Kodi mukudziwa zinthu izi zokhudza ventricle yakumanzere ya mtima wanu? (Kumanzere kwa Ventricular Non-Compaction - LVNC) Tiyeni tikambirane!

Lero tikambirana za vuto lovuta pang'ono, koma lomwe lingakhale lofunika kwambiri pamtima. Mwina simunamvepo izi kale. Limatchedwa Left Ventricular Non-Compaction (LVNC) monga momwe madokotala amalitchulira. Dzinalo lingamveke ngati nkhani yaikulu, koma musadandaule, tiyeni tisunge zinthu mosavuta.

Nanga kodi vuto la mtima losatsekeka kwa ventricle yakumanzere (LVNC) ndi chiyani?

Mwachidule, ichi ndi vuto lomwe limachitika pamene chipinda chapansi kumbali yakumanzere ya mtima wathu, Left Ventricle, sichikukula bwino. Taganizirani izi, nthawi zambiri ventricle yakumanzere iyi ya mtima wathu ndi nyama yolimba kwambiri komanso yosalala. Ndi gawo lalikulu lomwe limapopera magazi kupita ku thupi lathu lonse. Koma mwa munthu amene ali ndi (LVNC) iyi, ventricle yakumanzere imakhala ngati siponji, yokhuthala pang'ono, komanso yokonzedwa ngati ukonde. Ili ndi mapiri, ngati mkati mwa buledi.

Kawirikawiri izi zimaonedwa ngati vuto la mtima lobadwa nalo. Izi zikutanthauza kuti mungakhale ndi vutoli mumtima mwanu kuyambira nthawi yomwe munabadwa . Ngati simunalandire chithandizo choyenera, (LVNC) iyi ingayambitse mavuto aakulu a mtima, kutanthauza matenda a mtima.

Kodi vuto la LVNC limakhudza bwanji magwiridwe antchito a mtima?

Tsopano taonani, ventricle yakumanzere ya mtima wathu ili ndi ntchito yofunika kwambiri. Ndi iyi yomwe imapompa magazi olemera mpweya kuchokera m'mapapo kupita ku thupi lonse. Monga injini yamadzi. Komabe, pamene vutoli la (LVNC) lachitika, ventricle yakumanzere, yomwe ili ngati siponji, silingathe kupumula bwino. Izi zikutanthauza kuti, imakhala ndi vuto lomangirira ndikukankhira magazi patsogolo, kapena kupumulanso kuti iwadzaze ndi magazi. Chifukwa chake, zotsatira zake ndi zakuti ntchito yopopera magazi kupita ku thupi lonse sikuchitika bwino . Ichi ndichifukwa chake mavuto osiyanasiyana amayamba kubwera.

Kodi vutoli lotchedwa LVNC ndi losowa bwanji?

Uwu ndi matenda osowa kwambiri. Malinga ndi akatswiri azachipatala, anthu pafupifupi khumi ndi awiri okha pa miliyoni imodzi amapezeka ndi matendawa chaka chilichonse. Komabe, chiwerengero chenicheni chikhoza kukhala chokwera kwambiri . Chifukwa chake n'chakuti anthu ena sasonyeza zizindikiro zilizonse. Kenako sapita kwa dokotala, motero sapezeka ndi matendawa.

Kodi zizindikiro za LVNC ndi ziti?

Ichi ndiye chinthu chofunikira kwambiri. Anthu ena sangasonyeze zizindikiro zilizonse . Komabe, ena akhoza kukhala ndi mavuto aakulu a mtima. Mwachitsanzo, imfa yadzidzidzi ya mtima ingachitike. Pafupifupi anthu awiri pa atatu omwe ali ndi LVNC ali pachiwopsezo chotenga matenda a mtima .

Chabwino, tiyeni tiwone mtundu wa zizindikiro zomwe munthu amene ali ndi (LVNC) angasonyeze:

Zizindikiro zomwe zimawonedwa kawirikawiri :

• Magazi amaundana . Izi ndi zoopsa kwambiri, chifukwa ngati magazi amaundanawa apita ku ubongo kapena m'mapapo, zingakhale vuto lalikulu.
• Mungakhale ndi vuto lopuma mutagona pabedi.
• Kukomoka .
• Kugunda kwa mtima - Izi zingamveke ngati ng'oma ikugunda mkati mwa chifuwa, kapena ngati mtima ukuthamanga.
• Kulephera kuchita masewera olimbitsa thupi, kupuma movutikira ngakhale mutachita masewera olimbitsa thupi pang'ono (Dyspnea) .
• Kusakhazikika kwa mtima (arrhythmia) .
• Kutupa kwa miyendo (Lymphedema) - makamaka m'makolo.
• Kupuma movutikira / Kulephera kupuma - Kumva ngati walephera kupuma ngakhale mutayesetsa pang'ono.

N’chifukwa chiyani vuto la LVNC limachitika? Kodi zimayambitsa chiyani?

