Unoziva nezveHemophilia C here? Ngatitaurei nezvechirwere ichi chisingawanzoitiki!

Dzimwe nguva kunyange kucheka kudiki kunotora nguva kuti ropa rimire kubuda, handiti? Kana kuti wakambonzwa here kuti mumwe munhu mumhuri mako ane chirwere chine chekuita neropa? Nhasi tichataura nezvechirwere cheropa chisingawanzoitiki, asi chakakosha kuziva nezvacho. Ichi chinonzi Hemophilia C.

Chii chinonzi Hemophilia C?

Zvichitaurwa zviri nyore, hemophilia C imhando isingawanzoitiki yehemophilia. Hemophilia chirwere chekuti ropa rako harigwambi zvakanaka, zvichireva kuti kana uchibuda ropa, rinomira zvishoma nezvishoma kana kuti harimbomira. Vanhu vane hemophilia C vane protein yeropa inonzi clotting factor , inonzi Factor XI , inobatsira kugadzika kweropa. Izvi zvinonziwo Factor XI Deficiency uye dzimwe nguva inonzi Rosenthal syndrome .

Zvisinei, zviratidzo zvehemophilia C zvinowanzova zvishoma pane zvemamwe marudzi ehemophilia (A naB). Zvisinei, vanhu vane hemophilia C vanogona kubuda ropa kupfuura zvakajairika panguva yekuvhiyiwa kana kuvhiyiwa kwemazino. Vanachiremba vanorapa izvi neplasma itsva yakaomeswa nechando, iyo inogadzirwa neropa rinobva kune vakapihwa. Plasma iyi inobatsira kuumbwa kweropa.

Hemophilia C chirwere chinowanzoitika here?

Kwete, ichi chirwere chisingawanzoitiki . Fungidzira, munyika yakaita seAmerica, munhu mumwe chete pavanhurume nevakadzi 100,000 vanowana hemophilia C. Kana tikaenzanisa nedzimwe mhando dzehemophilia, hemophilia A inobata vanhu vanosvika gumi nevaviri pavanhurume 100,000, uye hemophilia B inobata vanhu vanosvika vana pavanhurume 100,000. Vaongorori havasati vava nechokwadi chekuti hemophilia A kana B inobata vakadzi kangani.

Ndeapi musiyano uripo pakati pehemophilia A, B, naC?

Mhando nhatu dzese dzehemophilia zvirwere zveropa zvinogara nhaka . Kureva kuti, kushanduka kwemajini kunokanganisa maitiro ekugwamba kweropa. Asi pane misiyano midiki pakati pemhando nhatu idzi. Ngatitarisei kuti ndedzipi:

• Hemophilia A neHemophilia B zvinoitika kana munhu akagara nhaka jini rakachinja kubva kune mumwe wevabereki vake chaivo. Zvisinei, muhemophilia C, jini risingawanzoitiki rinogona kugara nhaka kubva kuvabereki vese .
• Kusiyana nevanhu vane hemophilia A kana B, vanhu vane hemophilia C havawanzova nematambudziko ekubuda ropa anokanganisa majoini kana tsandanyama . Uyu mutsauko wakakosha.
• Kazhinji, zviratidzo zvevanhu vane hemophilia A kana B zvinoonekwa nemazinga emapuroteni anogwamba ropa, kana kuti 'zvinhu zvinogwamba', muropa ravo. Semuenzaniso, munhu ane hemophilia A yakanyanya anenge aine mazinga akaderera echinhu ichocho. Asi zvinoshamisa kuti munhu ane hemophilia C anogona kunge aine mazinga akaderera echinhu ichocho, asi zviratidzo zvake zvinogona kunge zvisina kusimba .
• Hemophilia A naB zvinogona kuitika kuvanhu vemarudzi ese nemarudzi ese. Zvisinei, hemophilia C inowanikwa zvakanyanya muvanhu verudzi rweAshkenazi Jewish group . Izvi hazvirevi kuti hapana mumwe munhu anogona kuiwana, asi inowanikwa zvakanyanya pakati pavo.
• Hemophilia A naB zvinowanikwa zvakanyanya muvarume kupfuura vakadzi, asi hemophilia C inobata varume nevakadzi zvakaenzana .

