Muviri wedu, kutaura chokwadi, muchina wakaoma uye unoshamisa. Kuti zvese zviri mumuchina uyu zvishande zvakanaka, mhando yakakosha yepuroteni inonzi 'enzymes' inokosha. Fungidzira, dzimwe nguva nekuda kwezvikonzero zvemajini, imwe enzyme ingasagadzirwa mumuviri wemunhu kana kuti ingangogadzirwa zvishoma. Pompe Disease chirwere chisingawanzoitiki asi chakakomba chinoitika nenzira iyi. Nhasi tichataura nezvekurapa kwakakosha kunopiwa kudzora chirwere ichi, kureva, mushonga unonzi Alglucosidase alfa.
Chii chinonzi Alglucosidase alfa?
Zvichitaurwa zviri nyore, Alglucosidase alfa ijekiseni rekunze reenzyme risina kukwana mumuviri wemunhu ane chirwere chePompe. Izvi zvakafanana nekuunza munhu wekunze kuti aite basa rakati kana mushandi asipo. Nzira iyi yekurapa inonzi Enzyme Replacement Therapy (ERT) musainzi yekurapa.
Chinhu chakakosha kurangarira pano ndechekuti iyi haisi mushonga wechirwere. Zvisinei, kurapwa uku kunogona kudzora zviratidzo, kuderedza kusasimba kwetsandanyama, uye kuvandudza hupenyu hwemurwere zvakanyanya. Mushonga uyu unogona kuwanikwa mumusika pasi pemazita emhando dzakadai se'Lumizyme' kana 'Myozyme'.
Zvinhu zvaunofanira kuudza chiremba wako usati watora mushonga uyu
Usati watanga chero kurapwa kwakatarwa, zvakakosha kuzivisa chiremba wako nezvenhoroondo yako yese yehutano. Kana chiremba wako aine hutano hwakakwana, kurapwa kwacho kuchava kwakachengeteka uye kunobudirira. Saka, kana chimwe chezvinotevera chichishanda kwauri, iva nechokwadi chekuzvitaura.
- Chirwere chemwoyo: Kana uine chirwere chemwoyo kana matambudziko ane chekuita nemoyo.
- Kutambudzika kwekufema: Kana uine chirwere chemapapu kana chero dambudziko rekufema.
- Kurwara: Kana uine allergies kune chimwe chinhu, unofanira kutiudza. Kunyanya:
- Kana wakambova neallergy yemushonga uyu kana chimwe chezvinhu zvirimo, zvakaita semannitol.
- Kana uine allergy kumapuroteni e hamster kana makonzo (izvi zvakakosha nekuti izvi zvinoshandiswa mukugadzira mimwe mishonga).
- Kana uine allergy kune chero mimwe mishonga, chikafu, zvinochengetedza kana madhayi.
- Kubata pamuviri: Kana uri nepamuviri parizvino, kana kuti uri kuedza kubata pamuviri munguva pfupi iri kutevera.
- Kana uri amai vanoyamwisa: Kana uri amai vari kuyamwisa mwana.
Kurapwa uku kunopiwa sei?
Mushonga uyu hausi mushonga wekumedza, uye hausi jekiseni rinogona kupiwa kumba.
Alglucosidase alfa inopinzwa netsinga (IVI). Zvichitaurwa zviri nyore, inopinzwa nenzira imwecheteyo nemushonga une saline.
Kurapwa uku kunongoitwa muchipatara kana kiriniki yakasarudzika, pasi pekutarisirwa kwakasimba kwevanachiremba nevashandi vekuchengeta varwere . Vacharamba vachitarisa kurova kwemoyo wako, BP, uye kufema kwako panguva yekurapwa.
Munopa vana vadiki izvi here?
Ehe, mushonga uyu unogona kunyorerwa kunyangwe vacheche vane mwedzi mumwe chete. Zvisinei, chiremba wevana chete ndiye anogona kuita sarudzo. Pane matanho akakosha ekudzivirira anofanira kutevedzerwa pakupa mushonga uyu kumwana.
Chii chaunofanira kuita kana ukanwa doro zvakanyanya?
Izvi zvinopihwa muchipatara, saka mikana yekuti izvi zviitike yakaderera. Zvisinei, kana uchifunga kuti watora mushonga uyu wakawandisa, zivisa vashandi vekurapa nekukasika. Kana paine emergency, unogona kufonera National Poisons Information Centre kuColombo National Hospital . Kana kuti unofanira kuenda kuEmergency Treatment Unit (ETU) iri pedyo.
Ko kana ndikatadza kurapwa?
Zvakakosha zvikuru kuenda kumusangano wako wakarongwa. Kana nekuda kwechimwe chikonzero usingakwanise kuenda, usachirega, asi fonera chiremba wako kana chipatara nekukasika kuti uronge rimwe zuva nenguva.
Ndezvipi zvinotarisirwa kuti zviitike?
Sezvinongoita chero mushonga upi zvawo, kurapwa uku kunogona kuva nemigumisiro yakaipa. Kunyange zvazvo yakawanda yacho iri midiki, pane zvimwe zvinhu zvatinofanira kungwarira zvikuru. Ngatitarisei izvi patafura kuti zvive nyore kunzwisisa.
| Rudzi rwemhedzisiro yakaipa | Hunhu |
|---|---|
| Migumisiro yakakomba inofanira kuziviswa kuna chiremba nekukasika |
|
| Migumisiro isingawanzova yakakomba, asi inofanira kutaurwa kuna chiremba kana ikaramba iripo |
Pane matambudziko here nemimwe mishonga?
Mushonga uyu kazhinji hauna hukama hwakawanda nemimwe mishonga. Zvisinei, zvakakosha kuudza chiremba wako nezvemishonga yese yauri kutora (kusanganisira mavhitamini nemiti), uye kana uchisvuta kana kunwa doro.
Mharidzo Yekuenda Nayo Kumba
- Alglucosidase alfa mushonga wechirwere chePompe unotsiva enzyme isipo mumuviri, asi hausi mushonga wechirwere chacho.
- Kurapwa uku kunongoitwa muchipatara chete, kuburikidza netsinga (infusion) pasi pekutarisirwa nachiremba.
- Usati watanga kurapwa, udza chiremba wako nhoroondo yako yese yehutano, kunyanya chero allergies.
- Tsvaga rubatsiro rwechiremba nekukasika kana ukaona zviratidzo zvakaita sekuoma kufema, kurwadziwa muchipfuva, kana kuti kusawirirana kwakanyanya.
- Usambofa wakarasikirwa nezuva rawakaronga kurapwa. Kana uine dambudziko, zivisa chiremba pachine nguva.
💬 Comments (0)
Hapana zvakataurwa parizvino. Isa mhinduro yako pano kekutanga.
Wedzera zvaunofunga