Kodi mumatuluka magazi ambiri kuchokera pachilonda chaching'ono? Tiyeni tikambirane za Bernard-Soulier Syndrome (BSS)!

Kodi mwaonapo kuti anthu ena amatuluka magazi ambiri ngakhale atakanda pang'ono kapena bala lochepa, kapena kuti mabalawo amatuluka mosavuta ndipo amatenga nthawi yayitali kuti achire? Nthawi zina izi zitha kukhala chifukwa cha vuto lomwe sitinamvepo zambiri, koma ndilofunika kwambiri kulidziwa. Limodzi mwa matenda otere ndi Bernard-Soulier Syndrome, kapena ``(BSS)`` mwachidule. Tiyeni tikambirane za izi mwatsatanetsatane lero.

Kodi Bernard-Soulier Syndrome (BSS) ndi chiyani?

Mwachidule, Bernard-Soulier Syndrome `(BSS)` ndi vuto losowa kwambiri. Chomwe chimachitika pamenepa ndichakuti njira yothira magazi m'thupi lathu, zomwe zikutanthauza kuti kutuluka magazi kumasiya tikavulala, imasokonekera. Tangoganizirani, muli ndi bala laling'ono padzanja lanu. Patapita kanthawi, kutuluka magazi kumasiya, sichoncho? Chabwino, chomwe chimathandiza ndi ma platelet, mtundu wa selo laling'ono m'magazi athu, ndi plasma, yomwe ndi gawo lamadzimadzi la magazi.

Munthu amene ali ndi matenda a Bernard-Soulier Syndrome (BSS) amakhala ndi ma platelet ochepa kuposa omwe ali wamba. Madokotala amatcha vutoli kuti thrombocytopenia. Komanso, ma platelet omwe alipo ndi akuluakulu kuposa ma platelet wamba. Chifukwa chake, pazifukwa izi, anthu omwe ali ndi BSS amatuluka magazi ndi kuvulala mosavuta.

Kodi vutoli ndi losowa bwanji?

Izi ndi matenda osowa kwambiri. Malinga ndi akatswiri azachipatala, matendawa amakhudza munthu m'modzi pa anthu miliyoni imodzi padziko lonse lapansi. Izi zikutanthauza kuti ngakhale ku Sri Lanka, anthu ochepa kwambiri ndi omwe akudwala matendawa.

Kodi zizindikiro za Bernard-Soulier Syndrome (BSS) ndi ziti?

Kawirikawiri, makanda omwe ali ndi BSS amayamba kusonyeza zizindikirozi ali aang'ono. Yang'anani ngati inu kapena munthu amene mumamudziwa ali ndi zizindikiro izi:

• Umavulala mosavuta, ndipo zimatenga nthawi yayitali kuti uchire: Ngakhale chilonda chosavuta pampando chingasiye chilonda chachikulu. Zingatenge milungu ingapo kuti chilondacho chipole.
• Kutuluka magazi ambiri ngakhale chifukwa cha mabala ang'onoang'ono: Kaya mwadula pang'ono mukamameta ndevu kapena kudula dzanja lanu ndi mpeni mukamadula ndiwo zamasamba, n'zovuta kuletsa kutuluka magazi.
• Kutuluka magazi m'mphuno pafupipafupi: Anthu ena amatcha izi `(epistaxis)`. Ngati mumatuluka magazi m'mphuno pafupipafupi popanda chifukwa, chimenechonso ndi chizindikiro.
• Kutuluka magazi pansi pa khungu: Izi zimawoneka ngati madontho ang'onoang'ono ofiira kapena ofiirira pamwamba pa khungu. Madokotala amatcha izi ``petechiae''.
• Kutuluka magazi ambiri panthawi ya msambo mwa akazi: Ngati kutuluka magazi kumatenga masiku angapo kuposa masiku onse, kapena ngati ndi kwakukulu (menorrhagia), imeneyonso ndi nkhani yodetsa nkhawa.

