Ese rimwe na rimwe bikugora guhaguruka ku ntebe, kuzamuka ingazi, cyangwa se gukora imirimo yoroshye nko gusokoza umusatsi wawe? Ese imitsi yawe yumva idafite imbaraga kandi nta buzima ifite? Impamvu y'iyi ndwara ishobora kuba indwara yitwa myopathy. Iri zina rishobora kuba ari rishya kuri wewe. Ariko ntugahangayike, tuzaganira kuri byose mu buryo bworoshye ushobora kumva.
Myopathy ni iki mu by'ukuri?
Mu magambo make, myopathy ni ijambo rusange risobanura intege nke z'imitsi yacu, imitsi ihuza n'amagufwa yacu ikadutwara. Tekereza umubiri wacu nk'imodoka. Iyi modoka ikoreshwa na moteri yitwa imitsi. Myopathy ni indwara aho imitsi iri muri iyi mitsi yangirika, bigatuma imbaraga z'iyo moteri zigabanuka. Iyi si indwara imwe, ahubwo ni itsinda ry'indwara.
Ese hari ubwoko bw'ingenzi bwa myopathy?
Yego, indwara ya myopathy ishobora kugabanywamo ubwoko bubiri bw'ingenzi. Ni nk'ibibazo bimwe na bimwe dukura kuva tuvutse ndetse n'ibindi bibazo bivuka uko tubayeho.
| Ubwoko bwa miyopathie | Mu magambo make ... |
|---|---|
| Myopathie y'Umurage | Izi ni indwara ziterwa n'ubusembwa bw'uturemangingo. Ni ukuvuga indwara ziterwa n'uturemangingo dufite inenge twarazwe na nyina cyangwa se. |
| Myopathie yabonetse | Ibi biterwa n'indi ndwara, ubwandu, imiti yafashwe, cyangwa indi mpamvu yo hanze mu buzima bwe. |
Noneho reka turebe ubwo bwoko mu buryo burambuye.
Myopathie y'Umurage
Ibi biterwa n'ibintu bigize imiterere y'umubiri, bityo akenshi biba ari ibyo mu muryango.
- Indwara za Myopathie zo mu gihe cy'ivuka:Izi ni indwara zibaho igihe cyo kuvuka. Hari abana bashobora kugaragaza ibimenyetso ako kanya. Ariko hari abantu bashobora kugaragaza ibimenyetso nyuma y’ubuzima, cyangwa ndetse no mu myaka ya nyuma y’ubuzima. Ikidasanzwe kuri ibi ni uko intege nke zigira ingaruka hafi ya zose mu mubiri, kandi akenshi zirushaho kwiyongera uko igihe kigenda gihita.
- Mitochondria Myopathies: Muri make, mitochondria ni bateri zitanga imbaraga ku turemangingo twacu. Iyo izi bateri zidakora neza, imitsi ntibona ingufu ikeneye, kandi iracika intege. Iyi ndwara ishobora kugira ingaruka ku mitsi gusa, ndetse no ku zindi ngingo zikenera ingufu nyinshi, nk'umutima, ubwonko, n'igogora.
- Myopathies ya Metabolic: Imitsi yacu ikenera imiti yihariye yitwa enzymes kugira ngo ikore neza. Iyi ndwara iterwa n'inenge iri mu turemangingo dukora izi enzymes. Muri iki gihe, hashobora kubaho ububabare bukomeye no guhindagura imitsi, cyane cyane mu bice nko mu bitugu no mu bibero, mu gihe cy'imyitozo ngororamubiri. Hari igihe indwara ikomeye yitwa ``Rhabdomyolysis``, aho imitsi icikagurika, ishobora kubaho.
- Kurwara imitsi: Ushobora kuba warigeze kumva iri zina mbere. Iyi ni indwara aho imitsi igenda icika intege buhoro buhoro bitewe no kubura poroteyine zikenewe kugira ngo imitsi ikomeze gukomera. Ibi bishobora kugira ingaruka ku mitsi y'amaboko, amaguru, ndetse rimwe na rimwe no mu maso no mu maso.
