Ngaba ukhathazekile ngendlela obume ngayo ubuso bomntwana wakho? Masithethe ngeBinder Syndrome!

Xa umntwana wakho wayezalwa, ngaba uphawule naluphi na utshintsho oluncinci kwimo yobuso bakhe? Ngamanye amaxesha impumlo yakhe isenokubonakala ngathi ithe tyaba, okanye umlebe wakhe ongasentla ungabi kwindawo efanelekileyo. Kuqhelekile ukuba umama okanye utata azive esoyika xa ebona into efana nale. Kodwa ungakhathazeki, namhlanje siza kuthetha ngemeko ebonisa iimpawu ezifanayo, kodwa engaqhelekanga, ebizwa ngokuba yiBinder Syndrome.

Yintoni iBinder Syndrome? Ngamafutshane...

I-Binder syndrome yimeko engaqhelekanga , yokuzalwa eyenzeka xa umntu ezalwa. Ibonakala ngamathambo embindini wobuso, ingakumbi impumlo nomhlathi ongaphezulu, angakhuli kakuhle. Ifana nendlela ezinye iindonga zendlu ezingakhiwanga kakuhle ngayo. Oku kunokubangela ukuba ubuso bomntwana bubonakale buhlukile kancinci.

Cinga nje, impumlo yethu kunye nomlomo ongasentla zimile ngenxa yamathambo angaphantsi. Ngoko ke xa loo mathambo eyeka ukukhula, imbonakalo yawo iyatshintsha. Abanye abantwana banokuba nobunzima bokuphefumla ngenxa yesi simo, kwaye banokuba neengxaki zokutya, ingakumbi xa bencancisa . Kodwa iindaba ezimnandi zezokuba, kukho unyango loku. Ngokwesiqhelo, xa umntwana emdala kancinci, oko kukuthi, xa efikelela kwiminyaka yobutsha (ngesiqhelo phakathi kweminyaka eli-15-19), la mathambo anokulungiswa kwaye imbonakalo yobuso inokubuyiselwa ngotyando lobuso kunye nomhlathi (`utyando lwe-maxillofacial`) .

Ngaba kukho amanye amagama eBinder Syndrome?

Ewe, oogqirha ngamanye amaxesha basebenzisa amanye amagama kwesi sifo. Kulungile ukwazi kuba ungaweva la magama:

• I-Binder phenotype - Eli lelinye igama le-Binder syndrome.
• Uhlobo lwe-Binder lwe-nasomaxillary dysplasia
• I-Maxillonasal dysplasia
• I-Nasomaxillary hypoplasia

Nangona la magama esenokubonakala entsonkothile kancinci, onke athetha into enye.

Ixhaphake kangakanani le meko ibizwa ngokuba yiBinder Syndrome?

Esi sisifo esingaqhelekanga ngokwenene. Ngokweengxelo ezithile, esi sifo senzeka kwiintsana ezingaphantsi kwe-1 kwi-10,000 ezisandul’ ukuzalwa. Ngoko ke musani ukoyika oku. Kodwa, nangona kunqabile, kubalulekile ukukwazi.

Ziziphi iimpawu zeBinder Syndrome?

Uphawu oluphambili lwale meko kukungabikho kokukhula embindini wobuso . Ngenxa yoko, ubuso bomntwana bunokubonisa utshintsho olulandelayo:

• Impumlo iba tyaba, kwaye umlebe ongasentla uba tyaba . Ingabonakala ngathi impumlo itshone ngaphakathi.
• Umhlathi ongezantsi uphuma phambili.Ibonakala ngolu hlobo. Oku kubonakala kuba umhlathi ophezulu ungena ngaphakathi kwaye umhlathi ongezantsi uvela phambili.
• Amazinyo aphezulu nasezantsi awahambelani kakuhle (i-malocclusion) . Oku kunokubangela ubunzima xa usitya naxa uthetha.
• Iimpumlo zithatha imo enxantathu okanye ende .

Ezi zezona mpawu zixhaphakileyo. Nangona kunjalo, ukongeza, ungabona ezi mpawu zilandelayo kwiimeko ezingaqhelekanga :

• Impumlo eqhekekileyo .
• Iziphene zentliziyo ezizalwa nazo .
• Ukuphazamiseka kokuva .
• Ukukhubazeka kwengqondo .
• Ukukhubazeka komqolo .
• I-Strabismus okanye amehlo anqamlezileyo .

Ayingabo bonke abantwana abaya kuba nazo zonke ezi mpawu. Abanye abantwana basenokuba nazo kuphela iimpawu ezisisiseko.

Kutheni iBinder Syndrome isenzeka? Zithini izizathu?

