꯄ.
- ꯁ꯭ꯄꯥꯏꯅꯦꯜ ꯀꯦꯅꯦꯜ ꯑꯗꯨ ꯀꯨꯄꯁꯤꯅꯕꯥ (Spinal Stenosis)꯫
- ꯑꯍꯜ ꯑꯣꯏꯔꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡꯗꯥ ꯁꯔꯨ ꯇꯥꯡꯁꯤꯡ ꯇꯔꯨ-ꯇꯅꯥꯅꯕꯥ (`Osteomalacia`)꯫
- ꯈꯣꯡꯅꯥ ꯆꯠꯂꯤꯉꯩꯗꯥ ꯕꯦꯂꯦꯟꯁ ꯃꯥꯡꯈꯤꯕꯥ, ꯈꯣꯡꯅꯥ ꯆꯠꯄꯗꯥ ꯑꯋꯥꯕꯥ꯫
- ꯃꯇꯝ ꯆꯨꯞꯄꯒꯤ ꯑꯣꯏꯅꯥ ꯍꯥꯀꯆꯥꯡ ꯃꯥꯡꯈꯤꯕꯥ꯫
- ꯂꯤꯒꯥꯃꯦꯟꯇꯁꯤꯡ ꯅꯠꯠꯔꯒꯥ ꯇꯦꯟꯗꯣꯅꯁꯤꯡ (tendons) ꯊꯤꯡꯖꯤꯅꯕꯥ ꯅꯠꯠꯔꯒꯥ ꯇꯞꯅꯥ ꯇꯞꯅꯥ ꯁꯣꯟꯊꯕꯥ꯫
- ꯁꯔꯨ ꯇꯥꯡꯁꯤꯡ (joint stiffness), ꯂꯦꯡ-ꯑꯣꯠꯄꯗꯥ ꯑꯋꯥꯕꯥ꯫
- ꯆꯥꯡ ꯅꯥꯏꯅꯥ ꯋꯥꯈꯜ ꯋꯥꯕꯥ꯫
- ꯐ꯭ꯔꯦꯀꯆꯔ ꯑꯃꯁꯨꯡ ꯄ꯭ꯁꯨꯗꯣꯐ꯭ꯔꯦꯀꯆꯔ (ꯃꯁꯤꯅꯥ ꯃꯔꯝ ꯑꯣꯏꯗꯨꯅꯥ ꯁꯔꯨ ꯇꯥꯡ ꯑꯃꯅꯥ ꯑꯦꯛꯁ-ꯔꯦꯗꯥ ꯐ꯭ꯔꯦꯀꯆꯔ ꯑꯃꯥ ꯑꯣꯏꯅꯥ ꯎꯕꯥ ꯐꯪꯏ, ꯑꯗꯨꯕꯨ ꯇꯁꯦꯡꯕꯗꯤ ꯃꯄꯨꯡꯐꯥꯕꯥ ꯕ꯭ꯔꯦꯛ ꯑꯃꯥ ꯑꯣꯏꯗꯦ)꯫
XLH ꯅꯥ ꯀꯔꯤꯅꯥ ꯊꯣꯀꯍꯅꯕꯒꯦ? ꯃꯁꯤ ꯀꯔꯤꯒꯤ ꯊꯣꯛꯂꯤꯕꯅꯣ?
ꯑꯣꯀꯦ, ꯍꯧꯖꯤꯛ ꯀꯔꯤꯒꯤꯗꯃꯛꯇꯥ ꯑꯦꯛꯁ.ꯑꯦꯜ.ꯑꯩꯆ. ꯃꯁꯤꯒꯤ ꯃꯔꯃꯗꯤ ꯑꯩꯈꯣꯌꯒꯤ ꯍꯀꯆꯥꯡꯗꯥ ꯂꯩꯔꯤꯕꯥ `PHEX ꯖꯤꯟ`ꯗꯥ ꯖꯦꯅꯦꯇꯤꯛ ꯃ꯭ꯌꯨꯇꯦꯁꯟ ꯑꯃꯥ ꯂꯩꯕꯅꯤ꯫. ꯃꯁꯤꯒꯤ `PHEX` ꯖꯤꯟ ꯑꯁꯤꯅꯥ `FGF23` (`ꯐꯥꯏꯕ꯭ꯔꯣꯕ꯭ꯂꯥꯁ꯭ꯠ ꯒ꯭ꯔꯣꯊ ꯐꯦꯛꯇꯔ 23`) ꯀꯧꯕꯥ ꯍꯣꯔꯃꯣꯟ ꯑꯃꯥ ꯁꯦꯝꯃꯤ꯫ ꯃꯁꯤꯒꯤ `FGF23` ꯍꯣꯔꯃꯣꯟ ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯃꯔꯨꯑꯣꯏ꯫ ꯃꯔꯃꯗꯤ, ꯃꯁꯤꯅꯥ ꯑꯩꯈꯣꯌꯒꯤ ꯍꯀꯆꯥꯡꯗꯥ ꯐꯣꯁꯐꯦꯠꯀꯤ ꯆꯥꯡ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯏ꯫ ꯑꯩꯈꯣꯌꯒꯤ ꯁꯔꯨꯁꯤꯡ ꯑꯁꯤ ꯍꯀꯆꯥꯡ ꯐꯅꯥ ꯊꯝꯅꯕꯒꯤꯗꯃꯛ ꯐꯣꯁꯐꯦꯠ ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯃꯔꯨꯑꯣꯏ꯫
