Mwana wenyu ari kutambura nekuvharika kwetsinga huru yeropa mumoyo make here? Ngatidzidzei nezveInterrupted Aortic Arch (IAA) nenzira iri nyore.

Mufaro waunonzwa paunotarisa mwana wako achangoberekwa hautsananguriki, handiti? Panguva imwe chete, pane mutoro mukuru mumoyo mako wehupenyu ihwohwo hudiki. Dzimwe nguva zvakajairika kunzwa kutya uye kunetseka paunonzwa nezvezvirwere zvinogona kutambura nevana vadiki. Nhasi, tiri kutaura nezvechirwere chemwoyo chakakomba chinogona kuitika muvacheche vachangobva kuzvarwa, asi chisingawanzoitiki, uye chinoda kurapwa nekukurumidza. Chirwere ichi chinonzi Interrupted Aortic Arch, kana (IAA) muchidimbu.

Zvichitaurwa zviri nyore, chii chinonzi Interrupted Aortic Arch (IAA)?

Kuti tinzwisise izvi, ngatitangei tatarisa mashandiro anoita mwoyo yedu. Funga nezvemwoyo wedu sepombi yemvura. Pombi iyi ine makamuri makuru mana. Maviri ari pamusoro uye maviri ari pasi. Ropa, iro rave richishandiswa nemuviri uye rine mwero weokisijeni wakaderera, uri webhuruu zvishoma, rinopinda mukamuri repamusoro rekurudyi. Kubva ipapo, rinoenda kukamuri repasi ropombwa kuenda kumapapu. Mumapapu, ropa iri rinowana okisijeni yakawanda uye rinova neruvara rutsvuku rwakanaka.

Zvino ropa dzvuku iri rine oxygen rinopinda mukamuri rekumusoro rekuruboshwe remoyo. Kubva ipapo, rinoenda mukamuri rekuruboshwe repasi uye rinopombwa mumuviri wese kuburikidza netsinga yeropa yakakura uye inonyanya kukosha mumuviri wedu, aorta . Iyi aorta yakafanana nehurongwa hukuru hwemapaipi hunotakura mvura kubva mutangi redu remvura kuenda kuimba yese. Yakaita setsvimbo yemasiwiti.

Saka, zvinoitika mumwana ane chirwere chinonzi Interrupted Aortic Arch (IAA) ndechekuti tsinga huru yeropa, aorta, haina kukwana. Pane chakavharika mukati mayo, senge mukaha wakatyoka. Zvichitaurwa zviri nyore, pombi huru yemvura yakatyoka pakati. Nekuda kweizvi, zvisinei nekuti mwoyo unopomba zvakaoma sei, ropa rakanaka rine oxygen hariendi kuzvikamu zvepasi zvemuviri.

Unoziva sei kana mwana wako aine chirwere ichi? Ndezvipi zviratidzo zvacho?

Vacheche vane IAA vanowanzotanga kuratidza zviratidzo mukati memaawa mashoma ekutanga kana mazuva mushure mekuzvarwa. Sevabereki, zvakakosha kuti muzive izvi.

Kana ukaona chimwe chezviratidzo izvi pamwana wako, unofanira kuona chiremba nekukasika kana kuendesa mwana wako kuchipatara cheEmergency Treatment Unit (ETU) nekukurumidza .

Sei izvi zvichiitika kuvana vacheche?

Paunonzwa chimwe chinhu chakadai, mubvunzo wekutanga unouya mupfungwa dzako semubereki ndewekuti, "Sei izvi zvakaitika kumwana wedu? Pane chatakaita chisina kunaka here?"

Zvichitaurwa zviri nyore, chirwere ichi chinoitika kana mwana ari kukura mudumbu, nekuda kwekurasikirwa nechikamu chidiki chechromosome chinokanganisa kuumbwa kwemwoyo netsinga huru dzeropa.

Vacheche vane IAA vanowanzova neDiGeorge syndrome.Izvi zvinogona kuitika nechirwere chimwe chinonzi DiGeorge syndrome. Izvi zvinokonzerwa nekurasikirwa kwechikamu chechromosome imwe chete sezvataurwa pamusoro apa. Vana vane DiGeorge syndrome vanogona kunge vaine hutachiona kakawanda uye vanogona kuchinja kumeso (sekunge muromo wakatsemuka).

Zvimwe zvikanganiso zvemwoyo zvinoperekedzwa neIAA

Vacheche vane IAA vanowanzova nechimwe kana zvimwe zvirwere zvemwoyo. Chimwe chezvirwere izvi chinowanzoonekwa iVentricular Septal Defect (VSD).