Inyaniso kukuba, iingcali azikafumani ukuba yintoni kanye kanye ebangela oku . Uninzi lwexesha, abantwana baba nale meko ngaphandle kwesizathu esicacileyo.

Nangona kunjalo, ekubeni abantwana abaninzi kwiintsapho ezithile benale meko, kurhanelwa ukuba kusenokubakho izinto ezibangela imfuza, oko kukuthi, impembelelo yemfuza . Nangona kunjalo, oku akukaqinisekiswa ngokuqinisekileyo.

Ukongeza, abaphandi bakholelwa ukuba izinto ezininzi ezichaphazela imekobume nazo zinokudlala indima. Ezi zinto ziquka:

• Ukusetyenziswa kotywala koomama ngexesha lokukhulelwa.
• Ukuchatshazelwa ngamayeza athile ngexesha lokukhulelwa. Imizekelo ibandakanya i-anti-epileptic phenytoin (Dilantin®, Phenytek®) kunye ne-blood thinner warfarin (Coumadin®, Jantoven®). (La mayeza kufuneka athathwe phantsi kweliso likagqirha ukuba kuyimfuneko, kodwa kufuneka kuthathwe unonophelo olukhethekileyo ngexesha lokukhulelwa.)
• Ukunqongophala kweVitamin K ngexesha lokukhulelwa.
• Ukulimala entloko okanye ebusweni ngexesha lokuzalwa.

Ezi zezona zinto zinobungozi ezichongiweyo ngoku.

Oogqirha bayifumanisa njani iBinder Syndrome?

Oogqirha baqala ngokuyikrokrela le meko ngokujonga inkangeleko yobuso bomntwana . Emva koko, ukuqinisekisa okanye ukuthintela loo ngxaki, benza uvavanyo olukhethekileyo olunokubona ngokucacileyo ulwakhiwo lwamathambo ebusweni . Olu lubizwa ngokuba:

• Iiskeni ze-CT
• Iiskeni zeMRI (`MRI`)
• Iiskeni ze-ultrasound (`i-ultrasound`)

Ngokusebenzisa ezi scan, sinokubona ngokuchanekileyo ukungakhuli kwamathambo ebusweni.

Ziziphi iindlela zonyango lwe-Binder Syndrome?

Unyango loku luyahluka kumntwana ngamnye, kwaye luxhomekeke nakubukhali beempawu.Iyahluka. Kukho iindlela ezimbini eziphambili zonyango:

1. Ukhathalelo lwamazinyo:

• Oku kuquka ukubeka iingcingo (`iibrace`) emlonyeni ukuze umhlathi namazinyo zilungelelaniswe kakuhle .
• Ngamanye amaxesha, ukuba iimpawu azikho qatha kakhulu, olu nyango lwamazinyo lodwa lunokwanela.
• Kwezinye iimeko, olu nyango lunokufuneka lwenziwe ngaphambi okanye emva kotyando.

2. Utyando:

• Le yindlela ephambili yonyango. Ugqirha otyanda ubuso (ugqirha ochwephesha kwintloko nasebusweni) wenza olu tyando.
• Kule meko, imo yempumlo iphinda ibunjwe kusetyenziswa ithambo, i-cartilage, okanye izinto ezenziwe ngokwenziwa ezithathwe emzimbeni womntwana . Oku kukwabizwa ngokuba yi-rhinoplasty .
• Kwakhona, uhlobo lotyando olubizwa ngokuba yi-Le Fort I okanye II osteotomy lunokwenziwa ukuze umhlathi ongaphezulu ube kwindawo efanelekileyo. Olu lutyando oluntsonkothileyo, kodwa oogqirha abanamava banokulwenza ngempumelelo.
• Oogqirha badla ngokucebisa ukuba ulinde de amathambo obuso bomntwana ayeke ukukhula ngokupheleleyo ngaphambi kokuba enze olu tyando, oludla ngokuba phakathi kweminyaka eli-15 neli-19 ubudala. Oku kungenxa yokuba ukuba lwenziwa ngaphambi koko, iingxaki zinokuphinda zivele njengoko amathambo eqhubeka ekhula.

Kubalulekile: Ayingabo bonke abantwana abaya kufuna unyango olubini. Abanye abantwana banokufuna unyango olunye kuphela. Oku kuya kugqitywa liqela lezonyango emva kokuvavanya umntwana.

Ngaba le meko ibizwa ngokuba yiBinder Syndrome ingathintelwa?

Ekubeni unobangela ochanekileyo woku ungaziwa, akunakwenzeka ukuqinisekisa ukuba unokuthintelwa ngokupheleleyo .