ꯃꯍꯧꯁꯥꯅꯥ ꯃꯁꯤ ꯊꯣꯀꯄꯅꯤ: ꯀꯔꯤꯒꯨꯝꯕꯥ ꯑꯩꯈꯣꯌꯒꯤ ꯍꯀꯆꯥꯡꯗꯥ ꯐꯣꯁꯐꯦꯠ ꯃꯔꯥꯡ ꯀꯥꯌꯅꯥ ꯂꯩꯔꯕꯗꯤ, ꯍꯣꯔꯃꯣꯟ `FGF23`ꯅꯥ ꯀꯤꯗꯅꯤꯗꯥ ꯍꯥꯌ, "ꯑꯣꯀꯦ, ꯍꯧꯖꯤꯛ ꯃꯇꯤꯛ ꯆꯥꯔꯦ, ꯌꯨꯔꯤꯅꯗꯥ ꯑꯍꯦꯅꯕꯥ ꯐꯣꯁꯐꯦꯠ ꯑꯗꯨ ꯂꯧꯊꯣꯛꯂꯁꯤ꯫" ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ, ꯀꯔꯤꯒꯨꯝꯕꯥ ꯍꯀꯆꯥꯡꯅꯥ ꯐꯣꯁꯐꯦꯠ ꯍꯦꯟꯅꯥ ꯃꯊꯧ ꯇꯥꯔꯕꯗꯤ, ꯍꯣꯔꯃꯣꯟ `FGF23` ꯄꯨꯊꯣꯀꯄꯥ ꯍꯟꯊꯔꯀꯏ꯫
ꯍꯧꯖꯤꯛꯇꯤ `PHEX` ꯖꯤꯅꯗꯥ ꯂꯩꯕꯥ ꯃ꯭ꯌꯨꯇꯦꯁꯟ ꯑꯁꯤꯅꯥ ꯑꯩꯈꯣꯌꯒꯤ ꯍꯀꯆꯥꯡꯗꯥ ꯃꯊꯧ ꯇꯥꯕꯗꯒꯤ ꯍꯦꯟꯅꯥ `FGF23` ꯍꯣꯔꯃꯣꯟ ꯄꯨꯊꯣꯀꯍꯜꯂꯤ꯫ ꯑꯍꯦꯅꯕꯥ ꯍꯣꯔꯃꯣꯟ ꯑꯁꯤꯅꯥ ꯃꯔꯝ ꯑꯣꯏꯗꯨꯅꯥ ꯍꯀꯆꯥꯡꯅꯥ ꯌꯨꯔꯤꯅꯗꯥ ꯃꯊꯧ ꯇꯥꯕꯗꯒꯤ ꯍꯦꯟꯅꯥ ꯐꯣꯁꯐꯦꯠ ꯊꯥꯗꯣꯀꯏ꯫ ꯃꯗꯨꯗꯥ ꯁꯔꯨ ꯑꯃꯁꯨꯡ ꯍꯥꯀꯆꯥꯡꯒꯤꯗꯃꯛꯇꯥ ꯃꯊꯧ ꯇꯥꯕꯥ ꯐꯣꯁꯐꯦꯠ ꯑꯗꯨ ꯃꯥꯡꯈꯤ, ꯑꯃꯁꯨꯡ XLHꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯎꯕꯥ ꯐꯪꯏ꯫ ꯑꯗꯣꯝꯅꯥ ꯈꯉꯕꯤꯔꯤꯕꯔꯥ?
ꯌꯥꯝꯅꯥ ꯂꯥꯏꯅꯥ ꯍꯥꯌꯔꯕꯗꯥ: ꯖꯤꯟ ꯑꯃꯗꯥ ꯑꯍꯣꯡꯕꯥ ꯑꯃꯥ -> ꯍꯣꯔꯃꯣꯟ `FGF23` ꯍꯦꯟꯅꯥ ꯄꯨꯊꯣꯀꯏ -> ꯍꯀꯆꯥꯡꯗꯒꯤ ꯐꯣꯁꯐꯦꯠ ꯍꯦꯟꯅꯥ ꯊꯥꯗꯣꯀꯏ -> ꯁꯔꯨꯁꯤꯡ ꯁꯣꯟꯊꯔꯀꯏ꯫
XLH ꯑꯁꯤ ꯍꯦꯔꯤꯇꯦꯖ ꯑꯣꯏꯕꯔꯥ?
ꯍꯣꯌ, XLH ꯀꯧꯕꯥ ꯀꯟꯗꯤꯁꯟ ꯑꯁꯤ X-ꯂꯤꯉ꯭ꯛ ꯇꯧꯔꯕꯥ ꯑꯣꯇꯣꯁꯣꯃꯜ ꯗꯣꯃꯤꯅꯦꯟꯇ ꯄꯦꯇꯔꯟ ꯑꯃꯗꯥ ꯏꯅꯍꯦꯔꯤ ꯇꯧꯏ . ꯃꯁꯤꯅꯥ ꯇꯥꯀꯄꯗꯤ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯀꯅꯥꯒꯨꯝꯕꯥ ꯑꯃꯗꯥ ꯖꯤꯅꯦꯇꯤꯛ ꯚꯦꯔꯤꯑꯦꯁꯟ ꯑꯗꯨꯒꯥ ꯂꯣꯌꯅꯅꯥ ꯖꯤꯟ ꯑꯗꯨ ꯂꯩꯔꯕꯗꯤ ꯃꯈꯣꯌꯗꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯂꯥꯛꯀꯅꯤ꯫ ꯃꯁꯤꯅꯥ ꯅꯨꯄꯥꯃꯆꯥꯁꯤꯡꯗꯥ ꯈꯔꯥ ꯍꯦꯟꯅꯥ ꯁꯣꯀꯍꯅꯕꯥ ꯌꯥꯏ .