Ndezvipi zviratidzo zve hemophilia C?

Vanhu vane hemophilia C vanogona kubuda ropa nguva dzose mushure mekuvhiyiwa kukuru, kukuvara kwakanyanya, kana kusununguka. Zvisinei, havabudi ropa risingadzoreki , uye ndipo panotanga kubuda ropa pasina chikonzero chakajeka.

Vanhu vane hemophilia C vanowanzo buda ropa zvisina kujairika mushure mekuvhiyiwa mazino, kubviswa mazino, kana kubviswa tonsillectomy.

Zvimwe zviratidzo zvinogona kusanganisira:

• Kubuda ropa mumhino nguva nenguva.
• Maronda pamuviri kunyangwe kubva kuchinhu chidiki diki.
• Ropa muweti .
• Kubuda ropa rakawanda mushure mekuchecheudzwa.
• Mavanga anorwadza uye akazvimba mushure mekuvhiyiwa.
• Kuvakadzi, kuenda kumwedzi kunogona kugara kwemazuva akati wandei, izvo zvinotora nguva yakareba zvisingawanzoitiki.

Ndezvipi zvikonzero zve hemophilia C?

Hemophilia C chirwere cheropa chinoberekwa nhaka . Chinoitika kana usina protein yeropa inonzi Factor XI , chimwe chezvinhu gumi nezvitatu zvinobatsira kudzikamisa kana kumisa kubuda kweropa. Izvi zvinokonzerwa nekuti hauna jini reF11 rakakodzera.

Kazhinji, jini iri reF11 rine mirairo yekugadzira Factor XI. Kana jini iri rikachinja, kureva kuti, kana rikava risina kujairika, hemophilia C inokura. Jini iri risina kujairika rinogona kusagadzira Factor XI yakakwana, kana kuti rinogona kusaita zvachose.

Varume nevakadzi vanogara nhaka hemophilia C chete kana vabereki vese vemuviri vakapfuudza jini rakachinja kumwana wavo . Kana mumwe munhu akagara nhaka jini rimwe chete reF11 uye jini rimwe chete risingajairiki, munhu iyeye anenge aine hemophilia C, asi haaratidzi zviratidzo.

Zvino, tarisa zvinogona kuitika kana vabereki vane jini iri risingawanzoitiki vakava nevana:

• Vana vanoberekwa nevabereki vane iyi F11 gene mutation vane mukana we25% wekuva nehemophilia C.
• Vana vanoberekwa nevabereki ivavo vane mukana we50% wekutakura chirwere ichi, zvichireva kuti vanongotakura jini racho vasina chirwere chacho.
• Vana vevabereki ivavo vane mukana we25% wekugara nhaka jini reF11 rakajairika.

Vanachiremba vanoongorora sei hemophilia C?

Unoziva here kuti vanachiremba vanoongorora sei hemophilia C? Vanotanga vakuongorora panyama yako . Zvadaro vanokubvunza nezvezviratidzo zvako, zvakaita sekubuda ropa mumhino kana kubuda ropa mushure mekuvhiyiwa mazino. Vanokubvunzawo nezvenhoroondo yemhuri yako uye kana paine munhu mumhuri yako ane hemophilia kana mamwe matambudziko eropa . Ruzivo urwu rwakakosha zvikuru pakuongorora chirwere chacho.

Ndezvipi zviedzo zvikuru zvinoshandiswa kusimbisa chirwere?

Chiremba wako achashandisa bvunzo mbiri huru kuti asimbise chirwere chako:

• Kuongororwa kwenguva yeropa kunoitwa partial thromboplastin (APTT): Iyi bvunzo inoshandiswa kuongorora hemophilia. Inobatsira chiremba wako kuziva kuti zvinotora nguva yakareba sei kuti ropa rako rigwambe .
• Kuongororwa kweropa: Kuongororwa kweropa uku kunoratidza rudzi rwehemophilia uye kuti yakanyanya sei .