Nangona kunjalo, ukuba ukhulelwe, unganciphisa umngcipheko wakho wokuba nale meko ukuya kuthi ga kwinqanaba elithile ngokunciphisa ukuvezwa kwakho kwezinye zezinto ezingqongileyo esizixubushileyo ngaphambili. Ungathetha nogqirha wakho ngale nto:

• Ukhuseleko lwamayeza ngexesha lokukhulelwa , ingakumbi i-phenytoin kunye ne-warfarin (musa ukuthatha naluphi na unyango ngaphandle kokuba unikwe ngugqirha, kwaye ukuba unikwe, thetha nogqirha wakho ngalo mba).
• Malunga nokunqongophala kweevithamini, ingakumbi ukunqongophala kwevithamini K. Kubaluleke kakhulu ukufumana isondlo esifanelekileyo ngexesha lokukhulelwa.

Iyintoni imbono yomntwana oneBinder Syndrome?

Ezi zezona ndaba zilungileyo. Kukho umbono olungileyo ngokubanzi ngale meko .

Uninzi lwabantwana aludingi naluphi na unyango emva kwe-rhinoplasty. Banokuphefumla ngokuqhelekileyo, batye ngokuqhelekileyo, kwaye inkangeleko yobuso babo iyaphucuka emva kotyando.Kunokwenzeka. Ngoko ke akukho nto ibalulekileyo, kodwa eyona nto ibalulekileyo kukufuna ingcebiso kagqirha ngokukhawuleza.

Ndingayibuza yiphi imibuzo ugqirha wam?

Ukuba ufumanisa ukuba wena okanye umntwana wakho uneBinder Syndrome, ungabuza ugqirha wakho imibuzo efana nale. Le iya kukunceda uqonde imeko:

• "Gqirha, yintoni enokuba ngunobangela wemeko yomntwana wam? "
• " Zeziphi iimvavanyo ezenziwayo ukuze kufunyaniswe ngokuchanekileyo esi sifo seBinder Syndrome? "
• " Zithini iindlela zonyango zoku? Yintoni elungele umntwana wam?"
• " Zithini amathuba okufuna unyango kwakhona ebomini? "
• "Ukuba ndinomnye umntwana, mangakanani amathuba okuba naye abe nale meko? "

Ukongeza kule mibuzo, buza ugqirha wakho nantoni na ocinga ngayo.

Ziziphi ezinye iimeko ezineempawu ezifanayo neBinder Syndrome?

Kukho ezinye iimeko ezininzi ezichaphazela ukukhula kwamathambo ebusweni kwaye zifana neBinder syndrome. Oogqirha nabo bakhathazekile ngezi. Eminye imizekelo yile:

• I-Acrodysostosis
• Isifo se-Apert
• Chondrodysplasia punctata, uhlobo lwerhizomelic (CDPR)
• I-Fetal warfarin syndrome (imeko ebangelwa kukuvezwa kwi-warfarin ngexesha lokukhulelwa)
• Isifo seKeutel
• Isifo se-Stickler

Qaphela la magama. Oogqirha baya kugqiba ukuba umntwana wakho unesifo esinjani kanye kanye.

Okokugqibela, izinto ekufuneka uzikhumbule (Umyalezo Wokuya Ekhaya)

Kulungile, masishwankathele oko sithethe ngako:

• I-Binder Syndrome yimeko engaqhelekanga kakhulu, ezalwa nayo .
• Oku kubangela ukwehla kokukhula kwamathambo embindini wobuso, ingakumbi impumlo nomhlathi ongaphezulu . Oku kubangela iimpawu ezifana nempumlo esicaba kunye nomhlathi ongezantsi ophumayo.
• Isizathu esichanekileyo soku asikaziwa , kodwa izinto zemfuza kunye neemeko ezingqongileyo zinokudlala indima.
• Le meko inokunyangeka ngempumelelo ngonyango lwamazinyo kunye/okanye utyando .
• Abantwana abaninzi bafumana iziphumo ezilungileyo kakhulu emva konyango kwaye banokuphila ubomi obuqhelekileyo.

Ukuba unenkxalabo okanye uxhalabile malunga nenkangeleko yobuso bomntwana wakho, nceda ubone ugqirha ofanelekileyo ngokukhawuleza . Eyona nto ibalulekileyo kukungabi naxhala, kodwa kukufumana ulwazi olufanelekileyo kunye nesikhokelo. Oogqirha bakhona ukukunceda.

Ndiyathemba ukuba olu lwazi luluncedo kuwe. Ndikunqwenelela impilo entle wena nosapho lwakho!

I- Binder Syndrome, i-Binder Syndrome, ukukhubazeka kobuso, izifo zokuzalwa, impilo yabantwana, utyando lwe-maxillofacial, utyando lwe-craniofacial