ꯍꯧꯖꯤꯛ ꯌꯦꯡꯎ, ꯅꯨꯄꯤꯃꯆꯥ ꯑꯃꯒꯤ X ꯀ꯭ꯔꯣꯃꯣꯖꯣꯝ ꯑꯅꯤ ꯂꯩ, ꯅꯨꯄꯥꯃꯆꯥ ꯑꯃꯒꯤ X ꯀ꯭ꯔꯣꯃꯣꯖꯣꯝ ꯑꯃꯥ ꯑꯃꯁꯨꯡ Y ꯀ꯭ꯔꯣꯃꯣꯖꯣꯝ ꯑꯃꯥ ꯂꯩ꯫ ꯑꯩꯈꯣꯌ ꯈꯨꯗꯤꯡꯃꯛꯅꯥ ꯑꯩꯈꯣꯌꯒꯤ ꯃꯃꯥ-ꯃꯄꯥꯁꯤꯡꯗꯒꯤ ꯁꯦꯛꯁ ꯀ꯭ꯔꯣꯃꯣꯖꯣꯝ ꯑꯃꯥ (X ꯅꯠꯠꯔꯒꯥ Y) ꯐꯪꯕꯅꯥ ꯃꯔꯝ ꯑꯣꯏꯗꯨꯅꯥ:
- XLHꯅꯥ ꯅꯥꯕꯥ ꯅꯨꯄꯤ ꯑꯃꯅꯥ ꯃꯍꯧꯁꯥꯅꯥ ꯃꯍꯥꯛꯀꯤ ꯑꯉꯥꯡꯗꯥ ꯖꯤꯟ ꯑꯁꯤ ꯄꯤꯕꯒꯤ ꯆꯥꯡ ꯑꯁꯤ 50% ꯑꯣꯏ꯫
- XLH ꯅꯥꯕꯥ ꯅꯨꯄꯥ ꯑꯃꯅꯥ ꯖꯤꯟ ꯑꯁꯤ ꯃꯍꯥꯛꯀꯤ ꯃꯆꯥꯅꯨꯄꯤ ꯄꯨꯝꯅꯃꯛꯇꯥ ꯄꯤꯖꯩ , ꯑꯗꯨꯕꯨ ꯃꯍꯥꯛꯀꯤ ꯃꯆꯥꯅꯨꯄꯥꯁꯤꯡꯗꯥ ꯄꯤꯗꯦ꯫
ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ, ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯇꯃꯗꯥ ꯃꯃꯥ-ꯃꯄꯥ ꯑꯃꯠꯇꯅꯥ XLH ꯂꯩꯇꯕꯁꯨ ꯑꯉꯥꯡ ꯑꯃꯗꯥ XLH ꯂꯥꯀꯄꯥ ꯌꯥꯏ꯫ ꯑꯁꯤꯒꯨꯝꯕꯥ ꯀꯦꯁꯁꯤꯡꯗꯗꯤ, ꯖꯤꯅꯦꯇꯤꯛ ꯑꯣꯏꯕꯥ ꯑꯍꯣꯡꯕꯥ ꯑꯁꯤ ꯔꯦꯟꯗꯝ ꯑꯣꯏꯅꯥ ꯊꯣꯀꯏ꯫
ꯅꯍꯥꯛꯅꯥ XLH ꯂꯩꯕ꯭ꯔꯥ ꯍꯥꯌꯕꯗꯨ ꯀꯔꯝꯅꯥ ꯈꯪꯒꯅꯤ?
ꯀꯔꯤꯒꯨꯝꯕꯥ ꯗꯣꯛꯇꯔ ꯑꯃꯅꯥ ꯅꯍꯥꯀꯄꯨ XLH ꯂꯩꯔꯦ ꯍꯥꯌꯅꯥ ꯆꯤꯡꯅꯔꯕꯗꯤ, ꯃꯈꯣꯌꯅꯥ ꯇꯦꯁ꯭ꯠ ꯀꯌꯥ ꯇꯧꯕꯥ ꯌꯥꯏ, ꯃꯈꯣꯌ ꯑꯗꯨꯗꯤ:
- ꯏ ꯅꯠꯠꯔꯒꯥ ꯌꯨꯔꯤꯟ ꯇꯦꯁ꯭ꯠ ꯇꯧꯕꯥ: ꯃꯁꯤꯅꯥ ꯐꯣꯁꯐꯦꯠ ꯑꯃꯁꯨꯡ ꯑꯦꯐ.ꯖꯤ.ꯑꯦꯐ.꯲꯳ ꯍꯣꯔꯃꯣꯅꯒꯤ ꯆꯥꯡ ꯌꯦꯡꯁꯤꯜꯂꯤ .
- ꯖꯦꯅꯦꯇꯤꯛ ꯇꯦꯁ꯭ꯇꯤꯡ: PHEX ꯖꯤꯅꯗꯥ ꯃ꯭ꯌꯨꯇꯦꯁꯟ ꯂꯩꯕ꯭ꯔꯥ ꯍꯥꯌꯕꯗꯨ ꯌꯦꯡꯎ꯫
- ꯕꯣꯟ ꯗꯦꯟꯁꯤꯇꯤ ꯇꯦꯁ꯭ꯇꯁꯤꯡ: ꯅꯍꯥꯛꯀꯤ ꯁꯔꯨꯁꯤꯡ ꯑꯗꯨ ꯀꯌꯥꯝ ꯃꯄꯥꯉ꯭ꯒꯜ ꯀꯅꯕꯥ ꯑꯣꯏꯕꯒꯦ ꯍꯥꯌꯕꯗꯨ ꯆꯦꯛ ꯇꯧ꯫
- ꯑꯦꯛꯁ-ꯔꯦ ꯅꯠꯠꯔꯒꯥ ꯑꯇꯩ ꯏꯃꯦꯖꯤꯡ ꯇꯦꯁ꯭ꯇꯁꯤꯡ: ꯁꯔꯨ ꯇꯥꯡꯁꯤꯡꯒꯤ ꯃꯑꯣꯡ-ꯃꯇꯧ ꯑꯃꯁꯨꯡ ꯑꯁꯣꯛ-ꯑꯄꯟ ꯂꯩꯕ꯭ꯔꯥ ꯍꯥꯌꯕꯗꯨ ꯆꯦꯛ ꯇꯧ꯫
XLHꯒꯤ ꯂꯥꯏꯌꯦꯡꯁꯤꯡ ꯑꯗꯨ ꯀꯔꯤꯅꯣ?
