Nthawi zina timamva zinthu monga, 'chotupa cha muubongo', 'Ndikudwala mutu ndipo ndidzachiyesa'. Zimandipangitsa mtima wanga kugwedezeka kwambiri ndikamva zinazake ngati zimenezo. Koma kodi mukudziwa, si zotupa zonse zomwe zimapangidwa muubongo zomwe ndi khansa yoopsa yomweyi. Pali zotupa zina zomwe zimakula pang'onopang'ono, zopanda vuto, kutanthauza kuti, sizimayambitsa khansa. Lero tikambirana za mitundu iwiri ya zotupa za muubongo, zomwe sizipezeka kawirikawiri, koma zofunika kuzidziwa. Izi ndi gangliocytoma ndi pineocytoma.
Kodi Gangliocytoma ndi Pineocytoma ndi chiyani?
Mwachidule, zonsezi ndi mitundu yosowa kwambiri, yopanda khansa - `yoyipa` ya zotupa za muubongo.
Gangliocytoma ndi mtundu wa chotupa chomwe chimakhudza mbali zina za dongosolo lanu la mitsempha (lomwe limadziwikanso kuti CNS).
Mtundu wina, pineocytoma, umakula mu pineal gland, kachiwalo kakang'ono komwe kali mkati mwa ubongo wanu. Pineal gland ndi kachiwalo komwe kamathandiza kulamulira tulo tathu. Tangoganizirani, kachiwalo kakang'ono aka n'kofunikira kwambiri pazinthu monga kugona usiku ndikudzuka m'mawa.
Mitundu yonse iwiri ya zotupa imakula pang'onopang'ono . Ndicho chifukwa chake nthawi zina zimatenga nthawi kuti zizindikiro ziwonekere. Madokotala nthawi zambiri amawachiza ndi opaleshoni ndipo nthawi zina ndi chithandizo cha radiation.
Ndani amene ali ndi mwayi waukulu wopeza mitundu iyi ya khansa ya muubongo?
Ndipotu, mtundu wa chotupa chotchedwa gangliocytoma ukhoza kufalikira mwa anthu azaka zilizonse. Izi zikutanthauza kuti ngakhale mwana wamng'ono kapena munthu wokalamba akhoza kukhala pachiwopsezo. Komabe, nthawi zambiri chimapezeka mwa achinyamata azaka zapakati pa 10 ndi 30 .
Matenda a Pineocytoma nthawi zambiri amakhudza akuluakulu, kutanthauza anthu azaka zapakati pa 20 ndi 64. Avereji ya zaka zomwe munthu amadwala matendawa ndi pafupifupi zaka 38.
Ndi mbali ziti za dongosolo lathu la mitsempha (CNS) zomwe ziphuphu za gangliocytoma zimayambira?
Ma gangliocytomas nthawi zambiri amakula m'magawo a ubongo wanu otchedwa temporal lobes . Awa amakhala kumbuyo kwa makutu anu. Ma temporal lobes awa amathandiza kulamulira zinthu monga kukumbukira kwanu, kumva, ndi malingaliro. Tangoganizirani, mukukumbukira chochitika chakale, kumvetsera nyimbo ndikusangalala nayo, ndikumva kusangalala kapena chisoni chifukwa cha ntchito ya ziwalozi.
Si zokhazo, chotupachi chingayambikenso m'malo otsatirawa pathupi lanu:
- Chigawo cha ubongo: Ichi ndi gawo la ubongo wanu longa mlatho lomwe limalumikiza gawo lapamwamba la ubongo wanu (ubongo), msana, ndi cerebellum. Limatumiza zizindikiro zomwe zimayang'anira ntchito zofunika monga kupuma kwanu ndi kugunda kwa mtima.
- Cerebellum:Gawo ili la ubongo wanu, lomwe lili kumbuyo kwa mutu wanu, limalamulira kuyenda bwino kwanu, kuyenda kwanu, komanso kuona kwanu. Taganizirani izi, gawo ili la ubongo wanu ndi lomwe limakusungani muli chilili mukamayenda, limakutetezani kuti musagwe, komanso limakuthandizani kufikira kuti mugwire mpira.
- Pansi pa ventricle yachitatu: Iyi ndi mphako yopapatiza kutsogolo kwa ubongo. Imateteza ubongo ku kuvulala ndipo imathandiza kusuntha zakudya ndi zinyalala.
- Msana: Iyi ndi njira yaikulu yomwe imanyamula zizindikiro za mitsempha kuchokera muubongo kupita ku thupi lanu komanso kuchokera m'thupi lanu kupita ku ubongo wanu. Zizindikiro za mitsempha izi ndi zomwe zimakupangitsani kumva zinthu (kutentha, kuzizira, kupweteka) ndikusuntha thupi lanu.
