Tiyeni tiphunzire za katemera wa Pegvaliase wa PKU.

Kodi inuyo kapena wina m'banja mwanu muli ndi vuto lotchedwa Phenylketonuria? Ngati ndi choncho, dokotala wanu mwina anakupatsani mankhwala otchedwa Pegvaliase. Popeza awa ndi mankhwala apadera, ndi zachilendo kukhala ndi mafunso ndi nkhawa zina zokhudza mankhwalawa. Lero, tiyeni tikambirane za mankhwalawa ndi zinthu zomwe muyenera kudziwa mukamawagwiritsa ntchito.

Kodi katemera wa Pegvaliase uyu ndi chiyani?

Mwachidule, Phenylketonuria (PKU) ndi vuto lomwe matupi athu sangathe kugaya bwino amino acid yotchedwa phenylalanine. Izi nthawi zambiri zimapezeka muzakudya zomwe timadya zokhala ndi mapuloteni ambiri. Pamene phenylalanine iyi imadziunjikira m'thupi la munthu yemwe ali ndi PKU, imasonkhana m'magazi ndipo imatha kuwononga, makamaka ubongo, pakapita nthawi.

Chifukwa chake, chomwe jakisoni wa Pegvaliase uyu amachita ndikuchepetsa kuchuluka kwa phenylalanine yosafunikira komanso yochulukirapo m'magazi. Nthawi zambiri imabwera pansi pa dzina la Palynziq.

Zinthu zomwe muyenera kuuza dokotala wanu musanamwe mankhwala

Musanayambe kumwa mankhwalawa, ndikofunikira kwambiri kulankhula ndi dokotala wanu za izi momveka bwino komanso moona mtima. Musabise chilichonse.

• Tiuzeni ngati muli ndi vuto lililonse la Pegvaliase kapena mankhwala ena aliwonse, chakudya, kapena utoto.
• Ngati muli ndi pakati kapena mukuyembekezera kutenga pakati, onetsetsani kuti mwanena zimenezo.
• Ngati ndinu mayi woyamwitsa, dziwitsani dokotala wanu za zimenezo.

Kutengera ndi izi, zidzakhala zosavuta kwa dokotala kusankha ngati mankhwalawa ndi oyenera kwa inu kapena ayi.

Kodi katemerayu angagwiritsidwe ntchito bwanji moyenera?

Iyi ndi jakisoni wopangidwa pansi pa khungu. Dokotala wanu kapena namwino nthawi zambiri amakupatsani malangizo omveka bwino a momwe mungadziperekere nokha kunyumba. Ndikofunikira kwambiri kutsatira malangizo awa molondola.

• Imwani mlingo woyenera, panthawi yoyenera: Imwani mankhwala pokhapokha ngati mwapatsidwa mlingo woyenera monga mwalangizidwira ndi dokotala. Musamwe mankhwala opitirira muyeso womwe mwalangizidwa.
• Tayani singano ndi ma syringe moyenera: Musataye singano ndi ma syringe ogwiritsidwa ntchito kale m'zinyalala. M'malo mwake, ziyikeni mu chidebe chapadera cha sharping. Ngati mulibe, funsani dokotala wanu.
• Kapepala kodziwitsa anthu za izi (MedGuide):Musanayambe chithandizo chilichonse, mudzapatsidwa kabuku kapadera ka 'MedGuide', komwe kali ndi tsatanetsatane wa mankhwalawo. Nthawi zonse muziwerenga mosamala.

Nanga bwanji ngati ndaphonya mlingo wa mankhwala?

Ngati mwadzidzidzi mwaphonya mlingo, musadandaule. Musamwe mlingo wophonya. Imwani mlingo wotsatira panthawi yanu yanthawi zonse. Musamwe mlingo wowirikiza kawiri.

Nanga bwanji ngati nditamwa mopitirira muyeso?

Ngati mukuganiza kuti mwamwa mankhwala ochulukirapo, imbani nthawi yomweyo ku National Poison Information Centre ku Colombo National Hospital, kapena pitani ku Emergency Treatment Unit (ETU) ya chipatala chapafupi. Izi ndi zadzidzidzi, musazengereze.

