Tangoganizirani, mwana wanu, makamaka mnyamata wamng'ono, mwadzidzidzi amayamba kugona kwa masiku ambiri. Ngakhale mutayesa kumudzutsa, amangogonanso. Amagona nthawi zonse kupatula kudya ndi kupita kuchimbudzi. Kodi pali mayi kapena bambo amene angaope akaona chinthu chonga ichi? N'zovuta kudziwa ngati ichi ndi vuto la maganizo kapena matenda ena. Lero tikulankhula za vuto losowa lomwe limayambitsa kugona kwambiri komwe kumatenga masiku ambiri m'njira yosazolowereka. Ndi Kleine-Levin Syndrome, kapena KLS mwachidule.
Kodi matenda a Kleine-Levin (KLS) ndi chiyani kwenikweni?
Mwachidule, matenda a Kleine-Levin Syndrome (KLS) ndi matenda osowa kwambiri okhudza kugona. Amafala kwambiri mwa anyamata aang'ono . 70% ya omwe ali ndi vutoli ali m'gulu la matenda amenewa.
Chizindikiro chachikulu cha matendawa ndi kugona tulo topitirira muyeso. Pa nthawi imeneyi, wodwalayo amatha kuoneka wathanzi komanso wabwinobwino. Ndiko kuti, popanda zizindikiro zilizonse.
Zizindikiro zimenezi zimagwirizana ndi gawo lofunika kwambiri la ubongo wathu. Ndilo hypothalamus . Gawo laling'ono limeneli limalamulira zinthu zambiri monga kugona kwathu, njala, ludzu, chilakolako, ndi chilakolako chogonana. Amakhulupirira kuti pankhani ya KLS, ntchito ya hypothalamus iyi imasokonekera kwakanthawi.
Malinga ndi zamankhwala, KLS imagawidwa m'gulu la matenda otchedwa hypersomnia, kutanthauza kugona kwambiri. Komabe, chifukwa zizindikiro zake zina zimafanana ndi matenda amisala, nthawi zina matendawa amaonedwa molakwika ngati matenda monga kuvutika maganizo.
Nkhani yabwino ndi yakuti zizindikirozi zimachepa pang'onopang'ono ndi ukalamba. N'zosowa kwambiri kuona zizindikiro za KLS mwa munthu wazaka zoposa 50.
Kodi pali chifukwa chenicheni cha KLS?
Ofufuza sanathe kunena motsimikiza chomwe chimayambitsa vutoli, koma akukayikira zinthu zina.
Kawirikawiri, vuto limeneli limayamba chifukwa cha matenda ena monga chimfine, chimfine, kapena matenda ena opatsirana ndi mavairasi .
Kuphatikiza apo, ofufuza ena amakhulupirira kuti kuvulala mutu, matenda, kapena matenda a chitetezo chamthupi kungakhale chifukwa chake. Komabe, si matenda obadwa nawo. N'zosowa kwambiri kuti anthu angapo a m'banja limodzi adwale matendawa.
Kodi zizindikiro za matenda a KLS ndi ziti?
Monga tanenera kale, mu matendawa, zizindikiro zimawonekera mu mawonekedwe a zochitika 'zadzidzidzi'. Gawo limodzi limatha kukhala kuyambira sabata imodzi mpaka miyezi iwiri . Pa avareji, pakhoza kukhala zochitika ziwiri kapena khumi ndi ziwiri pachaka.
Munthawi imeneyi, mutha kuwona kusintha kwakukulu pa khalidwe ndi thupi la wodwalayo. Kuwonjezera pa kugona kwambiri, zizindikiro zina zambiri zimaonekera.