ꯅꯨꯡꯉꯥꯏꯇꯕꯥ ꯋꯥꯐꯝ ꯑꯃꯅꯥ ꯍꯧꯖꯤꯛ ꯐꯥꯑꯣꯕꯗꯥ XLHꯒꯤ ꯂꯥꯏꯌꯦꯡ ꯑꯃꯠꯇꯥ ꯂꯩꯇꯦ꯫ ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ, ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯕꯥ ꯉꯝꯕꯥ ꯑꯃꯁꯨꯡ ꯁꯔꯨꯒꯤ ꯍꯀꯁꯦꯜ ꯉꯥꯛꯇꯨꯅꯥ ꯊꯝꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯕꯥ ꯌꯥꯕꯥ ꯂꯥꯏꯌꯦꯡꯁꯤꯡ ꯂꯩ꯫ ꯃꯐꯝ ꯑꯁꯤꯗꯥ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯄꯥꯟꯗꯃꯗꯤ ꯐꯣꯁꯐꯦꯠꯀꯤ ꯆꯥꯡ ꯑꯁꯤ ꯅꯣꯔꯃꯦꯜ ꯑꯣꯏꯅꯥ ꯑꯃꯨꯛ ꯍꯟꯅꯥ ꯄꯨꯔꯀꯄꯥ ꯅꯠꯇꯦ (ꯃꯁꯤ ꯑꯣꯏꯊꯣꯀꯄꯥ ꯉꯃꯗꯕꯥ ꯌꯥꯏ), ꯑꯗꯨꯕꯨ ꯁꯔꯨꯒꯤ ꯍꯀꯁꯦꯜ ꯉꯥꯛꯇꯨꯅꯥ ꯊꯝꯕꯅꯤ꯫
ꯂꯥꯏꯌꯦꯡꯕꯒꯤ ꯃꯑꯣꯡꯗꯥ ꯃꯈꯥꯗꯥ ꯄꯤꯔꯤꯕꯁꯤꯡꯁꯤ ꯄꯥꯡꯊꯣꯀꯄꯥ ꯌꯥꯏ:
- ꯐꯣꯁꯐꯦꯠ ꯁꯞꯂꯤꯃꯦꯟꯇꯁꯤꯡ ꯑꯃꯁꯨꯡ ꯀꯦꯂꯁꯤꯌꯝ (ꯚꯤꯇꯥꯃꯤꯟ Dꯒꯤ ꯃꯈꯜ ꯑꯃꯥ) ꯄꯤꯕꯥ꯫
- ꯕꯨꯔꯣꯁꯨꯃꯕ : ꯃꯁꯤ ꯍꯣꯔꯃꯣꯟ ꯑꯦꯐ.ꯖꯤ.ꯑꯦꯐ.꯲꯳ ꯕ꯭ꯂꯣꯛ ꯇꯧꯕꯥ ꯃꯣꯅꯣꯛꯂꯣꯅꯦꯜ ꯑꯦꯟꯇꯤꯕꯣꯗꯤ ꯑꯃꯅꯤ꯫
- ꯐꯤꯖꯤꯀꯦꯜ ꯊꯦꯔꯥꯄꯤ (PT): ꯃꯁꯂꯁꯤꯡ ꯃꯄꯥꯉ꯭ꯒꯜ ꯀꯅꯈꯠꯍꯅꯕꯥ ꯑꯃꯁꯨꯡ ꯈꯣꯡꯅꯥ ꯆꯠꯄꯗꯥ ꯂꯥꯏꯊꯣꯀꯍꯅꯕꯥ꯫
- ꯑꯣꯛꯌꯨꯄꯦꯁꯅꯦꯜ ꯊꯦꯔꯥꯄꯤ (OT): ꯅꯣꯡꯃꯒꯤ ꯑꯣꯏꯕꯥ ꯊꯕꯀꯁꯤꯡ ꯍꯦꯟꯅꯥ ꯐꯖꯅꯥ ꯄꯥꯡꯊꯣꯀꯄꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯏ꯫
- ꯕꯣꯟ ꯗꯤꯐꯣꯔꯃꯤꯇꯤꯁꯤꯡ (ꯈꯨꯗꯝ ꯑꯣꯏꯅꯥ, ꯈꯣꯡ ꯍꯥꯝꯂꯕꯥ ꯈꯣꯡ) ꯀꯣꯀꯍꯟꯅꯕꯥ ꯁꯔꯖꯔꯤ꯫
- ꯋꯥꯡꯃꯗꯥ ꯂꯩꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡꯗꯥ ꯒ꯭ꯔꯣꯊ ꯍꯣꯔꯃꯣꯟ ꯄꯤꯕꯥ꯫
- ꯇꯥꯕꯥ ꯉꯃꯗꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡꯒꯤꯗꯃꯛ ꯍꯤꯌꯥꯔꯤꯡ ꯑꯦꯗꯁꯤꯡ꯫
ꯃꯁꯤꯒꯤ ꯃꯊꯛꯇꯥ, ꯀꯔꯤꯒꯨꯝꯕꯥ ꯕꯣꯟ ꯐ꯭ꯔꯦꯀꯆꯔ ꯅꯠꯠꯔꯒꯥ ꯗꯦꯟꯇꯤꯁ꯭ꯠ ꯄ꯭ꯔꯣꯕ꯭ꯂꯦꯃꯒꯨꯝꯕꯥ ꯄꯣꯠꯁꯀꯁꯤꯡ ꯊꯣꯛꯂꯕꯗꯤ ꯃꯈꯣꯌꯗꯨꯁꯨ ꯁꯔꯖꯔꯤ ꯅꯠꯠꯔꯒꯥ ꯑꯇꯩ ꯂꯥꯏꯌꯦꯡꯒꯤ ꯃꯊꯧ ꯇꯥꯒꯅꯤ꯫
XLH ꯂꯩꯕꯥ ꯀꯅꯥꯒꯨꯝꯕꯥ ꯑꯃꯅꯥ ꯀꯔꯤ ꯑꯥꯁꯥ ꯇꯧꯕꯥ ꯌꯥꯕꯒꯦ?
ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛ ꯅꯠꯠꯔꯒꯥ ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯗꯥ XLH ꯂꯩꯔꯕꯗꯤ, ꯌꯥꯔꯤꯕꯃꯈꯩ ꯊꯨꯅꯥ ꯗꯥꯏꯑꯦꯒ꯭ꯅꯣꯁꯤꯁ ꯑꯃꯁꯨꯡ ꯂꯥꯏꯌꯦꯡ ꯂꯧꯕꯥ ꯍꯥꯌꯕꯁꯤ ꯌꯥꯝꯅꯥ ꯃꯔꯨꯑꯣꯏ . ꯃꯁꯤꯅꯥ ꯀꯃꯞꯂꯤꯀꯦꯁꯟ ꯀꯌꯥ ꯊꯤꯡꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯏ꯫ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯇꯃꯗꯥ, ꯕꯣꯟ ꯗꯤꯐꯣꯔꯃꯤꯇꯤ ꯈꯔꯗꯤ ꯃꯁꯥ ꯃꯊꯟꯇꯥ ꯂꯥꯀꯁꯤꯅꯕꯥ ꯌꯥꯏ, ꯅꯠꯠꯔꯒꯥ ꯃꯈꯣꯌꯅꯥ ꯄ꯭ꯔꯣꯕ꯭ꯂꯦꯝ ꯑꯃꯠꯇꯥ ꯊꯣꯀꯍꯟꯗꯕꯥ ꯌꯥꯏ꯫ ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ, ꯀꯦꯁ ꯈꯔꯗꯗꯤ ꯃꯈꯣꯌꯕꯨ ꯀꯣꯀꯍꯟꯅꯕꯥ ꯁꯔꯖꯔꯤ ꯅꯠꯠꯔꯒꯥ ꯐꯤꯖꯤꯀꯦꯜ ꯊꯦꯔꯥꯄꯤ ꯃꯊꯧ ꯇꯥꯕꯥ ꯌꯥꯏ꯫ ꯃꯁꯤꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯒꯥ ꯋꯥꯔꯤ ꯁꯥꯅꯗꯨꯅꯥ ꯀꯔꯤ ꯉꯥꯏꯔꯤꯕꯒꯦ ꯍꯥꯌꯅꯥ ꯍꯪꯕꯁꯤ ꯑꯐꯕꯥ ꯋꯥꯈꯜꯂꯣꯟ ꯑꯃꯅꯤ꯫
XLH ꯂꯩꯕꯥ ꯃꯤꯑꯣꯏ ꯑꯃꯒꯤ ꯄꯨꯟꯁꯤꯒꯤ ꯃꯇꯝ ꯑꯁꯤ ꯀꯌꯥꯅꯣ?
ꯁ꯭ꯇꯗꯤꯁꯤꯡꯅꯥ ꯇꯥꯛꯂꯤ ꯃꯗꯨꯗꯤ XLHꯅꯥ ꯅꯥꯕꯥ ꯃꯤꯑꯣꯏ ꯑꯃꯒꯤ ꯄꯨꯟꯁꯤ ꯑꯁꯤ ꯀꯟꯗꯤꯁꯟ ꯂꯩꯇꯕꯥ ꯃꯤꯑꯣꯏ ꯑꯃꯗꯒꯤ ꯆꯥꯎꯔꯥꯛꯅꯥ ꯆꯍꯤ 8 ꯍꯦꯟꯅꯥ ꯀꯨꯏꯅꯥ ꯂꯩꯕꯥ ꯌꯥꯏ꯫ ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ, ꯑꯈꯉ-ꯑꯍꯩꯁꯤꯡꯅꯥ ꯍꯧꯖꯤꯛ ꯐꯥꯑꯣꯕꯥ ꯄꯨꯟꯁꯤꯒꯤ ꯈꯦꯠꯅꯕꯥ ꯑꯁꯤ ꯇꯁꯦꯡꯅꯥ ꯀꯔꯤꯅꯥ ꯊꯣꯀꯍꯅꯕꯒꯦ ꯍꯥꯌꯕꯗꯨ ꯈꯉꯕꯥ ꯉꯃꯗ꯭ꯔꯤ꯫
XLH ꯑꯁꯤ ꯊꯤꯡꯕꯥ ꯉꯃꯒꯗ꯭ꯔꯥ?
XLH ꯑꯁꯤ ꯖꯦꯅꯦꯇꯤꯛ ꯀꯟꯗꯤꯁꯟ ꯑꯃꯅꯤ, ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯃꯁꯤ ꯊꯤꯡꯕꯥ ꯉꯃꯗꯦ꯫ ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ, ꯀꯔꯤꯒꯨꯝꯕꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯇꯣꯏꯅꯥ ꯈꯉꯗꯣꯛꯂꯕꯥ ꯑꯃꯁꯨꯡ ꯕꯨꯔꯣꯁꯨꯃꯕꯒꯨꯝꯕꯥ ꯂꯥꯏꯌꯦꯡ ꯍꯧꯔꯕꯗꯤ ꯑꯉꯥꯡꯁꯤꯡꯅꯥ ꯅꯣꯔꯃꯦꯜ ꯑꯣꯏꯅꯥ ꯑꯃꯁꯨꯡ ꯂꯥꯏꯑꯣꯡ ꯂꯩꯇꯅꯥ ꯂꯥꯀꯄꯥ ꯌꯥꯏ . ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ XLH ꯂꯩꯔꯕꯗꯤ ꯑꯃꯁꯨꯡ ꯇꯨꯡꯗꯥ ꯂꯥꯛꯀꯗꯕꯥ ꯑꯉꯥꯡꯁꯤꯡꯗꯥ ꯄꯤꯕꯒꯤ ꯑꯣꯏꯊꯣꯀꯄꯥ ꯂꯩꯔꯕꯗꯤ, ꯖꯦꯅꯦꯇꯤꯛ ꯀꯥꯎꯟꯁꯦꯂꯔ ꯑꯃꯒꯥ ꯋꯥꯔꯤ ꯁꯥꯅꯕꯥ ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯃꯔꯨꯑꯣꯏ .
ꯀꯔꯤꯒꯨꯝꯕꯥ ꯑꯩꯅꯥ XLH ꯂꯩꯔꯕꯗꯤ, ꯑꯩꯅꯥ ꯏꯁꯥꯕꯨ/ ꯑꯩꯒꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯕꯨ ꯀꯔꯝꯅꯥ ꯌꯦꯡꯁꯤꯅꯒꯅꯤ?
XLHꯒꯥ ꯂꯣꯌꯅꯅꯥ ꯍꯤꯡꯂꯤꯉꯩꯗꯥ, ꯄꯣꯠꯁꯀꯁꯤꯡ ꯑꯁꯤꯅꯥ ꯅꯍꯥꯀꯄꯨ ꯅꯍꯥꯛꯀꯤ ꯏꯁꯥ ꯑꯃꯁꯨꯡ ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯕꯨ ꯌꯦꯡꯁꯤꯅꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯒꯅꯤ:
- ꯖꯦꯅꯦꯇꯤꯛ ꯇꯦꯁ꯭ꯇꯤꯡ ꯇꯧꯕꯥ꯫ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯀꯅꯐꯥꯔꯝ ꯇꯧꯔꯕꯗꯤ, ꯅꯍꯥꯛꯅꯥ ꯌꯥꯔꯤꯕꯃꯈꯩ ꯂꯥꯏꯌꯦꯡ ꯍꯧꯕꯥ ꯌꯥꯏ꯫
- ꯅꯍꯥꯛꯀꯤ ꯍꯥꯀꯆꯥꯡ ꯑꯃꯁꯨꯡ ꯈꯣꯡꯗꯥ ꯂꯩꯔꯤꯕꯥ ꯄ꯭ꯔꯣꯕ꯭ꯂꯦꯃꯁꯤꯡ ꯑꯗꯨ ꯇꯣꯏꯅꯥ ꯈꯪꯗꯣꯀꯄꯥ ꯉꯝꯅꯕꯥ ꯆꯥꯡ ꯅꯥꯏꯅꯥ ꯗꯦꯟꯇꯤꯁ꯭ꯠ ꯑꯃꯒꯥ ꯇꯥꯟꯅꯧ꯫
- ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯒꯥ ꯎꯅꯔꯤꯕꯥ ꯅꯨꯃꯤꯠ ꯈꯨꯗꯤꯡꯒꯤ ꯐꯣꯂꯣ-ꯑꯞ ꯑꯦꯄꯣꯏꯟꯇꯃꯦꯟꯇꯁꯤꯡꯗꯥ ꯁꯣꯌꯗꯅꯥ ꯆꯠꯀꯗꯕꯅꯤ꯫ ꯐꯤꯖꯤꯀꯦꯜ ꯊꯦꯔꯥꯄꯤ (PT) ꯑꯃꯁꯨꯡ ꯑꯣꯛꯌꯨꯄꯦꯁꯅꯦꯜ ꯊꯦꯔꯥꯄꯤ (OT)ꯒꯨꯝꯕꯥ ꯄꯣꯠꯁꯀꯁꯤꯡ ꯑꯁꯤ ꯊꯥꯗꯣꯛꯂꯣꯏꯗꯕꯅꯤ꯫ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ ꯑꯅꯧꯕꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯂꯩꯔꯕꯗꯤ ꯅꯠꯠꯔꯒꯥ ꯅꯍꯥꯛꯀꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯗꯨ ꯍꯦꯟꯅꯥ ꯐꯠꯆꯤꯜꯂꯛꯂꯕꯗꯤ ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯗꯥ ꯈꯪꯍꯜꯂꯨ꯫
- ꯅꯍꯥꯛꯀꯤ ꯄ꯭ꯔꯦꯁ꯭ꯛꯔꯥꯏꯕ ꯇꯧꯔꯕꯥ ꯍꯤꯗꯥꯛ ꯑꯗꯨ ꯄ꯭ꯔꯦꯁ꯭ꯛꯔꯥꯏꯕ ꯇꯧꯔꯕꯥ ꯃꯇꯨꯡꯏꯟꯅꯥ, ꯃꯇꯝ ꯆꯥꯅꯥ ꯂꯧ꯫ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯍꯤꯗꯥꯛ-ꯂꯥꯡꯊꯛ ꯑꯗꯨ ꯀꯔꯝꯅꯥ ꯂꯧꯒꯗꯒꯦ ꯍꯥꯌꯕꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯋꯥꯍꯪ ꯑꯃꯠꯇꯥ ꯍꯪꯂꯕꯗꯤ, ꯅꯠꯠꯔꯒꯥ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ ꯁꯥꯏꯗ ꯏꯐꯦꯛꯇ ꯑꯃꯠꯇꯥ ꯂꯩꯔꯕꯗꯤ, ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯗꯥ ꯈꯪꯍꯜꯂꯨ꯫
- ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯅꯥ ꯔꯤꯀꯃꯦꯟꯗ ꯇꯧꯔꯀꯄꯒꯤ ꯃꯇꯨꯡꯏꯟꯅꯥ ꯐꯤꯖꯤꯀꯦꯜ ꯑꯦꯛꯇꯤꯚꯤꯇꯤꯁꯤꯡ ꯄꯥꯡꯊꯣꯀꯎ꯫ꯀꯔꯤ ꯁꯥꯐꯕꯥ ꯑꯦꯛꯁꯔꯁꯥꯏꯖꯁꯤꯡꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯁꯔꯨꯁꯤꯡ ꯑꯗꯨ ꯃꯄꯥꯉ꯭ꯒꯜ ꯀꯅꯈꯠꯍꯅꯒꯅꯤ ꯍꯥꯌꯅꯥ ꯃꯍꯥꯀꯄꯨ ꯍꯪꯕꯤꯌꯨ꯫
ꯑꯩꯅꯥ ꯀꯗꯥꯏꯗꯥ ꯗꯣꯛꯇꯔꯒꯥ ꯎꯅꯒꯗꯒꯦ?
ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯒꯤ ꯍꯀꯁꯦꯂꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯅꯠꯠꯔꯒꯥ ꯃꯈꯣꯌꯅꯥ ꯗꯤꯚꯦꯂꯄꯃꯦꯟꯇꯒꯤ ꯃꯥꯏꯂꯁ꯭ꯇꯣꯅꯁꯤꯡ ꯊꯦꯡꯅꯔꯤꯕ꯭ꯔꯥ ꯍꯥꯌꯕꯗꯨꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯋꯥꯈꯜ ꯋꯥꯕꯥ ꯂꯩꯔꯕꯗꯤ, ꯅꯍꯥꯛꯀꯤ ꯄꯦꯗꯤꯑꯦꯠꯔꯤꯀꯀꯥ ꯋꯥꯔꯤ ꯁꯥꯅꯕꯤꯌꯨ꯫ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯊꯧ ꯇꯥꯔꯕꯗꯤ ꯃꯈꯥ ꯇꯥꯕꯥ ꯇꯦꯁ꯭ꯇꯁꯤꯡ ꯇꯧꯅꯕꯥ ꯃꯍꯥꯛꯅꯥ ꯔꯤꯀꯃꯦꯟꯗ ꯇꯧꯒꯅꯤ꯫
ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ XLH ꯂꯩꯔꯕꯗꯤ, ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ ꯑꯅꯧꯕꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯂꯩꯔꯕꯗꯤ ꯅꯠꯠꯔꯒꯥ ꯅꯍꯥꯛꯀꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯗꯨ ꯍꯦꯟꯅꯥ ꯐꯠꯆꯤꯜꯂꯛꯂꯕꯗꯤ ꯈꯨꯗꯛꯇꯥ ꯗꯣꯛꯇꯔ ꯑꯃꯒꯥ ꯇꯥꯟꯅꯧ꯫
ꯅꯍꯥꯛꯅꯥ ꯀꯗꯥꯏꯗꯥ ꯏꯃꯔꯖꯦꯟꯁꯤ ꯇ꯭ꯔꯤꯇꯃꯦꯟꯇ ꯌꯨꯅꯤꯠ (ETU) ꯗꯥ ꯆꯠꯄꯥ ꯃꯊꯧ ꯇꯥꯕꯒꯦ ?
ꯗꯦꯟꯇꯤꯁ꯭ꯠ ꯑꯦꯃꯔꯖꯦꯟꯁꯤ ꯑꯃꯥ ꯂꯥꯀꯄꯥ ꯃꯇꯃꯗꯥ ꯗꯦꯟꯇꯤꯁ꯭ꯠ ꯑꯃꯒꯥ ꯇꯥꯟꯅꯧ꯫ ꯈꯨꯗꯝ ꯑꯣꯏꯅ:
- ꯁꯥꯊꯤꯕꯥ ꯍꯥꯠꯄꯥ ꯑꯃꯥ꯫
- ꯍꯥꯀꯆꯥꯡ ꯑꯃꯥ ꯐꯖꯅꯥ ꯁꯣꯀꯄꯥ ꯅꯠꯠꯔꯒꯥ ꯁꯣꯀꯄꯥ ꯌꯥꯏ꯫
- ꯂꯦꯡ-ꯑꯣꯠꯄꯒꯤ ꯃꯑꯣꯡ (extruded tooth)꯫
- ꯍꯥꯀꯆꯥꯡꯒꯤ ꯃꯔꯨꯃꯗꯥ ꯗꯦꯟꯇꯤꯁ꯭ꯠ ꯑꯦꯕꯁꯦꯁ (dental abscess) ꯑꯃꯥ ꯊꯣꯀꯏ, ꯃꯗꯨꯅꯥ ꯃꯥꯌ ꯑꯃꯁꯨꯡ ꯈꯣꯡꯗꯥ ꯁꯣꯀꯄꯥ ꯊꯣꯀꯍꯜꯂꯤ꯫
ꯑꯩꯅꯥ ꯗꯣꯛꯇꯔꯗꯥ ꯀꯔꯤ ꯋꯥꯍꯪ ꯍꯪꯒꯗꯒꯦ?
ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯒꯥ ꯎꯅꯔꯀꯄꯥ ꯃꯇꯃꯗꯥ ꯑꯁꯤꯒꯨꯝꯕꯥ ꯋꯥꯍꯪꯁꯤꯡ ꯑꯁꯤ ꯍꯪꯕꯅꯥ ꯃꯇꯦꯡ ꯑꯣꯏꯕꯥ ꯌꯥꯏ:
- ꯑꯩ/ ꯑꯩꯒꯤ ꯑꯉꯥꯡꯗꯥ ꯀꯔꯤ ꯂꯥꯏꯌꯦꯡꯕꯒꯤ ꯑꯣꯄꯁꯅꯁꯤꯡ ꯂꯩꯕꯒꯦ?
- ꯑꯩꯅꯥ ꯑꯩꯒꯤ/ ꯑꯩꯒꯤ ꯑꯉꯥꯡꯒꯤ ꯁꯔꯨꯒꯤ ꯍꯀꯁꯦꯜ ꯑꯁꯤ ꯀꯔꯝꯅꯥ ꯉꯥꯀꯊꯣꯀꯄꯥ ꯉꯃꯒꯅꯤ?