Nthawi zambiri, vuto la (LVNC) limeneli limayamba chifukwa cha kusintha kwa majini (mutation ya majini) komwe kumachitika musanabadwe. Ichi ndi chinthu chovuta kwambiri. Kusintha kwa majini kumeneku kungachitike mwachisawawa, kutanthauza popanda chifukwa, kapena kungachokere kwa makolo anu. Izi zikutanthauza kuti kungakhale chinthu chomwe chimachitika m'mabanja. Tangoganizani, mabanja ena ali ndi chiwerengero chachikulu cha matenda a mtima amtunduwu.

Komanso, akazi ochepa kwambiri amatha kukhala ndi LVNC koyamba panthawi ya mimba popanda chifukwa chomveka. Madokotala amaganiza kuti izi zitha kukhala chifukwa cha kupsinjika kwa minofu ya mtima panthawi ya mimba. Kwa akazi ena, zizindikirozi zimatha akabereka. Koma kwa ena, LVNC ikhoza kukhala ndi zotsatirapo za nthawi yayitali.

Kodi madokotala amazindikira bwanji vuto la LVNC?

Dokotala adzakuyesani kangapo kuti adziwe ngati muli ndi vuto la (LVNC) kapena ayi. Tiyeni tiwone zomwe zili:

• Echocardiogram: Izi zimayang'ana momwe mtima wanu ukupopera magazi, momwe ma valves akugwirira ntchito, komanso ngati pali vuto lililonse ndi ma valves. Zili ngati ultrasound scan ya mtima. Apa ndi pomwe mumawona koyamba momwe ventricle yakumanzere imakhalira ndi siponji.
• Electrocardiogram (ECG): Iyi imayesa momwe magetsi a mtima wanu amagwirira ntchito. Imatha kuzindikira mavuto aliwonse okhudza kugunda kwa mtima wanu.
• Mayeso apadera ojambulira: Izi zikuphatikizapo ma CT scan a mtima ndi magnetic resonance imaging (MRI). Izi zitha kuwonetsa kapangidwe ka mtima, monga momwe mtima umapangidwira komanso makulidwe a makoma ake. Mu LVNC, mawonekedwe ofanana ndi siponji amaonekera bwino pama scan awa.
• Coronary angiogram: Iyi imayesa momwe magazi amayendera kudzera m'mitsempha ya mtima yomwe imapereka magazi kumtima, komanso ngati pali zotsekeka zilizonse. Nthawi zina mayesowa angafunikenso kuti athetse matenda ena a mtima.

Kodi mankhwala a matenda a LVNC ndi ati?

Chithandizo cha LVNC chimasiyana malinga ndi zizindikiro zanu. Si aliyense amene amalandira chithandizo chofanana. Mwachitsanzo, ngati muli ndi vuto la mtima, dokotala wanu angakupatseni mankhwala monga:

• Mankhwala oletsa kusintha ma enzyme a Angiotensin (ACE inhibitors): Mwachitsanzo, benazepril (Lotensin®) kapena lisinopril (Prinivil®, Zestril®) kapena sacubitril-valsartan (Entresto®) (mankhwala oletsa angiotensin-neprilysin). Mankhwalawa amagwira ntchito popumitsa ndi kutsegula mitsempha yanu yamagazi (mitsempha ndi mitsempha) kuti magazi aziyenda mosavuta kudzera mwa iwo. Izi zimachepetsa ntchito ya mtima.
• Beta-blockers: Mwachitsanzo, metoprolol (Lopressor®, Toprol XL®) kapena atenolol (Tenormin®). Izi zimaletsa mahomoni ena (monga adrenaline), kuchepetsa kuthamanga kwa magazi ndi kuwongolera kugunda kwa mtima.
• Digoxin (Digoxin®, Lanoxin®): Izi zimalamulira kugunda kwa mtima wanu, zimawonjezera mphamvu ya mtima wanu, komanso zimathandiza kuti magazi aziyenda bwino.
• Mankhwala ochepetsa mphamvu ya madzi m'thupi kapena "mapiritsi a madzi": Mankhwalawa amagwira ntchito popangitsa thupi kutulutsa mchere ndi madzi ochulukirapo kudzera mu mkodzo. Izi zimachepetsa kutupa ndipo zimachepetsa ntchito ya mtima.

Nthawi zina, ngati pali chiopsezo cha kulephera kwa mtima mwadzidzidzi, dokotala angalimbikitse kuyika chipangizo chotchedwa Implantable Cardioverter Defibrillator (ICD) pansi pa khungu la mtima. Ichi ndi chipangizo chaching'ono chogwiritsidwa ntchito ndi batire. Chimazindikira kamvekedwe ka mtima kofulumira komanso koopsa ndipo chimabweretsa kugwedezeka kwamagetsi kumtima kuti abwezeretse kamvekedwe ka mtima. Pazochitika zoopsa kwambiri, ngati chithandizo china sichikuyenda bwino, kuyika mtima wina kungakhale kofunikira.

Kodi vuto la LVNC limeneli lingachiritsidwe kwathunthu? Kodi lingasinthe?