• Chirema cheMapaipi eVSD (VSD): Zvichitaurwa zviri nyore, iri buri riri pamadziro (septum) pakati pemakamuri maviri makuru ekupomba (ventricles) emwoyo. Kunyangwe izvi zvichiwanzova chikanganiso, VSD inogona kuponesa hupenyu hwemwana ane IAA kwenguva pfupi . Fungidzira kuti kana ropa risingakwanise kuyerera muaorta, rimwe ropa rine oxygen riri kuruboshwe rweaorta rinogona kuyerera nepaburi iri kuenda kurudyi, uko rinogona kuyerera kuenda kumapapu kuti ripe ropa kune zvikamu zvepasi zvemuviri. Zvakafanana nekuva nepaburi diki kana mugwagwa mukuru wakavharwa. Asi iyi ingori mhinduro yenguva pfupi.

Ndedzipi nzira dzekuongorora chirwere uye nzira dzekurapa?

Zvakakosha kuziva nekurapa chirwere ichi nekukurumidza sezvinobvira.

Kuongorora chirwere

Dambudziko iri rinowanzoonekwa neEchocardiogram . Tinongoti 'Echo test'. Izvi zvakafanana nekuongororwa kwemoyo. Kuongororwa uku kusingarwadzi kunogona kuona zvakajeka chimiro uye mashandiro emakamuri emwoyo, mavharuvhu, uye tsinga dzeropa. Dzimwe nguva, chirwere ichi chinogona kutoonekwa nekukurumidza nekuongororwa kunoitwa mwana achiri mudumbu.

Kurapa

Kurapa kweIAA kunoitwa kuvhiyiwa . Zvisinei, kusvika mwana agadzirira kuvhiyiwa, vanachiremba vanotanga vaita chimwe chinhu kuti vaponese hupenyu hwemwana.

1. Danho Rokutanga - Kuchengeta Mugero Wenguva Pfupi Wakavhurika:

Mwana wese achangoberekwa ane hukama hwechinguvana pakati pemwoyo, aorta, nechubhu inotakura ropa kuenda kumapapu inonzi Ductus Arteriosus . Izvi zvakakosha zvikuru mwana achiri mudumbu. Chubhu iyi inovhara yoga mukati memaawa mashoma ekuzvarwa.

Asi mumwana ane IAA, nekuti aorta yakabvaruka, nzira imwe chete yekuti ropa rine oxygen rifambe mumuviri ndeyekupfuura neDuctus Arteriosus. Saka chinhu chekutanga chinoitwa navanachiremba kupa mwana mushonga unonzi Prostaglandin E1 , unochengetedza chubhu iyoyo yenguva pfupi yakavhurika isina kuvhara. Izvi zvinobatsira kuchengetedza ropa mumuviri wemwana kusvika pakuvhiyiwa.

2. Danho rechipiri - Kuvhiyiwa:

Kana mamiriro emwana agadzikana, vanachiremba vane hunyanzvi vanomuvhiya. Izvi zvinosanganisira:

• Kutora mativi maviri akatyoka e aorta woabatanidza pamwe chete kuti pave netsinga yeropa yakakwana, isina kuvharwa.
• Kuvhara Ductus Arteriosus yenguva pfupi yakanga yavhurwa nekupa prostaglandin.
• Kana paine VSD (buri riri pamadziro emwoyo), richavharwawo panguva yekuvhiyiwa uku.

Mwana achazonzwa sei mushure mekuvhiyiwa?

Hapana chinhu chakaoma kuvabereki kupfuura kunzwa kuti mwana wavo achangoberekwa ane chirwere chinouraya. Asi kubva pane zvatakurukura, unogona kuona kuti chirwere ichi chinogona kurapwa zvinobudirira nekukurumidzira kurapwa.

Hutano hwevana mushure mekuvhiyiwa kweIAA hunogona kuva hwakanaka kwazvo . Zvichienderana nenhamba, kunyangwe makore gumi mushure mekuvhiyiwa, 81% yevana vachiri vapenyu. Izvi zvinoreva kuti mwero wekubudirira wakakwira zvikuru.

Asi izvi zvinongoitika zvekukurumidzira. Kana zviratidzo zvangoonekwa, mwana anofanira kugamuchirwa muchipatara (ICU) uye kurapwa kunofanira kutanga nekukasika. Kunyangwe mushure mekuvhiyiwa, zvakakosha kuramba uchiendesa mwana kukiriniki uye kuongororwa zvinodiwa, sezvinorayirwa navanachiremba.