Musaope kukhala ndi chimodzi kapena ziwiri mwa zizindikirozi, koma ngati zikupitirira, ndi bwino kufunafuna upangiri wa dokotala.

Kodi n’chiyani chimayambitsa matenda a Bernard-Soulier (BSS)?

Iyi ndi mfundo yofunika kwambiri. `(BSS)` ndi matenda a majini.Ndiko kuti, vuto lomwe limachitika tikabadwa chifukwa cha kusintha kwa majini athu. Izi ndi zobadwa nazo , zomwe zikutanthauza kuti ana akhoza kulandira kusintha kwa majini kuchokera kwa makolo awo.

Matendawa (BSS) amayamba chifukwa cha kusintha kwa majini a `GP1BA`, `GP1BB` kapena `GP9` makamaka. Majini onsewa ndi ofunikira kwambiri pa njira yothira magazi m'thupi lathu. Choncho pakakhala vuto ndi majini awa, kuthira magazi sikumachitika bwino.

Kodi mungadziwe bwanji ngati muli ndi matenda a Bernard-Soulier Syndrome (BSS)?

Ngati muli ndi zizindikiro izi, chinthu choyamba chomwe dokotala angachite akamakuonani ndi kukufunsani funso lozama. Kenako, adzalamula kuti muyesedwe magazi kangapo kuti atsimikizire vutoli.

• Kuyesa kuchuluka kwa ma platelet: Izi zimayang'ana kuchuluka kwa ma platelet m'magazi anu komanso ngati ali otsika.
• Mayeso a kusintha kwa majini: Izi zitha kuzindikira ngati pali kusintha kwa majini m'majini omwe atchulidwa kale a `GP1BA`, `GP1BB`, `GP9` omwe amayambitsa `(BSS)`.
• Kuwunika ma platelet pogwiritsa ntchito microscope: Chitsanzo cha magazi anu chimatengedwa ndikuwunika pogwiritsa ntchito microscope kuti muwone ngati ma platelet ndi akulu kwambiri.
• Kuchuluka kwa ma platelet flow cytometry: Ngakhale kuti ili ndi dzina lovuta, mayesowa amayesa kuchuluka kwa ma glycoprotein otchedwa `GP1BA`, `GP1BB`, `GP9` pamwamba pa ma platelet. Ngati awa ndi otsika, ndi chizindikiro cha `(BSS)`.

Kutengera zotsatira za mayesowa, dokotala adzakuuzani ngati muli ndi BSS kapena ayi.

Kodi mankhwala a Bernard-Soulier Syndrome (BSS) ndi ati?

Pakadali pano palibe mankhwala a BSS, chifukwa ndi matenda a majini. Komabe, pali zinthu zambiri zomwe mungachite kuti mupewe kutuluka magazi kwambiri komanso kuchepetsa mavuto ena omwe angabuke. Chithandizo chimayang'ana kwambiri pa zimenezo.

Zinthu zomwe mungachite kuti muchepetse kutuluka magazi:

Izi ndi zinthu zosavuta, koma zofunika kwambiri zomwe mungawonjezere pa moyo wanu watsiku ndi tsiku.