Kodi kusiyana pakati pa pineal cyst ndi pineocytoma ndi kotani?
Ichinso ndi chinthu chomwe chingasokoneze anthu ambiri. Taganizirani izi, pineal cyst ndi thumba lodzaza ndi madzi kapena mpweya . Lili ngati chithupsa chamadzi. Izi nthawi zambiri zimapezeka mwangozi panthawi yojambula. Komabe, pineocytoma ndi chotupa chomwe chimapangidwa ndi magulu ambiri a maselo osazolowereka .
Ma pineal cysts nthawi zambiri sakula, zomwe zikutanthauza kuti sasintha kukula kwake kawirikawiri. Komabe, ma pineocytomas amakula pang'onopang'ono. Komabe, onsewa ndi matenda abwinobwino (osakhala khansa). Izi zikutanthauza kuti si khansa.
Kodi zizindikiro zomwe zimayambitsidwa ndi matenda amenewa ndi ziti?
Nthawi zambiri, simungakhale ndi zizindikiro zilizonse ngakhale mutakhala ndi gangliocytoma. Nthawi zina, madokotala amapeza kuti matendawa amapezeka mwangozi akamayesa kujambula zithunzi (monga MRI kapena CT scan) kuti apeze vuto lina.
Komabe, mitundu yonse iwiri ya zotupa, gangliocytoma ndi pineocytoma, ingayambitse matenda ena okhala ndi zizindikiro zosiyana.
Zizindikiro zodziwika bwino za Gangliocytoma
Chotupa ichi chingayambitse zizindikiro monga:
- Kusintha kwa kayendedwe: Monga kulephera kulamulira minofu. Mwachitsanzo, kunjenjemera, kufooka, kufooka. Tangoganizirani, mwadzidzidzi mukupeza zovuta kugwira kapu, kapena miyendo yanu imamva ngati ikugwa mukamayenda.
- Kusintha kwa momwe munthu akumvera: Kumva dzanzi m'malo ena, monga kumva kunjenjemera mwendo.
- Mavuto olankhula: Kulankhula movutikira, ngati kuti simungathe kulankhula. Simungathe kunena zomwe mukufuna kunena momveka bwino.
- Kusintha kwa masomphenya: Masomphenya akhoza kukhala osawoneka bwino, kuoneka ngati mukuwona mbali ziwiri, ndipo nthawi zina zingamveke ngati mukutaya gawo la masomphenya anu.
Kodi Gangliocytoma ingayambitse matenda aakulu?
Inde, chotupa ichi chingayambitse matenda ena aakulu. Mwachitsanzo:
- Matenda a dongosolo la endocrine:Izi ndi zinthu zomwe zimachitika pamene kuchuluka kwa mahomoni opangidwa ndi tiziwalo ta m'thupi lanu kukuwonjezeka kapena kuchepa. Izi zitha kusokoneza ntchito zambiri za thupi lanu.
- Kugwidwa ndi khunyu: Mwina munamvapo izi, kutaya mwadzidzidzi chidziwitso ndi kugwedezeka. Zotupa izi zingayambitse vutoli mwa kulimbitsa ubongo.
- Kupanikizika kwambiri muubongo: Izi zingayambitse mutu, nseru, kusanza, ndi chisokonezo. Zingamveke ngati mutu wanu ukukanikizidwa kuchokera mkati.
- Matenda a Lhermitte-Duclos (LDD): Ichi ndi chotupa chosowa kwambiri komanso chopanda vuto. Chimayamba mu cerebellum yanu. Nthawi zina chimatchedwa dysplastic gangliocytoma ya cerebellum. Munthu amene ali ndi LDD akhoza kukhala ndi mutu, nseru, madzi muubongo (hydrocephalus), kuvutika kuyenda komanso kutaya bwino (ataxia), komanso mavuto a masomphenya. Anthu omwe ali ndi LDD angakhalenso ndi vuto la majini lotchedwa Cowden syndrome, lomwe limayambitsa zotupa pakhungu komanso chiopsezo chowonjezeka cha khansa.
Zizindikiro zodziwika bwino za Pineocytoma
Pineocytoma ingayambitse madzimadzi muubongo mwanu, zomwe zimapangitsa kuti kuthamanga kwa magazi kuchuluke. Izi zimatchedwa hydrocephalus . Ngati muli ndi hydrocephalus, mutha kuwona zizindikiro monga:
- Mavuto a kulinganiza bwino zinthu: Kutaya kulinganiza bwino zinthu mukuyenda, kumva ngati kuti mugwa.
- Mavuto oyenda ndi maso (`Parinaud syndrome`): Kuvutika kuyang'ana mmwamba, makamaka mukayang'ana patsogolo. Mwina simungathe kusuntha maso onse awiri nthawi imodzi.