Ayi. Pakadali pano palibe mankhwala a LVNC . Izi zikutanthauza kuti, sizingasinthe. Koma musadandaule. Chithandizo chingathandize kuti moyo wanu ukhale wabwino ndikuchepetsa mavuto omwe angabwere chifukwa cha matenda a mtima . Ndipo, monga ndanenera kale, nthawi zina pamakhala vuto lalikulu, kuyika mtima wina kungakhale kofunikira.

Kodi tingapewe bwanji vutoli la LVNC?

Palibe njira yopewera LVNC. Izi zili choncho chifukwa nthawi zambiri imayamba chifukwa cha majini. Komabe, ngati muli ndi kusintha kwa majini komwe kumayambitsa vutoli, kapena ngati mukuganiza kuti muli nalo (mwachitsanzo, ngati wina m'banja mwanu ali ndi vutoli), kuyezetsa majini kungathandize kwambiri.Mlangizi wa majini adzakufotokozerani zotsatira za mayeso anu kwa inu ndi banja lanu. Adzakuthandizani kumvetsetsa tanthauzo la kukhala ndi LVNC komanso chiopsezo chanu chopatsira ana anu matendawa.

Kodi pali matenda ena okhudzana ndi vuto la LVNC?

Inde. Nthawi zina vuto limeneli lotchedwa (LVNC) lingaonekenso ngati gawo la matenda ena a majini (syndromes). Izi ndi zovuta pang'ono, koma madokotala amaganiziranso matenda amenewa akamazindikira (LVNC). Nazi zitsanzo zingapo:

• Matenda a Barth
• Matenda a Noonan
• Matenda a Roifman
• Matenda a Toriello Carey

Kodi tsogolo la munthu amene ali ndi matenda a LVNC ndi lotani? Kodi nthawi yoti munthu akhale ndi moyo ndi yotani?

Chiyembekezo cha munthu amene ali ndi matenda a LVNC chingasiyane. Chimasiyana malinga ndi munthu. Ndi chithandizo chabwino, zizindikiro zimatha kuchepetsedwa , ndipo anthu ena amakhala ndi moyo wautali.

Matenda a mtima (LVNC) ndi matenda omwe angaphe anthu ambiri, koma nthawi zina sizimachitika nthawi zonse . Anthu ambiri omwe ali ndi matenda a mtima samwalira ndi matendawa. Chofunika kwambiri ndikuwonana ndi dokotala wa mtima nthawi zonse ndikuyesedwa . Iye angakuthandizeni kusamalira thanzi la mtima wanu ndikuchepetsa chiopsezo cha mavuto.

Ngati ine kapena mwana wanga ali ndi LVNC, ndi mafunso ati omwe ndiyenera kufunsa dokotala?

Ngati inu kapena mwana wanu ali ndi (LVNC), kapena ngati muli ndi nkhawa iliyonse, ndi bwino kufunsa dokotala wanu mafunso monga awa:

• Kodi ndi chifukwa chiyani chomwe chingayambitse vuto la LVNC la mwana wanga/wanga? (monga majini kapena china chake)
• Kodi mumalimbikitsa kuyezetsa majini a LVNC? Ngati ndi choncho, kodi zingakhale zofunikira kwa achibale ena?
• Kodi ndi mayeso otani omwe ine/mwana wanga amafunika kuti ndichite kuti ndizindikire matenda a LVNC? Kodi ndingayembekezere chiyani kuchokera kwa iwo?
• Kodi njira zochiritsira za LVNC ndi ziti? Ndi chithandizo chiti chomwe chili chabwino kwa ine/mwana wanga? Kodi pali zotsatirapo zilizonse pa chithandizochi?
• Ngati mwana wanga kapena ine tagwa mwadzidzidzi mtima, kodi zizindikiro zake ndi ziti? Kodi ndiyenera kuchita chiyani nthawi yomweyo?

Mafunso awa adzakuthandizani kukambirana ndi dokotala wanu ndikumvetsetsa bwino za vuto lanu.

Ndiye, ndi zinthu ziti zofunika kwambiri zomwe tiyenera kukumbukira kuchokera munkhaniyi?

Mtima wosagwira ntchito wa kumanzere kwa ventricle (LVNC) ndi matenda a mtima osowa, omwe nthawi zambiri amabadwa nawo. Apa ndi pamene ventricle yakumanzere ya mtima sikukula bwino. M'malo mokhala minofu yosalala komanso yolimba, imakhala yokhuthala komanso yolimba. Izi zimapangitsa kuti mtima usapompe magazi bwino.

Ngati muli ndi (LVNC),Chofunika kwambiri ndikuonana ndi dokotala wa mtima nthawi zonse ndikutsatira malangizo awo. Ngakhale kuti palibe mankhwala a izi, chithandizo chomwe dokotala wanu akukupatsani chingachepetse chiopsezo chanu cha zovuta ndikukweza moyo wanu. Ndikofunikira kuti musachite mantha ndikupeza chithandizo choyenera . Kumbukirani, simuli nokha, ndipo madokotala alipo kuti akuthandizeni.

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