Mune zvimwe zviitiko, chiremba wako anogona kukumbira mimwe miedzo mishoma:

• Kuverengwa kweropa kwakazara (CBC): Kuongororwa uku kunoyera uye kunoongorora masero eropa.
• Kuongororwa kwenguva yeprothrombin (PT): Izvi zvinotarisawo kuti ropa rako rinogwamba nekukurumidza zvakadii.
• Kuongororwa kweFibrinogen: Kuongororwa kweropa uku kunoyera huwandu hweprotein yeropa inonzi fibrinogen, iyo inobatsira kuumba ropa.

Zvakakosha kuziva kuti hemophilia C dzimwe nguva inogona kuoma kuona. Sei? Zvakabuda muongororo yeropa, kunyanya zvakabuda muongororo ye clotting factor, zvingasaenderana nezviratidzo zvemurwere. Semuenzaniso, bvunzo ye clotting factor inogona kuratidza kuti factor level yako yakaderera zvikuru, asi ungasave nezviratidzo. Zvakare, ungave uine zviratidzo zve hemophilia C kunyangwe factor level yako iri yakajairika. Saka chiremba achafunga nezveizvi zvese uye osvika pamhedziso.

Hemophilia C inorapwa sei?

Vanhu vane hemophilia C vangasada kurapwa kusvika vavhiyiwa kana kuvhiyiwa kumwe. Kana zvichidikanwa, vanachiremba vanoshandisa 'plasma itsva yakaomeswa', iyo inogadzirwa neropa rinopiwa.uye musanganiswa wemishonga inomisa kupatsanurwa kwe'zvinokonzera kuumbwa kwemasero' inopiwa senzira yekutsiva. Kana vakadzi vaine nguva yakawanda yekuenda kumwedzi, ichigara kwemazuva akati wandei, vanachiremba vanogona kunyora mapiritsi ekudzivirira pamuviri .

Hemophilia C inogona kudzivirirwa here?

Kwete, hemophilia C chirwere cheropa chinogara nhaka, saka hachigone kudzivirirwa . Zvisinei, kana iwe kana mumwe munhu mumhuri yako aine chirwere ichi, mazano ezvemajini anogona kukubatsira kunzwisisa njodzi yekuchipfuudza kuzvizvarwa zvinotevera.

Chii chingatarisirwa nemunhu ane hemophilia C?

Vanhu vazhinji vane hemophilia C vane zviratidzo zvishoma . Hazviwanzo kukonzera matambudziko makuru ehutano. Vanhu vazhinji havaratidzi zviratidzo kusvika vakura, uye zviratidzo izvozvo zvinowanzova zvishoma.

Zvisinei, unogona kunge uine matambudziko ekubuda ropa mushure mekuvhiyiwa kana kurapwa kwemazino. Kana uine hemophilia C, zvakakosha kubvunza chiremba wako nezve matanho aunofanira kutora . Semuenzaniso, kuzivisa chiremba wako usati wavhiyiwa uye kudzivirira mimwe mishonga inowedzera kubuda ropa (senge aspirin).

Chekupedzisira, zvimwe zvinhu zvakakosha zvaunofanira kurangarira

Zvakanaka, saka, pane zvinhu zvishoma zvaunofanira kurangarira kubva pane zvatataura nezvazvo:

• Hemophilia C chirwere cheropa chisingawanzoitiki .
• Kazhinji, zviratidzo zvayo hazvina kunyanya kuipa uye hazviwanzo kukonzera matambudziko makuru ehutano.
• Vanhu vazhinji vanongoratidza zviratidzo kana vakura.
• Zvisinei, unogona kubuda ropa rakawanda kupfuura mamwe panguva yekuvhiyiwa kana kurapwa kwemazino , saka zvakakosha kuzivisa chiremba wako muzviitiko zvakadaro.
• Kana wakawanikwa uine hemophilia C, usavhunduka. Taura nachiremba wako kuti uve nechokwadi chekuti unonzwisisa zvaunofanira kuziva uye matanho aunofanira kutora .

Yeuka, kunzwisisa chirwere chipi nechipi ndiyo nzira yakanakisisa yekugadzirisa dambudziko racho! Hausi wega, uye mazano ekurapa nerutsigiro zvinogara zviripo kwauri.

Hemophilia C, kugwinha kweropa, Factor XI, chirwere chemajini, kubuda ropa, zviratidzo, kurapwa