- Mutu: Mungakhale ndi mutu waukulu komanso wopitirira. Nthawi zina ululuwu umakula kwambiri mukadzuka m'mawa.
- Mavuto okumbukira: Kuiwala zinthu, kuvutika kukumbukira zinthu zatsopano.
- Kusanza ndi kusanza: Izi zitha kukhala zoipitsitsa, makamaka m'mawa.
- Matenda a tulo: Kusagona mokwanira, kapena kugona kwambiri. Izi zili choncho chifukwa chakuti pineal gland imagwira ntchito m'tulo.
- Kuvuta kuyenda: Zikumveka ngati simungathe kuyenda, miyendo yanu ikugwedezeka.
Kodi chifukwa chenicheni cha matenda a ubongo amenewa n’chiyani?
Monga zotupa zina zambiri, ma gangliocytomas ndi pineocytomas amakula pakasintha malangizo a majini a maselo athu. Taganizirani izi motere: maselo m'thupi lathu ali ngati mafakitale ang'onoang'ono. Amalandira malangizo ogwirira ntchito. Malangizo awa akasintha, maselo amayamba kugawikana mosalamulirika. Pamenepo ndi pamene amapanga chotupa.
Komabe, ofufuza sakudziwabe kuti ndi "choyambitsa" chiti chomwe chimayambitsa kusinthaku. Izi zikutanthauza kuti, palibe yankho lomveka bwino la chifukwa chake maselowa amayamba kuchita motere mwadzidzidzi.
Komabe, apeza kuti matenda a Cowden, omwe amagwirizanitsidwa ndi matenda a Lhermitte-Duclos, amayamba chifukwa cha kusintha kwa majini otchedwa PTEN. Jini ya PTEN iyi imapanga mapuloteni omwe amathandiza kulamulira momwe maselo amakulira ndikugawikana. Chifukwa chake, majini a PTEN akasinthidwa, kupanga mapuloteniwo kumasiya, ndipo maselo amayamba kukula mosalamulirika.
Kodi madokotala amazindikira bwanji zotupa izi? (Kuzindikira)
Ngati muli ndi zizindikiro izi, dokotala adzakufunsani kaye za zizindikiro zanu komanso ngati pali aliyense m'banja mwanu amene wakhalapo ndi matendawa ('mbiri ya thanzi la banja'). Kenako, adzakuyesani. Adzakuyesani 'mayeso a mitsempha', makamaka mayeso a mitsempha yanu . Izi zidzafufuza zotsatirazi:
- Momwe maso ndi pakamwa panu zimayendera.
- Mphamvu ya minofu.
- Kusinthasintha (monga ngati mwendo udzadumpha ukamenyedwa pa bondo ndi nyundo yaying'ono)
Komanso, dokotala akhoza kuchita mayeso awa:
- Kujambula Magnetic Resonance (MRI): Iyi ndi njira yoyesera yopanda ululu. Imagwiritsa ntchito maginito akuluakulu, mafunde a wailesi, ndi kompyuta kuti ipange zithunzi zomveka bwino za ziwalo ndi kapangidwe ka thupi lanu. Imagwiritsidwa ntchito kuona ngati pali zotupa zilizonse, kukula kwake, ndi komwe zili.
- Kujambula kwa CT (computed tomography): Izi zimagwiritsa ntchito X-ray ndi kompyuta kuti zipange zithunzi za minofu ndi mafupa anu ofewa. Monga MRI, imagwiritsidwa ntchito kupeza ndikuwunika zotupa.
- Kuyezetsa magazi: Izi zitha kuchitika kuti muwone ngati muli ndi kuchuluka kosazolowereka kwa melatonin m'magazi anu (makamaka ngati muli ndi pineocytoma, chifukwa imakhudzana ndi pineal gland).
- Kuboola msana (kuboola msana): Izi zimaphatikizapo kutenga chitsanzo cha madzi a m'mitsempha ya ubongo (CSF) omwe amazungulira ubongo wanu ndi msana wanu ndikuyang'ana maselo a chotupa.
- Kufufuza za khansa: Izi zimaphatikizapo kutenga zitsanzo zazing'ono za maselo ochokera ku chotupacho ndikuwayesa mu labu kuti adziwe mtundu weniweni wa chotupacho. Madokotala nthawi zambiri amagwiritsa ntchito njira zosavulaza kwambiri monga endoscopy kapena stereotactic needle biopsy.
Kodi Gangliocytoma imachiritsidwa bwanji?
Tangoganizirani kuti muli ndi gangliocytoma, koma mulibe zizindikiro zilizonse. Pa nthawi imeneyo, dokotala wanu adzakuuzani kuti, "Tiyeni tiwone." Izi zikutanthauza kuti, adzakuuzani kuti mubwere kudzayezetsa nthawi zonse kuti muwone ngati muli ndi zizindikiro zatsopano, kapena ngati chotupacho chasintha kapena chakula. Angachitirenso zinthu monga kuyesa zithunzi ndi kuyesa magazi.