- ꯅꯍꯥꯛꯅꯥ ꯀꯗꯥꯏꯗꯥ ꯏꯃꯔꯖꯦꯟꯁꯤ ꯔꯨꯝ (ETU) ꯗꯥ ꯆꯠꯀꯗꯒꯦ ?
- ꯑꯩꯅꯥ ꯅꯉꯕꯨ ꯀꯗꯥꯌꯗꯥ ꯑꯃꯨꯛ ꯎꯅꯒꯗꯒꯦ?
XLHꯅꯥ ꯅꯥꯕꯥ ꯑꯉꯥꯡꯁꯤꯡꯅꯥ ꯃꯤꯔꯣꯜꯂꯤꯉꯩ ꯃꯇꯃꯗꯥ ꯌꯧꯔꯀꯄꯔꯥ?
ꯍꯣꯌ, ꯃꯄꯨꯡ ꯐꯥꯅꯥ꯫ XLHꯅꯥ ꯅꯥꯕꯥ ꯑꯉꯥꯡꯁꯤꯡꯅꯥ ꯃꯤꯔꯣꯜꯂꯤꯉꯩ ꯃꯇꯃꯗꯥ ꯆꯠꯂꯤ ꯑꯃꯁꯨꯡ ꯑꯇꯩ ꯑꯉꯥꯡ ꯑꯃꯒꯨꯝꯅꯥ ꯒ꯭ꯔꯣꯊ ꯁ꯭ꯄꯔꯇꯁꯤꯡ ꯂꯩ꯫ ꯃꯗꯨꯗꯥ ꯑꯀꯤꯕꯥ ꯂꯩꯔꯣꯏꯗꯕꯅꯤ꯫
ꯑꯔꯣꯏꯕꯗꯥ, ꯀꯔꯤ ꯅꯤꯡꯁꯤꯡꯒꯗꯒꯦ꯫
ꯄꯨꯟꯁꯤ ꯆꯨꯞꯄꯥ ꯀꯟꯗꯤꯁꯟ ꯑꯃꯥ ꯂꯩꯔꯦ ꯍꯥꯌꯅꯥ ꯈꯪꯗꯣꯀꯄꯥ ꯍꯥꯌꯕꯁꯤ ꯈꯔꯥ ꯁꯣꯀꯍꯅꯕꯥ ꯌꯥꯏ꯫ ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡꯒꯤ ꯇꯨꯡꯒꯤ ꯄꯨꯟꯁꯤ – ꯅꯠꯠꯔꯒꯥ ꯅꯍꯥꯛꯀꯤ ꯏꯁꯥꯒꯤ ꯇꯨꯡꯒꯤ ꯐꯤꯕꯝ – XLHꯒꯥ ꯂꯣꯌꯅꯅꯥ ꯀꯔꯝꯅꯥ ꯑꯣꯏꯒꯅꯤ ꯍꯥꯌꯕꯁꯤ ꯅꯍꯥꯛꯅꯥ ꯈꯅꯕꯤꯕꯥ ꯌꯥꯏ꯫
ꯑꯗꯨꯕꯨ ꯅꯤꯡꯁꯤꯡꯕꯤꯌꯨ, XLHꯅꯥ ꯅꯥꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡꯅꯥ ꯃꯇꯝ ꯁꯥꯡꯅꯥ, ꯍꯀꯁꯦꯜ ꯐꯕꯥ ꯄꯨꯟꯁꯤ ꯑꯃꯥ ꯍꯤꯡꯕꯥ ꯉꯝꯃꯤ꯫ ꯉꯟꯅꯥ ꯈꯪꯗꯣꯀꯄꯥ ꯑꯃꯁꯨꯡ ꯃꯑꯣꯡ ꯆꯨꯝꯅꯥ ꯂꯥꯏꯌꯦꯡꯕꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯁꯔꯨꯁꯤꯡ ꯑꯗꯨ ꯃꯄꯥꯉ꯭ꯒꯜ ꯀꯅꯕꯥ ꯑꯃꯁꯨꯡ ꯍꯀꯆꯥꯡ ꯐꯅꯥ ꯂꯩꯍꯅꯕꯗꯥ ꯌꯥꯝꯅꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯏ꯫ ꯅꯍꯥꯛꯅꯥ ꯂꯩꯔꯤꯕꯥ ꯋꯥꯈꯜ ꯅꯨꯡꯉꯥꯏꯇꯕꯥ ꯅꯠꯠꯔꯒꯥ ꯋꯥꯍꯪ ꯑꯃꯍꯦꯛꯇꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯒꯥ ꯑꯃꯨꯛꯇꯪ ꯋꯥꯔꯤ ꯁꯥꯅꯕꯗꯥ ꯀꯩꯗꯧꯉꯩꯗꯥ ꯋꯥꯈꯜ ꯋꯥꯕꯥ ꯂꯩꯔꯣꯏꯗꯕꯅꯤ꯫ ꯃꯍꯥꯛꯅꯥ ꯅꯍꯥꯀꯄꯨ ꯃꯇꯦꯡ ꯄꯥꯡꯕꯥ ꯉꯃꯒꯅꯤ꯫
` XLH, X-Linked ꯍꯥꯏꯄꯣꯐꯣꯁꯐꯦꯇꯦꯃꯤꯌꯥ, ꯁꯔꯨꯒꯤ ꯂꯥꯌꯅꯥ, ꯖꯦꯅꯦꯇꯤꯛ ꯂꯥꯌꯅꯥ, ꯔꯤꯀꯦꯠ, ꯐꯣꯁꯐꯦꯠ, ꯑꯉꯥꯡꯁꯤꯡꯒꯤ ꯍꯀꯁꯦꯜ, FGF23











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