• Pewani mankhwala omwe amawonjezera chiopsezo cha kutuluka magazi: Mankhwala ena ochepetsa ululu, monga mankhwala oletsa kutupa omwe si a steroidal (NSAIDs), aspirin, ndi mankhwala ena oletsa kutupa amatha kuwonjezera chiopsezo cha kutuluka magazi. Chifukwa chake, musamwe mankhwalawa popanda kufunsa dokotala.
• Gwiritsani ntchito burashi ya mano yofewa potsuka mano anu: Izi zingathandize kuchepetsa kutuluka kwa magazi m'kamwa.
• Phunzirani njira yoyenera yoletsera kutuluka magazi m'mphuno: funsani dokotala wanu za momwe mungagwirire mphuno yanu komanso momwe mungagwirire mutu wanu.
• Chepetsani zakudya ndi zakumwa zina: Zakudya zokhala ndi mowa wambiri ndi shuga woyengedwa bwino zingakhudze kuchuluka kwa ma platelet m'magazi anu, choncho ndi bwino kuchepetsa zakudyazo momwe mungathere.
• Lembetsani ku malo omwe amapereka chithandizo chadzidzidzi cha maola 24: Izi zikuthandizani kupeza chithandizo mwachangu pakagwa ngozi, monga kutuluka magazi ambiri.
• Imwani mankhwala owonjezera a iron ngati muli ndi vuto la kusowa kwa iron: Kutuluka magazi pafupipafupi kungayambitse vuto la kusowa kwa iron. Imwani mapiritsi a iron monga momwe dokotala wanu wanenera.
• Valani chibangili kapena chizindikiro cha dokotala: Ndikofunikira kwambiri pa nthawi yadzidzidzi kuvala chibangili kapena chizindikiro chosonyeza momveka bwino kuti muli ndi `(BSS)`.

Chithandizo chamankhwala:

Nthawi zina, makamaka ngati magazi atuluka mwadzidzidzi kapena pokonzekera opaleshoni, madokotala angapereke chithandizo monga:

• Kuika magazi m'maselo: Iyi nthawi zambiri ndi njira yoyamba yothandizira pa vuto la kutuluka magazi mwadzidzidzi. Maselo ochokera kwa wopereka magazi amaperekedwa m'thupi lanu kudzera mu IV line. Maselo amenewa amathandiza magazi kuundana.
• Mankhwala oletsa kutupa: Awa ndi mankhwala omwe amathandiza magazi kuundana. Mwachitsanzo, tranexamic acid, yomwe mwina mudamvapo, imapezekanso pansi pa dzina lodziwika bwino la ``Cyklokapron®''. Izi zimathandiza kuchepetsa kutuluka kwa magazi.

Kodi matenda a Bernard-Soulier Syndrome (BSS) angapewedwe?

Mwatsoka, palibe njira yoletsera BSS kuti isakule chifukwa ndi matenda a majini.

Komabe, ngati wina m'banja mwanu ali ndi BSS, kapena ngati mukuganiza kuti muli ndi kusintha kwa majini kumeneku, mungafune kuganizira zoyezetsa majini . Ndikofunikanso kufunafuna uphungu wa majini . Mlangizi wa majini angakuuzeni zambiri za vutoli ndikufotokozera zoopsa zopatsira ana anu.

Kodi ndi zinthu ziti zomwe muyenera kuzidziwa mukakhala ndi matenda a Bernard-Soulier Syndrome (BSS)?

Anthu ambiri omwe ali ndi BSS amatha kukhala ndi moyo wabwinobwino, koma ayenera kusamala pang'ono kuti achepetse chiopsezo chovulala.

Mwachitsanzo, ndi bwino kupewa masewera olimbitsa thupi, chifukwa amakhala ndi chiopsezo chachikulu cha kuvulala komanso kutuluka magazi ambiri.

Ndikofunikanso kuonana ndi dokotala wanu nthawi zonse kuti mukhale ndi thanzi labwino. Ngati mukuchitidwa opaleshoni, kungakhale kofunikira kukonzekera nthawi yake pasadakhale ndipo mwina kuikidwa magazi m'magazi musanachite opaleshoniyo.

Ngati muli ndi matenda a Bernard-Soulier Syndrome (BSS), ndi mafunso ati omwe muyenera kufunsa dokotala wanu?