| Chizindikiro | Kufotokozera |
|---|---|
| Kugona mopitirira muyeso | Kugona maola pafupifupi 20 patsiku, osadzuka kupatulapo zinthu zofunika monga kudya kapena kupita kuchimbudzi. |
| Kusintha kwa khalidwe | Kukwiya popanda chifukwa, kukhala wankhanza, kusaganizira za ena, kuvutika maganizo, ndi nkhawa. |
| Kudya kwambiri | Kudya kwambiri kuposa momwe mumadyera nthawi zonse. Nthawi zina mungayesedwe kudya zinthu zachilendo. |
| Kugonana ndi amuna kapena akazi okhaokha | Kuwonjezeka kwa chilakolako chogonana komanso kulankhula kapena kuchita zinthu pafupipafupi. |
| Kusokonezeka ndi kuthawa zenizeni | Kumva ngati waulesi, wosokonezeka, komanso wolota ngakhale utakhala maso. Nthawi zina, ukhoza kuona zinthu zomwe sizilipo (zinthu zolota). |
| Kukumbukira ndi kusamala | Kuiwala zochitika, kulephera kuyang'ana kwambiri pa chinthu china. |
Popeza zochitika zimenezi zingayambe mwadzidzidzi, popanda chenjezo lililonse, anthu ambiri omwe ali ndi KLS amavala zinthu ngati zodzikongoletsera zachipatala zomwe zimafotokoza bwino za matenda awo.
Kodi mungazindikire bwanji matendawa? (Kuzindikira)
Kuzindikira izi n'kovuta pang'ono chifukwa palibe kuyezetsa magazi kapena kusanthula komwe kumachitika. Choncho madokotala amayesa kuchotsa matenda ena omwe ali ndi zizindikiro zofanana. Timatcha izi kuti 'kusazindikira'.
Matenda a KLS nthawi zambiri amatha kugwirizanitsidwa ndi izi:
- Matenda a Bipolar kapena Kuvutika Maganizo
- Matenda a Narcolepsy, vuto lina la kugona
- Khunyu
- Matenda a Multiple Sclerosis
- Zotupa za muubongo
- Mutu wopweteka kwambiri
- Zotsatirapo za mankhwala ena (monga Benzodiazepines) kapena mankhwala osokoneza bongo
Choncho, dokotala wanu adzafika pa mfundo yolondola mwa kulankhula osati ndi inu nokha, komanso ndi makolo anu ndi achibale anu omwe adakumanapo ndi matendawa.
Kodi mankhwala a KLS ndi otani?
Palibe mankhwala a KLS pakadali pano. Komabe, pali mankhwala omwe angathandize kuchepetsa zizindikiro ndikuwonjezera nthawi pakati pa zochitika. Cholinga chachikulu cha chithandizo ndikuchepetsa zizindikiro.
Pofuna kuchepetsa kugona kwambiri, madokotala angapereke mankhwala opatsa mphamvu. Mwachitsanzo:
- Amphetamines
- Methylphenidate
- Modafinil
Kuphatikiza apo, mankhwala a lithiamu nthawi zambiri amagwiritsidwa ntchito bwino poletsa zizindikiro ndikuwonjezera nthawi pakati pa zochitika. Lithium ndi mankhwala omwe amagwiritsidwanso ntchito pochiza matenda amisala. Amakhulupirira kuti mankhwalawa ndi othandiza chifukwa cha kufanana pakati pa KLS ndi matenda ena amisala.
Koma ichi ndi chinthu chomwe muyenera kukumbukira . Sikoyenera kugwiritsa ntchito mankhwala aliwonsewa popanda upangiri wa dokotala wanu. Dokotala yekha ndi amene angadziwe bwino matendawa ndikukupatsani mankhwala oyenera pamlingo woyenera.
Uthenga Wopita Nawo Kunyumba
- Matenda a Kleine-Levin (KLS) ndi matenda osowa omwe amakhudza kwambiri anyamata aang'ono ndipo amachititsa tulo tofa nato tomwe timakhala kwa masiku ambiri.
- Zizindikiro zake sizimangophatikizapo kugona kwambiri, komanso kusintha kwa khalidwe, chilakolako chofuna kudya kwambiri, komanso kusokonezeka maganizo.
- Uwu si matenda amisala, koma vuto la mitsempha lomwe limakhudza hypothalamus ya ubongo.
- Kuzindikira matendawa n'kovuta ndipo kumafuna kuchotsa matenda ena omwe ali ndi zizindikiro zofanana.
- Ngati inu kapena munthu amene mumamudziwa aona zizindikirozi, musachite mantha ndipo funsani upangiri kwa dokotala wodziwa bwino ntchito mwamsanga.
- Pali mankhwala othandiza oletsa zizindikiro, koma ayenera kumwedwa pokhapokha ngati dokotala wanena.











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