Koma,Ngati mukufuna chithandizo, madokotala nthawi zambiri amachita opaleshoni ya ubongo kuti achotse chotupacho. Mwamwayi, ma gangliocytomas sangabwererenso mutachotsa chotupacho.
Kodi Pineocytoma imachiritsidwa bwanji?
Nthawi zina pineocytoma, madokotala amatha kuchita opaleshoni ya ubongo kuti achotse chotupa chonse kapena gawo lake. Angagwiritsenso ntchito chithandizo chotchedwa radiation therapy .
Pa opaleshoni, ngati muli ndi hydrocephalus (vuto lomwe ubongo umadzaza ndi madzi ndipo kuthamanga kwa magazi kumawonjezeka), madokotala angaike chubu chaching'ono cha pulasitiki chotchedwa shunt mu ubongo wanu. Shunt iyi imachotsa madzi owonjezera a ubongo mu ubongo wanu, kuchepetsa kuthamanga kwa magazi mkati mwa mutu wanu. Izi zitha kuchepetsa kwambiri zizindikiro zanu.
Kodi pali njira yomwe tingapewere kuti zotupa za muubongo izi zisapangidwe?
Chabwino, palibe chomwe mungachite kuti mulepheretse zotupa izi kuti zisapangidwe . Monga tanenera kale, zimapangika maselo akasintha ndikuyamba kugawikana mosalamulirika. Pokhapokha ngati zikugwirizana ndi matenda a Cowden, ofufuza sakudziwabe chomwe chimayambitsa kusintha kumeneku. Matenda a Cowden amayamba chifukwa cha kusintha kwa majini omwe amalamulira kukula kwa maselo. Chifukwa chake, ichi si chinthu chomwe tingathe kulamulira.
Kodi chingachitike n’chiyani ngati muli ndi chotupa chonga ichi? Kodi mungayembekezere chiyani?
Nthawi zambiri, mutachita opaleshoni yochotsa chotupachi, mwayi woti chibwererenso umakhala wochepa kwambiri . Zimenezi n’zotonthoza kwambiri, sichoncho? Zimenezi zikutanthauza kuti mutha kukhala moyo wabwinobwino mutalandira chithandizo. Komabe, monga momwe dokotala akunenera, ndikofunikira kupita kukayezetsa matenda ena.
Kodi ndiyenera kupita kwa dokotala liti?
Kutengera ndi matenda anu, dokotala wanu angakupatseni nthawi yokumana ndi dokotala nthawi zonse kuti ayang'anire thanzi lanu lonse. Ngati munachitidwa opaleshoni kuti muchotse chotupa, angakulangizeninso kuti muyesedwe kuti muwone ngati chotupacho chabwerera kapena ngati chotupa chatsopano chapangidwa.
Chofunika kwambiri ndikuonana ndi dokotala nthawi iliyonse ngati mukuona zizindikiro za chotupa chomwe mudakumana nacho kale, kapena ngati muwona kusintha kulikonse kwatsopano komanso kokayikitsa m'thupi lanu . Musazengereze, chabwino? Chifukwa mukazindikira vutoli mwachangu, zimakhala zosavuta kuchiza.
Zinthu zofunika kwambiri zomwe tiyenera kukumbukira kuchokera pa zomwe takambirana (Uthenga Wopita Nawo Kunyumba)
Gangliocytoma ndi pineocytoma ndi zotupa ziwiri za muubongo zomwe sizimakula bwino, zomwe zimakula pang'onopang'ono komanso mosaopsa zomwe zimapezeka mu dongosolo lanu la mitsempha (CNS) ndi pineal gland.
Ngakhale kuti izi si khansa, zingayambitse matenda osiyanasiyana omwe angakhudze moyo wanu. Kutengera mtundu wa chotupa chomwe muli nacho, madokotala amatha kuchichiza ndi opaleshoni kapena chithandizo cha radiation. Zotupazi sizingabwererenso mutazichotsa ndi opaleshoni.
Ngati muli ndi chotupa chosaopsa ngati ichi, lankhulani ndi dokotala wanu za njira zomwe mungasankhire chithandizo, zomwe mungayembekezere mutalandira chithandizo, komanso zomwe muyenera kudziwa zokhudza kukhala ndi chotupa chamtunduwu. Musamabise chilichonse, mverani chilichonse . Chidzakupatsani mphamvu. Musachite mantha, chofunika kwambiri ndikudziwa zinthu izi ndikutsatira malangizo a dokotala wanu.
` Zotupa za muubongo, gangliocytoma, pineocytoma, CNS, pineal gland, zizindikiro, chithandizo











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