Ngati mukuganiza kuti muli ndi (BSS) kapena mwapezeka ndi matendawa, zingakhale zothandiza kwambiri kufunsa dokotala wanu mafunso monga awa:

• Kodi zizindikiro zoyamba za Bernard-Soulier Syndrome ndi ziti?
• Ndi mayeso ati omwe ndiyenera kuchita kuti ndidziwe ngati ndili ndi matenda a Bernard-Soulier?
• Kodi njira zochiritsira matenda a Bernard-Soulier ndi ziti?
• Ngati ndili ndi matenda a Bernard-Soulier, ndingatani kuti ndipewe kutuluka magazi ambiri?
• Ndi zochita ziti zomwe sindiyenera kuchita chifukwa chakuti ndili ndi matenda a Bernard-Soulier?
• Kodi pali mwayi wotani woti ana anga adzalandira matenda a Bernard-Soulier kuchokera kwa ine?

Kuwonjezera pa mafunso awa, musaope kulankhula ndi dokotala za chilichonse chomwe chimabwera m'maganizo mwanu.

Kodi kukhala ndi Bernard-Soulier Syndrome (BSS) panthawi ya mimba ndi chiopsezo kwa mwana?

Ngati muli ndi pakati ndipo muli ndi BSS, mudzafunika chithandizo chamankhwala chapadera (chisamaliro cha amayi oyembekezera komanso a hematology) . Kuchuluka kwa ma platelet anu ndi thanzi lanu lonse ziyenera kuyang'aniridwa nthawi zonse. Pa nthawi yobereka, simungathe kupatsidwa mankhwala oletsa ululu omwe amawonjezera chiopsezo cha kutuluka magazi.

Ngakhale mwana atabadwa, kuchuluka kwa ma platelet a mwana kuyenera kuyesedwa nthawi zonse. Chifukwa pali mwayi woti mwana wanu angatenge majini omwe amayambitsa ``(BSS)'' kuchokera kwa inu. Chifukwa chake, ndikofunikira kulankhula ndi dokotala wanu za izi ndikuchitapo kanthu kofunikira.

Kodi vuto lalikulu lomwe limabwera chifukwa cha Bernard-Soulier Syndrome (BSS) ndi liti?

Mwachidule, vuto lalikulu lomwe limabwera chifukwa cha "BSS" ndi kulephera kwa magazi kuundana . Ichi ndichifukwa chake kutuluka magazi ambiri komanso kuvulala mosavuta ndiye zizindikiro zodziwika bwino.

Ndi matenda ena ati omwe amayambitsa zizindikiro zofanana ndi Bernard-Soulier Syndrome (BSS)?

Pali matenda ena angapo omwe amayambitsa mavuto otuluka magazi ndi zizindikiro zofanana ndi za BSS. Ndi bwino kudziwa mayina a matenda awa okha:

• 'Hemophilia'
• `May-Hegglin anomaly`
• `Matenda a dziwe losungiramo zinthu`
• `Glanzmann thrombasthenia`
• Matenda a Von Willebrand

Kutengera ndi zizindikiro zanu, dokotala yekha ndi amene angadziwe matenda omwe ali.

Mawu athu omaliza

Bernard-Soulier Syndrome `(BSS)` ndi matenda osowa kwambiri omwe amatengera kwa makolo anu. Ngati muli ndi vutoli, mungakhale ndi mavuto ena okhudzana ndi kutsekeka kwa magazi. Komabe, sizikutanthauza kuti simungathe kukhala moyo wabwinobwino. Chofunika kwambiri ndi kupewa zinthu zoopsa zomwe zingayambitse kuvulala ndikutsatira malangizo a dokotala wanu nthawi zonse.

Pitani kwa dokotala wa banja lanu nthawi zonse. Iye akhoza kuyankha mafunso anu, kukuthandizani kuthana ndi vutoli, komanso kugwira nanu ntchito kuti mukhale ndi thanzi labwino. Musachite mantha, kuzindikira ndi kusamalira ndizo mphamvu zathu zazikulu tikakhala ndi vutoli.

Matenda a Bernard-Soulier, BSS, magazi kuundana, ma platelet, kutuluka magazi kwambiri, matenda a majini, kuvulala