Zinthu zofunika kusamala kwambiri mukamagwiritsa ntchito mankhwalawa:

Gawo ili ndi lofunika kwambiri. Muyenera kusamala ndi zinthu izi nthawi yonse yogwiritsira ntchito mankhwalawa.

Kupweteka Kwambiri kwa Thupi

Choopsa chachikulu komanso chachikulu kwambiri cha mankhwalawa ndi kuthekera kwa vuto lalikulu la ziwengo, kapena pankhani yazachipatala, anaphylaxis. Izi ndi ngozi yowopsa kwambiri.

Pachifukwa ichi, dokotala wanu nthawi zambiri amalemba epinephrine auto-injector, jakisoni wapadera womwe ungagwiritsidwe ntchito pakagwa ngozi. Muyenera kukhala nawo nthawi zonse.

Tangoganizani kuti mwalandira jakisoni ndipo pakapita nthawi yochepa, mukuvutika kupuma, nkhope ndi milomo yanu zimatupa, ndipo mukumva chizungulire. Zimenezi zingatanthauze kuti muli ndi vuto lalikulu la ziwengo. Ngati zimenezo zitachitika, muyenera kulandira jakisoni wa epinephrine nthawi yomweyo ndikupita ku chipinda chadzidzidzi cha chipatala (ETU) mwamsanga.

Chifukwa cha chiopsezo ichi, dokotala wanu nthawi zambiri amakuuzani kuti mukhale ndi munthu wina panthawi yolandira jakisoni komanso kwa ola limodzi mutatha kulandira jakisoni. Izi zili choncho kuti ngati muli ndi vuto lalikulu la ziwengo, munthuyo athe kukuthandizani ndikukutengerani kuchipatala mwachangu.

Kuyezetsa kuchipatala nthawi zonse komanso kuwongolera zakudya

• Mayeso azachipatala: Dokotala wanu adzakuyang'anirani nthawi zonse mukamamwa mankhwalawa. Adzayitanitsanso mayeso a magazi nthawi zonse (magazi) kuti awone kuchuluka kwa phenylalanine m'magazi mwanu. Musawaphonye.
• Zakudya: Mukukumbukira pamene tinkalankhula za zakudya zapadera zomwe muyenera kutsatira pa PKU? Mukamamwa mankhwalawa, muyeneranso kutsatira zakudya zapadera zomwe mwapatsidwa. Musasinthe zakudya zanu popanda kufunsa dokotala wanu.

Zotsatirapo zoyipa za mankhwalawa

Monga mankhwala ena aliwonse, mankhwalawa akhoza kukhala ndi zotsatirapo zina. Musadandaule, koma ndikofunikira kudziwa izi.

Kodi pangakhale mavuto ndi mankhwala ena?

Inde, mankhwala ena amatha kusokonezana ndi katemerayu. Mwachitsanzo, zinthu monga katemera wa medroxyprogesterone acetate, womwe umagwiritsidwa ntchito poletsa kubereka kapena mankhwala a mahomoni.

Iyi si mndandanda wathunthu. Choncho, uzani dokotala wanu za mankhwala onse omwe mukumwa (kuphatikizapo mavitamini, mankhwala azitsamba, ndi zowonjezera). Komanso, uzani dokotala wanu ngati mumasuta kapena kumwa mowa.

Kodi mungasunge bwanji mankhwala moyenera?

Izi ndizofunikira kwambiri. Kuti mankhwala apitirize kukhala abwino, ayenera kusungidwa bwino.

• Mufiriji: Sungani mankhwala mufiriji pamalo otentha pakati pa madigiri 2 ndi 8 Celsius. Musawasunge mufiriji.
• Kutentha kwa chipinda: Ngati kuli kofunikira, mutha kusunga mankhwalawa kutentha kwa chipinda (madigiri 20-25 Celsius) kwa masiku 30.
• Chofunika kwambiri: Ndikofunikira kwambiri kuti musabwezeretse mankhwala mufiriji mutachotsa mufiriji. Ngati asungidwa kutentha kwa chipinda, ayenera kugwiritsidwa ntchito mkati mwa masiku 30. Pambuyo pa masiku 30, tayani mosamala mankhwala otsalawo.
• Musagwiritse ntchito mankhwala omwe atha ntchito.