Myopathie yabonetse
Ibi si ibintu tuvukana, ahubwo ni ibintu bivuka bitewe n'impamvu zitandukanye mu buzima bwacu.
| Impamvu | Ingero n'ibisobanuro birambuye |
|---|---|
| Ibibazo by'ubudahangarwa bw'umubiri (Autoimmune/Inflammatory) | Ibintu bibaho iyo ubwirinzi bw'umubiri wacu (ubudahangarwa bw'umubiri) bwibasira ingirabuzimafatizo zabwo mu buryo butari bwo. |
| Uburozi cyangwa ibiyobyabwenge (Toxic Myopathy) | Hari ibintu bishobora kwangiza imitsi. Urugero, harimo kunywa inzoga nyinshi, guhumeka imyuka iva mu bwoko bumwe na bumwe bw'irangi, n'imiti imwe n'imwe (urugero: imiti igabanya cholesterol (statins), steroid (corticosteroids), n'imiti imwe n'imwe ikoreshwa mu kuvura agakoko gatera SIDA). |
| Ibibazo bya hormone (Endoprine Myopathies) | Intege nke z'imitsi zishobora guterwa n'imisemburo idakora neza mu mubiri. Urugero, harimo hypothyroidism cyangwa hypothyroidism ikora cyane (hyperthyroidism), ibibazo bya parathyroid hormones, n'indwara za adrenal gland. |
| Indwara (Myopathies Yanduye) | Indwara zitandukanye zishobora kugira ingaruka ku mitsi. Ingero zirimo: VIH, virusi nka grippe, indwara za bagiteri, n'indwara za parasites. |
| Kudahuza kwa Electrolyte | Kugabanuka cyangwa kwiyongera kw'ibinyabutabire by'ingenzi nka potasiyumu na manyeziyumu mu mubiri bigira ingaruka ku mikorere y'imitsi. |
| Indwara ikomeye ya Myopathy | Intege nke z'imitsi ziterwa no kurwara cyane ahantu nk'icyumba cyita ku barwayi barembye cyane (ICU), kumara igihe kirekire mu buriri, hamwe n'imiti ikomeye yatangwaga icyo gihe. |
Ni ibihe bimenyetso by'indwara ya myopathy?
Nubwo hari ubwoko bwinshi bwa myopathy, hari ibimenyetso byinshi bisanzwe bigaragara hafi ya byose.
- Intege nke z'imitsi: Intege nke, cyane cyane mu mitsi iri hafi y'igice cyo hagati cy'umubiri (ku bitugu, amaboko yo hejuru, ikibuno, n'amatako).
- Kunyeganyega kw'imitsi, gukomera no kubabara.
- Kumva unaniwe cyane nubwo wamaze gukora akazi gato.
- Kubura ingufu.
Ubu burwayi bukunze kugira ingaruka ku mpande zombi z'umubiri kimwe, bivuze ko ukuboko kw'ibumoso kumva gufite intege nke nk'ukuboko kw'iburyo.
Ubyumva ute kuri ubu ntege nke?
Ubu burwayi bw'imitsi bushobora gutuma gukora imirimo ya buri munsi bigorana. Tekereza...
- Ndetse n'imirimo yoroshye nko gusokoza umusatsi, kwambara imyenda no kwiyuhagira biragoye.
- Biragoye guhaguruka ku ntebe wicayeho.
- Kuzamuka ingazi birananiza cyane.
- Biragoye guterura ukuboko kwawe kugira ngo ufate ikintu ukoresheje ububiko buri hejuru y'umutwe wawe.
- Iyo ndushye gato, numva mfite ikibazo cyo guhumeka.
Uretse ibi, hari n'ibindi bimenyetso byihariye bishobora kugaragara bitewe n'ubwoko bwa myopathy. Urugero, bamwe mu bana bashobora gutinda gutangira kugenda no gusimbuka. Bashobora kudashobora kwiruka cyangwa gusimbuka iyo bakina na bagenzi babo. Bamwe bashobora kandi kugorwa no kumira no kuvuga amagambo mu buryo butunguranye iyo bavuga.
Namenya nte ko mfite iyi ndwara?
Niba ufite ibi bimenyetso, ikintu cy'ingenzi ugomba gukora ni ukubonana na muganga w'umuryango wawe. Azagukorera amateka arambuye y'ibimenyetso byawe, amateka y'ubuzima bw'umuryango wawe, n'imiti iyo ari yo yose ufata. Hanyuma azagukorera isuzuma ry'umubiri, nibiba ngombwa, akwohereze ku muganga w'inzobere, nka muganga w'indwara z'imitsi cyangwa rubagimpande.
Hashobora gukorwa ibizamini byinshi kugira ngo hemezwe ko indwara yanduye.
| Ikizamini | Ibi bigenzura iki? (Bigenzura iki?) |
|---|---|
| Ibipimo by'amaraso | Imisemburo irekurwa mu maraso iyo imitsi yangiritse (urugero: Creatine Kinase (CK)), urugero rw'amacandwe, urugero rw'imisemburo, n'ibimenyetso by'ibibazo by'ubudahangarwa bw'umubiri biragenzurwa. |
| Ikizamini cya EMG (Electromyography) | Ikizamini cyihariye cyohereza ibimenyetso by'amashanyarazi ku mitsi n'imitsi kugira ngo bipime imikorere yabyo n'ingano y'ibyangiritse. |
| Isuzuma rya MRI (Ishusho ya Magnetic Resonance) | Imiterere y'imitsi n'impinduka zabayemo biragaragara neza. |
| Ibipimo by'uturemangingo | Iyo habayeho gukeka ko hari indwara ya myopathy ivukanwa, iki kizamini gikorwa kugira ngo hemezwe niba hari inenge zikomoka kuri iyo ndwara. |
| Isuzuma ry'imitsi | Agace gato cyane k'ikibyimba gikekwaho karakurwaho hanyuma kagasuzumwa hakoreshejwe mikorosikopi kugira ngo hamenyekane neza indwara. |
Ni ubuhe buryo bwo kuvura indwara ya myopathy?
Ubuvuzi buterwa n'ubwoko bwa myopathy ufite. Nta buvuzi bungana bukwiriye bose.
- Ubuvuzi Rusange: Ubuvuzi bw'umubiri n'ubuvuzi bw'akazi ni ingenzi ku ndwara nyinshi za myopathic. Ibi bishobora gufasha gukomeza imbaraga z'imitsi no koroherwa no gukora imirimo ya buri munsi byoroshye.
- Ku bibazo by’ubudahangarwa bw’umubiri: Hatangwa imiti igabanya ubudahangarwa bw’umubiri, nka imiti igabanya ubudahangarwa bw’umubiri na kortikosteroidi.
- Ku ndwara zo mu mutwe zivukana: Nta muti uhamye uhari kuri izi ndwara nyinshi. Ariko ibimenyetso bishobora kugenzurwa no kunozwa ubuzima. Imiti mishya ubu iraboneka ku ndwara zimwe na zimwe (urugero: Duchenne muscular dystrophy, Pompe disease).
- Ku zindi ndwara zo mu bwoko bwa myopathies: Ubuvuzi bugamije impamvu nyamukuru itera myopathy. Urugero, iyo ari ikibazo cy’imisemburo, kirakosorwa, iyo ari ubwandu, imiti igabanya ubukana itangwa, cyangwa iyo biterwa n’umuti, umuti urahagarikwa.
Nkwiye kwiyitaho nte?
Nubwo indwara ya myopathy ari indwara y'igihe kirekire, ushobora kuyirwanya no kubaho ubuzima bwiza uhinduye uburyo ubayeho kandi ukayifata neza.
- Kurya indyo nziza kandi ifite intungamubiri. Indyo yuzuye irimo imboga n'imbuto nyinshi ni ingenzi cyane.
- Komeza gukora siporo. Irinde imyitozo ngororamubiri yoroheje. Ariko wibuke ko mbere yo gutangira gahunda iyo ari yo yose yo gukora siporo, ugomba kuvugana na muganga wawe akakubaza imyitozo ijyanye n'uburwayi bwawe.
- Komeza kugira ibiro bikwiye by'umubiri.
- Niba ugorwa no kumira, rya ibiryo byoroshye kandi byuzuyemo amazi. Kanda neza ibiryo hanyuma urye.
- Fata umuti wanditswe na muganga ku gihe nyacyo.
- Witondere impinduka mu mubiri wawe. Nubona impinduka cyangwa ibimenyetso byiyongera, menyesha muganga wawe ako kanya.
Ubutumwa bwo kujyana mu rugo
- Myopathy ni izina rusange ry'indwara nyinshi zituma imitsi icika intege.
- Ibi bishobora kuvukanwa (genetic) cyangwa bigakura mu buzima kubera izindi mpamvu.
- Intege nke z'imitsi, kunanuka, umunaniro ukabije ndetse n'utundi dukorwa duto ni byo bimenyetso by'ingenzi.
- Niba ufite ibi bimenyetso, ni ngombwa cyane gushaka inama kwa muganga vuba.
- Uburyo bwo kuvura buratandukanye bitewe n'icyateye iyo ndwara. Iyo habayeho ubuvuzi bukwiye, indwara nyinshi zishobora kugenzurwa neza kandi zigakomeza kubaho nk'uko bisanzwe.

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